Nā ʻano / palupalu-iʻa-sarcoma / hoʻomanawanui / keiki-palupalu-iʻa-maʻi-pdq

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ʻO ka hoʻomaʻamaʻa palu kamaliʻi Tissue Sarcoma (®) - Mana Mana Manaʻo

ʻO ka ʻike ākea e pili ana i ke kamaliʻi palupalu Tissue Sarcoma

NA MANA KUNI

  • ʻO ka sarcoma palupalu kamaliʻi kahi maʻi kahi maʻi malignant (cancer) i hoʻokumu ʻia i nā huna palaha o ke kino.
  • Hana ʻia kahi sarcoma palupalu i nā keiki a me nā mākua.
  • Loaʻa i kekahi mau maʻi a me nā maʻi hoʻoilina hiki ke hoʻonui i ka makaʻu o ka sarcoma palupalu o nā kamaliʻi.
  • ʻO ka hōʻailona maʻamau o ka sarcoma palupalu o ke kamaliʻi he puʻupuʻu ʻole a huʻi ʻole paha i nā mea palupalu o ke kino.
  • Hoʻohana ʻia nā hoʻokolohua diagnostics e huki (loaʻa) a hōʻike i ka sarcoma palupalu o nā kamaliʻi.
  • Inā hōʻike ʻia nā hoʻokolohua aia paha kahi sarcoma palupalu, hana ʻia kahi biopsy.
  • Nui a hewahewa nā ʻano sarcomas aʻa palupalu.
  • Tumele puʻupuʻu momona
  • ʻO nā iwi ʻiwi a iwi
  • Fibrous (hoʻohui) nā maʻi puʻupuʻu
  • Nā kūpikipiki iwi ʻiwi
  • Tumo mākala momona
  • ʻO nā tumors fibrohistiocytic i kapa ʻia
  • ʻO nā tumors sheath nerve
  • Nā Tumika Pericytic (Perivascular)
  • Nā Tumora o ke kumu pūnaewele ʻike ʻole ʻia
  • Nā Tumors ipu koko
  • Kū kekahi mau kumu i ka wānana (kahi o ke ola ʻana) a me nā koho lapaʻau.

ʻO ka sarcoma palupalu kamaliʻi kahi maʻi kahi maʻi malignant (cancer) i hoʻokumu ʻia i nā huna palaha o ke kino.

Hoʻopili, kākoʻo, a hoʻopuni nā mea palupalu o ke kino i nā ʻāpana a me nā ʻokena ʻē aʻe. Hoʻopili nā mea palupalu i kēia mau mea:

  • Momona.
  • Hoʻohui o ka iwi a me ka cartilage.
  • ʻIli kik Frorous.
  • Nā mākala.
  • Nā koʻo.
  • Tendons (nā kaula o nā mea i hoʻohui i nā mākala i nā iwi).
  • Nāʻaʻaʻa Synovial (nāʻaʻaʻa a puni nā hono).
  • Nā kīʻaha koko.
  • Nā moku Lymph.

Hiki ke loaʻa kahi sarcoma palupalu i nā wahi āpau o ke kino. I nā keiki, hana pinepine nā ʻōpū i nā lima, nā wāwae, ka umauma, a me ka ʻōpū.

Hana nā ʻano sarcoma palupalu i nā ʻano palupalu o ke kino, e pili ana i nā mākala, nā uaua, nā momona, nā kīʻaha koko, nā kīʻaha lymph, nā aʻa, a me nā aʻa e pili ana i nā hono.

Hana ʻia kahi sarcoma palupalu i nā keiki a me nā mākua.

Hiki i nā sarcoma palupalu ke pane i nā ʻano ʻokoʻa i ka mālama ʻana, a loaʻa paha kahi prognosis ʻoi aku ka maikaʻi ma mua o ka sarcoma palupalu i nā mākua. (E ʻike i ka hōʻuluʻulu e pili ana i ka hoʻomaʻamaʻa pilikino pilikino Tissue Sarcoma no ka ʻike e pili ana i ka mālama ʻana i nā mākua.)

Loaʻa i kekahi mau maʻi a me nā maʻi hoʻoilina hiki ke hoʻonui i ka makaʻu o ka sarcoma palupalu o nā kamaliʻi.

ʻO nā mea āpau e hoʻonui i kou makaʻu i ka loaʻa ʻana i kahi maʻi i kapa ʻia he kumu weliweli. ʻO ka loaʻa ʻana o kahi mea pilikia ʻaʻole ia he kumu e loaʻa ʻoe i ka maʻi ʻaʻai. ʻaʻohe o nā kumu pilikia ʻaʻole ia he kumu ʻaʻole ʻoe e loaʻa i ka maʻi ʻaʻai. E kamaʻilio me kāu kauka inā makemake ʻoe e pilikia paha kāu keiki.

ʻO nā kumu pilikia no ka sarcoma palupalu o ke kamaliʻi me ka loaʻa ʻana o nā maʻi hoʻoilina e hiki mai ana:

  • Li-Fraumeni maʻi.
  • Polyposis adenomatous ʻohana (FAP).
  • Loli ke ʻano RB1.
  • SMARCB1 (INI1) loli hoʻololi.
  • ʻO Neurofibromatosis ʻano 1 (NF1).
  • Werner maʻi maʻi.
  • Maʻi maʻi maʻi tuberous.
  • Adenosine deaminase-nele loa hui pū kekahi immunodeficiency.

ʻO nā kumu pilikia ʻē aʻe e pili pū me kēia:

  • Ka hana i hala me ka radiation radiation.
  • Loaʻa iā AIDS (loaʻa ka maʻi pale maʻi pale) a me ka maʻi ʻaʻai Epstein-Barr i ka manawa like.

ʻO ka hōʻailona maʻamau o ka sarcoma palupalu o ke kamaliʻi he puʻupuʻu ʻole a huʻi ʻole paha i nā mea palupalu o ke kino.

Hiki ke ʻike ʻia kahi sarcoma ma ke ʻano he puʻupuʻu ʻole ma lalo o ka ʻili, pinepine ma ka lima, ka wāwae, ka umauma, a me ka ʻōpū. ʻAʻohe paha hōʻailona a hōʻailona paha i ka mua. Ke piʻi a nui aʻe ka sarcoma a kaomi ma luna o nā mea kokoke, nā aʻa, nā mākala, a i ʻole nā ​​kīʻaha koko, hana ʻia nā hōʻailona a i ʻole nā ​​hōʻailona, ​​e like me ka ʻeha a nāwaliwali paha.

ʻO nā kumu ʻē aʻe paha ke kumu i nā hōʻailona like a me nā ʻōuli. E nīnau me ke kauka o kāu keiki inā loaʻa kēia pilikia i kāu keiki.

Hoʻohana ʻia nā hoʻokolohua diagnostics e huki (loaʻa) a hōʻike i ka sarcoma palupalu o nā kamaliʻi.

Hiki ke hoʻohana ʻia nā hoʻāʻo a me nā kaʻina hana aʻe:

  • ʻO ka hoʻāʻo kino a me ka mōʻaukala: kahi hōʻike o ke kino e nānā i nā hōʻailona laulā o ke olakino, e like me ka nānā ʻana i nā hōʻailona o ka maʻi, e like me nā puʻupuʻu a i ʻole nā ​​mea ʻē aʻe e ʻano ʻē. E lawe ʻia kahi moʻolelo o nā ʻano olakino o ka mea maʻi a me nā maʻi i hala a me nā mālama ʻana.
  • ʻO nā kukuna X: kahi x-ray kahi ʻano kukuna ikehu e hiki ke hele ma waena o ke kino i ke kiʻi ʻoniʻoni, e hana ana i nā kiʻi o nā wahi i loko o ke kino.
  • MRI (kiʻi resonance ʻume mākenēki): kahi hana e hoʻohana ai i ka magnet, nā nalu lekiō, a me kahi kamepiula e hana i nā kiʻi kikoʻī o nā wahi o ke kino, e like me ka umauma, ʻōpū, nā lima, a me nā wāwae. Kāhea ʻia kēia kaʻina hana he kiʻi nukelea kiʻi resonance (NMRI).
ʻO ke kiʻi ʻana o ka resonance ʻume mākenēki (MRI) o ka ʻōpū. Moe ke keiki ma ka papaʻaina e paheʻe i ka scanner MRI, e paʻi ana i nā kiʻi o loko o ke kino. Kōkua ka pale ma luna o ka ʻōpū o ke keiki e hoʻomaʻemaʻe i nā kiʻi.
  • CT scan (CAT scan): Kahi hana e hana ai i ka moʻo o nā kiʻi kikoʻī o nā wahi i loko o ke kino, e like me ka umauma a i ʻole ka ʻōpū, i lawe ʻia mai nā kihi ʻokoʻa. Hana ʻia nā kiʻi e kahi kamepiula i hoʻopili ʻia i kahi mīkini x-ray. Hoʻokomo ʻia paha ke kala i loko o ke aa a i ʻole ale ʻia e kōkua i nā ʻōpū a i ʻole nā ​​kino i hōʻike hou aku me ka maopopo. Kāhea ʻia kēia kaʻina hana he tomography i helu ʻia, kamepiula tomography, a i ʻole he tomography axial computerized.
ʻO ka scan tomography compute (CT) o ka ʻōpū. Moe ke keiki ma ka papaʻaina e paheʻe ai i ka scanner CT, e kiʻi ana i nā kiʻi x-ray o loko o ka ʻōpū.
  • ʻO ka hoʻāʻo ʻana o Ultrasound: kahi kaʻina hana e kipaku ʻia ai nā nalu kani ikaika (ultrasound) mai nā aʻa a i ʻole nā ​​ʻola a hana i nā leo. Hoʻokumu nā leo i kahi kiʻi o nā kino o ke kino i kapa ʻia he sonogram. Hiki ke paʻi ʻia ke kiʻi e nānā ma hope.

Inā hōʻike ʻia nā hoʻokolohua aia paha kahi sarcoma palupalu, hana ʻia kahi biopsy.

Pili ke ʻano o ka biopsy, i kekahi ʻāpana, i ka nui o ka nui a inā kokoke paha i ka ʻili o ka ʻili a i ʻole hohonu i kaʻiʻo. Hoʻohana maʻamau ʻia kekahi o nā ʻano biopsies:

  • ʻO ka biopsy o ka nila nui: ʻO ka hemo ʻana o nā kiko me ka hoʻohana ʻana i ka nila nui. Lawe ʻia nā laʻana ʻōnaehana lehulehu. Hiki ke alakaʻi ʻia kēia kaʻina hana me ka hoʻohana ʻana i ka ultrasound, CT scan, a i ʻole MRI.
  • ʻO Biopsy Incisional: ka hemo ʻana o kahi ʻāpana o kahi puʻupuʻu a i ʻole kahi laʻana o nā meaola.
  • ʻO Biopsy kūikawā: ʻO ka hemo ʻana o kahi puʻupuʻu āpau a i ʻole kahi o nā kiko i kū ʻole i ka nānā maʻamau. ʻIke kahi pathologist i ke kiko ma lalo o kahi microscope e nānā no nā hunaola maʻi ʻaʻai. Hiki ke hoʻohana ʻia kahi biopsy kūikawā e hemo loa i nā tumors liʻiliʻi e kokoke ana i ka ʻili. ʻAʻole hoʻohana pinepine ʻia kēia ʻano biopsy no ka mea e mau ana nā hunaola maʻi ʻaʻai ma hope o ka biopsy. Inā mau nā maʻi ʻaʻai, hoʻi mai paha ka maʻi ʻaʻai a pāhola paha i nā ʻāpana ʻē aʻe o ke kino.

Hana ʻia kahi MRI o ka tumo ma mua o ka biopsy kūikawā. Hana ʻia kēia e hōʻike i kahi i hoʻokumu ʻia ai ka tumo kumu a hoʻohana ʻia paha e alakaʻi i ke ʻoki ʻana a i ʻole ka radiation radiation.

Inā hiki, ʻo ke kauka nāna e hoʻoneʻe i kekahi tumo i loaʻa e komo pū i ka hoʻolālā ʻana i ka biopsy. ʻO ke kau ʻana o nā nila a i ʻole nā ​​ʻokiʻoki no ka biopsy hiki ke hoʻopili inā hiki ke hoʻoneʻe ʻia ka tumo holoʻokoʻa i ka wā o ke ʻoki hope.

