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Ubwana bwa Pleuropulmonary Blastoma yo kuvura

Amakuru Rusange Yerekeye Kuvura Pleuropulmonary Blastoma

INGINGO Z'INGENZI

  • Pleuropulmonary blastoma ni indwara ingirabuzimafatizo (kanseri) ziba mu ngingo z'ibihaha na pleura cyangwa ingingo ziri hagati y'ibihaha.
  • Hariho ubwoko butatu bwa pleuropulmonary blastoma.
  • Kugira impinduka runaka muri DICER1 byongera ibyago byo guturika kwa pleuropulmonary.
  • Ibimenyetso nibimenyetso bya pleuropulmonary blastoma harimo ikibazo cyo guhumeka no kwandura ibihaha.
  • Ibizamini bisuzuma igituza bikoreshwa mugufasha gusuzuma indwara ya pleuropulmonary blastoma.
  • Ibintu bimwe bigira ingaruka kubimenyekanisha (amahirwe yo gukira).

Pleuropulmonary blastoma ni indwara ingirabuzimafatizo (kanseri) ziba mu ngingo z'ibihaha na pleura cyangwa ingingo ziri hagati y'ibihaha.

Pleuropulmonary blastoma ikora mubice byamahaha na pleura (tissue itwikira ibihaha kandi igatondekanya imbere yigituza). Zishobora kandi kwibumbira mu ngingo ziri hagati y'ibihaha zirimo umutima, aorta, na arteriire, cyangwa muri diafragma (imitsi nyamukuru ihumeka munsi y'ibihaha).

Mubihe byinshi, pleuropulmonary blastoma ifitanye isano nimpinduka runaka muri gen DICER1.

Hariho ubwoko butatu bwa pleuropulmonary blastoma.

Ubwoko bwa pleuropulmonary blastoma burimo ibi bikurikira:

  • Ibibyimba byo mu bwoko bwa I ni ibibyimba bisa na cyst mu bihaha. Bikunze kugaragara cyane kubana bafite imyaka 2 nabato kandi bafite amahirwe menshi yo gukira. Ubwoko bwa Ir ibibyimba ni Ubwoko bwa I bwasubiye inyuma (bwabaye buto) cyangwa butarakura cyangwa bukwirakwira. Nyuma yo kuvurwa, ikibyimba cyo mu bwoko bwa I gishobora kugaruka nkikibyimba cyo mu bwoko bwa II cyangwa III.
  • Ubwoko bwa II ibibyimba ni cyst-nkibice bimwe bikomeye. Ibi bibyimba rimwe na rimwe bikwira mu bwonko cyangwa mu bindi bice by'umubiri.
  • Ubwoko bwa III ibibyimba bikomeye. Ibibyimba bikunze gukwirakwira mu bwonko cyangwa mu bindi bice byumubiri.

Kugira impinduka runaka muri DICER1 byongera ibyago byo guturika kwa pleuropulmonary.

Ikintu cyose cyongera amahirwe yo kwandura indwara cyitwa impanuka. Kugira ibintu bishobora guteza ibyago ntibisobanura ko uzarwara kanseri; kutagira ibyago bishobora gusobanura ko utazarwara kanseri. Vugana na muganga wumwana wawe niba utekereza ko umwana wawe ashobora guhura nibibazo.

Impamvu zishobora gutera pleuropulmonary blastoma zirimo ibi bikurikira:

  • Kugira impinduka runaka muri gen DICER1.
  • Kugira amateka yumuryango ya syndrome ya DICER1.

Ibimenyetso nibimenyetso bya pleuropulmonary blastoma harimo ikibazo cyo guhumeka no kwandura ibihaha.

Ibi nibindi bimenyetso nibimenyetso bishobora guterwa na pleuropulmonary blastoma cyangwa nibindi bihe.

