Nā ʻano / palupalu-iʻa-sarcoma / hoʻomanawanui / keiki-palupalu-iʻa-maʻi-pdq
Nā ʻikepili i loko
- 1 ʻO ka hoʻomaʻamaʻa palu kamaliʻi Tissue Sarcoma (®) - Mana Mana Manaʻo
- 1.1 ʻO ka ʻike ākea e pili ana i ke kamaliʻi palupalu Tissue Sarcoma
- 1.2 Nā pae o ke kamaliʻi Pōʻino Tissue Sarcoma
- 1.3 Kūleʻa a holomua hoʻi i ka wā kamaliʻi Tissue Sarcoma
- 1.4 Laulā Manaʻo Option Oponopono
- 1.5 Nā koho lapaʻau no ka mea hou Diagnosed Pōpeku Pilikia Tissue Sarcoma
- 1.6 Nā koho lapaʻau no ka hoʻi pinepine a me ka holomua o ke kamaliʻi Tissue Sarcoma
- 1.7 E aʻo hou e pili ana i ke kamaliʻi Tissue Sarcoma
ʻO ka hoʻomaʻamaʻa palu kamaliʻi Tissue Sarcoma (®) - Mana Mana Manaʻo
ʻO ka ʻike ākea e pili ana i ke kamaliʻi palupalu Tissue Sarcoma
NA MANA KUNI
- ʻO ka sarcoma palupalu kamaliʻi kahi maʻi kahi maʻi malignant (cancer) i hoʻokumu ʻia i nā huna palaha o ke kino.
- Hana ʻia kahi sarcoma palupalu i nā keiki a me nā mākua.
- Loaʻa i kekahi mau maʻi a me nā maʻi hoʻoilina hiki ke hoʻonui i ka makaʻu o ka sarcoma palupalu o nā kamaliʻi.
- ʻO ka hōʻailona maʻamau o ka sarcoma palupalu o ke kamaliʻi he puʻupuʻu ʻole a huʻi ʻole paha i nā mea palupalu o ke kino.
- Hoʻohana ʻia nā hoʻokolohua diagnostics e huki (loaʻa) a hōʻike i ka sarcoma palupalu o nā kamaliʻi.
- Inā hōʻike ʻia nā hoʻokolohua aia paha kahi sarcoma palupalu, hana ʻia kahi biopsy.
- Nui a hewahewa nā ʻano sarcomas aʻa palupalu.
- Tumele puʻupuʻu momona
- ʻO nā iwi ʻiwi a iwi
- Fibrous (hoʻohui) nā maʻi puʻupuʻu
- Nā kūpikipiki iwi ʻiwi
- Tumo mākala momona
- ʻO nā tumors fibrohistiocytic i kapa ʻia
- ʻO nā tumors sheath nerve
- Nā Tumika Pericytic (Perivascular)
- Nā Tumora o ke kumu pūnaewele ʻike ʻole ʻia
- Nā Tumors ipu koko
- Kū kekahi mau kumu i ka wānana (kahi o ke ola ʻana) a me nā koho lapaʻau.
ʻO ka sarcoma palupalu kamaliʻi kahi maʻi kahi maʻi malignant (cancer) i hoʻokumu ʻia i nā huna palaha o ke kino.
Hoʻopili, kākoʻo, a hoʻopuni nā mea palupalu o ke kino i nā ʻāpana a me nā ʻokena ʻē aʻe. Hoʻopili nā mea palupalu i kēia mau mea:
- Momona.
- Hoʻohui o ka iwi a me ka cartilage.
- ʻIli kik Frorous.
- Nā mākala.
- Nā koʻo.
- Tendons (nā kaula o nā mea i hoʻohui i nā mākala i nā iwi).
- Nāʻaʻaʻa Synovial (nāʻaʻaʻa a puni nā hono).
- Nā kīʻaha koko.
- Nā moku Lymph.
Hiki ke loaʻa kahi sarcoma palupalu i nā wahi āpau o ke kino. I nā keiki, hana pinepine nā ʻōpū i nā lima, nā wāwae, ka umauma, a me ka ʻōpū.
Hana ʻia kahi sarcoma palupalu i nā keiki a me nā mākua.
Hiki i nā sarcoma palupalu ke pane i nā ʻano ʻokoʻa i ka mālama ʻana, a loaʻa paha kahi prognosis ʻoi aku ka maikaʻi ma mua o ka sarcoma palupalu i nā mākua. (E ʻike i ka hōʻuluʻulu e pili ana i ka hoʻomaʻamaʻa pilikino pilikino Tissue Sarcoma no ka ʻike e pili ana i ka mālama ʻana i nā mākua.)
Loaʻa i kekahi mau maʻi a me nā maʻi hoʻoilina hiki ke hoʻonui i ka makaʻu o ka sarcoma palupalu o nā kamaliʻi.
ʻO nā mea āpau e hoʻonui i kou makaʻu i ka loaʻa ʻana i kahi maʻi i kapa ʻia he kumu weliweli. ʻO ka loaʻa ʻana o kahi mea pilikia ʻaʻole ia he kumu e loaʻa ʻoe i ka maʻi ʻaʻai. ʻaʻohe o nā kumu pilikia ʻaʻole ia he kumu ʻaʻole ʻoe e loaʻa i ka maʻi ʻaʻai. E kamaʻilio me kāu kauka inā makemake ʻoe e pilikia paha kāu keiki.
ʻO nā kumu pilikia no ka sarcoma palupalu o ke kamaliʻi me ka loaʻa ʻana o nā maʻi hoʻoilina e hiki mai ana:
- Li-Fraumeni maʻi.
- Polyposis adenomatous ʻohana (FAP).
- Loli ke ʻano RB1.
- SMARCB1 (INI1) loli hoʻololi.
- ʻO Neurofibromatosis ʻano 1 (NF1).
- Werner maʻi maʻi.
- Maʻi maʻi maʻi tuberous.
- Adenosine deaminase-nele loa hui pū kekahi immunodeficiency.
ʻO nā kumu pilikia ʻē aʻe e pili pū me kēia:
- Ka hana i hala me ka radiation radiation.
- Loaʻa iā AIDS (loaʻa ka maʻi pale maʻi pale) a me ka maʻi ʻaʻai Epstein-Barr i ka manawa like.
ʻO ka hōʻailona maʻamau o ka sarcoma palupalu o ke kamaliʻi he puʻupuʻu ʻole a huʻi ʻole paha i nā mea palupalu o ke kino.
Hiki ke ʻike ʻia kahi sarcoma ma ke ʻano he puʻupuʻu ʻole ma lalo o ka ʻili, pinepine ma ka lima, ka wāwae, ka umauma, a me ka ʻōpū. ʻAʻohe paha hōʻailona a hōʻailona paha i ka mua. Ke piʻi a nui aʻe ka sarcoma a kaomi ma luna o nā mea kokoke, nā aʻa, nā mākala, a i ʻole nā kīʻaha koko, hana ʻia nā hōʻailona a i ʻole nā hōʻailona, e like me ka ʻeha a nāwaliwali paha.
ʻO nā kumu ʻē aʻe paha ke kumu i nā hōʻailona like a me nā ʻōuli. E nīnau me ke kauka o kāu keiki inā loaʻa kēia pilikia i kāu keiki.
Hoʻohana ʻia nā hoʻokolohua diagnostics e huki (loaʻa) a hōʻike i ka sarcoma palupalu o nā kamaliʻi.
Hiki ke hoʻohana ʻia nā hoʻāʻo a me nā kaʻina hana aʻe:
- ʻO ka hoʻāʻo kino a me ka mōʻaukala: kahi hōʻike o ke kino e nānā i nā hōʻailona laulā o ke olakino, e like me ka nānā ʻana i nā hōʻailona o ka maʻi, e like me nā puʻupuʻu a i ʻole nā mea ʻē aʻe e ʻano ʻē. E lawe ʻia kahi moʻolelo o nā ʻano olakino o ka mea maʻi a me nā maʻi i hala a me nā mālama ʻana.
- ʻO nā kukuna X: kahi x-ray kahi ʻano kukuna ikehu e hiki ke hele ma waena o ke kino i ke kiʻi ʻoniʻoni, e hana ana i nā kiʻi o nā wahi i loko o ke kino.
- MRI (kiʻi resonance ʻume mākenēki): kahi hana e hoʻohana ai i ka magnet, nā nalu lekiō, a me kahi kamepiula e hana i nā kiʻi kikoʻī o nā wahi o ke kino, e like me ka umauma, ʻōpū, nā lima, a me nā wāwae. Kāhea ʻia kēia kaʻina hana he kiʻi nukelea kiʻi resonance (NMRI).
- CT scan (CAT scan): Kahi hana e hana ai i ka moʻo o nā kiʻi kikoʻī o nā wahi i loko o ke kino, e like me ka umauma a i ʻole ka ʻōpū, i lawe ʻia mai nā kihi ʻokoʻa. Hana ʻia nā kiʻi e kahi kamepiula i hoʻopili ʻia i kahi mīkini x-ray. Hoʻokomo ʻia paha ke kala i loko o ke aa a i ʻole ale ʻia e kōkua i nā ʻōpū a i ʻole nā kino i hōʻike hou aku me ka maopopo. Kāhea ʻia kēia kaʻina hana he tomography i helu ʻia, kamepiula tomography, a i ʻole he tomography axial computerized.
