Mhando / nyoro-tishu-sarcoma / murwere / mwana-vascular-mamota-kurapwa-pdq

Yevacheche Vascular Tumors Kurapa (®) -Patient Shanduro

Ruzivo Ruzhinji Nezvehucheche Vascular Tumors

PFUNGWA DZINOKOSHA

• Zvevacheche mamota mamota anoumba kubva kumasero anogadzira tsinga dzeropa kana lymph lymph.

• Miedzo inoshandiswa kuona (tsvaga) uye kuongorora huturu hwevascular tumors.

• Zvevacheche mamota mamota anogona kuiswa muzvikamu zvina.

• Benign mapundu

• Zvepakati (munharaunda zvine hukasha) mamota

• Pakati (kazhinji metastasizing) mamota

• Mamota akaipa

Zvevacheche mamota mamota anoumba kubva kumasero anogadzira tsinga dzeropa kana lymph lymph.

Vascular tumors inogona kuumba kubva kune isina kujairika yeropa mudziyo kana lymph mudziyo maseru chero kupi mumuviri. Vanogona kunge vari benign (kwete cancer) kana yakaipa (cancer). Kune mhando dzakawanda dzevascular tumors. Mhando yakajairika yehucheche vascular bundu ndeyecheche hemangioma, rinova bundu rinotyisa iro rinowanzo enda roga.

Nekuti zvinokonzeresa mamota etsinga asingawanzo muvana, hapana ruzivo rwakawanda pamusoro pekuti mushonga unoshanda zvakanyanya.

Miedzo inoshandiswa kuona (tsvaga) uye kuongorora huturu hwevascular tumors.

Iyi inotevera bvunzo uye maitiro anogona kushandiswa:

• Kuongorora kwepanyama uye nhoroondo: Kuongorora kwemuviri kutarisa zviratidzo zvehutano, kusanganisira kuongorora zviratidzo zvehosha, zvakadai semapundu, maronda, kana chero chinhu chinoratidzika sechisina kujairika. Nhoroondo yemaitiro ehutano hwemurwere uye kurwara kwakapfuura uye kurapwa kuchatorwawo.

• Ultrasound bvunzo: Maitiro umo ma-high-energy ruzha mafungu (ultrasound) anodonhedzwa kubva mukati memukati nyama kana nhengo uye anoita maungira. Maungira anoumba mufananidzo wemuviri munyama unonzi sonogram. Mufananidzo wacho unogona kudhindwa kuti utariswe gare gare.

Abdominal ultrasound. Ultrasound transducer yakabatana nekombuta inosvinwa yakanangana neganda remudumbu. Iyo transducer inovhuvhuta masaisai ezwi kubva mukati memukati uye matishu kuti aite maungira anoita iyo sonogram (komputa mufananidzo).

• CT scan (CAT scan): Maitiro anoita akateedzana emifananidzo yakajeka yenzvimbo dziri mukati memuviri, inotorwa kubva kumakona akasiyana. Mifananidzo yacho inogadzirwa nekombuta yakabatana neiyo x-ray muchina. Dhayi inogona kuiswa jekiseni kana kumedzwa kubatsira nhengo kana zvinyama kuratidza zvakajeka. Iyi nzira inonziwo computed tomography, computerized tomography, kana komputa axial tomography.

Computed tomography (CT) scan yemudumbu. Mwana akarara patafura inotsvedza kuburikidza neCT scanner, iyo inotora mifananidzo ye x-ray yemukati medumbu.

• MRI (magnetic resonance imaging): Maitiro anoshandisa magineti, masaisai eredhiyo, uye komputa kugadzira yakateedzana mifananidzo yakajeka yenzvimbo dziri mukati memuviri. Iyi nzira inonziwo nyukireya magnetic resonance imaging (NMRI).

Magnetic resonance imaging (MRI) yedumbu. Mwana akarara patafura inotsvedza ichipinda muMRI scanner, inotora mifananidzo yemukati memuviri. Iyo padhi padumbu remwana inobatsira kujekesa mifananidzo.

• Biopsy: Kubviswa kwemasero kana zvinyama kuitira kuti vagone kutariswa pasi pe microscope nachiremba wekutarisa zviratidzo zvecancer. Biopsy haigare ichidikanwa kuti iongorore bundu revascular.

Zvevacheche mamota mamota anogona kuiswa muzvikamu zvina.

Benign mapundu

Benign mamota haasi gomarara. Ichi chidimbu chine ruzivo nezve anotevera benign vascular tumors:

• Mucheche hemangioma.

• Kuberekwa hemangioma.

• Benign vascular tumors yechiropa.

• Chokurukisa sero hemangioma.

• Epithelioid hemangioma.

• Pyogenic granuloma (lobular capillary hemangioma).

• Angiofibroma.

• Vechidiki nasopharyngeal angiofibroma.

Zvepakati (munharaunda zvine hukasha) mamota

Mamota epakati ari munharaunda ane hukasha anowanzo pararira kunzvimbo yakatenderedza bundu. Pfupiso iyi ine ruzivo nezve anotevera emuno ane hasha emamota mamota.

• Kaposiform hemangioendothelioma uye tufted angioma.

Pakati (kazhinji metastasizing) mamota

Zvepakati (zvisingawanzo metastasizing) mamota dzimwe nguva anopararira kune dzimwe nhengo dzemuviri. Iyi pfupiso ine ruzivo nezve anotevera matumbu evascular ayo asingawanzo metastasize:

• Pseudomyogenic hemangioendotheliomaoma.

• Retiform hemangioendothelioma.

• Papillary intralymphatic angioendothelioma.

• Yakaumbwa hemangioendotheliomaoma.

• Kaposi sarcoma.

Mamota akaipa

Mamota akaipa ane kenza. Pfupiso iyi ine ruzivo nezve anotevera akaipa maronda emota.

• Epithelioid hemangioendotheliomaoma.

• Angiosarcoma yezvinyoro zvinyama.

Kurapa Sarudzo Kuongorora

PFUNGWA DZINOKOSHA

• Kune mhando dzakasiyana dzekurapa kwehudiki vascular tumors.

• Vana vane mamota ematumbo evacheche vanofanirwa kurapwa kwavo kuchirongwa nechikwata chevanoona nezvehutano vari nyanzvi pakurapa kenza muvana.

• Kurapa kwehudiki vascular tumors kunogona kukonzera mhedzisiro.

• Mimwe gumi neimwe yemhando yekurapa inoshandiswa:

• Beta-blocker kurapa

• Kuvhiya

• Photocoagulation

• Kubatanidza

• Chemotherapy

• Sclerotherapy

• Radiation kurapa

• Targeted kurapwa

• Immunotherapy

• Imwe mishonga yekurapa

• Kucherechedza

• Mhando nyowani dzekurapa dziri kuyedzwa mumakiriniki ekuedzwa.

• Varwere vangangoda kufunga nezve kutora chikamu mukutora kiriniki.

• Varwere vanogona kupinda mumakiriniki miedzo vasati, panguva, kana mushure mekutanga kwavo kenza kurapwa.

• Yekutevera-bvunzo inogona kudikanwa.

Kune mhando dzakasiyana dzekurapa kwehudiki vascular tumors.

Mhando dzakasiyana dzekurapa dzinowanikwa kune vana vane vascular tumors. Mamwe marapirwo akajairwa (iko kurapwa kwazvino kwashandiswa), uye kumwe kuedzwa mumakiriniki ekuedzwa A kurapwa kiriniki kutongwa chidzidzo chekutsvaga chakaitirwa kubatsira kuvandudza marapirwo azvino kana kuwana ruzivo nezvekurapa kutsva. Kana kiriniki miedzo ikaratidza kuti kurapwa kutsva kuri nani pane kwese kurapwa, kurapwa kutsva kunogona kuve kwakajairwa kurapwa.

Nekuti mamota evascular muvana haashoma, kutora chikamu mukuedzwa kwekiriniki kunofanirwa kutariswa. Mimwe miedzo yekiriniki yakavhurwa chete kune varwere vasina kutanga kurapwa.