Menyesha umuganga wumwana wawe niba umwana wawe afite kimwe muri ibi bikurikira:

  • Inkorora idashira.
  • Guhumeka.
  • Umuriro.
  • Indwara y'ibihaha, nk'umusonga.
  • Kubabara mu gatuza cyangwa mu nda.
  • Kubura ubushake bwo kurya.
  • Kugabanya ibiro nta mpamvu izwi.

Ibizamini bisuzuma igituza bikoreshwa mugufasha gusuzuma indwara ya pleuropulmonary blastoma.

Ibizamini hamwe nuburyo bukurikira birashobora gukoreshwa:

  • Ikizamini cyumubiri namateka yubuzima: Ikizamini cyumubiri kugirango ugenzure ibimenyetso rusange byubuzima, harimo no gusuzuma ibimenyetso byindwara, nkibibyimba cyangwa ikindi kintu cyose gisa nkidasanzwe. Hazafatwa kandi amateka yubuzima bwumurwayi nindwara zashize hamwe nubuvuzi.
  • Isanduku x-ray: X-ray yingingo namagufwa imbere yigituza. X-ray ni ubwoko bwingufu zishobora kunyura mumubiri no kuri firime, bigakora ishusho yibice byumubiri.
  • CT scan (CAT scan): Uburyo bukora urukurikirane rwamashusho arambuye yibice byimbere mumubiri, nkigituza ninda, byafashwe muburyo butandukanye. Amashusho yakozwe na mudasobwa ihujwe na mashini ya x-ray. Irangi rishobora guterwa mumitsi cyangwa kumirwa kugirango bifashe ingingo cyangwa ingirangingo kugaragara neza. Ubu buryo nabwo bwitwa computing tomografiya, tomografiya ya mudasobwa, cyangwa mudasobwa ya axial tomografiya.
Kubara tomografiya (CT) scan yinda. Umwana aryamye kumeza anyerera muri CT scaneri, ifata amashusho ya x-ray imbere yinda.
  • PET scan (positron emission tomografi scan): Uburyo bwo kubona selile mbi yibibyimba mumubiri. Umubare muto wa glucose ikora radio (isukari) yatewe mumitsi. PET scaneri izenguruka umubiri kandi ikora ishusho yerekana aho glucose ikoreshwa mumubiri. Utugingo ngengabuzima twibibyimba twerekana neza cyane ku ishusho kuko zikora cyane kandi zifata glucose nyinshi kuruta selile zisanzwe.
  • MRI (magnetic resonance imaging): Uburyo bukoresha rukuruzi , imiraba ya radio, na mudasobwa mugukora urukurikirane rwamashusho arambuye yibice byumubiri, nkumutwe. Ubu buryo bwitwa kandi magnetic magnetic resonance imaging (NMRI).
  • Gusikana amagufwa: Uburyo bwo kugenzura niba mu magufwa hari selile zigabanya vuba, nka selile kanseri. Umubare muto cyane wibikoresho bya radio bitera mumitsi kandi bikanyura mumaraso. Ibikoresho bya radiyoyakusanyiriza mu magufa hamwe na kanseri kandi bigaragazwa na scaneri.
Gusikana amagufwa. Umubare muto wibikoresho bya radio bitera mumitsi yumwana kandi bikanyura mumaraso. Ibikoresho bya radiyo bikusanya mumagufwa. Mugihe umwana aryamye kumeza anyerera munsi ya scaneri, hamenyekana ibikoresho bya radio bikora amashusho bigakorerwa kuri ecran ya mudasobwa.
  • Bronchoscopy: Uburyo bwo kureba imbere muri trachea n'inzira nini zo mu bihaha ahantu hadasanzwe. Bronchoscope yinjizwa mumazuru cyangwa umunwa muri trachea no mubihaha. Bronchoscope nigikoresho cyoroshye, gisa nigituba gifite urumuri ninzira yo kureba. Irashobora kandi kuba ifite igikoresho cyo gukuraho ingero za tissue, zisuzumwa munsi ya microscope kugirango ibimenyetso bya kanseri.
  • Thoracoscopy: Uburyo bwo kubaga kugirango urebe ingingo ziri mu gituza kugirango urebe ahantu hadasanzwe. Gukata (gukata) bikozwe hagati yimbavu ebyiri, hanyuma thoracoscope yinjizwa mu gituza. Thoracoscope nigikoresho cyoroshye, gisa nigituba gifite urumuri na lens yo kureba. Irashobora kandi kugira igikoresho cyo gukuraho ingirangingo cyangwa lymph node sample, zisuzumwa munsi ya microscope kugirango ibimenyetso bya kanseri. Rimwe na rimwe, ubu buryo bukoreshwa mu gukuraho igice cya esofagusi cyangwa ibihaha. Niba thoracoscope idashobora kugera ku ngingo zimwe na zimwe, ingingo, cyangwa lymph node, hashobora gukorwa thoracotomy. Muri ubu buryo, hakozwe intambwe nini hagati yimbavu nigituza kirakingurwa.