- ʻO ka hoʻāʻo ʻana o Ultrasound: kahi kaʻina hana e kipaku ʻia ai nā nalu kani ikaika (ultrasound) mai nā aʻa a i ʻole nā ʻola a hana i nā leo. Hoʻokumu nā leo i kahi kiʻi o nā kino o ke kino i kapa ʻia he sonogram. Hiki ke paʻi ʻia ke kiʻi e nānā ma hope.
Inā hōʻike ʻia nā hoʻokolohua aia paha kahi sarcoma palupalu, hana ʻia kahi biopsy.
Pili ke ʻano o ka biopsy, i kekahi ʻāpana, i ka nui o ka nui a inā kokoke paha i ka ʻili o ka ʻili a i ʻole hohonu i kaʻiʻo. Hoʻohana maʻamau ʻia kekahi o nā ʻano biopsies:
- ʻO ka biopsy o ka nila nui: ʻO ka hemo ʻana o nā kiko me ka hoʻohana ʻana i ka nila nui. Lawe ʻia nā laʻana ʻōnaehana lehulehu. Hiki ke alakaʻi ʻia kēia kaʻina hana me ka hoʻohana ʻana i ka ultrasound, CT scan, a i ʻole MRI.
- ʻO Biopsy Incisional: ka hemo ʻana o kahi ʻāpana o kahi puʻupuʻu a i ʻole kahi laʻana o nā meaola.
- ʻO Biopsy kūikawā: ʻO ka hemo ʻana o kahi puʻupuʻu āpau a i ʻole kahi o nā kiko i kū ʻole i ka nānā maʻamau. ʻIke kahi pathologist i ke kiko ma lalo o kahi microscope e nānā no nā hunaola maʻi ʻaʻai. Hiki ke hoʻohana ʻia kahi biopsy kūikawā e hemo loa i nā tumors liʻiliʻi e kokoke ana i ka ʻili. ʻAʻole hoʻohana pinepine ʻia kēia ʻano biopsy no ka mea e mau ana nā hunaola maʻi ʻaʻai ma hope o ka biopsy. Inā mau nā maʻi ʻaʻai, hoʻi mai paha ka maʻi ʻaʻai a pāhola paha i nā ʻāpana ʻē aʻe o ke kino.
Hana ʻia kahi MRI o ka tumo ma mua o ka biopsy kūikawā. Hana ʻia kēia e hōʻike i kahi i hoʻokumu ʻia ai ka tumo kumu a hoʻohana ʻia paha e alakaʻi i ke ʻoki ʻana a i ʻole ka radiation radiation.
Inā hiki, ʻo ke kauka nāna e hoʻoneʻe i kekahi tumo i loaʻa e komo pū i ka hoʻolālā ʻana i ka biopsy. ʻO ke kau ʻana o nā nila a i ʻole nā ʻokiʻoki no ka biopsy hiki ke hoʻopili inā hiki ke hoʻoneʻe ʻia ka tumo holoʻokoʻa i ka wā o ke ʻoki hope.
E hoʻolālā i ka lapaʻau maikaʻi loa, pono ka laʻana o nā kiko i wehe ʻia i ka wā o ka biopsy e lawa pono e ʻike i ke ʻano o ka sarcoma aʻa palupalu a hana i nā hoʻokolohua ʻē aʻe. Lawe ʻia nā laʻana o nā kele mai nā tumo mua, nā pūnana lymph, a me nā wahi ʻē aʻe i loaʻa i nā hunaola maʻi ʻaʻai. ʻIke kahi pathologist i ke kiko ma lalo o kahi microscope e nānā no nā hunaola maʻi ʻaʻai a e ʻike i ke ʻano a me ka papa o ka tumo. Aia ka papa o ka tumo i ka nānā ʻana o nā hunaola maʻi ʻino ma lalo o kahi microscope a me ka wikiwiki o ka hoʻokaʻawale ʻana o nā hunaola. ʻO nā tumors kiʻekiʻe-papa a me ka papa waena e ulu a laha wikiwiki aʻe ma mua o nā tumors haʻahaʻa.
Ma muli o ka paʻakikī o ka diagnose o ka sarcoma palupalu, pono e nānā ʻia ka laʻana o ke kiko e ka mea pathologist i loaʻa ka ʻike i ka diagnose sarcoma nā mea palupalu.
Hoʻokahi a ʻoi paha o nā hoʻokolohua keʻena hoʻokolohua e hana ʻia e hoʻopaʻa i nā kiko kiko.
- ʻImi Molecular: kahi hoʻokolohua hoʻokolohua e nānā ai no kekahi mau genes, nā protein, a i ʻole nā molekika ʻē aʻe i kahi laʻana o nā kiko, ke koko, a i ʻole ke kahe o ke kino. Hana ʻia kahi hoʻokolohua molekole me nā kaʻina hana ʻē aʻe, e like me biopsies, e kōkua i ke kuhi ʻana i kekahi ʻano maʻi ʻaʻai. Nānā nā hoʻokolohua Molecular no kekahi mau loli a i ʻole chromosome e loli i kekahi mau sarcomas palupalu.
- Hōʻike hoʻohuli huli - polymerase chain reaction (RT – PCR) hōʻike: kahi hoʻokolohua hoʻokolohua kahi e ana ʻia ai ka nui o kahi genetical genetical i kapa ʻia mRNA i hana ʻia e kekahi gen. Hoʻohana ʻia kahi enzyme i kapa ʻia ʻo transcriptase huli e hoʻololi i kahi ʻāpana kikoʻī o RNA i ʻāpana like o DNA, hiki ke hoʻonui ʻia (i hana ʻia i nā helu he nui) e kekahi enzyme i kapa ʻia ʻo DNA polymerase. Kōkua nā kope DNA i hoʻonui ʻia e haʻi inā e hana ʻia kahi mRNA kikoʻī e kahi ʻāpana. RT – PCR hiki ke hoʻohana e nānā i ka hoʻoulu ʻana o kekahi mau ʻāpana e hōʻike ai i ke kū ʻana o nā hunaola maʻi ʻaʻai. Hoʻohana ʻia kēia hoʻokolohua e nānā ai i kekahi mau loli i kahi moʻokūʻauhau a i ʻole chromosome, i hiki ke kōkua i ke kuhi ʻana i ka maʻi ʻaʻai.
- Nānā Cytogenetic: kahi hoʻokolohua hoʻokolohua kahi e helu ai nā chromosome o nā hunaola i kahi hāpana o kaʻiʻo tumora i helu ʻia a nānā ʻia no nā loli, e like me ka haki, nalowale, hoʻoponopono hou ʻia, a i ʻole nā chromosome keu. ʻO nā loli i kekahi mau chromosome he hōʻailona ia o ka maʻi ʻaʻai. Hoʻohana ʻia ka hoʻoponopono Cytogenetic e kōkua i ke kuhi ʻana i ka maʻi ʻaʻai, e hoʻolālā i ka lāʻau ʻana, a i ʻole e ʻike i ke ʻano o ka maikaʻi o ka mālama ʻana. ʻO ka fluorescence in situ hybridization (FISH) kahi ʻano o ka hoʻopili ʻana cytogenetic.
- Immunocytochemistry: kahi hoʻokolohua hoʻokolohua e hoʻohana ai i nā anti -antibodies e nānā ai no kekahi antigens (markers) i kahi laʻana o nā hunaola o ka mea maʻi. Hoʻopili pinepine ʻia nā mea ʻino i kekahi enzyme a i ʻole ka waihoʻoluʻu fluorescent. Ma hope o ka hoʻopili ʻana o nā mea ʻume i ka antigen i ka laʻana o nā hunaola o ka hoʻomanawanui, e hoʻoulu ʻia ka enzyme a i ʻole ke kala, a laila ʻike ʻia ka antigen ma lalo o kahi microscope. Hiki ke hoʻohana ʻia kēia ʻano hoʻokolohua e haʻi i ka ʻokoʻa ma waena o nā ʻano sarcoma pahee palupalu.
- ʻO ka microscopy mālamalama a me ka uila: ʻO kahi hoʻokolohua keʻena hoʻokolohua kahi e ʻike ʻia ai nā hunaola ma kahi hāpana o ke kiko ma lalo o nā microscope mana a kiʻekiʻe e nānā ai i kekahi mau hoʻololi i nā hunaola.
Nui a hewahewa nā ʻano sarcomas aʻa palupalu.
ʻO nā hunaola o kēlā me kēia ʻano sarcoma ke nānā ʻokoʻa ma lalo o kahi microscope. Hoʻohui ʻia nā tumors palupalu ma muli o ke ʻano o ka puʻupuʻu palupalu kahi i hana mua ai lākou.