Vana vane mamota ematumbo evacheche vanofanirwa kurapwa kwavo kuchirongwa nechikwata chevanoona nezvehutano vari nyanzvi pakurapa kenza muvana.

Kurapa kunozoonekwa nachiremba wevana oncologist, chiremba ane hunyanzvi hwekurapa vana vane gomarara. Vanachiremba oncologist vanoshanda nevamwe vana vanopa hutano vezvehutano avo vari nyanzvi pakurapa vana vane gomarara uye vanoziva mune dzimwe nzvimbo dzemishonga. Izvi zvinogona kusanganisira vanachiremba vanotevera:

• Pediatric vascular anomaly nyanzvi (nyanzvi yekurapa vana vane vascular tumors).

• Chiremba wechiremba wechiremba.

• Chiremba wemabhonzo.

• Radiation oncologist.

• Mukoti wechiremba nyanzvi.

• Rehabilitation nyanzvi.

• Nyanzvi yezvepfungwa.

• Wezvemagariro.

Kurapa kwehudiki vascular tumors kunogona kukonzera mhedzisiro.

Kuti uwane ruzivo nezve mhedzisiro inotanga panguva yekurapa kenza, ona yedu Side Mhedzisiro peji.

Kumwe kurapwa, senge chemotherapy uye radiation radiation, kunokonzeresa mhedzisiro inoenderera kana kuoneka mwedzi kana makore mushure mekurapwa kwapera. Izvi zvinonzi kunonoka kuitika. Mhedzisiro mhedzisiro yekurapa inogona kusanganisira zvinotevera:

• Zvinetso zvepanyama.

• Shanduko mumanzwiro, manzwiro, kufunga, kudzidza, kana ndangariro.

• Gomarara repiri (mhando nyowani dzekenza).

Mimwe mhedzisiro mhedzisiro inogona kurapwa kana kudzorwa. Izvo zvakakosha kuti utaure navanachiremba vemwana wako nezve zvingangoitika zvinononoka mhedzisiro zvinokonzerwa nekumwe kurapwa. (Ona pfupiso ye pamusoro peMagumo Ekurapa kweKenza Yevacheche kuti uwane rumwe ruzivo).

Mimwe gumi neimwe yemhando yekurapa inoshandiswa:

Beta-blocker kurapa

Beta-blockers mishonga inoderedza kukwira kweropa uye kurova kwemoyo. Kana ikashandiswa muvarwere vane mamota etsinga, beta-blockers anogona kubatsira kudzikisira mamota. Beta-blocker therapy inogona kupihwa nevein (IV), nemuromo, kana kuiswa paganda (topical). Nzira iyo beta-blocker therapy inopihwa inoenderana nerudzi rwevascular tumors uye pakatanga kuumbwa bundu.

Iyo beta-blocker propranolol inowanzo kuve yekutanga kurapwa kwehemangiomas. Vacheche vanorapwa neIV propranolol vangangoda kuti kurapwa kwavo kutange muchipatara. Propranolol inoshandiswawo kubata benign vascular bundu rechiropa uye kaposiform hemangioendothelioma.

Mamwe beta-blockers anoshandiswa kurapa tumarara tumasumbu anosanganisira atenolol, nadolol, uye timolol.

Infantile hemangioma inogona kurapwa nepropranolol uye steroid therapy kana propranolol uye topical beta-blocker therapy.

Ona pfupiso yeruzivo rwezvinodhaka paPropranolol Hydrochloride kuti uwane rumwe ruzivo.

Kuvhiya

Aya anotevera marudzi ekuvhiya anogona kushandiswa kubvisa mhando zhinji dzematumbo evasosi:

• Excision: Kuvhiya kubvisa iro bundu rese uye mamwe eakagwinya mativi akarikomberedza.

• Kuvhiya kweLaser: Maitiro ekuvhiya anoshandisa laser beam (danda rakamanikana rechiedza chakasimba) sebanga rekucheka zvisina ropa muzvinyama kana kubvisa ronda reganda rakadai bundu. Kuvhiya ine pulsed dhayi laser inogona kushandiswa kune mamwe mahemangiomas. Mhando iyi yemalaser inoshandisa danda rechiedza rinotarisa tsinga dzeropa muganda. Chiedza chinoshandurwa kuita kupisa uye tsinga dzeropa dzinoparadzwa pasina kukuvadza ganda riri padyo.

• Curettage: Maitiro anobviswa zvinyama zvisina kujairika uchishandisa chishandiso chidiki chakaita chipunu chinonzi curette.

• Yakazara hepatectomy uye kuisirwa kwechiropa: Maitiro ekuvhiya kubvisa chiropa chose chinoteverwa nekuiswa kwechiropa chine hutano kubva kune anenge apa.

Mhando yekuvhiya inoshandiswa inoenderana nerudzi rwevascular tumor uye apo bundu rakaumbwa mumuviri.

Kumamota akaipa, mushure mekunge chiremba abvisa kenza yese inoonekwa panguva yekuvhiyiwa, vamwe varwere vanogona kupihwa chemotherapy kana radiation radiation mushure mekuvhiyiwa kuuraya chero gomarara maseru akasara. Mushonga wakapihwa mushure mekuvhiyiwa, kudzikisa njodzi yekuti gomarara richadzoka, inonzi adjuvant therapy.

Photocoagulation

Photocoagulation iko kushandiswa kwedanda rakasimba rechiedza, senge laser, kuvhara mitsipa yeropa kana kuparadza nyama. Inoshandiswa kurapa pyogenic granuloma.

Kubatanidza

Embolization inzira inoshandisa zvidimbu, senge madiki gelatin masiponji kana hura, kuvharira tsinga dzeropa muchiropa. Inogona kushandiswa kurapa mamwe anonamira vascular tumors yechiropa uye kaposiform hemangioendothelioma.

Chemotherapy

Chemotherapy kurapwa kunoshandisa mishonga kumisa kukura kwemarara maseru, kungave nekuuraya maseru kana nekuamisa iwo kubva pakupatsanuka. Kune nzira dzakasiyana dzekupa chemotherapy:

• Systemic chemotherapy: Kana chemotherapy ikatorwa nemuromo kana kujowa mutsinga kana mhasuru, iwo madhiragi anopinda muropa uye anogona kusvika mumarara maseru mumuviri wese. Dzimwe nguva zvinopfuura imwe anticancer mushonga unopihwa. Izvi zvinonzi mubatanidzwa chemotherapy.

• Misoro chemotherapy: Kana chemotherapy ichishandiswa paganda mukirimu kana mafuta, mishonga iyi inokanganisa maseru emarara munzvimbo inorapwa.

• Regional chemotherapy: Kana chemotherapy ikaiswa yakananga mucerebrospinal fluid, nhengo, kana muviri mhasuru senge dumbu, mishonga inowanzo kukanganisa maseru emarara munzvimbo idzodzo.

Nzira iyo chemotherapy inopihwa inoenderana nerudzi rwevascular tumor iri kurapwa. Systemic uye topical chemotherapy inoshandiswa kurapa mamwe mamota evascular.

Sclerotherapy

Sclerotherapy kurapwa kunoshandiswa kuparadza ropa reropa rinotungamira kubundu uye bundu. Mvura inoiswa mukati meropa, ichikonzera kuti ive nekupwanya uye kuparara. Nekufamba kwenguva, iro rakaparadzwa reropa reropa rinosungirwa munyama chaiyo. Ropa rinoyerera nemitsinga ine hutano iri padyo. Sclerotherapy inoshandiswa pakurapa epithelioid hemangioma.

Radiation kurapa

Radiation kurapa kurapwa kunoshandisa yakakwira-simba x-rays kana mamwe marudzi emwaranzi kuuraya mamota maseru kana kuachengetedza kuti asakura. Kune mhando mbiri dze radiation radiation:

• External radiation therapy inoshandisa muchina kunze kwemuviri kutumira radiation kune bundu.

• Yemukati radiation kurapa inoshandisa radioactive chinhu chakanamwa mune tsono, mhodzi, waya, kana makateti anoiswa akananga mukati kana padyo nebundu.