Ibintu bimwe bigira ingaruka kubimenyekanisha (amahirwe yo gukira).

Kumenyekanisha biterwa na:

  • Ubwoko bwa pleuropulmonary blastoma.
  • Niba kanseri yarakwirakwiriye mu bindi bice by'umubiri mugihe cyo gusuzuma.
  • Niba kanseri yarakuweho burundu no kubagwa.

Ibyiciro bya Pleuropulmonary Blastoma

INGINGO Z'INGENZI

  • Nyuma yo gupimwa pleuropulmonary blastoma, hakorwa ibizamini kugirango hamenyekane niba selile ya kanseri yakwirakwiriye mu turere twegereye cyangwa mu bindi bice by'umubiri.
  • Hariho uburyo butatu kanseri ikwirakwira mu mubiri.
  • Kanseri irashobora gukwirakwira aho yatangiriye no mu bindi bice byumubiri.

Nyuma yo gupimwa pleuropulmonary blastoma, hakorwa ibizamini kugirango hamenyekane niba selile ya kanseri yakwirakwiriye mu turere twegereye cyangwa mu bindi bice by'umubiri.

Inzira ikoreshwa kugirango tumenye niba pleuropulmonary blastoma yakwirakwiriye mu ngingo zo mu gatuza cyangwa mu bindi bice byumubiri byitwa guterana. Amakuru yakusanyirijwe mubikorwa byateguwe akoreshwa mugutegura imiti. Ibisubizo by'ibizamini n'inzira zikoreshwa mu gusuzuma kanseri akenshi nazo zikoreshwa mu gutera indwara.

Hariho uburyo butatu kanseri ikwirakwira mu mubiri.

Kanseri irashobora gukwirakwira binyuze mu ngingo, sisitemu ya lymph, n'amaraso:

  • Tissue. Kanseri ikwirakwira aho yatangiriye ikurira mu turere twegereye.
  • Sisitemu ya Lymph. Kanseri ikwirakwira aho yatangiriye yinjira muri sisitemu ya lymph. Kanseri inyura mu mitsi ya lymph igana mu bindi bice by'umubiri.
  • Amaraso. Kanseri ikwirakwira aho yatangiriye yinjira mu maraso. Kanseri inyura mu mitsi y'amaraso igana mu bindi bice by'umubiri.

Kanseri irashobora gukwirakwira aho yatangiriye no mu bindi bice byumubiri.

Iyo kanseri ikwirakwira mu kindi gice cy'umubiri, yitwa metastasis. Ingirabuzimafatizo za kanseri zitandukana aho zatangiriye (ikibyimba kibanza) zikanyura muri sisitemu ya lymph cyangwa maraso.

  • Sisitemu ya Lymph. Kanseri yinjira muri sisitemu ya lymph, ikanyura mu mitsi ya lymph, igakora ikibyimba (ikibyimba metastatike) mu kindi gice cy'umubiri.
  • Amaraso. Kanseri yinjira mu maraso, ikanyura mu mitsi y'amaraso, igakora ikibyimba (ikibyimba metastatike) mu kindi gice cy'umubiri.