ʻO kēia hōʻuluʻulu e pili ana i nā ʻano o nā sarcoma aʻa palupalu:
Tumele puʻupuʻu momona
Liposarcoma. He maʻi ʻaʻai kēia o nā hunaola momona. Hoʻokumu pinepine ka Liposarcoma i ka momona momona ma lalo o ka ʻili. I nā keiki a me nā ʻōpio, he haʻahaʻa haʻahaʻa ka liposarcoma (e ulu a hohola mālie paha). Aia kekahi mau ʻano liposarcoma, e like me:
- ʻO Myxoid liposarcoma. ʻO kēia ka maʻi ʻaʻai haʻahaʻa haʻahaʻa e pane maikaʻi i ka mālama ʻana.
- Liposarcoma Pleomorphic. ʻO kēia ka maʻamau he maʻi ʻaʻai nui kiʻekiʻe ka liʻiliʻi e pane maikaʻi i ka mālama ʻana.
ʻO nā iwi ʻiwi a iwi
ʻO nā iwi iwi a me ka iwi he hui o nā iwi iwi a me nā aʻa o ke kino. ʻO nā iwi ʻiwi a me ka iwi i nā ʻano aʻe:
- Extrondreletal mesenchymal chondrosarcoma. Hoʻopili pinepine kēia ʻano iwi a me nā tumo cartilage i nā ʻōpio makua a kū i ke poʻo a me ka ʻāʻī.
- Osteosarcoma Extraskeletal. Kākaʻikahi loa kēia ʻano iwi a me nā tumo cartilage i nā keiki a me nā ʻōpio. E hoʻi paha ia ma hope o ka hoʻomaʻamaʻa a pāhola paha i nā ake māmā.
Fibrous (hoʻohui) nā maʻi puʻupuʻu
ʻO nā puʻupuʻu fibrous (hoʻohui) nā ʻano aʻe:
- Desmoid-type fibromatosis (i kapa ʻia ʻo desmoid tumor a i ʻole fibromatosis agresive). He pae haʻahaʻa kēia fibrousʻaʻaʻaʻaʻaʻa (e ulu mālie paha). E hoʻi paha ia i nā pūnaewele kokoke akā ʻaʻole hoʻolaha pinepine i nā ʻāpana mamao o ke kino. I kekahi manawa hiki i ka desibrid-type fibromatosis ke hoʻōki i ka ulu ʻana no kahi manawa lōʻihi. Kākaʻikahi, hiki ke nalo ke tumo me ka mālama ʻole ʻia.
Hiki i nā tumo Desmoid i kekahi manawa i nā keiki me nā loli o ka ʻāpana APC. Hiki i nā loli i kēia ʻenekua ke kumu i ka polyposis adenomatous ʻohana (FAP). He kūlana hoʻoilina ʻo FAP (hoʻoili ʻia mai nā mākua a hiki i nā pua) kahi i nui ai nā polyps (nā ulu ma nā membrane mucous) e kū ana ma nā paia o ka kolone a me ka pā. Kūkākūkā genetic (kahi kūkākūkā me kahi loea i hoʻomaʻamaʻa e pili ana i nā maʻi hoʻoilina a me nā koho no ka hoʻāʻo ʻana i ka ʻaoʻao) pono paha.
- Nā Dermatofibrosarcoma protuberans. He tumo kēia o nā papa hohonu o ka ʻili e hana pinepine ʻia i ka pahu, nā lima, a me nā wāwae. Loaʻa i nā hunaola o kēia tumo kahi loli kūlohelohe i kapa ʻia he translocation (ʻāpana o ka kola COL1A1 hoʻololi i nā wahi me ka ʻāpana o ka ʻāpana PDGFRB). No ke kuhi ʻana i nā protuberans dermatofibrosarcoma, nānā ʻia nā hunaola tumora no kēia loli. ʻAʻole pālahalaha nā protuberans Dermatofibrosarcoma i nā lymph node a i ʻole nā ʻāpana ʻē aʻe o ke kino.
- Tumo myofibroblastic ʻōpala. Hana ʻia kēia maʻi ʻaʻa o nā hunaola pūnana, nā pūnaewele hoʻopili hoʻopili, a me kekahi o nā hunaola pale. Kū i loko o nā keiki a me nā ʻōpio. Hoʻokumu pinepine ia i nā mea palupalu, nā mumū, nā palapū, a me ka umauma. Hoʻi pinepine ia ma hope o ka lapaʻau ʻana akā ʻaʻole pāhola iki i nā wahi mamao o ke kino. Ua loaʻa kahi loli kūpili ma kahi o ka hapalua o kēia mau tumors.
ʻO Fibrosarcoma.
ʻElua ʻano fibrosarcoma i nā keiki a me nā ʻōpio:
- ʻO fibrosarcoma Infantile (i kapa ʻia hoʻi ʻo fibrosarcoma congenital). Kū pinepine kēia ʻano fibrosarcoma i nā keiki mai ka makahiki 1 a ʻoi paha a ʻike ʻia paha i kahi hōʻike ultrasound prenatal. Ke ulu wikiwiki nei kēia tumo a nui pinepine i ka hōʻailona. ʻAʻole pāhola iki i nā ʻāpana mamao o ke kino. Loaʻa i nā hunaola o kēia tumo kahi loli kūlohelohe i kapa ʻia he translocation (ʻāpana o kahi chromosome hoʻololi i nā wahi me kahi ʻāpana o kahi chromosome ʻē aʻe). No ke kuhi ʻana i ka fibrosarcoma pēpē, nānā ʻia nā hunaola tumora no kēia loli. Ua ʻike ʻia kekahi tumo like i nā keiki makua, akā ʻaʻohe ona translocation e ʻike pinepine ʻia i nā keiki liʻiliʻi.
- Fibrosarcoma makua. ʻO kēia ke ʻano o ka fibrosarcoma i loaʻa i nā mākua. ʻAʻohe o nā hunaola o kēia tumo ka loli i loaʻa i ka fibrosarcoma pēpē. (E ʻike i ka hōʻuluʻulu e pili ana i ka hoʻomaʻamaʻa pilikino Tissue Sarcoma no ka ʻike hou aku.)
- Myxofibrosarcoma. ʻO kēia kahi tumo fibrous kikoʻī liʻiliʻi e hana pinepine ʻia i nā keiki ma mua o ka poʻe mākua.
- ʻO ka sarcoma fibromyxoid haʻahaʻa haʻahaʻa. ʻO kēia kahi tumo ulu lohi e ulu hohonu ana i nā lima a i ʻole nā wāwae a ʻo ka hapanui ka hopena i nā ʻōpio a me nā mākua waena. Hiki ke hoʻi i ka tumo i mau makahiki he nui ma hope o ka hoʻomaʻamaʻa ʻana a hoʻolaha ʻia i nā akemāmā a me ka uhi o ka paia umauma. Pono ka mālama ʻana i ke ola holoʻokoʻa.
- ʻO Sclerosing epithelioid fibrosarcoma. ʻO kēia kahi tumo kikoola fibrous ulu ulu wikiwiki. Hiki iā ia ke hoʻi a hoʻolaha i nā ʻāpana ʻē aʻe o ke kino i mau makahiki ma hope o ka mālama ʻana. Pono ka ukali wā lōʻihi.
Nā kūpikipiki iwi ʻiwi
Hoʻopili ka mākala iwi i nā iwi a kōkua i ke kino e neʻe.
- Rhabdomyosarcoma. ʻO Rhabdomyosarcoma ka sarcoma palupalu o ka wā kamaliʻi maʻamau i nā keiki 14 mau makahiki a ʻoi. (E ʻike i ka hōʻuluʻulu e pili ana i ka mālama ʻana iā Rhabdomyosarcoma Childhood no ka ʻike hou aku.)
Tumo mākala momona
Hoʻomaʻamaʻa nā mākala mānoanoa i ka loko o nā kīʻaha koko a hollow i nā mea pono o loko e like me ka ʻōpū, nā ʻōpū, loko, a me ka pūpū.
- Leiomyosarcoma. Ua hoʻopili ʻia kēia tumo puʻupuʻu me ka maʻi Epstein-Barr i nā keiki i loaʻa i ka maʻi HIV a me ka maʻi AIDS. Leiomyosarcoma hiki ke hana ma ke ʻano he maʻi ʻaʻai ʻelua i nā mea i pakele o retinoblastoma hoʻoilina, i kekahi manawa i mau makahiki he nui ma hope o ka lapaʻau mua no retinoblastoma.
ʻO nā tumors fibrohistiocytic i kapa ʻia
- Tumo fibrohistiocytic plexiform. ʻO kēia kahi tumo laha ʻole e hoʻopili pinepine i nā keiki a me nā ʻōpio ʻōpio. Hoʻomaka ka hoʻomaka ʻana o ka tumo ma ke ʻano he ulu ʻeha ʻole ma lalo o ka ʻili ma ka lima, lima a lima paha. ʻAʻole pāhola paha ia i nā lymph node kokoke a i ʻole i nā akemāmā.
ʻO nā tumors sheath nerve
Hana ʻia ka uhi nerve i nā pale pale o ka myelin e uhi ana i nā hunaola nerve ʻaʻole ia he ʻāpana o ka lolo a i ʻole ka iwi kuamoo. Loaʻa i nā tumors sheath nerve nā ʻano aʻe:
- Tumo huluhulu ʻaʻano maʻi malignant. ʻO kekahi mau keiki i loaʻa i kahi tumory nerve peripheral nerve malignant he ʻano laha ʻole i kapa ʻia neurofibromatosis type 1 (NF1). Hiki i kēia tumo he papa haʻahaʻa a he papa kiʻekiʻe paha.