Nzira iyo marapi ekurapa anopiwa anoenderana nerudzi rwevascular tumor iri kurapwa. Radiation yekunze inoshandiswa kurapa mamwe mamota etsinga.

Targeted kurapwa

Targeted therapy mhando yekurapa inoshandisa zvinodhaka kana zvimwe zvinhu kurwisa chaiwo mamota maseru. Marapirwo akanangwa anowanzo kukonzera kukuvara kushoma kune masero akajairwa kupfuura chemotherapy kana radiation radiation inoita. Mhando dzakasiyana dzerapi yakanangwa irikushandiswa kana kudzidza kurapa hudiki vascular tumors

• Angiogenesis inhibitors: Angiogenesis inhibitors mishonga inomisa maseru kubva pakupatsanuka uye kudzivirira kukura kwemidzi mitsva yeropa iyo mamota anoda kukura. Iyo yakanangwa kurapa zvinodhaka thalidomide, sorafenib, pazopanib, uye sirolimus maangiogenesis inhibitors anoshandiswa kurapa hudiki vascular tumors.

• Mamia mamaliya chinangwa che rapamycin (mTOR) inhibitors: mTOR inhibitors inovhara puroteni inonzi mTOR, inogona kuchengetedza maseru emukenza kukura uye kudzivirira kukura kwemitsipa yeropa mitsva inoda kukura.

• Kinase inhibitors: Kinase inhibitors anovharira zviratidzo zvinodiwa kuti mamota akure. Trametinib iri kuongororwa kurapa epithelioid hemangioendothelioma.

Immunotherapy

Immunotherapy kurapwa kunoshandisa immune system yemurwere kurwisa chirwere. Zvinhu zvakagadzirwa nemuviri kana zvinogadzirwa murabhoritari zvinoshandiswa kusimudzira, kunongedza, kana kudzorera kudzivirira kwemuviri kuchirwere.

Aya anotevera marudzi eunonotherapy ari kushandiswa pakurapa kwehudiki vascular tumors:

• Interferon imhando yemununotherapy inoshandiswa kurapa hura hwevascular tumors. Iyo inokanganisa kupatsanurwa kwemamota maseru uye inogona kudzora bundu kukura. Inoshandiswa pakurapa kwevechidiki nasopharyngeal angiofibroma, kaposiform hemangioendothelioma, uye epithelioid hemangioendothelioma.

• Immune checkpoint inhibitor therapy: Dzimwe mhando dzemasero ekudzivirira muviri, senge T maseru, uye mamwe maseru emukenza ane mamwe mapuroteni, anonzi ekuongorora mapuroteni, pamusoro pavo anochengetedza mhinduro dzemumuviri. Kana masero ekenza aine huwandu hwakawanda hweaya mapuroteni, haazorwiswa nekuuraiwa nemaT seli. Immune checkpoint inhibitors inovhara mapuroteni aya uye kugona kwemasero eT kuuraya maseru ekenza kunowedzerwa.

Kune maviri marudzi e immune checkpoint inhibitor therapy:

• CTLA-4 inhibitor: CTLA-4 ipuroteni iri pamusoro peT maseru ayo anobatsira kuchengetedza mhinduro dzemumuviri. CTLA-4 painobatirira kune imwe protein inonzi B7 pane kenza kenza, inomisa iyo T cell kuuraya kenza kenza. CTLA-4 inhibitors inonamira kuCTLA-4 uye inobvumira iwo maseru eT kuuraya maseru ekenza Ipilimumab rudzi rweCTLA-4 inhibitor iri kudzidziswa mukurapa angiosarcoma yeiyo yakapfava nyama.

Immune checkpoint inhibitor. Checkpoint mapuroteni, akadai seB7-1 / B7-2 pane antigen-anouya maseru (APC) uye CTLA-4 pane T maseru, anobatsira kuchengetedza mhinduro dzemumuviri. Kana iyo T-cell receptor (TCR) inosunga kune antigen uye makuru histocompatibility complex (MHC) mapuroteni paAPC uye CD28 inosunga kuna B7-1 / B7-2 paAPC, iyo T cell inogona kumisikidzwa. Nekudaro, kusunga kweB7-1 / B7-2 kusvika CTLA-4 kunoita kuti maT cell ari munzvimbo isingashande saka havakwanise kuuraya maseru emota mumuviri (kuruboshwe pani). Kuvhara kusunga kweB7-1 / B7-2 kusvika CTLA-4 ine immune checkpoint inhibitor (anti-CTLA-4 antibody) inobvumira iwo maseru eT kuti ave anoshanda uye kuuraya tumarara maseru (kurudyi pani).

• PD-1 inhibitor: PD-1 ipuroteni iri pamusoro peT maseru ayo anobatsira kuchengetedza mhinduro dzemumuviri. Kana PD-1 yakanamatira kune imwe protein inonzi PDL-1 pane kenza kenza, inomisa iyo T cell kuuraya kenza kenza. PD-1 inhibitors inonamira kuPDL-1 uye inobvumira iwo maseru eT kuuraya maseru ekenza. Nivolumab rudzi rwePD-1 inhibitor iri kudzidziswa mukurapa angiosarcoma yezvinyoro zvinyoro.

Immune checkpoint inhibitor. Checkpoint mapuroteni, akadai sePD-L1 pane maseru emota uye PD-1 pane T maseru, anobatsira kuchengetedza mhinduro dzemumuviri. Iko kusungwa kwePD-L1 kusvika PD-1 kunoita kuti masero eT arege kuuraya tumarara maseru mumuviri (kuruboshwe pani). Kuvhara kusunga kwePD-L1 kusvika PD-1 ine immune checkpoint inhibitor (anti-PD-L1 kana anti-PD-1) inobvumira iwo maseru eT kuuraya matumbo maseru (kurudyi pani).

Imwe mishonga yekurapa

Mimwe mishonga inoshandiswa kurapa hura hwevascular tumors kana kugadzirisa mhedzisiro yavo inosanganisira zvinotevera:

• Steroid kurapa: Steroid mahormone akagadzirwa zvakasikwa mumuviri. Izvo zvinogona zvakare kugadzirwa murabhoritari uye kushandiswa semishonga. Steroid zvinodhaka zvinobatsira kudzora mamwe mamota etsinga. Corticosteroids, senge prednisone uye methylprednisolone, inoshandiswa kurapa mucheche hemangioma.

• Asiri-steroidal anti-anogumbura zvinodhaka (NSAIDs): NSAIDs anowanzo shandiswa kudzikisira fivha, kuzvimba, kurwadziwa, uye kutsvuka. Mienzaniso yeNSAIDs aspirin, ibuprofen, uye naproxen. Mukurapa kwemamota etsinga, NSAIDs dzinogona kuwedzera kuyerera kweropa kuburikidza nemamota uye nekudzora mukana wekuti ropa risingadiwe rinozoita.

• Antifibrinolytic therapy: Iyi mishonga inobatsira ropa kuwanda mune varwere vane Kasabach-Merritt syndrome. Fibrin ndiyo protein yakakura muropa rinovhara iro rinobatsira kumisa kubuda kweropa nekuporesa maronda. Mamwe mamota etsinga anokonzeresa fibrin kutsemuka uye ropa remurwere harivhare zvakajairika, zvichikonzera kubuda ropa kusingadzorwe. Antifibrinolytics inobatsira kudzivirira kuparara kwe fibrin.

Kucherechedza

Kucherechedza kuri kunyatsoongorora mamiriro emurwere pasina kupa chero kurapwa kusvikira zviratidzo kana zviratidzo zvaonekwa kana kuchinja.

Mhando nyowani dzekurapa dziri kuyedzwa mumakiriniki ekuedzwa.

Ruzivo nezve kiriniki miedzo inowanikwa kubva kuNCI webhusaiti.

Varwere vangangoda kufunga nezve kutora chikamu mukutora kiriniki.