E hoʻolālā i ka lapaʻau maikaʻi loa, pono ka laʻana o nā kiko i wehe ʻia i ka wā o ka biopsy e lawa pono e ʻike i ke ʻano o ka sarcoma aʻa palupalu a hana i nā hoʻokolohua ʻē aʻe. Lawe ʻia nā laʻana o nā kele mai nā tumo mua, nā pūnana lymph, a me nā wahi ʻē aʻe i loaʻa i nā hunaola maʻi ʻaʻai. ʻIke kahi pathologist i ke kiko ma lalo o kahi microscope e nānā no nā hunaola maʻi ʻaʻai a e ʻike i ke ʻano a me ka papa o ka tumo. Aia ka papa o ka tumo i ka nānā ʻana o nā hunaola maʻi ʻino ma lalo o kahi microscope a me ka wikiwiki o ka hoʻokaʻawale ʻana o nā hunaola. ʻO nā tumors kiʻekiʻe-papa a me ka papa waena e ulu a laha wikiwiki aʻe ma mua o nā tumors haʻahaʻa.

Ma muli o ka paʻakikī o ka diagnose o ka sarcoma palupalu, pono e nānā ʻia ka laʻana o ke kiko e ka mea pathologist i loaʻa ka ʻike i ka diagnose sarcoma nā mea palupalu.

Hoʻokahi a ʻoi paha o nā hoʻokolohua keʻena hoʻokolohua e hana ʻia e hoʻopaʻa i nā kiko kiko.

  • ʻImi Molecular: kahi hoʻokolohua hoʻokolohua e nānā ai no kekahi mau genes, nā protein, a i ʻole nā ​​molekika ʻē aʻe i kahi laʻana o nā kiko, ke koko, a i ʻole ke kahe o ke kino. Hana ʻia kahi hoʻokolohua molekole me nā kaʻina hana ʻē aʻe, e like me biopsies, e kōkua i ke kuhi ʻana i kekahi ʻano maʻi ʻaʻai. Nānā nā hoʻokolohua Molecular no kekahi mau loli a i ʻole chromosome e loli i kekahi mau sarcomas palupalu.
  • Hōʻike hoʻohuli huli - polymerase chain reaction (RT – PCR) hōʻike: kahi hoʻokolohua hoʻokolohua kahi e ana ʻia ai ka nui o kahi genetical genetical i kapa ʻia mRNA i hana ʻia e kekahi gen. Hoʻohana ʻia kahi enzyme i kapa ʻia ʻo transcriptase huli e hoʻololi i kahi ʻāpana kikoʻī o RNA i ʻāpana like o DNA, hiki ke hoʻonui ʻia (i hana ʻia i nā helu he nui) e kekahi enzyme i kapa ʻia ʻo DNA polymerase. Kōkua nā kope DNA i hoʻonui ʻia e haʻi inā e hana ʻia kahi mRNA kikoʻī e kahi ʻāpana. RT – PCR hiki ke hoʻohana e nānā i ka hoʻoulu ʻana o kekahi mau ʻāpana e hōʻike ai i ke kū ʻana o nā hunaola maʻi ʻaʻai. Hoʻohana ʻia kēia hoʻokolohua e nānā ai i kekahi mau loli i kahi moʻokūʻauhau a i ʻole chromosome, i hiki ke kōkua i ke kuhi ʻana i ka maʻi ʻaʻai.
  • Nānā Cytogenetic: kahi hoʻokolohua hoʻokolohua kahi e helu ai nā chromosome o nā hunaola i kahi hāpana o kaʻiʻo tumora i helu ʻia a nānā ʻia no nā loli, e like me ka haki, nalowale, hoʻoponopono hou ʻia, a i ʻole nā ​​chromosome keu. ʻO nā loli i kekahi mau chromosome he hōʻailona ia o ka maʻi ʻaʻai. Hoʻohana ʻia ka hoʻoponopono Cytogenetic e kōkua i ke kuhi ʻana i ka maʻi ʻaʻai, e hoʻolālā i ka lāʻau ʻana, a i ʻole e ʻike i ke ʻano o ka maikaʻi o ka mālama ʻana. ʻO ka fluorescence in situ hybridization (FISH) kahi ʻano o ka hoʻopili ʻana cytogenetic.
  • Immunocytochemistry: kahi hoʻokolohua hoʻokolohua e hoʻohana ai i nā anti -antibodies e nānā ai no kekahi antigens (markers) i kahi laʻana o nā hunaola o ka mea maʻi. Hoʻopili pinepine ʻia nā mea ʻino i kekahi enzyme a i ʻole ka waihoʻoluʻu fluorescent. Ma hope o ka hoʻopili ʻana o nā mea ʻume i ka antigen i ka laʻana o nā hunaola o ka hoʻomanawanui, e hoʻoulu ʻia ka enzyme a i ʻole ke kala, a laila ʻike ʻia ka antigen ma lalo o kahi microscope. Hiki ke hoʻohana ʻia kēia ʻano hoʻokolohua e haʻi i ka ʻokoʻa ma waena o nā ʻano sarcoma pahee palupalu.
  • ʻO ka microscopy mālamalama a me ka uila: ʻO kahi hoʻokolohua keʻena hoʻokolohua kahi e ʻike ʻia ai nā hunaola ma kahi hāpana o ke kiko ma lalo o nā microscope mana a kiʻekiʻe e nānā ai i kekahi mau hoʻololi i nā hunaola.

Nui a hewahewa nā ʻano sarcomas aʻa palupalu.

ʻO nā hunaola o kēlā me kēia ʻano sarcoma ke nānā ʻokoʻa ma lalo o kahi microscope. Hoʻohui ʻia nā tumors palupalu ma muli o ke ʻano o ka puʻupuʻu palupalu kahi i hana mua ai lākou.

ʻO kēia hōʻuluʻulu e pili ana i nā ʻano o nā sarcoma aʻa palupalu:

Tumele puʻupuʻu momona

Liposarcoma. He maʻi ʻaʻai kēia o nā hunaola momona. Hoʻokumu pinepine ka Liposarcoma i ka momona momona ma lalo o ka ʻili. I nā keiki a me nā ʻōpio, he haʻahaʻa haʻahaʻa ka liposarcoma (e ulu a hohola mālie paha). Aia kekahi mau ʻano liposarcoma, e like me:

  • ʻO Myxoid liposarcoma. ʻO kēia ka maʻi ʻaʻai haʻahaʻa haʻahaʻa e pane maikaʻi i ka mālama ʻana.
  • Liposarcoma Pleomorphic. ʻO kēia ka maʻamau he maʻi ʻaʻai nui kiʻekiʻe ka liʻiliʻi e pane maikaʻi i ka mālama ʻana.

ʻO nā iwi ʻiwi a iwi

ʻO nā iwi iwi a me ka iwi he hui o nā iwi iwi a me nā aʻa o ke kino. ʻO nā iwi ʻiwi a me ka iwi i nā ʻano aʻe:

  • Extrondreletal mesenchymal chondrosarcoma. Hoʻopili pinepine kēia ʻano iwi a me nā tumo cartilage i nā ʻōpio makua a kū i ke poʻo a me ka ʻāʻī.
  • Osteosarcoma Extraskeletal. Kākaʻikahi loa kēia ʻano iwi a me nā tumo cartilage i nā keiki a me nā ʻōpio. E hoʻi paha ia ma hope o ka hoʻomaʻamaʻa a pāhola paha i nā ake māmā.

Fibrous (hoʻohui) nā maʻi puʻupuʻu

ʻO nā puʻupuʻu fibrous (hoʻohui) nā ʻano aʻe:

  • Desmoid-type fibromatosis (i kapa ʻia ʻo desmoid tumor a i ʻole fibromatosis agresive). He pae haʻahaʻa kēia fibrousʻaʻaʻaʻaʻaʻa (e ulu mālie paha). E hoʻi paha ia i nā pūnaewele kokoke akā ʻaʻole hoʻolaha pinepine i nā ʻāpana mamao o ke kino. I kekahi manawa hiki i ka desibrid-type fibromatosis ke hoʻōki i ka ulu ʻana no kahi manawa lōʻihi. Kākaʻikahi, hiki ke nalo ke tumo me ka mālama ʻole ʻia.

Hiki i nā tumo Desmoid i kekahi manawa i nā keiki me nā loli o ka ʻāpana APC. Hiki i nā loli i kēia ʻenekua ke kumu i ka polyposis adenomatous ʻohana (FAP). He kūlana hoʻoilina ʻo FAP (hoʻoili ʻia mai nā mākua a hiki i nā pua) kahi i nui ai nā polyps (nā ulu ma nā membrane mucous) e kū ana ma nā paia o ka kolone a me ka pā. Kūkākūkā genetic (kahi kūkākūkā me kahi loea i hoʻomaʻamaʻa e pili ana i nā maʻi hoʻoilina a me nā koho no ka hoʻāʻo ʻana i ka ʻaoʻao) pono paha.

  • Nā Dermatofibrosarcoma protuberans. He tumo kēia o nā papa hohonu o ka ʻili e hana pinepine ʻia i ka pahu, nā lima, a me nā wāwae. Loaʻa i nā hunaola o kēia tumo kahi loli kūlohelohe i kapa ʻia he translocation (ʻāpana o ka kola COL1A1 hoʻololi i nā wahi me ka ʻāpana o ka ʻāpana PDGFRB). No ke kuhi ʻana i nā protuberans dermatofibrosarcoma, nānā ʻia nā hunaola tumora no kēia loli. ʻAʻole pālahalaha nā protuberans Dermatofibrosarcoma i nā lymph node a i ʻole nā ​​ʻāpana ʻē aʻe o ke kino.
  • Tumo myofibroblastic ʻōpala. Hana ʻia kēia maʻi ʻaʻa o nā hunaola pūnana, nā pūnaewele hoʻopili hoʻopili, a me kekahi o nā hunaola pale. Kū i loko o nā keiki a me nā ʻōpio. Hoʻokumu pinepine ia i nā mea palupalu, nā mumū, nā palapū, a me ka umauma. Hoʻi pinepine ia ma hope o ka lapaʻau ʻana akā ʻaʻole pāhola iki i nā wahi mamao o ke kino. Ua loaʻa kahi loli kūpili ma kahi o ka hapalua o kēia mau tumors.

ʻO Fibrosarcoma.

ʻElua ʻano fibrosarcoma i nā keiki a me nā ʻōpio:

  • ʻO fibrosarcoma Infantile (i kapa ʻia hoʻi ʻo fibrosarcoma congenital). Kū pinepine kēia ʻano fibrosarcoma i nā keiki mai ka makahiki 1 a ʻoi paha a ʻike ʻia paha i kahi hōʻike ultrasound prenatal. Ke ulu wikiwiki nei kēia tumo a nui pinepine i ka hōʻailona. ʻAʻole pāhola iki i nā ʻāpana mamao o ke kino. Loaʻa i nā hunaola o kēia tumo kahi loli kūlohelohe i kapa ʻia he translocation (ʻāpana o kahi chromosome hoʻololi i nā wahi me kahi ʻāpana o kahi chromosome ʻē aʻe). No ke kuhi ʻana i ka fibrosarcoma pēpē, nānā ʻia nā hunaola tumora no kēia loli. Ua ʻike ʻia kekahi tumo like i nā keiki makua, akā ʻaʻohe ona translocation e ʻike pinepine ʻia i nā keiki liʻiliʻi.
  • Fibrosarcoma makua. ʻO kēia ke ʻano o ka fibrosarcoma i loaʻa i nā mākua. ʻAʻohe o nā hunaola o kēia tumo ka loli i loaʻa i ka fibrosarcoma pēpē. (E ʻike i ka hōʻuluʻulu e pili ana i ka hoʻomaʻamaʻa pilikino Tissue Sarcoma no ka ʻike hou aku.)
  • Myxofibrosarcoma. ʻO kēia kahi tumo fibrous kikoʻī liʻiliʻi e hana pinepine ʻia i nā keiki ma mua o ka poʻe mākua.
  • ʻO ka sarcoma fibromyxoid haʻahaʻa haʻahaʻa. ʻO kēia kahi tumo ulu lohi e ulu hohonu ana i nā lima a i ʻole nā ​​wāwae a ʻo ka hapanui ka hopena i nā ʻōpio a me nā mākua waena. Hiki ke hoʻi i ka tumo i mau makahiki he nui ma hope o ka hoʻomaʻamaʻa ʻana a hoʻolaha ʻia i nā akemāmā a me ka uhi o ka paia umauma. Pono ka mālama ʻana i ke ola holoʻokoʻa.
  • ʻO Sclerosing epithelioid fibrosarcoma. ʻO kēia kahi tumo kikoola fibrous ulu ulu wikiwiki. Hiki iā ia ke hoʻi a hoʻolaha i nā ʻāpana ʻē aʻe o ke kino i mau makahiki ma hope o ka mālama ʻana. Pono ka ukali wā lōʻihi.

Nā kūpikipiki iwi ʻiwi

Hoʻopili ka mākala iwi i nā iwi a kōkua i ke kino e neʻe.

  • Rhabdomyosarcoma. ʻO Rhabdomyosarcoma ka sarcoma palupalu o ka wā kamaliʻi maʻamau i nā keiki 14 mau makahiki a ʻoi. (E ʻike i ka hōʻuluʻulu e pili ana i ka mālama ʻana iā Rhabdomyosarcoma Childhood no ka ʻike hou aku.)