- Tumo Triton malignant . ʻO kēia nā tumors e ulu wikiwiki ana i nā manawa pinepine i nā keiki me NF1.
- ʻO Ectomesenchymoma. He tumo ulu ulu kēia e ulu nui ana i nā keiki. Hiki ke hana ʻo Ectomesenchymomas i ka maka o ka maka, ʻōpū, nā lima, a me nā wāwae.
Nā Tumika Pericytic (Perivascular)
Hana ʻia nā tumo Pericytic i loko o nā hunaola e hoʻopuni i nā kīʻaha koko. Loaʻa nā tumors Pericytic i kēia mau ʻano:
- ʻO Myopericytoma. ʻO ka hemangiopericytoma infantile kahi ʻano o myopericytoma. ʻO nā keiki ma mua o 1 mau makahiki i ka manawa o ka hōʻailona hiki ke loaʻa i kahi prognosis ʻoi aku ka maikaʻi. I nā mea maʻi ma mua o 1 makahiki, ʻoi aku ka palahalaha ʻana o ka hemangiopericytoma pēpē i nā ʻāpana ʻē aʻe o ke kino, e like me nā lymph node a me nā akemāmā.
- Myofibromatosis Infantile. ʻO myofibromatosis Infantile kekahi ʻano o myopericytoma. He tumo fibrous ia e hana pinepine i nā makahiki 2 mua o ke ola. Aia paha kekahi nodule ma lalo o ka ʻili, ma ke poʻo a me ka ʻāʻī (myofibroma), a i ʻole he mau nodule i ka ʻili, nā mākala, a me nā iwi (myofibromatosis). I nā mea maʻi me ka myofibromatosis pēpē, hoʻolaha paha ka maʻi ʻaʻai i nā meaola. Hele paha kēia mau tumors me ka ʻole o ka lapaʻau.
Nā Tumora o ke kumu pūnaewele ʻike ʻole ʻia
ʻO nā tumors o ke kumu ʻole ʻike ʻole ʻia (ʻo ke ʻano o ke kele i ʻike ʻole ʻia ka tumo i ʻike ʻole ʻia) e komo pū me nā ʻano aʻe:
- ʻO ka sarcoma Synovial. ʻO ka sarcoma Synovial kahi ʻano maʻamau o ka sarcoma palupalu i nā keiki a me nā ʻōpio. Hana ʻia ia i nā pūnaewele a puni nā hono i nā lima a i ʻole nā wāwae, akā hana ʻia paha i ke kumu, poʻo, a ʻāʻī paha. Loaʻa i nā hunaola o kēia tumo kahi loli kūlohelohe i kapa ʻia he translocation (ʻāpana o kahi chromosome hoʻololi i nā wahi me kahi ʻāpana o kahi chromosome ʻē aʻe). ʻOi aku ka makaʻu o nā tumors ʻoi aku ka nui o ka hoʻolaha ʻana i nā ʻāpana ʻē aʻe o ke kino, e like me nā akemāmā. ʻO nā keiki ma mua o 10 mau makahiki nona ka ʻōpuʻu he 5 kenimika a ʻoi iki paha a ua hana i nā lima a i nā wāwae i kahi wānana maikaʻi.
- Pākuʻi ʻo Epithelioid. He sarcoma laha ʻole kēia e hoʻomaka pinepine i ka hohonu i loko o nā mea palupalu ma ke ʻano he ulu lohi a paʻa paʻa a hohola paha i nā lymph node. Inā hana ʻia ka maʻi ʻaʻai ma nā lima, nā wāwae, a me nā ʻūhā paha, e hana ʻia kahi biopsy lymph node sentinel e nānā ai no ka maʻi ʻaʻai i nā lymph node.
- ʻO Sarvea ʻāpana palupalu ʻo Alveolar. He tumo kākaʻikahi kēia o nā mea kākoʻo palupalu e hoʻopili a hoʻopuni i nā ʻokena a me nā mea ʻē aʻe. Hana ʻia ia i nā lima a me nā wāwae akā hiki ke hana i nā kinona o ka waha, nā ā, a me ka maka. E ulu mālie paha ia a pālahalaha pinepine i nā ʻāpana ʻē aʻe o ke kino. Loaʻa i kahi ʻalalā ʻāpana ʻo Alveolar palupalu i kahi wānana ʻoi aku ke 5 centimika a ʻoi aku paha ka liʻiliʻi a i ʻole ke hoʻopau loa ʻia ka tumo e ke ʻoki. Loaʻa i nā hunaola o kēia tumo kahi loli kūpili i kapa ʻia he translocation (ʻāpana o ka moʻokūʻauhau ASSPL e hoʻololi i nā wahi me ka ʻāpana o ka ʻāpana TFE3). No ke kuhi ʻana i ka sarcoma ʻāpana palupalu alveolar, nānā ʻia nā hunaola tumora no kēia loli.
- E hoʻomaʻemaʻe i ka sarcoma o ka pūnaewele. ʻO kēia kahi tumo ulu ulu palupalu e hoʻomaka i kahi kahena (uaua, fibrous, kaula e like me ke kaula e hoʻopili i nā mākala i ka iwi a i kekahi ʻāpana o ke kino). Hiki ke hana maʻamau i ka sarcoma pūnaewele ma nā kiko hohonu o ka wāwae, ka heʻe wāwae, a me nā kuʻekuʻe wāwae. Hoʻolahalaha paha ia i nā kiko lymph kokoke. Loaʻa i nā hunaola o kēia tumo kahi loli kūpili i kapa ʻia he translocation (ʻāpana o ka ʻāpana EWSR1 kuapo i nā wahi me ka ʻāpana o ka ʻāpana ATF1 a i ʻole CREB1). No ke kuhi ʻana i ka sarcoma o ka ʻili maʻemaʻe o nā mea palupalu, nānā ʻia nā hunaola tumora no kēia loli.
- Extraseletal myxoid chondrosarcoma. Hiki ke ʻano o kēia ʻano sarcoma palupalu i nā keiki a me nā ʻōpio. Ma ka holo ʻana o ka manawa, hele a pālahalaha aku ia i nā ʻāpana ʻē aʻe o ke kino, me nā lymph node a me nā akemāmā. Hiki ke hoʻi i ka tumo i mau makahiki ma hope o ka lapaʻau ʻana.
- ʻO sarcoma Extremeeletal Ewing. E ʻike i ka hōʻuluʻulu ma Ewing Sarcoma Hana no ka ʻike.
- Desmoplastic liʻiliʻi a puni ka puʻupuʻu tum Tumele. Hoʻokumu pinepine kēia tumo i ka peritoneum i loko o ka ʻōpū, pelvis, a me / a i ʻole ka peritoneum i loko o ka scrotum, akā e hana paha ia i ka puʻupaʻa a i ʻole nā mea paʻa ʻē aʻe. Hiki i nā tumors liʻiliʻi ke hana i ka peritoneum. Hiki i ka Desmoplastic puʻupuʻu liʻiliʻi a puni ke kele ke laha i nā akemāmā a me nā ʻāpana ʻē aʻe o ke kino. Loaʻa i nā hunaola o kēia tumo kahi loli kūlohelohe i kapa ʻia he translocation (ʻāpana o kahi chromosome hoʻololi i nā wahi me kahi ʻāpana o kahi chromosome ʻē aʻe). No ke kuhikuhi ʻana i nā tumm liʻiliʻi liʻiliʻi a puni desmoplastic, nānā ʻia nā hunaola tumo no kēia loli.
- ʻO ke tumo rhabdoid keu-renal (extracranial). ʻO kēia tumo e ulu nei me ka wikiwiki e hana i nā mea palupalu e like me ke ake a me ka ʻai. Hana ʻia ia i nā keiki ʻōpio, me nā keiki hānau hou, akā hiki ke hana ʻia i nā keiki nui a me nā mākua. Hiki ke hoʻopili ʻia nā tumors Rhabdoid i kahi loli i kahi ʻenemi suppressor tumor i kapa ʻia ʻo SMARCB1. Hana kēia ʻano gen i kahi protein i kōkua i ka mālama ʻana i ka ulu ʻana o ka cell. Hiki ke hoʻoilina ʻia nā hoʻololi i ka moʻokūʻauhau SMARCB1. Kūkākūkā genetic (kahi kūkākūkā me kahi loea i aʻo ʻia e pili ana i nā maʻi hoʻoilina a me kahi pono e pono ai no ka hoʻāʻo ʻana i nā ʻaoʻao) pono paha.
- ʻO nā tumors cell epithelioid perivascular (PEComas). Kū paha ʻo Benign PEComas i nā keiki me kahi ʻano hoʻoilina i kapa ʻia ʻo tuberous sclerosis. Kū lākou i loko o ka ʻōpū, ʻōpū, akemāmā, a me nā genitourinary. Piʻi mālie nā PEComas a ʻaʻole paha hoʻolaha ka hapa nui.
- ʻO sarcoma i hoʻokaʻawale ʻole ʻia. Kū pinepine kēia mau tumors i nā iwi a i ʻole nā mākala e pili ana i nā iwi a kōkua i ka neʻe ʻana o ke kino.