Kune vamwe varwere, kutora chikamu mumuedzo wekiriniki inogona kunge iri sarudzo yekurapa yakanyanya kunaka. Zvemakiriniki miedzo chikamu chekutsvaga kwacho. Zvemakiriniki miedzo inoitwa kuti uone kana marapirwo matsva akachengeteka uye achishanda kana zvirinani pane akajairwa kurapwa.

Mazhinji emazuva ano marapirwo akajairwa akavakirwa pamavambo emakiriniki ekuedzwa. Varwere vanotora chikamu mukuyedzwa kwekiriniki vanogona kuwana kurapwa kwakaringana kana kuve pakati pevekutanga kurapwa kutsva.

Varwere vanotora chikamu mumakiriniki ekuedzwa vanobatsira zvakare kugadzirisa marapirwo anozoitwa chirwere mune ramangwana. Kunyangwe kana miedzo yemakiriniki isinga tangire kumarapirwo matsva anoshanda, anowanzo pindura mibvunzo yakakosha uye anobatsira kufambisira mberi kutsvagurudza.

Varwere vanogona kupinda mumakiriniki miedzo vasati, panguva, kana mushure mekutanga kwavo kenza kurapwa.

Mimwe miedzo yekiriniki inosanganisira chete varwere vasati vagamuchira kurapwa. Mimwe miedzo yekuedza kurapwa kwevarwere vane mamota asina kuve nani. Kune zvekare makiriniki ekuedzwa anoedza nzira nyowani dzekumisa mamota kubva kudzokororazve (kudzoka) kana kudzikisira mhedzisiro yekurapwa.

Kuedzwa kwemakiriniki kuri kuitika munzvimbo zhinji dzenyika. Ruzivo nezve kiriniki miedzo inotsigirwa neNCI inogona kuwanikwa paNCI yekiriniki miedzo yekutsvaga peji rewebhu. Kliniki miedzo inotsigirwa nemamwe masangano inogona kuwanikwa pane yeClinicalTrials.gov webhusaiti.

Yekutevera-bvunzo inogona kudikanwa.

Mimwe miedzo yakaitwa kuongorora huturu hwevascular inogona kudzokororwa. Dzimwe bvunzo dzinodzokororwa kuitira kuti vaone kuti kurapa kuri kushanda sei. Sarudzo nezvekuti uenderere mberi, shandura, kana kumisa kurapwa kunogona kunge kuchibva pamhedzisiro yeiyi bvunzo.

Mimwe bvunzo ichaenderera ichiitwa nguva nenguva mushure mekunge kurapwa kwapera. Mhedzisiro yeiyi bvunzo inogona kuratidza kana mamiriro emwana wako achinja kana kana bundu radzokazve (dzoka). Iyi bvunzo dzimwe nguva inonzi yekuteedzera-bvunzo kana kuongorora-kumusoro.

Benign Tumors

Muchikamu chino

• Mucheche Hemangioma

• Kuberekwa Hemangioma

• Benign Vascular Tumors yeRopa

• Chokurukisa Cell Hemangioma

• Epithelioid Hemangioma

• Pyogenic Granuloma

• Angiofibroma

• Vechidiki Nasopharyngeal Angiofibroma

Kuti uwane ruzivo nezve marapirwo akanyorwa pazasi, ona iyo Chikamu Sarudzo Yekutarisa Chikamu.

Mucheche Hemangioma

Infantile hemangiomas ndiyo yakajairika mhando yebenign vascular bundu muvana. Infantile hemangiomas inogadzira kana maseru asina kusimba ayo akafanirwa kuumba tsinga dzeropa dzinoita bundu pachinzvimbo. Chicheche hemangioma inogona zvakare kunzi "sitirobheri chiratidzo."

Aya mamota haawanzoonekwa pakuzvarwa asi anoonekwa kana mucheche aine mavhiki matatu kusvika matanhatu ekuberekwa. Mazhinji hemangiomas anokura kwemwedzi mishanu obva amira kukura. Iyo hemangiomas inononoka kupera mukati memakore akati wandei anotevera, asi mucherechedzo mutsvuku kana kusununguka kana kuunyana ganda rinosara. Kashoma kuti mucheche hemangioma adzoke.

Infantile hemangiomas inogona kunge iri paganda, munyama iri pazasi peganda, uye / kana nhengo. Iwo anowanzo ari mumusoro nemutsipa asi anogona kuve chero paari kana mumuviri. Hemangiomas inogona kuoneka seyese maronda, rimwe kana akawanda maronda anopararira pamusoro penzvimbo yakakura yemuviri, kana maronda mazhinji mune inopfuura chikamu chimwe chemuviri. Maronda akapararira pamusoro penzvimbo yakakura yemuviri kana maronda mazhinji anogona kukonzera matambudziko.

Infantile hemangioma ine kukura kushoma kana kusungwa (IH-MAG) ndeimwe mhando yehumucheche hemangioma iyo inoonekwa pakuzvarwa uye isingadi kukura. Iyo ronda rinoratidzika seyakajeka uye nerima nzvimbo dzehutsvuku muganda. Maronda acho anowanzo kuve pane wezasi muviri asi anogona kunge ari pamusoro nemutsipa. Hemangiomas erudzi urwu anoenda nekufamba kwenguva pasina kurapwa.

Njodzi Zviitiko

Chero chipi zvacho chinowedzera njodzi yako yekuwana chirwere chinonzi njodzi chinhu. Kuva nenjodzi hazvireve kuti uchawana chirwere. kusava nenjodzi hazvireve kuti hauzowani chirwere. Taura nachiremba wemwana wako kana iwe uchifunga kuti mwana wako angave ari panjodzi.

Infantile hemangiomas yakajairika mune zvinotevera:

• Vasikana.

• Varungu.

• Vana vasati vazvarwa.

• Mapatya, katatu, kana kumwe kuberekwa kwakawanda.

• Vacheche vevana amai vakura panguva yekuzvitakura kana vane matambudziko nepacenta panguva yekuzvitakura.

Zvimwe zvinokuvadza zvevacheche hemangiomas zvinosanganisira zvinotevera:

• Kuve nenhoroondo yemhuri yevecheche hemangioma, kazhinji muna amai, baba, hanzvadzi, kana mukoma.

• Kuva nedzimwe syndromes.

• PHACE syndrome: Chirwere umo hemangioma inopararira munzvimbo yakakura yemuviri (kazhinji musoro kana kumeso). Mamwe matambudziko ehutano anokanganisa iyo hombe midziyo yeropa, moyo, maziso, uye / kana huropi zvinogona zvakare kuitika.

• LUMBAR / PELVIS / SACRAL syndrome: Chirwere umo hemangioma inopararira munzvimbo yakakura yezasi kumashure. Mamwe matambudziko ehutano anokanganisa urinary system, sikarudzi, rectum, anus, brain, musana, uye tsinga basa zvinogona kuitika.

Kuva neanopfuura hemangioma imwe kana yendege kana ophthalmic hemangioma inowedzera mukana wekuve nemamwe matambudziko ehutano.

• Multiple hemangiomas: Kuva neanopfuura mashanu hemangiomas paganda chiratidzo chekuti panogona kuve nehemangiomas munhengo. Chiropa chinokanganisa kazhinji. Matambudziko emoyo, mhasuru, uye thyroid gland anogona zvakare kuitika.

• Airway hemangiomas: Hemangiomas mumhepo inowanzoitika pamwe nenzvimbo hombe, yakaita ndebvu yehemangioma kumeso (kubva munzeve, kutenderera muromo, zasi chirebvu, uye pamberi pemutsipa). Izvo zvakakosha kuti nzira yemumhepo hemangiomas inorapwa mwana asati anetseka kufema.

• Ophthalmic hemangiomas: Hemangiomas inosanganisira ziso inogona kukonzera matambudziko ekuona kana hupofu. Infantile hemangiomas inogona kuitika mune iyo conjunctiva (membrane iyo inoisa mukati memukati meziso uye inovhara chikamu chepamberi cheziso). Aya mahemangiomas anogona kuve akabatana nemamwe mamiriro asina kujairika eziso. Izvo zvakakosha kuti vana vane ophthalmic hemangioma vaongororwe na ophthalmologist.