Ikibyimba metastatike nubwoko bumwe bwa kanseri nkibibyimba byibanze. Kurugero, niba pleuropulmonary blastoma ikwirakwira mubwonko, kanseri ya kanseri mubwonko mubyukuri selile pleuropulmonary blastoma. Indwara ni metastatike pleuropulmonary blastoma, ntabwo ari kanseri yubwonko.

Indwara ya Pleuropulmonary Blastoma

Indwara ya pleuropulmonary blastoma yagarutse (garuka) nyuma yo kuvurwa.

Incamake yo kuvura

INGINGO Z'INGENZI

  • Hariho uburyo butandukanye bwo kuvura kubana bafite pleuropulmonary blastoma.
  • Abana barwaye pleuropulmonary blastoma bagomba gutegurwa nubuvuzi bwitsinda ryabaganga ninzobere mu kuvura kanseri yo mu bwana.
  • Ubwoko bubiri bwubuvuzi busanzwe bukoreshwa kuri pleuropulmonary blastoma:
  • Kubaga
  • Chimoterapi
  • Ubwoko bushya bwo kuvura burimo kugeragezwa mubigeragezo byamavuriro.
  • Ubuvuzi bugamije
  • Umuti wa pleuropulmonary blastoma urashobora gutera ingaruka.
  • Abarwayi barashobora kwifuza gutekereza kubijyanye no kwipimisha kwa muganga.
  • Abarwayi barashobora kwipimisha kwa muganga mbere, mugihe, cyangwa nyuma yo gutangira kuvura kanseri.
  • Ibizamini byo gukurikirana birashobora gukenerwa.

Hariho uburyo butandukanye bwo kuvura kubana bafite pleuropulmonary blastoma.

Bumwe mu buryo busanzwe (ubuvuzi bukoreshwa ubu), kandi bumwe burimo kugeragezwa mubigeragezo byamavuriro. Ikigeragezo kivura ni ubushakashatsi bwakozwe bugamije gufasha kunoza imiti igezweho cyangwa kubona amakuru ku buvuzi bushya ku barwayi ba kanseri. Iyo ibizamini byo kwa muganga byerekana ko ubuvuzi bushya buruta ubuvuzi busanzwe, ubuvuzi bushya bushobora kuba ubuvuzi busanzwe.

Kubera ko kanseri mu bana idasanzwe, kugira uruhare mu igeragezwa ry’amavuriro bigomba kwitabwaho. Ibigeragezo bimwe na bimwe bivura abarwayi batatangiye kwivuza.

Abana barwaye pleuropulmonary blastoma bagomba gutegurwa nubuvuzi bwitsinda ryabaganga ninzobere mu kuvura kanseri yo mu bwana.

Umuti uzakurikiranwa n’umuganga w’abana oncologue, umuganga winzobere mu kuvura abana barwaye kanseri. Inzobere mu kuvura indwara z'abana ikorana n'abandi bahanga mu by'ubuzima bw'abana b'inzobere mu kuvura abana barwaye kanseri kandi bazobereye mu bice bimwe na bimwe by'ubuvuzi. Ibi birashobora kubamo inzobere zikurikira nabandi:

  • Umuganga w'abana.
  • Umuganga ubaga abana.
  • Inzobere mu by'indwara.
  • Inzobere mu baforomo b'abana.
  • Ushinzwe imibereho myiza.
  • Inzobere mu gusubiza mu buzima busanzwe.
  • Umuhanga mu by'imitekerereze ya muntu.
  • Inzobere mu buzima bw'umwana.

Ubwoko bubiri bwubuvuzi busanzwe bukoreshwa kuri pleuropulmonary blastoma:

Kubaga

Kubaga kugirango ukureho ibice byose by ibihaha hamwe na kanseri bikoreshwa mu kuvura indwara ya pleuropulmonary blastoma.

Chimiotherapie irashobora gutangwa mbere yo kubagwa kugirango ikureho ikibyimba. Iyo itanzwe mbere yo kubagwa, chimiotherapie izagabanya ikibyimba kandi igabanye urugero rwimitsi igomba gukurwaho mugihe cyo kubagwa. Umuti watanzwe mbere yo kubagwa witwa preoperative therapy cyangwa neoadjuvant therapy.