- ʻO ka sarcoma pleomorphic pono ʻole / histiocytoma fibrous malignant (kūlana kiʻekiʻe). Hiki ke hana i kēia ʻano tumo palupalu i nā ʻāpana o ke kino kahi i loaʻa ai i nā mea maʻi i ka radiation radiation i ka wā i hala, a i ʻole he maʻi ʻaʻai ʻelua i nā keiki me retinoblastoma. Hana ʻia ka tumo i nā lima a i ʻole nā wāwae a pāhola paha i nā ʻāpana ʻē aʻe o ke kino. (E nānā i ka hōʻuluʻulu ma Osteosarcoma a me Malignant Fibrous Histiocytoma o Bone Treatment no ka ʻike e pili ana i ka histiocytoma fibrous malignant o ka iwi.)
Nā Tumors ipu koko
ʻO nā tumors moku koko nā ʻano aʻe:
- Epithelioid hemangioendothelioma. Hiki i nā Epithelioid hemangioendotheliomas ke hana i nā keiki akā ʻike pinepine ʻia i nā mākua ma waena o 30 a 50 mau makahiki. Kū pinepine lākou i ke ake, ka akemāmā, a iwi paha. E ulu wikiwiki ana paha lākou a ulu lohi paha. Ma kahi o ka hapakolu o nā hihia, pāhola koke ka tumo i nā ʻāpana ʻē aʻe o ke kino. (E ʻike i ka hōʻuluʻulu e pili ana i ka hoʻomaʻamaʻa ʻana o ka Tumua Vascular Tumors no ka ʻike hou aku.)
- Angiosarcoma o ka palupalu. ʻO Angiosarcoma o nā mea palupalu kahi tumo ulu wikiwiki e hana i nā kīʻaha koko a i ʻole nā kīʻaha lymph i kēlā me kēia ʻāpana o ke kino. Aia ka hapanui o nā angiosarcomas ma lalo a i ʻole ma lalo o ka ʻili. ʻO ka poʻe i loko o nā mea palupalu hohonu e hiki ke hana i ke akepaʻa, ka palapū, a i ʻole ka akemāmā. He kākaʻikahi loa lākou i nā keiki, ʻoi aku ka nui o nā tumo i ka ʻili a i ke akepaʻa i kekahi manawa. Kākaʻikahi, hiki i ka hemangioma pēpē ke lilo i angiosarcoma o nā mea palupalu. (E ʻike i ka hōʻuluʻulu e pili ana i ka hoʻomaʻamaʻa ʻana o ka Tumua Vascular Tumors no ka ʻike hou aku.)
E ʻike i nā hōʻuluʻulu aʻe e pili ana i ka ʻike e pili ana i nā ʻano sarcoma puʻupuʻu palu ʻaʻole i hoʻokomo ʻia i kēia hōʻuluʻulu manaʻo:
- ʻO ka mālama ʻana iā Rhabdomyosarcoma Childhood
- Hoʻomaʻo Ewing Sarcoma
- ʻO Osteosarcoma a me Malignant Fibrous Histiocytoma o ka mālama ʻana i ka iwi
- Nā maʻi ʻōlohelohe ʻole o ka mālama ʻana i ke kamaliʻi (ʻōpū stromal gastrointestinal)
Kū kekahi mau kumu i ka wānana (kahi o ke ola ʻana) a me nā koho lapaʻau.
ʻO ka wānana (loaʻa o ke ola) a me nā koho lapaʻau e pili i kēia:
- ʻO ka ʻāpana o ke kino kahi i hana mua ai ka tumo.
- Ka nui a me ka papa o ka tumo.
- Ke ʻano o ka sarcoma puʻupuʻu palupalu.
- Pehea ka hohonu o ka tumo ma lalo o ka ʻili.
- Inā ua pālahalaha ka tumo i nā wahi ʻē aʻe o ke kino a kahi i pālahalaha ai.
- ʻO ka nui o nā tumo i koe ma hope o ke kaha ʻana e wehe iā ia.
- Inā hoʻohana ʻia ka radiation radiation e mālama i ka tumo.
- Inā ua hōʻoia wale ʻia ka maʻi ʻaʻai a i ʻole ua hoʻi hou (hoʻi.
Nā pae o ke kamaliʻi Pōʻino Tissue Sarcoma
NA MANA KUNI
- Ma hope o ka ʻike ʻia ʻana o kahi sarcoma palupalu o ka wā kamaliʻi, hana ʻia nā hoʻokolohua e ʻike inā ua hoʻolaha ʻia nā hunaola maʻi ʻaʻai i nā ʻāpana ʻē aʻe o ke kino.
- ʻEkolu ala e hoʻolaha ai ka maʻi ʻaʻai i loko o ke kino.
- E laha paha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i nā ʻāpana ʻē aʻe o ke kino.
Ma hope o ka ʻike ʻia ʻana o kahi sarcoma palupalu o ka wā kamaliʻi, hana ʻia nā hoʻokolohua e ʻike inā ua hoʻolaha ʻia nā hunaola maʻi ʻaʻai i nā ʻāpana ʻē aʻe o ke kino.
ʻO ke kaʻina hana e ʻike inā ua pālahalaha ka maʻi ʻaʻai i loko o ka mū palupalu a i ʻole nā ʻāpana ʻē aʻe o ke kino i kapa ʻia he staging ʻAʻohe ʻōnaehana hoʻonohonoho maʻamau no ka sarcoma palupalu o nā kamaliʻi.
E hoʻolālā i ka mālama ʻana, he mea nui e ʻike i ke ʻano o ka sarcoma palupalu, inā hiki ke hemo ʻia ka tumo ma ke ʻoki ʻana, a inā ua pāhola ka maʻi ʻaʻai i nā ʻāpana ʻē aʻe o ke kino.
Hiki ke hoʻohana i nā kaʻina hana e ʻike ai inā ua laha ka maʻi ʻaʻai.
- ʻO ka biopsy lymph node Sentinel: ʻO ka lawe ʻana i ka lymph node sentinel i ke kau ʻana. ʻO ka lymph node sentinel ka lua o nā lymph node i kahi hui o nā lymph node e loaʻa ai ka hoʻokahe ʻana i ka lymphatic mai ka tumo mua. ʻO ia ka pūnana lymph mua e laha aku ai ka maʻi ʻaʻai mai a ka tumo mua. Hoʻokomo ʻia kahi mea lekiō a me / a i ʻole ke kala polū ma kahi kokoke i ka tumo. Kahe ka mea a kala paha ma o nā kahena lymph i nā lymph node. Lawe ʻia ka pona lymph mua e loaʻa ai ka waiwai a kala paha. ʻIke kahi pathologist i ke kiko ma lalo o kahi microscope e nānā no nā hunaola maʻi ʻaʻai. Inā ʻaʻole i loaʻa nā hunaola maʻi ʻaʻai, ʻaʻole pono paha e hemo i nā pūnana lymph. I kekahi manawa, loaʻa kahi lymph node sentinel i kahi ʻoi aku o hoʻokahi hui o nā aka. Hoʻohana ʻia kēia kaʻina hana no ka epithelioid a me ka sarcoma pūnaewele paʻa.
- CT scan (CAT scan): Kahi hana e hana ai i ka moʻo o nā kiʻi kikoʻī o nā wahi i loko o ke kino, e like me ka pahu, i lawe ʻia mai nā ʻaoʻao ʻokoʻa. Hana ʻia nā kiʻi e kahi kamepiula i hoʻopili ʻia i kahi mīkini x-ray. Hoʻokomo ʻia paha ke kala i loko o ke aa a i ʻole ale ʻia e kōkua i nā ʻōpū a i ʻole nā kino i hōʻike hou aku me ka maopopo. Kāhea ʻia kēia kaʻina hana he tomography i helu ʻia, kamepiula tomography, a i ʻole he tomography axial computerized.
- ʻO ka scan PET: ʻo kahi scan PET kahi hana e loaʻa ai nā pūnaewele tumo malignant i loko o ke kino. Hoʻokomo ʻia kahi liʻiliʻi o ka glucose radioactive (kō) i loko o kahi aa koko. Hoʻopili ka scanner PET a puni ke kino a hana i kahi kiʻi o kahi e hoʻohana ʻia ai ka glucose i ke kino. ʻOi aku ka mālamalama o nā hunaola tumo ma ke kiʻi no ka mea ʻoi aku ka hana a lawe i ka glucose ma mua o ka hana ʻana o nā hunaola maʻamau. Kāhea ʻia kēia kaʻina hana he positron emission tomography (PET) scan NineManga.com
- Nānā PET-CT: kahi hana e hoʻohui i nā kiʻi mai kahi PET scan a me kahi scan tomography i helu ʻia (CT). Hana ʻia nā paʻi PET a me CT ma ka manawa like ma ka mīkini like. Hoʻohui ʻia nā kiʻi mai nā kiʻi ʻelua e hana i kahi kiʻi kikoʻī ma mua o nā hōʻike ʻelua e hana ʻia e ia iho.
ʻEkolu ala e hoʻolaha ai ka maʻi ʻaʻai i loko o ke kino.