Zviratidzo uye Zviratidzo

Infantile hemangiomas inogona kukonzera chero eanotevera zviratidzo nezviratidzo. Tarisa nechiremba wemwana wako kana mwana wako ane chero chinotevera:

• Zvipembenene zveganda: Nzvimbo yemitsipa yekutsvaira kana ganda rakavhenekerwa kana rakatsvuka rinogona kuoneka hemangioma isati yaita. Hemangiomas inoitika seyakaomarara, inodziya, inopenya kutsvuka kusvika kune crimson maronda paganda kana inogona kuita kunge kupwanya. Maronda anoumba maronda anorwadzawo. Gare gare, mahemangiomas paanoenda, anotanga kupera mukati asati agadzikana uye achirasa ruvara.

• Maronda pazasi peganda: Maronda anokura pasi peganda mumafuta anogona kuoneka sebhuruu kana pepuru. Kana maronda akadzika zvakakwana pasi peganda, anogona kunge asiri kuoneka.

• Maronda munhengo: Panogona kunge pasina zviratidzo zvekuti hemangiomas yaumbwa panhengo.

Kunyangwe mazhinji emacheche hemangiomas asina chekutya nazvo, kana mwana wako akagadzira chero mapundu kana matsvuku kana bhuruu mamaki paganda tarisa nachiremba wemwana wako. Iye kana iye anogona kuendesa mwana kune nyanzvi kana zvichidikanwa.

Kuongorora Kwekuongorora

Kuongorora kwepanyama uye nhoroondo zvinowanzo kuve zvese izvo zvinodiwa kuti uongorore infantile hemangiomas. Kana paine chimwe chinhu nezve bundu rinotaridzika kunge risinganzwisisike, biopsy inogona kuitwa. Kana iyo hemangioma yakadzika mukati memuviri isina shanduko paganda, kana maronda akapararira munzvimbo yakakura yemuviri, iyo ultrasound inogona kuitwa. Ona iyo General Ruzivo chikamu kune tsananguro yeaya mabvunzo uye maitiro.

Kana iyo hemangiomas iri chikamu chechirwere, mimwe miedzo inogona kuitwa, senge echocardiogram, MRI, magnetic resonance angiogram, uye kuongorora kweziso.

Kurapa

Mazhinji hemangiomas anopera uye anodzokera pasina kurapwa. Kana iyo hemangioma yakakura kana ichikonzera mamwe matambudziko ehutano, kurapwa kunogona kusanganisira zvinotevera:

• Propranolol kana imwe beta-blocker therapy.

• Steroid therapy, beta-blocker therapy isati yatanga kana kana beta-blockers isingakwanise kushandiswa.

• Pulsed dhayi laser kuvhiyiwa, kune hemangiomas ane maronda kana asina kunyatsoenda.

• Kuvhiya (kucheka) kwehemangiomas ane maronda, kukonzera matambudziko ekuona, kana kusati kwaenda zvachose. Kuvhiya kunogona zvakare kushandiswa maronda pachiso ayo asingapindure kune kumwe kurapwa.

• Nyaya yepamusoro beta-blocker therapy yehemangiomas iri mune imwe nzvimbo yeganda.

• Yakasanganiswa kurapwa, senge propranolol uye steroid kurapa kana propranolol uye topical beta-blocker kurapa.

• Kuongororwa kwekiriniki ye beta-blocker therapy (nadolol uye propranolol).

• Kuongororwa kwekiriniki kwetopical beta-blocker therapy (timolol).

Kuberekwa Hemangioma

Congenital hemangioma ibundu rinotyisa revascular iro rinotanga kuumbwa asati aberekwa uye rinozara zvakakwana kana mwana achinge azvarwa. Ivo vanowanzo kuve paganda asi vanogona kuve mune imwe nhengo. Iyo yekuzvarwa hemangioma inogona kuitika sekuputika kwemavara epepuru uye ganda rakatenderedza nzvimbo rinogona kunge rakareruka.

Kune matatu marudzi ekuberekwa hemangiomas:

• Inokurumidza kusanganisa kuberekwa hemangioma: Aya mamota anoenda ega ari gumi nemaviri kusvika gumi nemashanu mwedzi mushure mekuzvarwa. Vanogona kuumba maronda, kubuda ropa, uye kukonzeresa kwenguva pfupi matambudziko ekuvhara ropa. Ganda rinogona kutaridzika rakatosiyana kunyangwe mushure mekunge mahemangiomas aenda.

• Partial involuting congenital hemangioma: Aya mamota haapere zvachose.

• Asiri-asingabatanidzi congenital hemangioma: Aya mamota haatomboenda pachawo.

Kuongorora Kwekuongorora

Ona iyo General Ruzivo chikamu cherondedzero yemiedzo nemaitiro, senge ultrasound, inoshandiswa kuongorora congenital hemangioma.

Kurapa

Kurapa kwekukurumidza kusanganisa kuberekwa hemangioma uye chikamu chisina kusarudzika congenital hemangioma inogona kusanganisira zvinotevera:

• Kuongorora chete.

Kurapa kweasina-kubatanidza kuberekwa hemangioma kunogona kusanganisira zvinotevera:

• Kuvhiya kubvisa bundu, zvinoenderana nekuti iripi uye kuti iri kukonzera zviratidzo.

Benign Vascular Tumors yeRopa

Bhenign vascular tumors yechiropa inogona kunge iri yevascular lesion maronda (imwe ronda mune imwe nzvimbo yechiropa), akawanda maronda echiropa (akawanda maronda mune imwe nzvimbo yechiropa), kana kuparadzira maronda echiropa (akawanda maronda munzvimbo dzinopfuura imwechete ye chiropa).

Chiropa chine mabasa mazhinji, kusanganisira kusefa ropa uye kugadzira mapuroteni anodikanwa ekugwamba kweropa. Dzimwe nguva, ropa iro rinowanzo kuyerera kuburikidza nechiropa rinovharwa kana kunonoka nebundu. Izvi zvinotumira ropa rakananga pamoyo risingapfuure nepachiropa uye inonzi chiropa shunt. Izvi zvinogona kukonzera kutadza kwemoyo uye matambudziko nekugwamba kweropa.

Focal Vascular Lesions

Focal vascular maronda anowanzo kukurumidza kusanganisa congenital hemangiomas kana asiri-anomiririra congenital hemangiomas.

Kuongorora Kwekuongorora

Ona iyo General Ruzivo chikamu cherondedzero yemiyedzo uye maitiro anoshandiswa kuongorora ari mukati mevascular maronda echiropa.

Kurapa

Kurapa kwezvakakosha zvevascular maronda echiropa kunoenderana nekuti zviratidzo zvinoitika uye zvinogona kusanganisira zvinotevera:

• Kucherechedza.

• Zvinodhaka zvekurapa zviratidzo, zvinosanganisira kutadza kwemoyo uye matambudziko ekuvhara ropa.

• Kubatanidzwa kwechiropa kurapa zviratidzo.

• Kuvhiya, kune maronda asingapindure kune kumwe kurapwa.

Akawanda uye Anoparadzira Zvironda zveRopa

Multifocal uye akapararira maronda echiropa anowanzove echeche hemangiomas. Kupararira maronda echiropa kunogona kukonzera zvakakomba mhedzisiro, kusanganisira matambudziko neiyo thyroid gland uye nemoyo. Chiropa chinogona kuwedzera, kumanikidza pane dzimwe nhengo, uye kukonzera zvimwe zviratidzo.

Kuongorora Kwekuongorora

Ona iyo General Ruzivo chikamu cherondedzero yemiyedzo uye maitiro anoshandiswa kuongorora multifocal kana kuparadzira benign vascular maronda.

Kurapa

Kurapa kwezvakawanda maronda echiropa kunogona kusanganisira zvinotevera:

• Kucherekedza maronda asingakonzere zviratidzo.

• Beta-blocker therapy (propranolol) yezvironda zvinotanga kukura.