Tumo mākala momona

Hoʻomaʻamaʻa nā mākala mānoanoa i ka loko o nā kīʻaha koko a hollow i nā mea pono o loko e like me ka ʻōpū, nā ʻōpū, loko, a me ka pūpū.

  • Leiomyosarcoma. Ua hoʻopili ʻia kēia tumo puʻupuʻu me ka maʻi Epstein-Barr i nā keiki i loaʻa i ka maʻi HIV a me ka maʻi AIDS. Leiomyosarcoma hiki ke hana ma ke ʻano he maʻi ʻaʻai ʻelua i nā mea i pakele o retinoblastoma hoʻoilina, i kekahi manawa i mau makahiki he nui ma hope o ka lapaʻau mua no retinoblastoma.

ʻO nā tumors fibrohistiocytic i kapa ʻia

  • Tumo fibrohistiocytic plexiform. ʻO kēia kahi tumo laha ʻole e hoʻopili pinepine i nā keiki a me nā ʻōpio ʻōpio. Hoʻomaka ka hoʻomaka ʻana o ka tumo ma ke ʻano he ulu ʻeha ʻole ma lalo o ka ʻili ma ka lima, lima a lima paha. ʻAʻole pāhola paha ia i nā lymph node kokoke a i ʻole i nā akemāmā.

ʻO nā tumors sheath nerve

Hana ʻia ka uhi nerve i nā pale pale o ka myelin e uhi ana i nā hunaola nerve ʻaʻole ia he ʻāpana o ka lolo a i ʻole ka iwi kuamoo. Loaʻa i nā tumors sheath nerve nā ʻano aʻe:

  • Tumo huluhulu ʻaʻano maʻi malignant. ʻO kekahi mau keiki i loaʻa i kahi tumory nerve peripheral nerve malignant he ʻano laha ʻole i kapa ʻia neurofibromatosis type 1 (NF1). Hiki i kēia tumo he papa haʻahaʻa a he papa kiʻekiʻe paha.
  • Tumo Triton malignant . ʻO kēia nā tumors e ulu wikiwiki ana i nā manawa pinepine i nā keiki me NF1.
  • ʻO Ectomesenchymoma. He tumo ulu ulu kēia e ulu nui ana i nā keiki. Hiki ke hana ʻo Ectomesenchymomas i ka maka o ka maka, ʻōpū, nā lima, a me nā wāwae.

Nā Tumika Pericytic (Perivascular)

Hana ʻia nā tumo Pericytic i loko o nā hunaola e hoʻopuni i nā kīʻaha koko. Loaʻa nā tumors Pericytic i kēia mau ʻano:

  • ʻO Myopericytoma. ʻO ka hemangiopericytoma infantile kahi ʻano o myopericytoma. ʻO nā keiki ma mua o 1 mau makahiki i ka manawa o ka hōʻailona hiki ke loaʻa i kahi prognosis ʻoi aku ka maikaʻi. I nā mea maʻi ma mua o 1 makahiki, ʻoi aku ka palahalaha ʻana o ka hemangiopericytoma pēpē i nā ʻāpana ʻē aʻe o ke kino, e like me nā lymph node a me nā akemāmā.
  • Myofibromatosis Infantile. ʻO myofibromatosis Infantile kekahi ʻano o myopericytoma. He tumo fibrous ia e hana pinepine i nā makahiki 2 mua o ke ola. Aia paha kekahi nodule ma lalo o ka ʻili, ma ke poʻo a me ka ʻāʻī (myofibroma), a i ʻole he mau nodule i ka ʻili, nā mākala, a me nā iwi (myofibromatosis). I nā mea maʻi me ka myofibromatosis pēpē, hoʻolaha paha ka maʻi ʻaʻai i nā meaola. Hele paha kēia mau tumors me ka ʻole o ka lapaʻau.

Nā Tumora o ke kumu pūnaewele ʻike ʻole ʻia

ʻO nā tumors o ke kumu ʻole ʻike ʻole ʻia (ʻo ke ʻano o ke kele i ʻike ʻole ʻia ka tumo i ʻike ʻole ʻia) e komo pū me nā ʻano aʻe:

  • ʻO ka sarcoma Synovial. ʻO ka sarcoma Synovial kahi ʻano maʻamau o ka sarcoma palupalu i nā keiki a me nā ʻōpio. Hana ʻia ia i nā pūnaewele a puni nā hono i nā lima a i ʻole nā ​​wāwae, akā hana ʻia paha i ke kumu, poʻo, a ʻāʻī paha. Loaʻa i nā hunaola o kēia tumo kahi loli kūlohelohe i kapa ʻia he translocation (ʻāpana o kahi chromosome hoʻololi i nā wahi me kahi ʻāpana o kahi chromosome ʻē aʻe). ʻOi aku ka makaʻu o nā tumors ʻoi aku ka nui o ka hoʻolaha ʻana i nā ʻāpana ʻē aʻe o ke kino, e like me nā akemāmā. ʻO nā keiki ma mua o 10 mau makahiki nona ka ʻōpuʻu he 5 kenimika a ʻoi iki paha a ua hana i nā lima a i nā wāwae i kahi wānana maikaʻi.
  • Pākuʻi ʻo Epithelioid. He sarcoma laha ʻole kēia e hoʻomaka pinepine i ka hohonu i loko o nā mea palupalu ma ke ʻano he ulu lohi a paʻa paʻa a hohola paha i nā lymph node. Inā hana ʻia ka maʻi ʻaʻai ma nā lima, nā wāwae, a me nā ʻūhā paha, e hana ʻia kahi biopsy lymph node sentinel e nānā ai no ka maʻi ʻaʻai i nā lymph node.
  • ʻO Sarvea ʻāpana palupalu ʻo Alveolar. He tumo kākaʻikahi kēia o nā mea kākoʻo palupalu e hoʻopili a hoʻopuni i nā ʻokena a me nā mea ʻē aʻe. Hana ʻia ia i nā lima a me nā wāwae akā hiki ke hana i nā kinona o ka waha, nā ā, a me ka maka. E ulu mālie paha ia a pālahalaha pinepine i nā ʻāpana ʻē aʻe o ke kino. Loaʻa i kahi ʻalalā ʻāpana ʻo Alveolar palupalu i kahi wānana ʻoi aku ke 5 centimika a ʻoi aku paha ka liʻiliʻi a i ʻole ke hoʻopau loa ʻia ka tumo e ke ʻoki. Loaʻa i nā hunaola o kēia tumo kahi loli kūpili i kapa ʻia he translocation (ʻāpana o ka moʻokūʻauhau ASSPL e hoʻololi i nā wahi me ka ʻāpana o ka ʻāpana TFE3). No ke kuhi ʻana i ka sarcoma ʻāpana palupalu alveolar, nānā ʻia nā hunaola tumora no kēia loli.
  • E hoʻomaʻemaʻe i ka sarcoma o ka pūnaewele. ʻO kēia kahi tumo ulu ulu palupalu e hoʻomaka i kahi kahena (uaua, fibrous, kaula e like me ke kaula e hoʻopili i nā mākala i ka iwi a i kekahi ʻāpana o ke kino). Hiki ke hana maʻamau i ka sarcoma pūnaewele ma nā kiko hohonu o ka wāwae, ka heʻe wāwae, a me nā kuʻekuʻe wāwae. Hoʻolahalaha paha ia i nā kiko lymph kokoke. Loaʻa i nā hunaola o kēia tumo kahi loli kūpili i kapa ʻia he translocation (ʻāpana o ka ʻāpana EWSR1 kuapo i nā wahi me ka ʻāpana o ka ʻāpana ATF1 a i ʻole CREB1). No ke kuhi ʻana i ka sarcoma o ka ʻili maʻemaʻe o nā mea palupalu, nānā ʻia nā hunaola tumora no kēia loli.
  • Extraseletal myxoid chondrosarcoma. Hiki ke ʻano o kēia ʻano sarcoma palupalu i nā keiki a me nā ʻōpio. Ma ka holo ʻana o ka manawa, hele a pālahalaha aku ia i nā ʻāpana ʻē aʻe o ke kino, me nā lymph node a me nā akemāmā. Hiki ke hoʻi i ka tumo i mau makahiki ma hope o ka lapaʻau ʻana.
  • ʻO sarcoma Extremeeletal Ewing. E ʻike i ka hōʻuluʻulu ma Ewing Sarcoma Hana no ka ʻike.
  • Desmoplastic liʻiliʻi a puni ka puʻupuʻu tum Tumele. Hoʻokumu pinepine kēia tumo i ka peritoneum i loko o ka ʻōpū, pelvis, a me / a i ʻole ka peritoneum i loko o ka scrotum, akā e hana paha ia i ka puʻupaʻa a i ʻole nā ​​mea paʻa ʻē aʻe. Hiki i nā tumors liʻiliʻi ke hana i ka peritoneum. Hiki i ka Desmoplastic puʻupuʻu liʻiliʻi a puni ke kele ke laha i nā akemāmā a me nā ʻāpana ʻē aʻe o ke kino. Loaʻa i nā hunaola o kēia tumo kahi loli kūlohelohe i kapa ʻia he translocation (ʻāpana o kahi chromosome hoʻololi i nā wahi me kahi ʻāpana o kahi chromosome ʻē aʻe). No ke kuhikuhi ʻana i nā tumm liʻiliʻi liʻiliʻi a puni desmoplastic, nānā ʻia nā hunaola tumo no kēia loli.
  • ʻO ke tumo rhabdoid keu-renal (extracranial). ʻO kēia tumo e ulu nei me ka wikiwiki e hana i nā mea palupalu e like me ke ake a me ka ʻai. Hana ʻia ia i nā keiki ʻōpio, me nā keiki hānau hou, akā hiki ke hana ʻia i nā keiki nui a me nā mākua. Hiki ke hoʻopili ʻia nā tumors Rhabdoid i kahi loli i kahi ʻenemi suppressor tumor i kapa ʻia ʻo SMARCB1. Hana kēia ʻano gen i kahi protein i kōkua i ka mālama ʻana i ka ulu ʻana o ka cell. Hiki ke hoʻoilina ʻia nā hoʻololi i ka moʻokūʻauhau SMARCB1. Kūkākūkā genetic (kahi kūkākūkā me kahi loea i aʻo ʻia e pili ana i nā maʻi hoʻoilina a me kahi pono e pono ai no ka hoʻāʻo ʻana i nā ʻaoʻao) pono paha.
  • ʻO nā tumors cell epithelioid perivascular (PEComas). Kū paha ʻo Benign PEComas i nā keiki me kahi ʻano hoʻoilina i kapa ʻia ʻo tuberous sclerosis. Kū lākou i loko o ka ʻōpū, ʻōpū, akemāmā, a me nā genitourinary. Piʻi mālie nā PEComas a ʻaʻole paha hoʻolaha ka hapa nui.
  • ʻO sarcoma i hoʻokaʻawale ʻole ʻia. Kū pinepine kēia mau tumors i nā iwi a i ʻole nā ​​mākala e pili ana i nā iwi a kōkua i ka neʻe ʻana o ke kino.
  • ʻO ka sarcoma pleomorphic pono ʻole / histiocytoma fibrous malignant (kūlana kiʻekiʻe). Hiki ke hana i kēia ʻano tumo palupalu i nā ʻāpana o ke kino kahi i loaʻa ai i nā mea maʻi i ka radiation radiation i ka wā i hala, a i ʻole he maʻi ʻaʻai ʻelua i nā keiki me retinoblastoma. Hana ʻia ka tumo i nā lima a i ʻole nā ​​wāwae a pāhola paha i nā ʻāpana ʻē aʻe o ke kino. (E nānā i ka hōʻuluʻulu ma Osteosarcoma a me Malignant Fibrous Histiocytoma o Bone Treatment no ka ʻike e pili ana i ka histiocytoma fibrous malignant o ka iwi.)