Hiki ke pālahalaha ʻia ka maʻi ʻaʻai ma o nā meaola, ka ʻōnaehana lymph, a me ke koko.
- Kāpena. Hoʻolahalaha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i ka ulu ʻana i nā wahi kokoke.
- ʻŌnaehana Lymph. Hoʻolahalaha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i ke komo ʻana i ka ʻōnaehana lymph. Hele ka maʻi ʻaʻai ma o nā kīʻaha lymph i nā ʻāpana ʻē aʻe o ke kino.
- Koko. Hoʻolahalaha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i ke komo ʻana i ke koko. Hele ka maʻi ʻaʻai ma o nā kīʻaha koko i nā ʻāpana ʻē aʻe o ke kino.
E laha paha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i nā ʻāpana ʻē aʻe o ke kino.
Ke pālahalaha ʻia ka maʻi ʻaʻai i kekahi ʻāpana o ke kino, ua kapa ʻia ia ʻo metastasis. E haki nā hunaola maʻi 'aʻai mai kahi a lākou i hoʻomaka ai (ka tumo mua) a hele i loko o ka ʻōnaehana lymph a i ʻole ke koko.
- ʻŌnaehana Lymph. Komo ka maʻi ʻaʻai i loko o ka ʻōnaehana lymph, hele ma waena o nā kīʻaha lymph, a hana i kahi tumo (tumo metastatic) i kekahi ʻāpana o ke kino.
- Koko. Komo ke kanesa i loko o ke koko, hele ma waena o nā kīʻaha koko, a hana i kahi tumo (tumo metastatic) i kekahi ʻāpana o ke kino.
ʻO ka tumo metastatic ka ʻano like o ke kanesa me ka tumo mua. ʻO kahi laʻana, inā pālahalaha ka sarcoma ʻili palupalu i ka hū, ʻo nā hunaola maʻi ʻaʻai i loko o ka akemāmā nā hunaola sarcoma aʻa palupalu. ʻO ka maʻi he sarcoma palupalu metastatic, ʻaʻole ʻo ka maʻi ʻaʻa lung.
Kūleʻa a holomua hoʻi i ka wā kamaliʻi Tissue Sarcoma
ʻO ka sarcoma palupalu hou o ka wā kamaliʻi ka maʻi ʻaʻai i hoʻi hou (hoʻi hou) ma hope o ka mālama ʻia ʻana. Ua hoʻi paha ka maʻi ʻaʻai ma ka wahi like a i ʻole nā ʻāpana ʻē aʻe o ke kino.
ʻO ka sarcoma palupalu ʻōpio holomua ka maʻi ʻaʻai i pane ʻole i ka lāʻau.
Laulā Manaʻo Option Oponopono
NA MANA KUNI
- Aia nā ʻano lapaʻau like ʻole no nā mea maʻi me ka sarcoma palupalu o nā kamaliʻi.
- ʻO nā keiki me ka sarcoma palupalu o ka wā kamaliʻi e pono e hoʻolālā ʻia e kahi hui o nā lawelawe mālama ola he loea i ka mālama ʻana i ka maʻi ʻaʻai i nā keiki.
- ʻO ka mālama ʻana no ka sarcoma palupalu o nā kamaliʻi i kumu i nā hopena ʻaoʻao.
- Hoʻohana ʻia ʻehiku ʻano o ka mālama maʻamau.
- ʻOki kino
- Lapaʻau hoʻomākala
- ʻO Chemotherapy
- Nānā
- Pahuhopu kau ʻia
- Immunotherapy
- Nā Laau Lapaʻau ʻē aʻe
- Ke hoʻāʻo ʻia nei nā ʻano lapaʻau hou i nā hoʻokolohua hoʻokolohua.
- Hoʻopau Gene
- Makemake paha nā mea maʻi e noʻonoʻo e pili ana i ka hoʻokolokolo ʻana.
- Hiki i nā mea maʻi ke komo i nā hoʻokolohua hoʻokolohua ma mua, i ka wā, a ma hope paha o ka hoʻomaka ʻana i kā lākou mālama maʻi ʻaʻai.
- Pono paha nā hoʻokolohua ukali.
Aia nā ʻano lapaʻau like ʻole no nā mea maʻi me ka sarcoma palupalu o nā kamaliʻi.
Loaʻa nā ʻano lapaʻau like ʻole no nā mea maʻi me ka sarcoma palupalu o nā kamaliʻi. Kūlana maʻamau kekahi mau hōʻailona (ʻo ka lāʻau i hoʻohana ʻia i kēia manawa), a ʻo kekahi e hoʻāʻo ʻia nei i nā hoʻokolohua hoʻokolohua. ʻO kahi hoʻokolohua hoʻokolohua lapaʻau kahi noiʻi noiʻi i manaʻo ʻia e kōkua i ka hoʻomaikaʻi ʻana i nā mālama ʻana i kēia manawa a i ʻole loaʻa ka ʻike e pili ana i nā mālama hou no nā maʻi me ka maʻi ʻaʻai. Ke hōʻike nā hoʻokolohua hoʻokolohua ʻoi aku ka maikaʻi o kahi lapaʻau hou ma mua o ka maʻamau maʻamau, lilo paha ka lāʻau hou i ka lapaʻau maʻamau.
Ma muli o ka loaʻa ʻole o ka maʻi ʻaʻai i nā keiki, pono e noʻonoʻo ʻia i ka hoʻokolokolo ʻana. ʻO kekahi mau hoʻokolohua hoʻokolohua e hāmama wale i nā mea maʻi i hoʻomaka ʻole i ka lāʻau.
ʻO nā keiki me ka sarcoma palupalu o ka wā kamaliʻi e pono e hoʻolālā ʻia e kahi hui o nā lawelawe mālama ola he loea i ka mālama ʻana i ka maʻi ʻaʻai i nā keiki.
E mālama ʻia ka lapaʻau ʻana e kahi oncologist pediatric, he kauka i loea i ka mālama ʻana i nā keiki me ka maʻi ʻaʻai. Hana ka oncologist pediatric me nā mea lawelawe olakino ʻē aʻe i loea i ka mālama ʻana i nā keiki me ka sarcoma palupalu a me ka poʻe loea i kekahi mau wahi o ka lāʻau. Hiki i kēia ke komo i kahi kauka lāʻau pediatric me ka hoʻomaʻamaʻa kūikawā i ka hemo ʻana o nā sarcomas aʻa momona. Hoʻokomo pū ʻia nā loea e hiki mai ana:
- Kahuna Pediatrician.
- Oncologist uila.
- Hematologist Pediatric.
- ʻO ka loea kahu maʻi Pediatric.
- Lapaʻau hoʻōla.
- ʻOlogistlapa psychologist.
- Limahana limahana.
- Loea loea-ola keiki.
ʻO ka mālama ʻana no ka sarcoma palupalu o nā kamaliʻi i kumu i nā hopena ʻaoʻao.
No ka ʻike e pili ana i nā hopena i hoʻomaka i ka wā o ka mālama ʻana no ka maʻi ʻaʻai, ʻike i kā mākou ʻaoʻao ʻaoʻao ʻaoʻao.
ʻO nā hopena ʻē aʻe mai ka mālama ʻana i ka maʻi ʻaʻai e hoʻomaka ma hope o ka mālama ʻana a hoʻomau no nā mahina a i ʻole mau makahiki e kapa ʻia nā hopena hopena. Hiki i nā hopena hope loa o ka mālama ʻana i ka maʻi ʻaʻai ke:
- Nā pilikia o ke kino.
- Nā loli i ke ʻano, nā manaʻo, ka noʻonoʻo, ke aʻo ʻana, a me ka hoʻomanaʻo paha.
- Nā maʻi ʻelua (nā ʻano maʻi ʻaʻai hou).
E mālama a kāohi ʻia paha kekahi mau hopena hopena. He mea nui e kamaʻilio pū me nā kauka o kāu keiki e pili ana i nā hopena o ka mālama ʻana i ka maʻi ʻaʻai i kāu keiki. (E ʻike i ka hōʻuluʻulu e pili ana i nā hopena hope o ka mālama ʻana no ka maʻi ʻaʻai kamaliʻi no ka ʻike hou aku.)
Hoʻohana ʻia ʻehiku ʻano o ka mālama maʻamau.
ʻOki kino
ʻO ke kaha e hemo loa ai ka sarcoma aʻa palupalu ke hana ʻia i ka wā hiki. Inā nui loa ka tumo, hāʻawi mua ʻia ka radiation therapy a chemotherapy paha, e hoʻoliʻiliʻi ai i ka tumo a hoʻoliʻiliʻi i ka nui o nā mea pono e hemo i ka wā o ke ʻoki. Kapa ʻia kēia ʻo neoadjuvant (preoperative) therapy.
Hiki ke hoʻohana i nā ʻano o ke kaha ʻana:
- ʻO ka laulā kūloko: Ka hemo ʻana o ka tumo a me kekahi mea maʻamau a puni ia.
- Hoʻonui: ʻoki e wehe i nā mea āpau a ʻāpana paha o ka lima a me ka wāwae me ka maʻi ʻaʻai.
- Lymphadenectomy: Ka hemo ʻana o nā lymph node me ka maʻi ʻaʻai.