Kurapa kwekupararira kwechironda maronda kunogona kusanganisira zvinotevera:

• Beta-blocker kurapa (propranolol).

• Chemotherapy.

• Steroid kurapa.

• Yese hepatectomy uye kuisirwa kwechiropa, kana maronda asinga pindure pakurapwa kwemishonga. Izvi zvinoitwa chete kana maronda apararira zvakanyanya muchiropa uye nhengo inopfuura imwechete yatadza.

Kana chironda chevascular chechiropa chisinga pindure kune marapirwo akajairwa, biopsy inogona kuitwa kuti uone kana bundu racho rave rakaipa.

Chokurukisa Cell Hemangioma

Spindle cell hemangiomas ine masero anonzi spindle masero. Pasi pemaikorosikopu, masero ekurukisa anotaridzika akareba uye akatetepa.

Njodzi Zviitiko

Chero chipi zvacho chinowedzera njodzi yako yekuwana chirwere chinonzi njodzi chinhu. Kuva nenjodzi hazvireve kuti uchawana chirwere. kusava nenjodzi hazvireve kuti hauzowani chirwere. Taura nachiremba wemwana wako kana iwe uchifunga kuti mwana wako angave ari panjodzi. Spindle cell hemangiomas inogona kuitika muvana vane syndromes anotevera:

• Maffucci syndrome, iyo inokanganisa shwashwa uye ganda.

• Klippel-Trenaunay syndrome, iyo inokanganisa tsinga dzeropa, zvinyoro nyoro, uye mapfupa.

Zviratidzo

Chokurukisa masero hemangiomas anoonekwa kana pasi peganda. Iwo anorwadza akatsvuka-bhuru kana bhuruu maronda ayo anowanzoonekwa pamaoko kana makumbo. Vanogona kutanga sechironda chimwe uye vozoita maronda anopfuura makore.

Kuongorora Kwekuongorora

Ona iyo General Ruzivo chikamu cherondedzero yemiyedzo uye maitiro anoshandiswa kuongorora spindle cell hemangioma.

Kurapa

Iko hakuna kurapwa kwakajairwa kwespindle cell hemangiomas. Kurapa kunogona kusanganisira zvinotevera:

• Kuvhiya kubvisa bundu.

Spindle cell hemangiomas inogona kudzoka mushure mekuvhiyiwa.

Epithelioid Hemangioma

Epithelioid hemangiomas inowanzo gadzira kana mukati meganda, kunyanya musoro, asi inogona kuitika mune dzimwe nzvimbo, senge pfupa.

Zviratidzo uye Zviratidzo

Epithelioid hemangiomas dzimwe nguva inokonzerwa nekukuvara. Pane iro ganda, vanogona kuoneka seyakaomarara pinki kune matsvuku mapundu uye inogona kunge ichinhuwidza. Epithelioid hemangioma yebhonzo inogona kukonzera kuzvimba, kurwadziwa, uye kupera simba pfupa munzvimbo yakakanganiswa.

Kuongorora Kwekuongorora

Ona iyo General Ruzivo chikamu cherondedzero yemiyedzo uye maitiro anoshandiswa kuongorora epithelioid hemangioma.

Kurapa

Iko hakuna maitiro akajairwa epithelioid hemangiomas. Kurapa kunogona kusanganisira zvinotevera:

• Kuvhiya (curettage kana resection).

• Sclerotherapy.

• Radiation kurapa mune zvisingawanzoitika zviitiko.

Epithelioid hemangiomas inowanzodzoka mushure mekurapwa.

Pyogenic Granuloma

Pyogenic granuloma inonziwo lobular capillary hemangioma. Inowanzoitika muvana vakura uye vechidiki vakuru asi inogona kuitika chero pazera.

Iwo maronda acho dzimwe nguva anokonzerwa nekukuvara kana kubva mukushandiswa kwemimwe mishonga, kusanganisira mapiritsi ekudzivirira kubereka uye retinoid. Vanogona zvakare kuumba pasina chikonzero chinozivikanwa mukati mem capillaries (iyo midiki midzi midzi yeropa), tsinga, tsinga, kana dzimwe nzvimbo dzomuviri. Kazhinji panongova neronda rimwe chete, asi dzimwe nguva maronda mazhinji anoitika munzvimbo imwechete kana maronda anogona kupararira kune dzimwe nzvimbo dzemuviri.

Zviratidzo

Pyogenic granulomas anomutswa, akajeka matsvuku maronda anogona kunge ari madiki kana makuru uye akatsetseka kana ane bundu. Vanokura nekukurumidza pamusoro pevhiki kusvika kumwedzi uye vanogona kubuda ropa rakawanda. Aya maronda anowanzo kuve pamusoro peganda, asi anogona kuumbika munyama dziri pazasi peganda uye anotaridzika semamwe maronda etsinga.

Kuongorora Kwekuongorora

Ona iyo General Ruzivo chikamu cherondedzero yemiyedzo uye maitiro anoshandiswa kuongorora pyogenic granuloma

Kurapa

Mamwe pyogenic granulomas anoenda asina kurapwa. Mamwe pyogenic granulomas anoda kurapwa kunogona kusanganisira zvinotevera:

• Kuvhiya (kubvisa kana kurapwa) kubvisa ronda.

• Photocoagulation.

• Nyaya yepamusoro beta-blocker therapy.

Pyogenic granulomas inowanzodzoka mushure mekurapa.

Angiofibroma

Angiofibromas hazviwanzo. Iwo ane maronda eganda anowanzoitika aine mamiriro anonzi tuberous sclerosis (chirwere chakagarwa nhaka chinokonzeresa maronda eganda, kugwinha, uye hurema hwepfungwa).

Zviratidzo

Angiofibromas anoonekwa semapundu matsvuku kumeso.

Kuongorora Kwekuongorora

Ona iyo General Ruzivo chikamu cherondedzero yemiyedzo uye maitiro anoshandiswa kuongorora angiofibroma

Kurapa

Kurapa kweangofibromas kunogona kusanganisira zvinotevera:

• Kuvhiya (excision) kubvisa bundu.

• Laser kurapa.

• Targeted therapy (sirolimus).

Vechidiki Nasopharyngeal Angiofibroma

Vana vechidiki nasopharyngeal angiofibromas vane mamota ane huturu asi anogona kukura kuita nyama iri pedyo. Vanotanga mumhino uye vanogona kupararira kune nasopharynx, zvitadzo zveparanasal, bhonzo rakakomberedza maziso, uye dzimwe nguva kuuropi.

Kuongorora Kwekuongorora

Ona iyo General Ruzivo chikamu cherondedzero yemiyedzo uye maitiro anoshandiswa kuongorora vechidiki nasopharyngeal angiofibroma.

Kurapa

Kurapa kwevechidiki nasopharyngeal angiofibromas kunogona kusanganisira zvinotevera:

• Kuvhiya (excision) kubvisa bundu.

• Radiation kurapa.

• Chemotherapy.

• Immunotherapy (interferon).

• Targeted therapy (sirolimus).

Zvepakati Mamota Anopararira Munzvimbo

Muchikamu chino

• Kaposiform Hemangioendothelioma uye Tufted Angioma

Kuti uwane ruzivo nezve marapirwo akanyorwa pazasi, ona iyo Chikamu Sarudzo Yekutarisa Chikamu.

Kaposiform Hemangioendothelioma uye Tufted Angioma

Kaposiform hemangioendotheliomas uye tufted angiomas ndiwo maropa emidziyo yeropa inoitika muvacheche kana vana vadiki. Aya mamota anogona kukonzera Kasabach-Merritt chiitiko, mamiriro ayo iro ropa risingakwanise kuvhara uye kubuda kwakanyanya kubuda ropa kunogona kuitika. MuKasabach-Merritt chiitiko, bundu rinoteya uye rinoparadza maplatelet (masero anovhara ropa). Zvino hapana maplatelet akakwana muropa kana zvichidikanwa kumisa kubuda kweropa. Rudzi urwu rwevascular tumor harina hukama neKaposi sarcoma.