Nā Tumors ipu koko

ʻO nā tumors moku koko nā ʻano aʻe:

  • Epithelioid hemangioendothelioma. Hiki i nā Epithelioid hemangioendotheliomas ke hana i nā keiki akā ʻike pinepine ʻia i nā mākua ma waena o 30 a 50 mau makahiki. Kū pinepine lākou i ke ake, ka akemāmā, a iwi paha. E ulu wikiwiki ana paha lākou a ulu lohi paha. Ma kahi o ka hapakolu o nā hihia, pāhola koke ka tumo i nā ʻāpana ʻē aʻe o ke kino. (E ʻike i ka hōʻuluʻulu e pili ana i ka hoʻomaʻamaʻa ʻana o ka Tumua Vascular Tumors no ka ʻike hou aku.)
  • Angiosarcoma o ka palupalu. ʻO Angiosarcoma o nā mea palupalu kahi tumo ulu wikiwiki e hana i nā kīʻaha koko a i ʻole nā ​​kīʻaha lymph i kēlā me kēia ʻāpana o ke kino. Aia ka hapanui o nā angiosarcomas ma lalo a i ʻole ma lalo o ka ʻili. ʻO ka poʻe i loko o nā mea palupalu hohonu e hiki ke hana i ke akepaʻa, ka palapū, a i ʻole ka akemāmā. He kākaʻikahi loa lākou i nā keiki, ʻoi aku ka nui o nā tumo i ka ʻili a i ke akepaʻa i kekahi manawa. Kākaʻikahi, hiki i ka hemangioma pēpē ke lilo i angiosarcoma o nā mea palupalu. (E ʻike i ka hōʻuluʻulu e pili ana i ka hoʻomaʻamaʻa ʻana o ka Tumua Vascular Tumors no ka ʻike hou aku.)

E ʻike i nā hōʻuluʻulu aʻe e pili ana i ka ʻike e pili ana i nā ʻano sarcoma puʻupuʻu palu ʻaʻole i hoʻokomo ʻia i kēia hōʻuluʻulu manaʻo:

  • ʻO ka mālama ʻana iā Rhabdomyosarcoma Childhood
  • Hoʻomaʻo Ewing Sarcoma
  • ʻO Osteosarcoma a me Malignant Fibrous Histiocytoma o ka mālama ʻana i ka iwi
  • Nā maʻi ʻōlohelohe ʻole o ka mālama ʻana i ke kamaliʻi (ʻōpū stromal gastrointestinal)

Kū kekahi mau kumu i ka wānana (kahi o ke ola ʻana) a me nā koho lapaʻau.

ʻO ka wānana (loaʻa o ke ola) a me nā koho lapaʻau e pili i kēia:

  • ʻO ka ʻāpana o ke kino kahi i hana mua ai ka tumo.
  • Ka nui a me ka papa o ka tumo.
  • Ke ʻano o ka sarcoma puʻupuʻu palupalu.
  • Pehea ka hohonu o ka tumo ma lalo o ka ʻili.
  • Inā ua pālahalaha ka tumo i nā wahi ʻē aʻe o ke kino a kahi i pālahalaha ai.
  • ʻO ka nui o nā tumo i koe ma hope o ke kaha ʻana e wehe iā ia.
  • Inā hoʻohana ʻia ka radiation radiation e mālama i ka tumo.
  • Inā ua hōʻoia wale ʻia ka maʻi ʻaʻai a i ʻole ua hoʻi hou (hoʻi.

Nā pae o ke kamaliʻi Pōʻino Tissue Sarcoma

NA MANA KUNI

  • Ma hope o ka ʻike ʻia ʻana o kahi sarcoma palupalu o ka wā kamaliʻi, hana ʻia nā hoʻokolohua e ʻike inā ua hoʻolaha ʻia nā hunaola maʻi ʻaʻai i nā ʻāpana ʻē aʻe o ke kino.
  • ʻEkolu ala e hoʻolaha ai ka maʻi ʻaʻai i loko o ke kino.
  • E laha paha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i nā ʻāpana ʻē aʻe o ke kino.

Ma hope o ka ʻike ʻia ʻana o kahi sarcoma palupalu o ka wā kamaliʻi, hana ʻia nā hoʻokolohua e ʻike inā ua hoʻolaha ʻia nā hunaola maʻi ʻaʻai i nā ʻāpana ʻē aʻe o ke kino.

ʻO ke kaʻina hana e ʻike inā ua pālahalaha ka maʻi ʻaʻai i loko o ka mū palupalu a i ʻole nā ​​ʻāpana ʻē aʻe o ke kino i kapa ʻia he staging ʻAʻohe ʻōnaehana hoʻonohonoho maʻamau no ka sarcoma palupalu o nā kamaliʻi.

E hoʻolālā i ka mālama ʻana, he mea nui e ʻike i ke ʻano o ka sarcoma palupalu, inā hiki ke hemo ʻia ka tumo ma ke ʻoki ʻana, a inā ua pāhola ka maʻi ʻaʻai i nā ʻāpana ʻē aʻe o ke kino.

Hiki ke hoʻohana i nā kaʻina hana e ʻike ai inā ua laha ka maʻi ʻaʻai.

  • ʻO ka biopsy lymph node Sentinel: ʻO ka lawe ʻana i ka lymph node sentinel i ke kau ʻana. ʻO ka lymph node sentinel ka lua o nā lymph node i kahi hui o nā lymph node e loaʻa ai ka hoʻokahe ʻana i ka lymphatic mai ka tumo mua. ʻO ia ka pūnana lymph mua e laha aku ai ka maʻi ʻaʻai mai a ka tumo mua. Hoʻokomo ʻia kahi mea lekiō a me / a i ʻole ke kala polū ma kahi kokoke i ka tumo. Kahe ka mea a kala paha ma o nā kahena lymph i nā lymph node. Lawe ʻia ka pona lymph mua e loaʻa ai ka waiwai a kala paha. ʻIke kahi pathologist i ke kiko ma lalo o kahi microscope e nānā no nā hunaola maʻi ʻaʻai. Inā ʻaʻole i loaʻa nā hunaola maʻi ʻaʻai, ʻaʻole pono paha e hemo i nā pūnana lymph. I kekahi manawa, loaʻa kahi lymph node sentinel i kahi ʻoi aku o hoʻokahi hui o nā aka. Hoʻohana ʻia kēia kaʻina hana no ka epithelioid a me ka sarcoma pūnaewele paʻa.
  • CT scan (CAT scan): Kahi hana e hana ai i ka moʻo o nā kiʻi kikoʻī o nā wahi i loko o ke kino, e like me ka pahu, i lawe ʻia mai nā ʻaoʻao ʻokoʻa. Hana ʻia nā kiʻi e kahi kamepiula i hoʻopili ʻia i kahi mīkini x-ray. Hoʻokomo ʻia paha ke kala i loko o ke aa a i ʻole ale ʻia e kōkua i nā ʻōpū a i ʻole nā ​​kino i hōʻike hou aku me ka maopopo. Kāhea ʻia kēia kaʻina hana he tomography i helu ʻia, kamepiula tomography, a i ʻole he tomography axial computerized.
  • ʻO ka scan PET: ʻo kahi scan PET kahi hana e loaʻa ai nā pūnaewele tumo malignant i loko o ke kino. Hoʻokomo ʻia kahi liʻiliʻi o ka glucose radioactive (kō) i loko o kahi aa koko. Hoʻopili ka scanner PET a puni ke kino a hana i kahi kiʻi o kahi e hoʻohana ʻia ai ka glucose i ke kino. ʻOi aku ka mālamalama o nā hunaola tumo ma ke kiʻi no ka mea ʻoi aku ka hana a lawe i ka glucose ma mua o ka hana ʻana o nā hunaola maʻamau. Kāhea ʻia kēia kaʻina hana he positron emission tomography (PET) scan NineManga.com
  • Nānā PET-CT: kahi hana e hoʻohui i nā kiʻi mai kahi PET scan a me kahi scan tomography i helu ʻia (CT). Hana ʻia nā paʻi PET a me CT ma ka manawa like ma ka mīkini like. Hoʻohui ʻia nā kiʻi mai nā kiʻi ʻelua e hana i kahi kiʻi kikoʻī ma mua o nā hōʻike ʻelua e hana ʻia e ia iho.

ʻEkolu ala e hoʻolaha ai ka maʻi ʻaʻai i loko o ke kino.

Hiki ke pālahalaha ʻia ka maʻi ʻaʻai ma o nā meaola, ka ʻōnaehana lymph, a me ke koko.

  • Kāpena. Hoʻolahalaha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i ka ulu ʻana i nā wahi kokoke.
  • ʻŌnaehana Lymph. Hoʻolahalaha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i ke komo ʻana i ka ʻōnaehana lymph. Hele ka maʻi ʻaʻai ma o nā kīʻaha lymph i nā ʻāpana ʻē aʻe o ke kino.
  • Koko. Hoʻolahalaha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i ke komo ʻana i ke koko. Hele ka maʻi ʻaʻai ma o nā kīʻaha koko i nā ʻāpana ʻē aʻe o ke kino.

E laha paha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i nā ʻāpana ʻē aʻe o ke kino.

Ke pālahalaha ʻia ka maʻi ʻaʻai i kekahi ʻāpana o ke kino, ua kapa ʻia ia ʻo metastasis. E haki nā hunaola maʻi 'aʻai mai kahi a lākou i hoʻomaka ai (ka tumo mua) a hele i loko o ka ʻōnaehana lymph a i ʻole ke koko.

  • ʻŌnaehana Lymph. Komo ka maʻi ʻaʻai i loko o ka ʻōnaehana lymph, hele ma waena o nā kīʻaha lymph, a hana i kahi tumo (tumo metastatic) i kekahi ʻāpana o ke kino.
  • Koko. Komo ke kanesa i loko o ke koko, hele ma waena o nā kīʻaha koko, a hana i kahi tumo (tumo metastatic) i kekahi ʻāpana o ke kino.

ʻO ka tumo metastatic ka ʻano like o ke kanesa me ka tumo mua. ʻO kahi laʻana, inā pālahalaha ka sarcoma ʻili palupalu i ka hū, ʻo nā hunaola maʻi ʻaʻai i loko o ka akemāmā nā hunaola sarcoma aʻa palupalu. ʻO ka maʻi he sarcoma palupalu metastatic, ʻaʻole ʻo ka maʻi ʻaʻa lung.

Kūleʻa a holomua hoʻi i ka wā kamaliʻi Tissue Sarcoma

ʻO ka sarcoma palupalu hou o ka wā kamaliʻi ka maʻi ʻaʻai i hoʻi hou (hoʻi hou) ma hope o ka mālama ʻia ʻana. Ua hoʻi paha ka maʻi ʻaʻai ma ka wahi like a i ʻole nā ​​ʻāpana ʻē aʻe o ke kino.

ʻO ka sarcoma palupalu ʻōpio holomua ka maʻi ʻaʻai i pane ʻole i ka lāʻau.

Laulā Manaʻo Option Oponopono

NA MANA KUNI

  • Aia nā ʻano lapaʻau like ʻole no nā mea maʻi me ka sarcoma palupalu o nā kamaliʻi.
  • ʻO nā keiki me ka sarcoma palupalu o ka wā kamaliʻi e pono e hoʻolālā ʻia e kahi hui o nā lawelawe mālama ola he loea i ka mālama ʻana i ka maʻi ʻaʻai i nā keiki.
  • ʻO ka mālama ʻana no ka sarcoma palupalu o nā kamaliʻi i kumu i nā hopena ʻaoʻao.
  • Hoʻohana ʻia ʻehiku ʻano o ka mālama maʻamau.
  • ʻOki kino
  • Lapaʻau hoʻomākala
  • ʻO Chemotherapy
  • Nānā
  • Pahuhopu kau ʻia
  • Immunotherapy
  • Nā Laau Lapaʻau ʻē aʻe
  • Ke hoʻāʻo ʻia nei nā ʻano lapaʻau hou i nā hoʻokolohua hoʻokolohua.
  • Hoʻopau Gene
  • Makemake paha nā mea maʻi e noʻonoʻo e pili ana i ka hoʻokolokolo ʻana.
  • Hiki i nā mea maʻi ke komo i nā hoʻokolohua hoʻokolohua ma mua, i ka wā, a ma hope paha o ka hoʻomaka ʻana i kā lākou mālama maʻi ʻaʻai.
  • Pono paha nā hoʻokolohua ukali.

Aia nā ʻano lapaʻau like ʻole no nā mea maʻi me ka sarcoma palupalu o nā kamaliʻi.

Loaʻa nā ʻano lapaʻau like ʻole no nā mea maʻi me ka sarcoma palupalu o nā kamaliʻi. Kūlana maʻamau kekahi mau hōʻailona (ʻo ka lāʻau i hoʻohana ʻia i kēia manawa), a ʻo kekahi e hoʻāʻo ʻia nei i nā hoʻokolohua hoʻokolohua. ʻO kahi hoʻokolohua hoʻokolohua lapaʻau kahi noiʻi noiʻi i manaʻo ʻia e kōkua i ka hoʻomaikaʻi ʻana i nā mālama ʻana i kēia manawa a i ʻole loaʻa ka ʻike e pili ana i nā mālama hou no nā maʻi me ka maʻi ʻaʻai. Ke hōʻike nā hoʻokolohua hoʻokolohua ʻoi aku ka maikaʻi o kahi lapaʻau hou ma mua o ka maʻamau maʻamau, lilo paha ka lāʻau hou i ka lapaʻau maʻamau.