- ʻOki kino Mohs: kahi kaʻina hana e hoʻohana ai i ka maʻi ʻaʻai i ka ʻili. Lawe ʻia nā papa pākahi o nā maʻi ʻaʻai a nānā ʻia ma lalo o ka microscope i kēlā me kēia manawa a hiki i ka lawe ʻia ʻana o nā maʻi ʻaʻai āpau. Hoʻohana ʻia kēia ʻano ʻoki e mālama i nā protuberans dermatofibrosarcoma.
Kāhea ʻia nō hoʻi ʻo ia ʻo Mohs micrographic surgery.
- Hepatectomy: Keʻoki e wehe i nā mea āpau a ʻāpana paha o ke ake.
Pono paha kahi ʻoki ʻelua e:
- Wehe i nā hunaola maʻi ʻino i koe.
- E nānā i ka wahi a puni kahi i lawe ʻia aku ai ka tumo no nā hunaola maʻi ʻaʻai a laila e hemo i nā kikoʻī ke pono aʻe
Inā loaʻa ka maʻi ʻaʻai i ke ake, hiki ke hana ʻia kahi hepatectomy a me ke akepaʻa o ke ake (hemo ka ate a pani ʻia me kahi olakino mai kahi mea hāʻawi).
Ma hope o ka hemo ʻana o ke kauka i nā maʻi ʻaʻai āpau i hiki ke ʻike ʻia i ka manawa o ke ʻoki ʻana, hiki i kekahi mau mea maʻi ke hāʻawi ʻia i ka chemotherapy a i ʻole ka radiation therapy ma hope o ke kaha ʻana e luku i nā hunaola maʻi ʻea i koe. ʻO ka lāʻau i hāʻawi ʻia ma hope o ke kaha ʻana, e hoʻohaʻahaʻa i ka makaʻu e hoʻi mai ka maʻi ʻaʻai, i kapa ʻia ʻo adjuvant therapy.
Lapaʻau hoʻomākala
ʻO ka radiation radiation kahi lāʻau maʻi maʻi maʻi e hoʻohana i nā kukuna x nui ikaika a i ʻole nā ʻano radiation e hoʻomake i nā hunaola maʻi ʻaʻai a mālama ʻole paha i ka ulu ʻana. ʻElua ʻano o radiation radiation:
- Hoʻohana ka radiation radiation kūwaho i kahi mīkini ma waho o ke kino e hoʻouna i ka radiation i ka maʻi ʻaʻai. Hiki i kekahi mau ala o ka hāʻawi ʻana i ka radiation therapy ke pale i ka radiation mai ka hōʻino ʻana i nā mea olakino kokoke. Hiki i kēia ʻano radiation radiation ke hoʻopili i kēia mau mea:
- Hoʻoikaika kino kino Stereotactic: He ʻano radiation radiation kino ʻo Stereotactic. Hoʻohana ʻia nā pono kūikawā e hoʻonoho i ka mea maʻi ma ke kūlana like no kēlā me kēia hoʻomaʻamaʻa radiation. Hoʻokahi manawa i ka lā no kekahi mau lā, kuhi ka mīkini radiation i kahi ʻoi aku ka nui ma mua o ka maʻamau maʻamau o ka radiation ma ka tumo. Ma ka loaʻa ʻana o ka mea maʻi ma ke kūlana like no kēlā me kēia lapaʻau, ʻoi aku ka liʻiliʻi o ka hōʻino ʻana i nā mea olakino kokoke. Kapa ʻia kēia kaʻina hana ʻo stereotactic waho-kukuna radiation radiation a me stereotaxic radiation therapy.
- Hoʻohana ka radiation radiation i loko i kahi lāʻau radioactive i hoʻopaʻa ʻia i nā nila, nā hua, nā uea, a i ʻole nā catheters i kau pololei ʻia i loko a kokoke paha i ka maʻi ʻaʻai.
Hāʻawi ʻia ka radiation radiation ma mua a ma hope paha o ke kaha ʻana e wehe i ka maʻi ʻaʻai e pili ana i ka ʻano a me ke kahua o ka maʻi ʻaʻai e mālama ʻia ai, inā mau kekahi maʻi ʻaʻai ma hope o ke kaha ʻana, a me nā hopena i manaʻo ʻia o ka lapaʻau. Hoʻohana ʻia ka radiation radiation kūwaho a me loko e mālama i ka sarcoma palupalu o nā kamaliʻi.
ʻO Chemotherapy
ʻO Chemotherapy kahi lāʻau lapaʻau maʻi maʻi e hoʻohana i nā lāʻau e hōʻoki i ka ulu ʻana o nā hunaola maʻi ʻaʻai, ma ka luku ʻana i nā hunaola a i ʻole ke kāpae ʻana iā lākou mai ka hoʻokaʻawale. Ke lawe ʻia ka chemotherapy e ka waha a i ʻole injected i loko o kahi aa koko a i ʻole nā mākala, komo nā lāʻau i ke kahe o ke koko a hiki ke kiʻi i nā hunaola maʻi ʻōpio i loko o ke kino (chemotherapy ʻōnaehana). Ke waiho pololei ʻia ka chemotherapy i loko o ka wai cerebrospinal, kahi hui, a i ʻole ke kino o ke kino e like me ka ʻōpū, ʻo nā lāʻau lapaʻau ka mea nui e hoʻopili i nā hunaola maʻi ʻaʻai i kēlā mau wahi (chemotherapy āpau). Hoʻohui ʻia ʻo chemotherapy ka hoʻohana ʻana o nā lāʻau anticancer ʻoi aku ma mua o hoʻokahi.
Hāʻawi ʻia ke ala o ka chemotherapy ma muli o ke ʻano o ka mālama ʻana i ka sarcoma palupalu. ʻAʻole pane ka hapa nui o nā ʻano sarcoma palupalu i ka mālama ʻana me ka chemotherapy.
E ʻike i nā lāʻau i ʻae ʻia no ka Tissue Tissue Sarcoma no ka ʻike hou aku.
Nānā
Ke nānā pono nei i ka nānā ʻana i ke kūlana o ka mea maʻi me ka ʻole o ka hāʻawi ʻana i nā lāʻau a hiki i ka wā e ʻike ʻia ai nā hōʻailona a i ʻole nā loli. Hiki ke nānā ʻia ke:
- ʻAʻole hiki ke hoʻopau loa i ka tumo.
- ʻAʻole loaʻa nā lapaʻau ʻē aʻe.
- ʻAʻole hiki i ka tumo ke hoʻopōʻino i nā mea ola āpau.
Hiki ke hoʻohana ʻia ka nānā ʻana e mālama ai i ka fibromatosis desmoid-type, fibrosarcoma pēpē, PEComa, a i ʻole epithelioid hemangioendothelioma.
Pahuhopu kau ʻia
ʻO ka therapy target kahi ʻano lapaʻau e hoʻohana i nā lāʻau a i ʻole nā mea ʻē aʻe e hoʻouka aku i nā hunaola maʻi ʻaʻai. Hoʻohui pinepine nā therapies i hoʻomākaukau ʻia e hōʻemi i ka pōʻino i nā hunaola maʻamau ma mua o ka chemotherapy a i ʻole ka radiation.
- Paʻa nā mea hoʻohālua Kinase i kahi enzyme i kapa ʻia kinase (kahi ʻano protein. Aia kekahi ʻano o nā kinase i ke kino i loaʻa nā ʻano ʻokoʻa.
- Hiki i nā mea pāpā ʻo ALK ke kū i ka maʻi ʻaʻai mai ka ulu a pālahalaha ʻana. Hiki ke hoʻohana ʻia ʻo Crizotinib e mālama ai i ka tumo myofibroblastic inflammatory a me ka fibrosarcoma pēpē.
- Hoʻopili nā mea kāohi Tyrosine kinase (TKI) i nā hōʻailona pono e ulu nā tumors. Hoʻohana ʻia ʻo Imatinib e mālama i nā protuberans dermatofibrosarcoma. Hiki paha ke hoʻohana ʻia ʻo Pazopanib e mālama i ka desmoid-type fibromatosis, epithelioid hemangioendothelioma, a me kekahi ʻano sarcoma palupalu hou a holomua hoʻi o ka holomua. Hiki ke hoʻohana ʻia ʻo Sorafenib e mālama i ka desmoid-type fibromatosis a me ka epithelioid hemangioendothelioma. Hiki ke hoʻohana ʻia ʻo Sunitinib e mālama i ka sarcoma ʻāpana palupalu alveolar. Hoʻohana ʻia ʻo Larotrectinib e mālama i ka fibrosarcoma pēpē. Hoʻohana ʻia ʻo Ceritinib e mālama i ka tumo myofibroblastic ʻōpala.
- ʻO nā mea kāwili mTOR kahi ʻano o ka hoʻomōhala hoʻomāka ʻia e kū ana i ka protein i kōkua i nā hunaola e māhele a ola. Hoʻohana ʻia nā mea kāohi mTOR e mālama i nā tumors liʻiliʻi liʻiliʻi a puni desmoplastic, PEComas, a me epithelioid hemangioendothelioma a ke hoʻopaʻa ʻia nei e mālama i ka tumigne maʻi āpau maʻi āpau. ʻO Sirolimus a me temsirolimus kekahi ʻano o ka mTOR mea hoʻōla lāʻau.