Zviratidzo uye Zviratidzo

Kaposiform hemangioendotheliomas uye tufted angiomas zvinowanzoitika paganda remaoko nemakumbo, asi zvinogona zvakare kuumba mumatumbu akadzika, senge mhasuru kana pfupa, kana muchipfuva kana mudumbu.

Zviratidzo nezviratidzo zvinogona kusanganisira zvinotevera:

• Nzvimbo dzakasimba, dzinorwadza dzeganda dzinoratidzika kunge dzakakuvara.

• Akapepuru kana akatsvukuruka-akatsvuka nzvimbo dzeganda.

• Kupwanya kuri nyore.

• Kubuda ropa kupfuura yakajairwa huwandu kubva mucous membranes, maronda, uye mamwe matishu.

Varwere vane kaposiform hemangioendothelioma uye tufted angioma vanogona kunge vane chirwere chekushaya ropa (kushaya simba, kunzwa kuneta, kana kutarisika kuchena).

Kuongorora Kwekuongorora

Ona iyo General Ruzivo chikamu cherondedzero yemiyedzo uye maitiro anoshandiswa kuongorora kaposiform hemangioendothelioma.

Kana bvunzo dzepanyama uye MRI ichiratidza zvakajeka kuti bundu iri kaposiform hemangioendothelioma kana tufted angioma, biopsy inogona kunge isingadiwe. Bhiopsy haiwanzo kuitwa nekuti kubuda ropa kwakanyanya kunogona kuitika.

Kurapa

Kurapa kwekaposiform hemangioendotheliomas uye tufted angiomas kunoenderana nezviratidzo zvemwana. Utachiona, kunonoka kurapwa, uye kuvhiyiwa kunogona kukonzera kubuda ropa kuri kutyisidzira hupenyu. Kaposiform hemangioendotheliomas uye tufted angiomas zvinonyatsorapwa neyevascular anomaly nyanzvi.

Kurapa uye kuchengetedza kutsigira kubata kubuda ropa kunogona kusanganisira zvinotevera:

• Steroid therapy iyo inogona kuteverwa nekemotherapy.

• Asiri-steroidal anti-anogumbura zvinodhaka (NSAIDs), akadai asipurini.

• Immunotherapy (interferon).

• Antifibrinolytic therapy yekuvandudza kugwamba kweropa.

• Chemotherapy neimwe kana yakawanda anticancer zvinodhaka.

• Beta-blocker kurapa (propranolol).

• Kuvhiya (kubvisa) kubvisa bundu, riine kana risina kubatanidzwa.

• Targeted therapy (sirolimus), ine kana isina steroid kurapa.

• Kuongororwa kwekiriniki kwechemotherapy kana kurapwa kwakanangwa (sirolimus).

Kunyangwe nekurapwa, aya mamota haanyatso kupera uye anogona kudzoka. Marwadzo uye kuzvimba kunogona kuwedzera zvakanyanya nezera, kazhinji kutenderedza nguva yekuyaruka. Yakareba-mhedzisiro mhedzisiro inosanganisira kusingaperi kurwadziwa, moyo kutadza, matambudziko emapfupa, uye lymphedema (iyo kuvaka kweiyo lymph fluid mumatukisi).

Zvepakati Mamota ayo Anowanzo Kupararira

Muchikamu chino

• Pseudomyogenic Hemangioendotheliomaoma

• Retiform Hemangioendotheliomaoma

• Papillary Intralymphatic Angioendothelioma

• Yakaumbwa Hemangioendotheliomaoma

• Kaposi Sarcoma

Kuti uwane ruzivo nezve marapirwo akanyorwa pazasi, ona iyo Chikamu Sarudzo Yekutarisa Chikamu.

Pseudomyogenic Hemangioendotheliomaoma

Pseudomyogenic hemangioendothelioma inogona kuitika muvana, asi inowanzoitika kuvarume vari pakati pemakore makumi maviri nemakumi mashanu ekuberekwa. Aya mamota haana kujairika, uye anowanzoitika mukati kana pasi peganda, kana mupfupa. Dzinogona kupararira kumatishu ari pedyo, asi kazhinji hadzipararire kune dzimwe nhengo dzomuviri. Muzviitiko zvakawanda, pane akawanda mamota.

Zviratidzo uye Zviratidzo

Pseudomyogenic hemangioendotheliomas inogona kuoneka sebundu mune zvinyoro nyoro kana inogona kukonzera marwadzo munzvimbo yakakanganiswa.

Kuongorora Kwekuongorora

Ona iyo General Ruzivo chikamu cherondedzero yemiyedzo uye maitiro anoshandiswa kuongorora pseudomyogenic hemangioendothelioma.

Kurapa

Kurapa kwepseudomyogenic hemangioendotheliomas kunogona kusanganisira zvinotevera:

• Kuvhiya kubvisa bundu pazvinogoneka. Kudimurwa kunogona kudikanwa kana paine mamota mazhinji mufupa.

• Chemotherapy.

• Targeted therapy (mTOR inhibitors).

Nekuti pseudomyogenic hemangioendothelioma isingawanzo muvana, sarudzo dzekurapa dzinoenderana nemiedzo yemakiriniki muvakuru.

Retiform Hemangioendotheliomaoma

Retiform hemangioendotheliomas iri kunonoka kukura, mapundu akapwanyika anowanikwa mune vechidiki vakuru uye dzimwe nguva vana. Aya mamota anowanzoitika pane kana pasi peganda remaoko, makumbo, uye hunde. Aya mamota kazhinji haaparadzire kune dzimwe nhengo dzemuviri.

Kuongorora Kwekuongorora

Ona iyo General Ruzivo chikamu cherondedzero yemiyedzo uye maitiro anoshandiswa kuongorora retiform hemangioendothelioma.

Kurapa

Kurapa kweretiform hemangioendotheliomas kunogona kusanganisira zvinotevera:

• Kuvhiya (excision) kubvisa bundu. Kuteedzera kunosanganisira kuongorora kuti uone kuti bundu rinodzoka here.

• Radiation kurapa uye chemotherapy apo kuvhiya hakugone kuitwa kana kana bundu radzoka.

Retiform hemangioendothelioma inogona kudzoka mushure mekurapwa.

Papillary Intralymphatic Angioendothelioma

Papillary intralymphatic angioendotheliomas anonziwo mapundu eDabska. Aya mamota anoumba mukati kana pasi peganda chero pamuviri. Lymph nodes dzimwe nguva inobatwa.

Zviratidzo

Papillary intralymphatic angioendotheliomas inogona kuoneka seyakasimba, yakasimudzwa, yepepuru mapundu, angave ari madiki kana makuru.

Kuongorora Kwekuongorora

Ona iyo General Ruzivo chikamu cherondedzero yemiyedzo uye maitiro anoshandiswa kuongorora papillary intralymphatic angioendothelioma.

Kurapa

Kurapa kwepapillary intralymphatic angioendotheliomas kunogona kusanganisira zvinotevera:

• Kuvhiya (excision) kubvisa bundu.

Yakaumbwa Hemangioendotheliomaoma

Rakaumbwa hemangioendotheliomas ine maficha ezvese ane hutachiona uye akaipa maronda emamota. Aya mamota anowanzoitika pane kana pasi peganda pamaoko kana makumbo. Zvinogonawo kuitika pamusoro, mutsipa, kana pachifuva. Composite hemangioendotheliomas haigone metastasize (kupararira) asi vanogona kudzoka munzvimbo imwechete. Kana bundu rikasasana, rinowanzopararira kune ma lymph node ari padyo.

Kuongorora Kwekuongorora

Ona iyo General Ruzivo chikamu cherondedzero yemiyedzo uye maitiro anoshandiswa kuongorora chinoumbwa hemangioendothelioma uye uone kana bundu rapararira.

Kurapa

Kurapa kweanoumbwa hemangioendotheliomas kunogona kusanganisira zvinotevera:

• Kuvhiya kubvisa bundu.

• Radiation kurapa uye chemotherapy yemamota akapararira.