Ma muli o ka loaʻa ʻole o ka maʻi ʻaʻai i nā keiki, pono e noʻonoʻo ʻia i ka hoʻokolokolo ʻana. ʻO kekahi mau hoʻokolohua hoʻokolohua e hāmama wale i nā mea maʻi i hoʻomaka ʻole i ka lāʻau.

ʻO nā keiki me ka sarcoma palupalu o ka wā kamaliʻi e pono e hoʻolālā ʻia e kahi hui o nā lawelawe mālama ola he loea i ka mālama ʻana i ka maʻi ʻaʻai i nā keiki.

E mālama ʻia ka lapaʻau ʻana e kahi oncologist pediatric, he kauka i loea i ka mālama ʻana i nā keiki me ka maʻi ʻaʻai. Hana ka oncologist pediatric me nā mea lawelawe olakino ʻē aʻe i loea i ka mālama ʻana i nā keiki me ka sarcoma palupalu a me ka poʻe loea i kekahi mau wahi o ka lāʻau. Hiki i kēia ke komo i kahi kauka lāʻau pediatric me ka hoʻomaʻamaʻa kūikawā i ka hemo ʻana o nā sarcomas aʻa momona. Hoʻokomo pū ʻia nā loea e hiki mai ana:

  • Kahuna Pediatrician.
  • Oncologist uila.
  • Hematologist Pediatric.
  • ʻO ka loea kahu maʻi Pediatric.
  • Lapaʻau hoʻōla.
  • ʻOlogistlapa psychologist.
  • Limahana limahana.
  • Loea loea-ola keiki.

ʻO ka mālama ʻana no ka sarcoma palupalu o nā kamaliʻi i kumu i nā hopena ʻaoʻao.

No ka ʻike e pili ana i nā hopena i hoʻomaka i ka wā o ka mālama ʻana no ka maʻi ʻaʻai, ʻike i kā mākou ʻaoʻao ʻaoʻao ʻaoʻao.

ʻO nā hopena ʻē aʻe mai ka mālama ʻana i ka maʻi ʻaʻai e hoʻomaka ma hope o ka mālama ʻana a hoʻomau no nā mahina a i ʻole mau makahiki e kapa ʻia nā hopena hopena. Hiki i nā hopena hope loa o ka mālama ʻana i ka maʻi ʻaʻai ke:

  • Nā pilikia o ke kino.
  • Nā loli i ke ʻano, nā manaʻo, ka noʻonoʻo, ke aʻo ʻana, a me ka hoʻomanaʻo paha.
  • Nā maʻi ʻelua (nā ʻano maʻi ʻaʻai hou).

E mālama a kāohi ʻia paha kekahi mau hopena hopena. He mea nui e kamaʻilio pū me nā kauka o kāu keiki e pili ana i nā hopena o ka mālama ʻana i ka maʻi ʻaʻai i kāu keiki. (E ʻike i ka hōʻuluʻulu e pili ana i nā hopena hope o ka mālama ʻana no ka maʻi ʻaʻai kamaliʻi no ka ʻike hou aku.)

Hoʻohana ʻia ʻehiku ʻano o ka mālama maʻamau.

ʻOki kino

ʻO ke kaha e hemo loa ai ka sarcoma aʻa palupalu ke hana ʻia i ka wā hiki. Inā nui loa ka tumo, hāʻawi mua ʻia ka radiation therapy a chemotherapy paha, e hoʻoliʻiliʻi ai i ka tumo a hoʻoliʻiliʻi i ka nui o nā mea pono e hemo i ka wā o ke ʻoki. Kapa ʻia kēia ʻo neoadjuvant (preoperative) therapy.

Hiki ke hoʻohana i nā ʻano o ke kaha ʻana:

  • ʻO ka laulā kūloko: Ka hemo ʻana o ka tumo a me kekahi mea maʻamau a puni ia.
  • Hoʻonui: ʻoki e wehe i nā mea āpau a ʻāpana paha o ka lima a me ka wāwae me ka maʻi ʻaʻai.
  • Lymphadenectomy: Ka hemo ʻana o nā lymph node me ka maʻi ʻaʻai.
  • ʻOki kino Mohs: kahi kaʻina hana e hoʻohana ai i ka maʻi ʻaʻai i ka ʻili. Lawe ʻia nā papa pākahi o nā maʻi ʻaʻai a nānā ʻia ma lalo o ka microscope i kēlā me kēia manawa a hiki i ka lawe ʻia ʻana o nā maʻi ʻaʻai āpau. Hoʻohana ʻia kēia ʻano ʻoki e mālama i nā protuberans dermatofibrosarcoma.

Kāhea ʻia nō hoʻi ʻo ia ʻo Mohs micrographic surgery.

  • Hepatectomy: Keʻoki e wehe i nā mea āpau a ʻāpana paha o ke ake.

Pono paha kahi ʻoki ʻelua e:

  • Wehe i nā hunaola maʻi ʻino i koe.
  • E nānā i ka wahi a puni kahi i lawe ʻia aku ai ka tumo no nā hunaola maʻi ʻaʻai a laila e hemo i nā kikoʻī ke pono aʻe

Inā loaʻa ka maʻi ʻaʻai i ke ake, hiki ke hana ʻia kahi hepatectomy a me ke akepaʻa o ke ake (hemo ka ate a pani ʻia me kahi olakino mai kahi mea hāʻawi).

Ma hope o ka hemo ʻana o ke kauka i nā maʻi ʻaʻai āpau i hiki ke ʻike ʻia i ka manawa o ke ʻoki ʻana, hiki i kekahi mau mea maʻi ke hāʻawi ʻia i ka chemotherapy a i ʻole ka radiation therapy ma hope o ke kaha ʻana e luku i nā hunaola maʻi ʻea i koe. ʻO ka lāʻau i hāʻawi ʻia ma hope o ke kaha ʻana, e hoʻohaʻahaʻa i ka makaʻu e hoʻi mai ka maʻi ʻaʻai, i kapa ʻia ʻo adjuvant therapy.

Lapaʻau hoʻomākala

ʻO ka radiation radiation kahi lāʻau maʻi maʻi maʻi e hoʻohana i nā kukuna x nui ikaika a i ʻole nā ​​ʻano radiation e hoʻomake i nā hunaola maʻi ʻaʻai a mālama ʻole paha i ka ulu ʻana. ʻElua ʻano o radiation radiation:

  • Hoʻohana ka radiation radiation kūwaho i kahi mīkini ma waho o ke kino e hoʻouna i ka radiation i ka maʻi ʻaʻai. Hiki i kekahi mau ala o ka hāʻawi ʻana i ka radiation therapy ke pale i ka radiation mai ka hōʻino ʻana i nā mea olakino kokoke. Hiki i kēia ʻano radiation radiation ke hoʻopili i kēia mau mea:
  • Hoʻoikaika kino kino Stereotactic: He ʻano radiation radiation kino ʻo Stereotactic. Hoʻohana ʻia nā pono kūikawā e hoʻonoho i ka mea maʻi ma ke kūlana like no kēlā me kēia hoʻomaʻamaʻa radiation. Hoʻokahi manawa i ka lā no kekahi mau lā, kuhi ka mīkini radiation i kahi ʻoi aku ka nui ma mua o ka maʻamau maʻamau o ka radiation ma ka tumo. Ma ka loaʻa ʻana o ka mea maʻi ma ke kūlana like no kēlā me kēia lapaʻau, ʻoi aku ka liʻiliʻi o ka hōʻino ʻana i nā mea olakino kokoke. Kapa ʻia kēia kaʻina hana ʻo stereotactic waho-kukuna radiation radiation a me stereotaxic radiation therapy.
  • Hoʻohana ka radiation radiation i loko i kahi lāʻau radioactive i hoʻopaʻa ʻia i nā nila, nā hua, nā uea, a i ʻole nā ​​catheters i kau pololei ʻia i loko a kokoke paha i ka maʻi ʻaʻai.

Hāʻawi ʻia ka radiation radiation ma mua a ma hope paha o ke kaha ʻana e wehe i ka maʻi ʻaʻai e pili ana i ka ʻano a me ke kahua o ka maʻi ʻaʻai e mālama ʻia ai, inā mau kekahi maʻi ʻaʻai ma hope o ke kaha ʻana, a me nā hopena i manaʻo ʻia o ka lapaʻau. Hoʻohana ʻia ka radiation radiation kūwaho a me loko e mālama i ka sarcoma palupalu o nā kamaliʻi.

ʻO Chemotherapy

ʻO Chemotherapy kahi lāʻau lapaʻau maʻi maʻi e hoʻohana i nā lāʻau e hōʻoki i ka ulu ʻana o nā hunaola maʻi ʻaʻai, ma ka luku ʻana i nā hunaola a i ʻole ke kāpae ʻana iā lākou mai ka hoʻokaʻawale. Ke lawe ʻia ka chemotherapy e ka waha a i ʻole injected i loko o kahi aa koko a i ʻole nā ​​mākala, komo nā lāʻau i ke kahe o ke koko a hiki ke kiʻi i nā hunaola maʻi ʻōpio i loko o ke kino (chemotherapy ʻōnaehana). Ke waiho pololei ʻia ka chemotherapy i loko o ka wai cerebrospinal, kahi hui, a i ʻole ke kino o ke kino e like me ka ʻōpū, ʻo nā lāʻau lapaʻau ka mea nui e hoʻopili i nā hunaola maʻi ʻaʻai i kēlā mau wahi (chemotherapy āpau). Hoʻohui ʻia ʻo chemotherapy ka hoʻohana ʻana o nā lāʻau anticancer ʻoi aku ma mua o hoʻokahi.

Hāʻawi ʻia ke ala o ka chemotherapy ma muli o ke ʻano o ka mālama ʻana i ka sarcoma palupalu. ʻAʻole pane ka hapa nui o nā ʻano sarcoma palupalu i ka mālama ʻana me ka chemotherapy.

E ʻike i nā lāʻau i ʻae ʻia no ka Tissue Tissue Sarcoma no ka ʻike hou aku.

Nānā

Ke nānā pono nei i ka nānā ʻana i ke kūlana o ka mea maʻi me ka ʻole o ka hāʻawi ʻana i nā lāʻau a hiki i ka wā e ʻike ʻia ai nā hōʻailona a i ʻole nā ​​loli. Hiki ke nānā ʻia ke:

  • ʻAʻole hiki ke hoʻopau loa i ka tumo.
  • ʻAʻole loaʻa nā lapaʻau ʻē aʻe.
  • ʻAʻole hiki i ka tumo ke hoʻopōʻino i nā mea ola āpau.

Hiki ke hoʻohana ʻia ka nānā ʻana e mālama ai i ka fibromatosis desmoid-type, fibrosarcoma pēpē, PEComa, a i ʻole epithelioid hemangioendothelioma.

Pahuhopu kau ʻia

ʻO ka therapy target kahi ʻano lapaʻau e hoʻohana i nā lāʻau a i ʻole nā ​​mea ʻē aʻe e hoʻouka aku i nā hunaola maʻi ʻaʻai. Hoʻohui pinepine nā therapies i hoʻomākaukau ʻia e hōʻemi i ka pōʻino i nā hunaola maʻamau ma mua o ka chemotherapy a i ʻole ka radiation.

  • Paʻa nā mea hoʻohālua Kinase i kahi enzyme i kapa ʻia kinase (kahi ʻano protein. Aia kekahi ʻano o nā kinase i ke kino i loaʻa nā ʻano ʻokoʻa.
  • Hiki i nā mea pāpā ʻo ALK ke kū i ka maʻi ʻaʻai mai ka ulu a pālahalaha ʻana. Hiki ke hoʻohana ʻia ʻo Crizotinib e mālama ai i ka tumo myofibroblastic inflammatory a me ka fibrosarcoma pēpē.
  • Hoʻopili nā mea kāohi Tyrosine kinase (TKI) i nā hōʻailona pono e ulu nā tumors. Hoʻohana ʻia ʻo Imatinib e mālama i nā protuberans dermatofibrosarcoma. Hiki paha ke hoʻohana ʻia ʻo Pazopanib e mālama i ka desmoid-type fibromatosis, epithelioid hemangioendothelioma, a me kekahi ʻano sarcoma palupalu hou a holomua hoʻi o ka holomua. Hiki ke hoʻohana ʻia ʻo Sorafenib e mālama i ka desmoid-type fibromatosis a me ka epithelioid hemangioendothelioma. Hiki ke hoʻohana ʻia ʻo Sunitinib e mālama i ka sarcoma ʻāpana palupalu alveolar. Hoʻohana ʻia ʻo Larotrectinib e mālama i ka fibrosarcoma pēpē. Hoʻohana ʻia ʻo Ceritinib e mālama i ka tumo myofibroblastic ʻōpala.
  • ʻO nā mea kāwili mTOR kahi ʻano o ka hoʻomōhala hoʻomāka ʻia e kū ana i ka protein i kōkua i nā hunaola e māhele a ola. Hoʻohana ʻia nā mea kāohi mTOR e mālama i nā tumors liʻiliʻi liʻiliʻi a puni desmoplastic, PEComas, a me epithelioid hemangioendothelioma a ke hoʻopaʻa ʻia nei e mālama i ka tumigne maʻi āpau maʻi āpau. ʻO Sirolimus a me temsirolimus kekahi ʻano o ka mTOR mea hoʻōla lāʻau.