Chimoterapi

Chimoterapi ni umuti wa kanseri ukoresha ibiyobyabwenge kugirango uhagarike imikurire ya kanseri, haba mu kwica selile cyangwa kubabuza gutandukana. Iyo chimiotherapie ifashwe numunwa cyangwa igaterwa mumitsi cyangwa imitsi, imiti yinjira mumaraso kandi irashobora kugera kanseri ya kanseri mumubiri (chimiotherapie sisitemu).

Ubwoko bushya bwo kuvura burimo kugeragezwa mubigeragezo byamavuriro.

Iki gice cyincamake gisobanura imiti irimo kwigwa mubigeragezo byamavuriro. Ntishobora kuvuga ubuvuzi bushya burimo kwigwa. Amakuru yerekeye ibizamini byamavuriro araboneka kurubuga rwa NCI.

Ubuvuzi bugamije

Ubuvuzi bugamije ni uburyo bwo kuvura bukoresha ibiyobyabwenge cyangwa ibindi bintu byibasira kanseri. Ubuvuzi bugamije ubusanzwe butera kwangirika kwingirabuzimafatizo zisanzwe kuruta chimiotherapie cyangwa imiti ivura imirasire.

Ubuvuzi bugamije burimo kwigwa kuvura pleuropulmonary blastoma yagarutse (garuka).

Umuti wa pleuropulmonary blastoma urashobora gutera ingaruka.

Kumakuru yingaruka zitangira mugihe cyo kuvura kanseri, reba urupapuro rwuruhande rwacu.

Ingaruka ziterwa no kuvura kanseri zitangira nyuma yo kuvurwa zikomeza amezi cyangwa imyaka byitwa ingaruka zitinze. Ingaruka zo kuvura kanseri zishobora kubamo:

  • Ibibazo byumubiri.
  • Impinduka mumyumvire, ibyiyumvo, gutekereza, kwiga, cyangwa kwibuka.
  • Kanseri ya kabiri (ubwoko bushya bwa kanseri) cyangwa ibindi bihe.

Ingaruka zimwe zitinze zishobora kuvurwa cyangwa kugenzurwa. Ni ngombwa kuganira n'abaganga b'umwana wawe ku ngaruka zishobora gutinda ziterwa no kuvurwa.

Abarwayi barashobora kwifuza gutekereza kubijyanye no kwipimisha kwa muganga.

Ku barwayi bamwe, kwitabira ikizamini cyamavuriro birashobora kuba uburyo bwiza bwo kuvura. Ibigeragezo bivura biri mubikorwa byubushakashatsi bwa kanseri. Igeragezwa rya Clinical rikorwa kugirango hamenyekane niba imiti mishya ya kanseri itekanye kandi ifite akamaro cyangwa nziza kuruta ubuvuzi busanzwe.

Benshi mubuvuzi busanzwe bwa kanseri bushingiye kubigeragezo byambere byubuvuzi. Abarwayi bitabiriye kwipimisha barashobora kuvurwa bisanzwe cyangwa kuba mubambere bahawe imiti mishya.

Abarwayi bitabira ibizamini byo kwa muganga nabo bafasha kunoza uburyo kanseri izavurwa mugihe kizaza. Nubwo ibigeragezo bivura bitaganisha ku buvuzi bushya, akenshi basubiza ibibazo byingenzi kandi bigafasha gutera imbere ubushakashatsi.

Abarwayi barashobora kwipimisha kwa muganga mbere, mugihe, cyangwa nyuma yo gutangira kuvura kanseri.

Igeragezwa rimwe na rimwe ririmo abarwayi bataravurwa. Ibindi bigeragezo bipima abarwayi bafite kanseri itameze neza. Hariho kandi ibizamini byo kwa muganga bipima uburyo bushya bwo guhagarika kanseri kongera kugaruka (kugaruka) cyangwa kugabanya ingaruka zo kuvura kanseri.