Kaposi Sarcoma

Kaposi sarcoma igomarara rinokonzera maronda kukura muganda; mucous membranes inonamira mukanwa, mhino, nehuro; node node; kana dzimwe nhengo. Inokonzerwa neKaposi sarcoma herpes virus (KSHV). MuUnited States, inoitika kazhinji muvana vane immune system isina kusimba inokonzerwa nehutachiona hwehutachiona husingawanzoitika, hutachiona hweHIV, kana mishonga inoshandiswa pakuisazve nhengo.

Zviratidzo

Zviratidzo muvana zvinogona kusanganisira zvinotevera:

• Zvipuka muganda, mukanwa, kana pahuro. Zvipembenene zveganda zvitsvuku, zvepepuru, kana shava uye zvinoshanduka kubva pakapetwa, kusvika pakukwirwa, kuenda kunzvimbo dzine makanda dzinonzi mabara, kusvika kumajuru.

• Kuzvimba lymph node.

Kuongorora Kwekuongorora

Ona iyo General Ruzivo chikamu cherondedzero yemiyedzo uye maitiro anoshandiswa kuongorora Kaposi sarcoma.

Kurapa

Kurapa kweKaposi sarcoma kunogona kusanganisira zvinotevera:

• Chemotherapy.

• Immunotherapy (interferon).

• Radiation kurapa.

Nekuti Kaposi sarcoma isingawanzo kuitika muvana, dzimwe nzira dzekurapa dzinoenderana nemakiriniki ekuedzwa muvanhu vakuru. Ona pfupiso ye paKaposi Sarcoma Kurapa kweruzivo nezve Kaposi sarcoma muvakuru.

Malignant Tumors

Muchikamu chino

• Epithelioid Hemangioendotheliomaoma

• Angiosarcoma yeSoft Tissue

Kuti uwane ruzivo nezve marapirwo akanyorwa pazasi, ona iyo Chikamu Sarudzo Yekutarisa Chikamu.

Epithelioid Hemangioendotheliomaoma

Epithelioid hemangioendotheliomas inogona kuitika muvana, asi yakajairika muvakuru pakati pemakore makumi matatu kusvika makumi mashanu ekuberekwa. Zvinowanzoitika muchiropa, mapapu, kana pfupa. Vanogona kunge vachikurumidza kukura kana kunonoka kukura. Munenge chetatu chezviitiko, bundu rinopararira kune dzimwe nhengo dzomuviri nekukurumidza.

Zviratidzo uye Zviratidzo

Zviratidzo nezviratidzo zvinoenderana panowanikwa bundu:

• Pane iro ganda, mamota anogona kukwidziridzwa uye kutenderedzwa kana akati sandara, matsvuku-mashava makwapa anonzwa kudziya.

• Mumapapu, pangave pasina zviratidzo zvekutanga. Zviratidzo nezviratidzo zvinogona kuitika zvinosanganisira:

• Kurwadziwa pachifuva.

• Kusvipa ropa.

• Anemia (kushaya simba, kunzwa kuneta, kana kutaridzika kuchena).

• Kutambudzika kufema (kubva kune maronda emapapu tishu).

• Mune pfupa, mamota anogona kukonzera mabhureki.

Mamota anowanikwa muchiropa kana zvinyoro nyoro anogona zvakare kukonzera zviratidzo nezviratidzo.

Kuongorora Kwekuongorora

Epithelioid hemangioendotheliomas muchiropa anowanikwa aine CT scans uye MRI scans. Ona chikamu cheGeneral Information kuti uwane tsananguro yeiyi bvunzo uye maitiro anoshandiswa kuongorora epithelioid hemangioendothelioma uye uone kana bundu rapararira. X-ray inogona zvakare kuitwa.

Kurapa

Kurapa kweinononoka kukura epithelioid hemangioendotheliomas inosanganisira zvinotevera:

• Kucherechedza.

Kurapa kweepithelioid hemangioendotheliomas inokurumidza kukura inogona kusanganisira zvinotevera:

• Kuvhiya kubvisa bundu pazvinogoneka.

• Immunotherapy (interferon) uye yakanangwa kurapa (thalidomide, sorafenib, pazopanib, sirolimus) yemamota angangopararira.

Chemotherapy.

• Yese hepatectomy uye chiropa chinotamisa kana bundu riri muchiropa.

• Kuongororwa kwekiriniki kweakanangwa kurapwa (trametinib).

• Kuongororwa kwekiriniki kwechemotherapy uye kwakanangwa kurapwa (pazopanib).

Angiosarcoma yeSoft Tissue

Angiosarcomas mamota anokura nekukurumidza ayo anoumba mumidziyo yeropa kana lymph lymph mune chero chikamu chemuviri, kazhinji muzvinyoro. Mazhinji angiosarcomas ari mukati kana padyo neganda. Avo vari munyama dzakadzika dzakadzika vanogona kuumba muchiropa, spleen, uye mapapu.

Aya mamota haana kujairika muvana. Vana dzimwe nguva vane zvinopfuura kamwe bundu muganda uye / kana chiropa.

Njodzi Zviitiko

Chero chipi zvacho chinowedzera njodzi yako yekuwana chirwere chinonzi njodzi chinhu. Kuva nenjodzi hazvireve kuti uchawana chirwere. kusava nenjodzi hazvireve kuti hauzowani chirwere. Taura nachiremba wemwana wako kana iwe uchifunga kuti mwana wako angave ari panjodzi. Njodzi dzinokonzera angiosarcomas dzinosanganisira zvinotevera:

• Kuve pachena kune radiation.

• Chisingaperi (chenguva refu) lymphedema, mamiriro umo mamwe lymph fluid inovaka mumatumbu uye inokonzera kuzvimba.

• Kuva nebenign vascular tumor. Bundu rinotyisa, rakadai sehemangioma, rinogona kuita angiosarcoma asi izvi hazviwanzo.

Zviratidzo

Zviratidzo zveangososarcoma zvinoenderana nekuti bundu riripi uye zvinogona kusanganisira zvinotevera:

• Mavara matsvuku paganda raibuda ropa zviri nyore.

• Mapundu epepuru.

Kuongorora Kwekuongorora

Ona iyo General Ruzivo chikamu cherondedzero yemiyedzo uye maitiro anoshandiswa kuongorora angiosarcoma uye uone kana bundu rapararira.

Kurapa

Kurapa kweAngiosarcoma kunogona kusanganisira zvinotevera:

• Kuvhiya kubvisa zvachose bundu.

• Mubatanidzwa wekuvhiya, chemotherapy, uye radiation radiation yeangososcomcom yakapararira.

• Targeted therapy (bevacizumab) uye chemotherapy yeangiosarcomas iyo yakatanga senge infantile hemangiomas.

• Kuongororwa kwekiriniki kwemakemotherapy pamwe kana isina yakanangwa kurapwa (pazopanib).

• Kuongororwa kwekiriniki ye immunotherapy (nivolumab uye ipilimumab).

Kuti udzidze Zvakawanda Nezvehucheche Vascular Tumors

Kuti uwane rumwe ruzivo nezvehudiki vascular tumors, ona zvinotevera:

• Tissue Nyoro Sarcoma Peji Peji

• Computed Tomography (CT) Scans uye Cancer

• Targeted Cancer Therapies

• MyPART - Yangu Yevacheche uye Yevakuru Rare Tumor Network

Kuti uwane rumwe ruzivo rwegomarara rehucheche uye zvimwe zvecancer zviwanikwa, ona zvinotevera:

• Nezve Kenza

• Cancers Yevacheche

• Kurapa Kutsvaga Kwevana Cancer Buda Disclaimer

• Mahedhi Ekupedzisira Ekurapwa kweKenza Yevacheche

• Vechidiki uye Vechidiki Vakuru vane Cancer

• Vana vane Cancer: Nhungamiro Yevabereki

• Kenza muVana neVachiri kuyaruka

• Stage

• Kurarama neCancer

• Mibvunzo Yekubvunza Wako Chiremba nezveCancer

• Kune Vakapona uye Vanotarisira