Ke aʻo ʻia nei nā ʻano mea like ʻole o ka tyrosine kinase inhibitors e like me:

  • Entrectinib no ka fibrosarcoma pēpē.
  • Trametinib no epithelioid hemangioendothelioma.

Ke aʻo ʻia nei kekahi ʻano ʻano lāʻau hoʻomōkōkō ʻia i nā hoʻokolohua hoʻokolohua, e like me kēia:

  • ʻO nā mea kāohi Angiogenesis kahi ʻano o ka hoʻomōhala hoʻomāka ʻia e pale ai i ka ulu ʻana o nā kīʻaha koko e pono ai no ka ulu ʻana o nā tumors. Ke aʻo ʻia nei nā mea hōʻoki Angiogenesis, e like me cediranib, sunitinib, a me thalidomide e mālama ai i ka sarcoma ʻāpana alveolar a me epithelioid hemangioendothelioma. Hoʻohana ʻia ʻo Bevacizumab e mālama ai i ka angiosarcoma.
  • Hoʻonohonoho ʻia nā mea hoʻohālua Histone methyltransferase (HMT) i nā lāʻau lapaʻau e hana i loko o nā hunaola maʻi ʻaʻa a me nā hōʻailona poloka e pono ai e ulu nā tumors. Ke hoʻopaʻa ʻia nei nā mea hoʻohālua o ka HMT, e like me tazemetostat, no ka mālama ʻana i ka tumath sheath nerve āpau malignant, epithelioid sarcoma, extraskeletal myxoid chondrosarcoma, a me ka tumar rhabdoid extrarenal (extracranial).
  • Hoʻopaʻa nā mea hoʻopili protein-shock protein i kekahi mau protein i pale i nā hunaola tumora a kōkua iā lākou e ulu. ʻO Ganetespib kahi mea hoʻonāukiuki hoʻohiwahiwa wela e hoʻopaʻa ʻia me ka hui pū me ka mTOR mea pale sirolimus no nā maʻi ʻōpū o ke kino āpau i hiki ʻole ke hemo e ke ʻoki.
  • ʻO nā mea kāohi ala NOTCH kahi ʻano o ka hoʻomōhala hoʻomāka ʻia e hana i loko o nā hunaola maʻi ʻaʻai a ālai i nā hōʻailona pono no ka ulu ʻana o nā tumors.

Ke aʻo ʻia nei nā mea pāpāho ala NOTCH no ka mālama ʻana i ka fibromatosis ʻano desmoid.

E ʻike i nā lāʻau i ʻae ʻia no ka Tissue Tissue Sarcoma no ka ʻike hou aku.

Immunotherapy

ʻO ka Immunotherapy kahi lapaʻau e hoʻohana i ka ʻōnaehana pale maʻi o ka mea maʻi e hakakā i ka maʻi ʻaʻai. Hoʻohana ʻia nā mea i hana ʻia e ke kino a i hana ʻia paha i kahi keʻena hoʻokolohua e hoʻonui, kuhikuhi, a hoʻihoʻi hou i nā pale kūlohelohe o ke kino i ka maʻi ʻaʻai. Kapa ʻia kēia ʻano lapaʻau ʻo biotherapy a i ʻole biologic therapy.

ʻO Interferon a me immune checkpoint inhibitor therapy kekahi ʻano o ka immunotherapy.

  • Hoʻopilikia ʻo Interferon i ka mahele o nā hunaola tumora a hiki ke hoʻolohi i ka ulu ulu ʻana. Hoʻohana ʻia ia e mālama i ka epithelioid hemangioendothelioma.
  • Pilikia pūkaʻina hoʻohiamoe maʻi pale: ʻO kekahi ʻano o nā hunaola pale, e like me nā hunaola T, a me kekahi mau pūnaʻi maʻi ʻaʻai i loaʻa kekahi mau protein, i kapa ʻia he checkpoint proteins, ma ko lākou ʻaoʻao e mālama ana i nā pane pale pale i ka helu. Ke loaʻa ka nui o kēia mau protein i nā hunaola maʻi ʻaʻai, ʻaʻole lākou e hoʻouka ʻia a make ʻia e nā hunaola T. Pale aku nā mea hoʻopale nānā Immune i kēia mau protein a hoʻonui ʻia ka hiki o nā hunaola T e pepehi i nā hunaola maʻi ʻaʻai.

ʻElua ʻano o ka checkpoint inhibitor therapy:

  • Mea kāohi CTLA-4: ʻO ka CTLA-4 kahi protein i ka ʻili o nā pūnaewele T e kōkua ai e mālama i nā pane pale o ke kino. Ke hoʻopili aku ʻo CTLA-4 i kahi protein ʻē aʻe i kapa ʻia ʻo B7 ma ke kolamu maʻi ʻaʻai, kū ia i ka hunaola T mai ka luku ʻana i ka pūnaeho maʻi maʻi. Hoʻopili ka mea pāpālina CTLA-4 i CTLA-4 a ʻae i nā hunaola T e pepehi i nā hunaola maʻi ʻaʻai. ʻO Ipilimumab kahi ʻano o ka mea kāohi iā CTLA-4 e hoʻopaʻa ʻia nei e mālama i ka angiosarcoma.
Mea hoʻopukapuka hōʻoiaʻiʻo pale pale. ʻO nā protein checkpoint, e like me B7-1 / B7-2 ma nā hunaola e hōʻike nei i nā antigen (APC) a me CTLA-4 ma nā pūnaewele T, e kōkua i ka mālama ʻana i nā pane pale o ke kino i ka nānā ʻana. Ke nakinaki ka mea loaʻa ʻo T-cell (TCR) i ka antigen a me nā protein histocompatibility complex (MHC) nui ma ka APC a me CD28 e hoʻopili iā B7-1 / B7-2 ma ka APC, hiki ke hoʻoulu ʻia ka pūnaewele T. Eia nō naʻe, ʻo ka hoʻopaʻa ʻana o B7-1 / B7-2 i CTLA-4 mālama i nā hunaola T i ke ʻano hana ʻole no laila ʻaʻole hiki iā lākou ke pepehi i nā hunaola tumora i loko o ke kino (panel hema). Ke kāpae nei i ka hoʻopaʻa ʻana o B7-1 / B7-2 i CTLA-4 me kahi mea hōʻoki pale pale pale (anti-CTLA-4 antibody) e ʻae i nā pūnaewele T e hana a make a make i nā pūhaka tumora (ʻaoʻao ʻākau).
  • Mea kāohi PD-1: ʻO PD-1 kahi protein i ka ʻili o nā hunaola T e kōkua ai i ka mālama ʻana i nā pane pale o ke kino. Ke hoʻopili aku ʻo PD-1 i kahi protein ʻē aʻe i kapa ʻia ʻo PDL-1 ma kahi hunaola maʻi ʻoki, paʻa ia i ke kele T mai ka luku ʻana i ka pūnaeho maʻi maʻi. Hoʻopili nā mea pale PD-1 i PDL-1 a ʻae i nā hunaola T e pepehi i nā hunaola maʻi ʻaʻai. ʻO Pembrolizumab kahi ʻano o ka mea kāohi PD-1 i hoʻohana ʻia e mālama i ka sarcoma palupalu holomua a hoʻi hou. ʻO Nivolumab kahi ʻano o ka mea kāohi PD-1 e hoʻopaʻa ʻia nei e mālama i ka angiosarcoma.
Mea hoʻopukapuka hōʻoiaʻiʻo pale pale. ʻO nā protein checkpoint, e like me PD-L1 ma nā hunaola tumo a me PD-1 ma nā hunaola T, e kōkua i ka mālama ʻana i nā pane pale ʻole. Mālama ka paʻa ʻana o PD-L1 iā PD-1 mālama i nā hunaola T mai ka pepehi ʻana i nā hunaola tumora i loko o ke kino (panel hema). Ke kāpae nei i ka hoʻopaʻa ʻana o PD-L1 iā PD-1 me kahi mea pale pale pale pale pale (anti-PD-L1 a i ʻole anti-PD-1) ʻae i nā hunaola T e pepehi i nā hunaola tumera (ʻaoʻao ʻākau)

Nā Laau Lapaʻau ʻē aʻe

Loaʻa nā hopena antitumor i ka lāʻau steroid steroid i nā tumors myofibroblastic.

ʻO ka Hormone therapy kahi lapaʻau maʻi ʻaʻai e hoʻoneʻe i nā homone a i ʻole ālai i kā lākou hana a kāpae i nā hunaola maʻi maʻi mai ka ulu ʻana. ʻO nā Hormones nā mea i hana ʻia e nā glands i loko o ke kino a hoʻolaha ʻia i ke kahe o ke koko. Hiki i kekahi mau hormoni ke hoʻoulu i kekahi mau maʻi ʻaʻai. Inā hōʻike ʻia nā hōʻike i ka loaʻa ʻana o nā hunaola maʻi ʻaʻai i mau wahi kahi e hoʻopili ai nā homone (nā mea loaʻa), nā lāʻau, ke ʻoki ʻana, a i ʻole ka radiation therapy e hōʻemi ai i ka hana ʻana o nā hormones a i ʻole keakea iā lākou mai ka hana ʻana Hiki ke hoʻohana ʻia nā antiestrogens (nā lāʻau e ālai ana i ka estrogen), e like me tamoxifen, e mālama ai i ka fibromatosis ʻano desmoid. Ke aʻo ʻia nei ʻo Prasterone no ka mālama ʻana i ka sarcoma synovial.

ʻO nā lāʻau anti-inflammatory Nonsteroidal (NSAIDs) he lāʻau lapaʻau (e like me aspirin, ibuprofen, a me naproxen) i hoʻohana mau ʻia e hoʻemi i ke kuni, ka pehu ʻana, ka ʻeha, a me ka ʻulaʻula. I ka mālama ʻana i ka desibrid-type fibromatosis, hiki ke hoʻohana ʻia kahi NSAID i kapa ʻia ʻo sulindac e kōkua i ka pale ʻana i ka ulu ʻana o nā hunaola maʻi ʻaʻai.

Ke hoʻāʻo ʻia nei nā ʻano lapaʻau hou i nā hoʻokolohua hoʻokolohua.

Hōʻike kēia ʻāpana hōʻuluʻulu manaʻo i nā mālama e hoʻopaʻa ʻia nei i nā hoʻokolohua hoʻokolohua. ʻAʻole paha ia e ʻōlelo i kēlā me kēia lapaʻau hou e hoʻopaʻa ʻia ana. Loaʻa nā ʻike e pili ana i nā hoʻokolohua hoʻokolohua mai ka pūnaewele NCI.

Hoʻopau Gene

Ke aʻo ʻia nei ka genotherapy no ka sarcoma synovial o ke keiki i hoʻi hou, pālahalaha, a i ʻole hiki ʻole ke hemo e ke ʻoki. Lawe ʻia kekahi o nā hunaola T (kahi ʻano o ke keʻokeʻo koko keʻokeʻo) a hoʻololi ʻia nā genes i nā hunaola i loko o kahi keʻena hoʻokolohua (genetically engineered) i mea e hoʻouka ai i nā hunaola maʻi ʻaʻai. Hoʻihoʻi ʻia lākou i ka mea maʻi ma o ka hoʻoulu ʻana.

Makemake paha nā mea maʻi e noʻonoʻo e pili ana i ka hoʻokolokolo ʻana.

No kekahi mau mea maʻi, ke komo nei i ka hoʻokolohua hoʻokolohua ke koho lapaʻau maikaʻi loa paha. ʻO nā hoʻokolohua hoʻokolohua kahi ʻāpana o ka noiʻi ʻana o ka maʻi ʻaʻai. Hana ʻia nā hoʻokolohua hoʻokolohua e ʻike inā palekana a maikaʻi a maikaʻi paha nā hoʻomaʻamaʻa maʻi ʻaʻai ma mua o ka maʻamau maʻamau.

ʻO ka hapa nui o nā hana maʻamau no ka maʻi ʻaʻai i kau ʻia ma nā hoʻokolohua hoʻokolohua mua. ʻO nā mea maʻi i komo i ka hoʻokolokolo hoʻokolohua hiki ke loaʻa i ka lāʻau maʻamau a i ʻole i waena o nā mea mua i loaʻa kahi lāʻau hou.