Igeragezwa rya Clinical ririmo kubera mu bice byinshi by'igihugu. Amakuru yerekeye ibizamini byamavuriro ashyigikiwe na NCI urashobora kubisanga kurubuga rwa NCI. Ibizamini bya Clinical bishyigikiwe nandi mashyirahamwe murashobora kubisanga kurubuga rwa ClinicalTrials.gov.

Ibizamini byo gukurikirana birashobora gukenerwa.

Bimwe mubizamini byakozwe mugupima kanseri cyangwa kumenya icyiciro cya kanseri birashobora gusubirwamo. Ibizamini bimwe bizasubirwamo kugirango harebwe uburyo ubuvuzi bukora neza. Ibyemezo bijyanye no gukomeza, guhindura, cyangwa guhagarika ubuvuzi birashobora gushingira kubisubizo byibi bizamini.

Bimwe mubizamini bizakomeza gukorwa buri gihe nyuma yubuvuzi burangiye. Ibisubizo by'ibi bizamini birashobora kwerekana niba imiterere y'umwana wawe yarahindutse cyangwa niba kanseri yarongeye (garuka). Ibi bizamini rimwe na rimwe byitwa gukurikirana-ibizamini cyangwa kugenzura.

Umuti wa Pleuropulmonary Blastoma

Kumakuru yerekeye imiti yavuzwe hepfo, reba igice cyo kuvura.

Umuti wa pleuropulmonary blastoma urashobora kubamo ibi bikurikira:

  • Kubaga kugirango ukureho lobe yose yibihaha kanseri irimo, kubwoko bwa I na Type Ir pleuropulmonary blastoma.
  • Kubaga kugirango ukureho ibice byose by ibihaha kanseri irimo, hamwe na chimiotherapie cyangwa idafite imiti, kubwoko bwa II na III pleuropulmonary blastoma.

Koresha ubushakashatsi bwamavuriro kugirango ushakishe NCI ifashwa na kanseri ivura abarwayi. Urashobora gushakisha ibigeragezo ukurikije ubwoko bwa kanseri, imyaka yumurwayi, n’aho ibizamini bikorerwa. Amakuru rusange yerekeye ibizamini byamavuriro nayo arahari.

Ubuvuzi bwa Pleuropulmonary Blastoma

Kumakuru yerekeye imiti yavuzwe hepfo, reba igice cyo kuvura.

Kuvura indwara ya pleuropulmonary blastoma isubirwamo mubana irashobora kuba ikubiyemo ibi bikurikira:

  • Igeragezwa rya clinique risuzuma icyitegererezo cyibibyimba byumurwayi kugirango hahindurwe gene. Ubwoko bwo kuvura bugenewe umurwayi biterwa n'ubwoko bw'imihindagurikire ya gene.

Kugira ngo umenye byinshi kuri Pleuropulmonary Blastoma

Ushaka amakuru menshi yikigo cyigihugu cya kanseri kubyerekeye pleuropulmonary blastoma, reba ibi bikurikira:

  • Kanseri y'ibihaha Urupapuro
  • Kubara Tomografiya (CT) Gusikana na Kanseri
  • Intego zo kuvura Kanseri

Kubindi bisobanuro bya kanseri yo mu bwana hamwe nubundi buryo rusange bwa kanseri, reba ibi bikurikira:

  • Ibyerekeye Kanseri
  • Kanseri yo mu bwana
  • Umuti wo Gushakisha Kanseri Yabana Kureka
  • Ingaruka Zitinze Kuvura Kanseri Yabana
  • Ingimbi n'abangavu bafite kanseri
  • Abana barwaye Kanseri: Imfashanyigisho ku babyeyi
  • Kanseri mu bana n'ingimbi
  • Gutegura
  • Guhangana na Kanseri
  • Ibibazo byo Kubaza Muganga wawe kuri Kanseri
  • Abacitse ku icumu n'abarezi