ʻO nā mea maʻi i komo i nā hoʻokolohua hoʻokolohua kōkua pū kekahi i ka hoʻomaikaʻi ʻana i ke ʻano o ka mālama ʻana i ka maʻi ʻaʻai i ka wā e hiki mai ana. ʻOiai ʻaʻole nā ​​alakaʻi hoʻokolohua e alakaʻi i nā hoʻoponopono hou maikaʻi, pane pinepine lākou i nā nīnau nui a kōkua i ka neʻe i mua o ka noiʻi.

Hiki i nā mea maʻi ke komo i nā hoʻokolohua hoʻokolohua ma mua, i ka wā, a ma hope paha o ka hoʻomaka ʻana i kā lākou mālama maʻi ʻaʻai.

Hoʻopili wale kekahi mau hoʻokolohua hoʻokolohua i nā mea maʻi i loaʻa ʻole ka lapaʻau. ʻO nā hoʻokolohua ʻē aʻe e hōʻoia i nā mālama ʻana no ka poʻe maʻi i loaʻa ʻole ka maikaʻi o ka maʻi ʻaʻai. Aia kekahi mau hoʻokolohua hoʻokolohua e hoʻāʻo i nā ala hou e hōʻoki i ka maʻi ʻaʻai mai ka hoʻi hou ʻana (hoʻi ʻana) a hōʻemi paha i nā hopena o ka mālama ʻana i ka maʻi ʻaʻai.

Ke mālama ʻia nei nā hoʻokolohua hoʻokolohua ma nā wahi he nui o ka ʻāina. Hiki ke ʻike ʻia ka ʻike e pili ana i nā hoʻokolohua hoʻokolohua e kākoʻo ʻia e NCI ma ka pūnaewele ʻimi noiʻi hoʻokolohua a NCI. Hiki ke loaʻa nā hoʻokolohua hoʻokolohua i kākoʻo ʻia e nā hui ʻē aʻe ma ka pūnaewele ClinicalTrials.gov.

Pono paha nā hoʻokolohua ukali.

ʻO kekahi o nā hoʻokolohua i hana ʻia e hōʻoia i ka maʻi ʻaʻai a i ʻole e ʻike i ke kahua o ka maʻi ʻaʻaʻa e hana hou ʻia paha. E hana hou ʻia kekahi mau hōʻike i mea e ʻike ai i ka maikaʻi o ka mālama ʻana. Hoʻoholo ʻia nā hoʻoholo e pili ana inā e hoʻomau, hoʻololi, a kū paha i ka lāʻau ʻana ma nā hopena o kēia mau hoʻāʻo.

E hoʻomau ʻia kekahi o nā hoʻokolohua mai kēlā me kēia manawa ma hope o ka pau ʻana o ka lāʻau. Hiki i nā hopena o kēia mau hoʻāʻo ke hōʻike inā ua loli ke ʻano o kāu keiki a i ʻole ua hoʻi hou ke kanesa. Kapa ʻia kēia mau hoʻāʻo i kekahi manawa nā hoʻokolohua ukali a i ʻole nā ​​loiloi.

Nā koho lapaʻau no ka mea hou Diagnosed Pōpeku Pilikia Tissue Sarcoma

Ma keia Pauku

  • ʻO nā tumo momona
  • Liposarcoma
  • Nā Tumole iwi a me ka iwi
  • Extrondreletal mesenchymal chondrosarcoma
  • Osteosarcoma Extraskeletal
  • ʻO Fibrous (Connective) nā Tumiko Tissue
  • Fibromatosis ʻano-Desmoid
  • Nā Dermatofibrosarcoma protuberans
  • Tumo myofibroblastic ʻōpala
  • ʻO Fibrosarcoma
  • Myxofibrosarcoma
  • ʻO ka sarcoma fibromyxoid haʻahaʻa haʻahaʻa
  • ʻO Sclerosing epithelioid fibrosarcoma
  • Nā Tumo Musele iwi
  • Rhabdomyosarcoma
  • Nā Tumo Muso Mele
  • Leiomyosarcoma
  • ʻO nā Tumors Fibrohistiocytic i kapa ʻia
  • Tumo fibrohistiocytic plexiform
  • Nā Tumors Pūnaewele Nerve
  • Tumo huluhulu ʻaʻano maʻi malignant
  • Tumo Triton malignant
  • ʻO Ectomesenchymoma
  • Nā Tumika Pericytic (Perivascular)
  • ʻO Hemangiopericytoma Infantile
  • Myofibromatosis Infantile
  • Nā Tumors o ka Cell Cell Unknown (kahi i ʻike ʻole ʻia ai ka tumo)
  • ʻO ka sarcoma Synovial
  • Pākuʻi ʻo Epithelioid
  • ʻO Sarvea ʻāpana palupalu ʻo Alveolar
  • E hoʻomaʻemaʻe i ka sarcoma o ka pūnaewele
  • Extraseletal myxoid chondrosarcoma
  • ʻO sarcoma Extremeeletal Ewing
  • Desmoplastic liʻiliʻi a puni ka puʻupuʻu tum Tumele
  • ʻOi nui-hōʻeha (extracranial) tumo rhabdoid
  • ʻO nā tumors cell epithelioid perivascular (PEComas)
  • Sarcoma i hoʻokaʻawale ʻia / Unclassified
  • ʻO ka sarcoma pleomorphic ponoʻole / malignant fibrous histiocytoma (kūlana kiʻekiʻe)
  • ʻO nā Tumors Kapuna Koko
  • Epithelioid hemangioendothelioma
  • Angiosarcoma o nā mea palupalu
  • ʻO Tissue Sarcoma Pōʻino Metastatic

No ka ʻike e pili ana i nā lāʻau i helu ʻia ma lalo, e ʻike i ka ʻaoʻao Overtion Option Overview

ʻO nā tumo momona

Liposarcoma

Hiki i ka mālama ʻana i ka liposarcoma ke hoʻopili i kēia mau mea:

  • ʻO ke kaha e hemo loa ai ka tumo. Inā ʻaʻole pau ka maʻi ʻaʻai, hana ʻia paha kahi ʻoki ʻelua.
  • Chemotherapy e hoʻoliʻiliʻi i ka tumer, a ukali ʻia e ke kahakaha.
  • ʻO ka radiation radiation ma mua a ma hope paha o ke kaha ʻana.

Nā Tumole iwi a me ka iwi

Extrondreletal mesenchymal chondrosarcoma

ʻO ka mālama ʻana i extrondreletal mesenchymal chondrosarcoma hiki ke hoʻopili ʻia i kēia mau mea:

  • ʻO ke kaha e hemo loa ai ka tumo. Hāʻawi ʻia ka radiation radiation ma mua a / a ma hope paha o ke kaha ʻana.
  • Chemotherapy ukali ʻia me ke ʻoki kino. Hāʻawi ʻia ʻo Chemotherapy me a i ʻole a ʻole me ka radiation radiation ma hope o ke kaha ʻana.

Osteosarcoma Extraskeletal

ʻO ka mālama ʻana i ka osteosarcoma extraskeletal hiki ke hoʻopili ʻia i kēia mau mea:

  • ʻO ke ʻoki kino e hemo loa i ka tumo, a ukali ʻia e chemotherapy.

E ʻike i ka hōʻuluʻulu ma Osteosarcoma a me Malignant Fibrous Histiocytoma o Bone Treatment no ka ʻike hou aku e pili ana i ka mālama ʻana i ka osteosarcoma.

ʻO Fibrous (Connective) nā Tumiko Tissue

Fibromatosis ʻano-Desmoid

ʻO ka mālama ʻana i ka fibromatosis ʻano desmoid hiki ke hoʻopili ʻia i kēia mau mea:

  • ʻO ke kaha e hemo loa ai ka tumo.
  • ʻO ka nānā ʻana, no nā ʻōpū ʻaʻole i hoʻoneʻe loa ʻia e ke ʻoki a i ʻole i hoʻi hou (hoʻi hou) a ʻaʻole paha e hōʻino i nā mea ola āpau.
  • Chemotherapy no nā hikoko ʻaʻole i hoʻopau loa ʻia e ke ʻoki a i ʻole ua hoʻi hou.
  • Hoʻolālā pahuhopu (sorafenib a i ʻole pazopanib).
  • Nonsteroidal anti-inflammatory drug (NSAID) therapy.
  • Pāpaʻi lāʻau antiestrogen.
  • Lapaʻau hoʻomākala.
  • ʻO kahi hoʻokolohua hoʻokolohua o ka hoʻomāka hoʻomāka ʻia me kahi mea hoʻopuka ala NOTCH.

Nā Dermatofibrosarcoma protuberans

Hiki i ka mālama ʻana i nā protuberans dermatofibrosarcoma ke hoʻopili i kēia mau mea:

  • ʻO ke kaha e hemo loa ai ka tumo ke hiki. Pākuʻi ʻia paha kēia iā Mohs.
  • ʻO ka radiation radiation ma mua a ma hope paha o ke kaha ʻana.
  • ʻO ka radiation radiation a me ka hoʻomālama ʻia (imatinib) inā ʻaʻole hiki ke hemo a hoʻi mai paha ka tumo.

Tumo myofibroblastic ʻōpala

ʻO ka mālama ʻana i ka tumo myofibroblastic ʻōpala e hoʻopili i kēia mau mea:

  • ʻO ke kaha e hemo loa ai ka tumo ke hiki.
  • ʻO Chemotherapy.
  • Pākuʻi steroid.
  • Nonsteroidal anti-inflammatory drug (NSAID) therapy.
  • Hoʻolālā pahuhopu (crizotinib a me ceritinib).

ʻO Fibrosarcoma

Fibrosarcoma Infantile

Hiki i ka mālama ʻana i ka fibrosarcoma pēpē ke hoʻopili i kēia mau mea:

  • ʻO ke ʻoki kino e hemo ai i ka tumo ke hiki, a ukali ʻia e ka nānā ʻana.
  • ʻO ke ʻoki lāʻau i ukali ʻia e chemotherapy.
  • Chemotherapy e hoʻoliʻiliʻi i ka tumer, a ukali ʻia e ke kahakaha.
  • Hoʻolālā pahuhopu (crizotinib a me larotrectinib).
  • ʻO kahi hoʻokolohua hoʻokolohua e nānā i kahi laʻana o ka tumo o ka mea maʻi no kekahi ʻano loli. ʻO ke ʻano o ka hoʻomālama ʻia e hāʻawi ʻia i ka mea maʻi e pili ana i ka ʻano o ka loli.
  • ʻO kahi hoʻokolohua hoʻokolohua o ka lāʻau hoʻomoe ʻia (larotrectinib a i ʻole entrectinib).

Fibrosarcoma makua

Hiki i ka mālama ʻana i ka fibrosarcoma makua ke hoʻopili i kēia mau mea:

  • ʻO ke kaha e hemo loa ai ka tumo ke hiki.

Myxofibrosarcoma

Hiki i ka mālama ʻana i ka myxofibrosarcoma ke hoʻopili i kēia mau mea:

  • ʻO ke kaha e hemo loa ai ka tumo.

ʻO ka sarcoma fibromyxoid haʻahaʻa haʻahaʻa

Hoʻomaʻamaʻa ʻia i ka sarcoma fibromyxoid haʻahaʻa haʻahaʻa i kēia mau mea:

  • ʻO ke kaha e hemo loa ai ka tumo.

ʻO Sclerosing epithelioid fibrosarcoma

ʻO ka mālama ʻana i ka sclerosing epithelioid fibrosarcoma hiki ke hoʻopili ʻia i kēia mau mea:

  • ʻO ke kaha e hemo loa ai ka tumo.

Nā Tumo Musele iwi

Rhabdomyosarcoma

E ʻike i ka hōʻuluʻulu e pili ana i ka mālama ʻana iā Rhabdomyosarcoma Childhood.

Nā Tumo Muso Mele

Leiomyosarcoma

Hiki i ka mālama ʻana i ka leiomyosarcoma ke hoʻopili i kēia mau mea:

  • ʻO Chemotherapy.

ʻO nā Tumors Fibrohistiocytic i kapa ʻia

Tumo fibrohistiocytic plexiform

ʻO ka mālama ʻana i ka tumo plexiform fibrohistiocytic e hoʻopili pū paha i kēia mau mea:

  • ʻO ke kaha e hemo loa ai ka tumo.

Nā Tumors Pūnaewele Nerve

Tumo huluhulu ʻaʻano maʻi malignant

ʻO ka hoʻomaʻamaʻa ʻana i ka tumer nerve peripheral nerve sheath e hoʻopili pū i kēia mau mea:

  • ʻO ke kaha e hemo loa ai ka tumo ke hiki.
  • ʻO ka radiation radiation ma mua a ma hope paha o ke kaha ʻana.
  • ʻO Chemotherapy, no nā tumors i hiki ʻole ke hemo e ke ʻoki.
  • ʻO kahi hoʻokolohua hoʻokolohua e nānā i kahi laʻana o ka tumo o ka mea maʻi no kekahi ʻano loli. ʻO ke ʻano o ka hoʻomālama ʻia e hāʻawi ʻia i ka mea maʻi e pili ana i ka ʻano o ka loli.
  • ʻO kahi hoʻokolohua hoʻokolohua o ka lāʻau hoʻomoʻa ʻia.
  • ʻO kahi hoʻokolohua hoʻokolohua o ka lāʻau i hoʻomoe ʻia (tazemetostat).

ʻAʻole maopopo inā hāʻawi ʻana i ka radiation therapy a chemotherapy paha ma hope o ke kaha ʻana e hoʻomaikaʻi ai i ka pane a ka tumo i ka lāʻau.

Tumo Triton malignant

Hiki ke mālama ʻia nā tumors Triton malignant e like me ka rhabdomyosarcomas a hoʻopili pū ʻia me ke kaha ʻana, chemotherapy, a i ʻole radiation therapy. ʻAʻole maopopo inā hāʻawi ʻana i ka radiation therapy a chemotherapy paha e hoʻomaikaʻi ai i ka pane a ka tumo i ka lāʻau.

ʻO Ectomesenchymoma

Hiki i ka mālama ʻana i ectomesenchymoma ke hoʻopili i kēia mau mea:

  • ʻOki kino.
  • ʻO Chemotherapy.
  • Lapaʻau hoʻomākala.

Nā Tumika Pericytic (Perivascular)

ʻO Hemangiopericytoma Infantile

ʻO ka mālama ʻana i ka hemangiopericytoma pēpē e hoʻopili i kēia mau mea:

  • ʻO Chemotherapy.

Myofibromatosis Infantile

Hiki i ka mālama ʻana i ka myofibromatosis pēpē ke hoʻopili i kēia mau mea:

Hoʻohui chemotherapy.

Nā Tumors o ka Cell Cell Unknown (kahi i ʻike ʻole ʻia ai ka tumo)

ʻO ka sarcoma Synovial

Hiki i ka mālama ʻana i ka sarcoma synovial ke hoʻopili i kēia mau mea:

  • ʻOki kino. Hāʻawi ʻia ka radiation radiation a me / a chemotherapy paha ma mua a ma hope paha o ke kaha ʻana.
  • ʻO Chemotherapy.
  • Hoʻoikaika radiation radiation Stereotactic no nā tumors i palahalaha aʻe i ka lung.
  • ʻO kahi hoʻokolohua hoʻokolohua o ka gen therapy.
  • ʻO kahi hoʻokolohua hoʻokolohua o ka hoʻomaʻamaʻa hormone.

Pākuʻi ʻo Epithelioid

Hoʻomaʻamaʻa ʻia ka epithelioid sarcoma i kēia mau mea:

  • Hoʻopau ke ʻoki e wehe i ka tumer inā hiki.
  • ʻO Chemotherapy.
  • ʻO ka radiation radiation ma mua a ma hope paha o ke kaha ʻana.
  • ʻO kahi hoʻokolohua hoʻokolohua o ka lāʻau i hoʻomoe ʻia (tazemetostat).

ʻO Sarvea ʻāpana palupalu ʻo Alveolar

ʻO ka mālama ʻana i ka sarcoma ʻāpana palupalu alveolar hiki i kēia mau mea:

  • ʻO ke kaha e hemo loa ai ka tumo ke hiki.
  • ʻO ka radiation radiation ma mua a ma hope paha o ke kaha ʻana, inā ʻaʻole hiki ke hoʻopau loa ʻia ka tumo e ke ʻoki.
  • Hoʻolālā pahuhopu (sunitinib).
  • ʻO kahi hoʻokolohua hoʻokolohua o ka lāʻau i hoʻomākaukau ʻia (cediranib a i ʻole sunitinib) no nā keiki.

E hoʻomaʻemaʻe i ka sarcoma o ka pūnaewele

ʻO ka mālama ʻana i ka sarcoma pūnaewele ʻino o nā mea palupalu e hoʻopili pū i ka mea aʻe:

  • Hoʻopau ke ʻoki e wehe i ka tumer inā hiki.
  • ʻO ka radiation radiation ma mua a ma hope paha o ke kaha ʻana.

Extraseletal myxoid chondrosarcoma

ʻO ka mālama ʻana i ka myxoid extraseletal chondrosarcoma hiki ke hoʻopili ʻia i kēia mau mea:

  • Hoʻopau ke ʻoki e wehe i ka tumer inā hiki.
  • Lapaʻau hoʻomākala.
  • ʻO kahi hoʻokolohua hoʻokolohua o ka lāʻau i hoʻomoe ʻia (tazemetostat).

ʻO sarcoma Extremeeletal Ewing

E ʻike i ka hōʻuluʻulu ma ʻo Ewing Sarcoma lapaʻau.

Desmoplastic liʻiliʻi a puni ka puʻupuʻu tum Tumele

ʻAʻohe mālama maʻamau no ka desmoplastic puʻupuʻu liʻiliʻi a puni. Hoʻomaopopo ʻia ka hana penei:

  • ʻO ke kaha e hemo loa ai ka tumo ke hiki.
  • Chemotherapy ukali ʻia me ke ʻoki kino.
  • Lapaʻau hoʻomākala.
  • Chemotherapy a me ka hoʻomohala hoʻomohala ʻia (temsirolimus), no nā tumors hou.

ʻOi nui-hōʻeha (extracranial) tumo rhabdoid

ʻO ka mālama ʻana i ke tumo rhabdoid keu-renal (extracranial) hiki ke hoʻopili ʻia i kēia mau mea:

  • Hoʻopau ke ʻoki e wehe i ka tumer inā hiki.
  • ʻO Chemotherapy.
  • Lapaʻau hoʻomākala.
  • ʻO kahi hoʻokolohua hoʻokolohua e nānā i kahi laʻana o ka tumo o ka mea maʻi no kekahi ʻano loli. ʻO ke ʻano o ka hoʻomālama ʻia e hāʻawi ʻia i ka mea maʻi e pili ana i ka ʻano o ka loli.
  • ʻO kahi hoʻokolohua hoʻokolohua o ka lāʻau i hoʻomoe ʻia (tazemetostat).

ʻO nā tumors cell epithelioid perivascular (PEComas)

ʻO ka mālama ʻana i nā tumors cell epithelioid perivascular e komo pū paha me kēia:

  • ʻOki kino e wehe i ka hikoko.
  • ʻO ka nānā ʻana ma hope o ke kaha ʻana.
  • ʻO ka therapy target (sirolimus), no nā tumors i loaʻa kekahi mau loli a ʻaʻole hiki ke hemo ʻia e ke kaʻe.

Sarcoma i hoʻokaʻawale ʻia / Unclassified

ʻO ka sarcoma pleomorphic ponoʻole / malignant fibrous histiocytoma (kūlana kiʻekiʻe)

ʻAʻohe mālama maʻamau no kēia mau tumors.

E ʻike i ka hōʻuluʻulu ma Osteosarcoma a me Malignant Fibrous Histiocytoma o Bone Treatment no ka ʻike e pili ana i ka mālama ʻana i ka histocytoma fibrous malignant o ka iwi.

ʻO nā Tumors Kapuna Koko

Epithelioid hemangioendothelioma

ʻO ka mālama ʻana i ka epithelioid hemangioendothelioma hiki ke hoʻopili ʻia i kēia mau mea:

  • Nānā.
  • Hoʻopau ke ʻoki e wehe i ka tumer inā hiki.
  • Immunotherapy (interferon) a me ka hoʻomōhala hoʻomōhala (thalidomide, sorafenib, pazopanib, sirolimus) no nā tumors e laha paha.
  • ʻO Chemotherapy.
  • Huina hepatectomy a me ke kuhi ʻana o ke ake i ka manawa o ka tumo i ke ake.
  • ʻO kahi hoʻokolohua hoʻokolohua o ka lāʻau i hoʻomoe ʻia (trametinib).

Angiosarcoma o nā mea palupalu

Hiki i ka mālama ʻana i angiosarcoma ke hoʻopili i kēia mau mea:

  • ʻO ke kaha e hemo loa ai ka tumo.
  • Hoʻohui ʻia o ke kaha ʻana, chemotherapy, a me radiation therapy no angiosarcomas i pālahalaha ʻia.
  • ʻO ka therapy target (bevacizumab) a me ka chemotherapy no angiosarcomas i hoʻomaka ma ke ʻano he hemangiomas pēpē.
  • ʻO kahi hoʻokolohua hoʻokolohua o ka chemotherapy me a i ʻole me ka ʻole o ka lāʻau hoʻomoe (pazopanib).
  • ʻO kahi hoʻokolohua hoʻokolohua o ka immunotherapy (nivolumab a me ipilimumab).

ʻO Tissue Sarcoma Pōʻino Metastatic

ʻO ka mālama ʻana i ka sarcoma palupalu o ka wā kamaliʻi i pālahalaha ʻia i nā ʻāpana ʻē aʻe o ke kino ma ke kuhi ʻana e komo pū paha me kēia:

  • ʻO Chemotherapy a me radiation therapy. Hiki ke hana ʻoki e wehe i nā tumors i palahalaha aʻe i ka akemāmā.
  • ʻO ka radiation radiation body Stereotactic no nā tumors i palahalaha aʻe i ka lung.

No ka mālama ʻana i nā ʻano tumo kikoʻī, e ʻike i nā koho Koina no ka ʻāpana Pahu Paʻa Pulu Tissue Sarcoma.

Nā koho lapaʻau no ka hoʻi pinepine a me ka holomua o ke kamaliʻi Tissue Sarcoma

Hoʻomaʻamaʻa ʻia i ka sarcoma palupalu o ka wā kamaliʻi e holomua a holomua paha i kēia mau mea:

  • ʻO ke ʻoki kino e hemo ai i ka maʻi ʻaʻai i hoʻi mai i kahi i hana mua ai a i pāhola paha i ka akemāmā.
  • ʻO ke ʻoki lāʻau e ukali ʻia e ka radiation radiation kūwaho a i ʻole ʻoloko, inā ʻaʻole i hāʻawi ʻia ʻia ka radiation radiation.
  • ʻO ke keʻoki e wehe i ka lima a me ka wāwae me ka maʻi ʻaʻai, inā i hāʻawi ʻia ʻia ka radiation therapy.
  • ʻO ke kaha me me ka ʻole o ka chemotherapy no ka sarcoma synovial hou.
  • ʻO Chemotherapy.
  • Hoʻolālā pahuhopu (pazopanib).
  • Immunotherapy (pembrolizumab).
  • ʻO ka radiation radiation body Stereotactic no ka maʻi ʻaʻai i pālahalaha ʻia i nā ʻāpana ʻē aʻe o ke kino, ʻo ia hoʻi ka akemāmā.
  • ʻO kahi hoʻokolohua hoʻokolohua o kahi regima chemotherapy hou me me a i ʻole me ka lāʻau i hoʻomāka ʻia (pazopanib).
  • ʻO kahi hoʻokolohua hoʻokolohua e nānā i kahi laʻana o ka tumo o ka mea maʻi no kekahi ʻano loli. ʻO ke ʻano o ka hoʻomālama ʻia e hāʻawi ʻia i ka mea maʻi e pili ana i ka ʻano o ka loli.

E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.

E aʻo hou e pili ana i ke kamaliʻi Tissue Sarcoma

No ka ʻike hou aku mai ka National Cancer Institute e pili ana i ka sarcoma palupalu o nā kamaliʻi, e ʻike i ka mea aʻe:

  • ʻAoʻao Home Tissue Sarcoma Palapala
  • Computers Tomography (CT) Scans a me ka maʻi ʻaʻai
  • Ua ʻae ʻia nā lāʻau no Sarcoma Tissue Kaha
  • ʻO nā Therapy Cancer i kau ʻia
  • MyPART - ʻO kaʻu Pediatric a me nā mākua ʻo ka Launa Tumor Rare

No ka ʻike hou aku i ka maʻi ʻaʻai kamaliʻi a me nā kumuwaiwai maʻi ʻaʻai ʻē aʻe, e ʻike i ka mea aʻe:

  • E pili ana i ka maʻi ʻaʻai
  • Nā maʻi ʻōpio
  • Huli ʻo Cure no ka hōʻole ʻana i nā maʻi ʻaʻai keiki
  • Nā hopena hope loa o ka mālama ʻana no ka maʻi ʻaʻai kamaliʻi
  • ʻO nā ʻōpio a me nā ʻōpio me ka maʻi ʻaʻai
  • Nā keiki me ka maʻi ʻaʻai: He alakaʻi no nā mākua
  • Ka maʻi ʻaʻai ma nā keiki a me nā ʻōpio
  • Ke hoʻokū nei
  • Ke kāohi nei i ka maʻi ʻaʻai
  • Nā nīnau e nīnau ai i kāu kauka e pili ana i ka maʻi ʻaʻai
  • No nā mea ola a me nā mea mālama