Ke aʻo ʻia nei nā ʻano mea like ʻole o ka tyrosine kinase inhibitors e like me:
- Entrectinib no ka fibrosarcoma pēpē.
- Trametinib no epithelioid hemangioendothelioma.
Ke aʻo ʻia nei kekahi ʻano ʻano lāʻau hoʻomōkōkō ʻia i nā hoʻokolohua hoʻokolohua, e like me kēia:
- ʻO nā mea kāohi Angiogenesis kahi ʻano o ka hoʻomōhala hoʻomāka ʻia e pale ai i ka ulu ʻana o nā kīʻaha koko e pono ai no ka ulu ʻana o nā tumors. Ke aʻo ʻia nei nā mea hōʻoki Angiogenesis, e like me cediranib, sunitinib, a me thalidomide e mālama ai i ka sarcoma ʻāpana alveolar a me epithelioid hemangioendothelioma. Hoʻohana ʻia ʻo Bevacizumab e mālama ai i ka angiosarcoma.
- Hoʻonohonoho ʻia nā mea hoʻohālua Histone methyltransferase (HMT) i nā lāʻau lapaʻau e hana i loko o nā hunaola maʻi ʻaʻa a me nā hōʻailona poloka e pono ai e ulu nā tumors. Ke hoʻopaʻa ʻia nei nā mea hoʻohālua o ka HMT, e like me tazemetostat, no ka mālama ʻana i ka tumath sheath nerve āpau malignant, epithelioid sarcoma, extraskeletal myxoid chondrosarcoma, a me ka tumar rhabdoid extrarenal (extracranial).
- Hoʻopaʻa nā mea hoʻopili protein-shock protein i kekahi mau protein i pale i nā hunaola tumora a kōkua iā lākou e ulu. ʻO Ganetespib kahi mea hoʻonāukiuki hoʻohiwahiwa wela e hoʻopaʻa ʻia me ka hui pū me ka mTOR mea pale sirolimus no nā maʻi ʻōpū o ke kino āpau i hiki ʻole ke hemo e ke ʻoki.
- ʻO nā mea kāohi ala NOTCH kahi ʻano o ka hoʻomōhala hoʻomāka ʻia e hana i loko o nā hunaola maʻi ʻaʻai a ālai i nā hōʻailona pono no ka ulu ʻana o nā tumors.
Ke aʻo ʻia nei nā mea pāpāho ala NOTCH no ka mālama ʻana i ka fibromatosis ʻano desmoid.
E ʻike i nā lāʻau i ʻae ʻia no ka Tissue Tissue Sarcoma no ka ʻike hou aku.
Immunotherapy
ʻO ka Immunotherapy kahi lapaʻau e hoʻohana i ka ʻōnaehana pale maʻi o ka mea maʻi e hakakā i ka maʻi ʻaʻai. Hoʻohana ʻia nā mea i hana ʻia e ke kino a i hana ʻia paha i kahi keʻena hoʻokolohua e hoʻonui, kuhikuhi, a hoʻihoʻi hou i nā pale kūlohelohe o ke kino i ka maʻi ʻaʻai. Kapa ʻia kēia ʻano lapaʻau ʻo biotherapy a i ʻole biologic therapy.
ʻO Interferon a me immune checkpoint inhibitor therapy kekahi ʻano o ka immunotherapy.
- Hoʻopilikia ʻo Interferon i ka mahele o nā hunaola tumora a hiki ke hoʻolohi i ka ulu ulu ʻana. Hoʻohana ʻia ia e mālama i ka epithelioid hemangioendothelioma.
- Pilikia pūkaʻina hoʻohiamoe maʻi pale: ʻO kekahi ʻano o nā hunaola pale, e like me nā hunaola T, a me kekahi mau pūnaʻi maʻi ʻaʻai i loaʻa kekahi mau protein, i kapa ʻia he checkpoint proteins, ma ko lākou ʻaoʻao e mālama ana i nā pane pale pale i ka helu. Ke loaʻa ka nui o kēia mau protein i nā hunaola maʻi ʻaʻai, ʻaʻole lākou e hoʻouka ʻia a make ʻia e nā hunaola T. Pale aku nā mea hoʻopale nānā Immune i kēia mau protein a hoʻonui ʻia ka hiki o nā hunaola T e pepehi i nā hunaola maʻi ʻaʻai.
ʻElua ʻano o ka checkpoint inhibitor therapy:
- Mea kāohi CTLA-4: ʻO ka CTLA-4 kahi protein i ka ʻili o nā pūnaewele T e kōkua ai e mālama i nā pane pale o ke kino. Ke hoʻopili aku ʻo CTLA-4 i kahi protein ʻē aʻe i kapa ʻia ʻo B7 ma ke kolamu maʻi ʻaʻai, kū ia i ka hunaola T mai ka luku ʻana i ka pūnaeho maʻi maʻi. Hoʻopili ka mea pāpālina CTLA-4 i CTLA-4 a ʻae i nā hunaola T e pepehi i nā hunaola maʻi ʻaʻai. ʻO Ipilimumab kahi ʻano o ka mea kāohi iā CTLA-4 e hoʻopaʻa ʻia nei e mālama i ka angiosarcoma.

- Mea kāohi PD-1: ʻO PD-1 kahi protein i ka ʻili o nā hunaola T e kōkua ai i ka mālama ʻana i nā pane pale o ke kino. Ke hoʻopili aku ʻo PD-1 i kahi protein ʻē aʻe i kapa ʻia ʻo PDL-1 ma kahi hunaola maʻi ʻoki, paʻa ia i ke kele T mai ka luku ʻana i ka pūnaeho maʻi maʻi. Hoʻopili nā mea pale PD-1 i PDL-1 a ʻae i nā hunaola T e pepehi i nā hunaola maʻi ʻaʻai. ʻO Pembrolizumab kahi ʻano o ka mea kāohi PD-1 i hoʻohana ʻia e mālama i ka sarcoma palupalu holomua a hoʻi hou. ʻO Nivolumab kahi ʻano o ka mea kāohi PD-1 e hoʻopaʻa ʻia nei e mālama i ka angiosarcoma.

Nā Laau Lapaʻau ʻē aʻe
Loaʻa nā hopena antitumor i ka lāʻau steroid steroid i nā tumors myofibroblastic.
ʻO ka Hormone therapy kahi lapaʻau maʻi ʻaʻai e hoʻoneʻe i nā homone a i ʻole ālai i kā lākou hana a kāpae i nā hunaola maʻi maʻi mai ka ulu ʻana. ʻO nā Hormones nā mea i hana ʻia e nā glands i loko o ke kino a hoʻolaha ʻia i ke kahe o ke koko. Hiki i kekahi mau hormoni ke hoʻoulu i kekahi mau maʻi ʻaʻai. Inā hōʻike ʻia nā hōʻike i ka loaʻa ʻana o nā hunaola maʻi ʻaʻai i mau wahi kahi e hoʻopili ai nā homone (nā mea loaʻa), nā lāʻau, ke ʻoki ʻana, a i ʻole ka radiation therapy e hōʻemi ai i ka hana ʻana o nā hormones a i ʻole keakea iā lākou mai ka hana ʻana Hiki ke hoʻohana ʻia nā antiestrogens (nā lāʻau e ālai ana i ka estrogen), e like me tamoxifen, e mālama ai i ka fibromatosis ʻano desmoid. Ke aʻo ʻia nei ʻo Prasterone no ka mālama ʻana i ka sarcoma synovial.
ʻO nā lāʻau anti-inflammatory Nonsteroidal (NSAIDs) he lāʻau lapaʻau (e like me aspirin, ibuprofen, a me naproxen) i hoʻohana mau ʻia e hoʻemi i ke kuni, ka pehu ʻana, ka ʻeha, a me ka ʻulaʻula. I ka mālama ʻana i ka desibrid-type fibromatosis, hiki ke hoʻohana ʻia kahi NSAID i kapa ʻia ʻo sulindac e kōkua i ka pale ʻana i ka ulu ʻana o nā hunaola maʻi ʻaʻai.
Ke hoʻāʻo ʻia nei nā ʻano lapaʻau hou i nā hoʻokolohua hoʻokolohua.
Hōʻike kēia ʻāpana hōʻuluʻulu manaʻo i nā mālama e hoʻopaʻa ʻia nei i nā hoʻokolohua hoʻokolohua. ʻAʻole paha ia e ʻōlelo i kēlā me kēia lapaʻau hou e hoʻopaʻa ʻia ana. Loaʻa nā ʻike e pili ana i nā hoʻokolohua hoʻokolohua mai ka pūnaewele NCI.
Hoʻopau Gene
Ke aʻo ʻia nei ka genotherapy no ka sarcoma synovial o ke keiki i hoʻi hou, pālahalaha, a i ʻole hiki ʻole ke hemo e ke ʻoki. Lawe ʻia kekahi o nā hunaola T (kahi ʻano o ke keʻokeʻo koko keʻokeʻo) a hoʻololi ʻia nā genes i nā hunaola i loko o kahi keʻena hoʻokolohua (genetically engineered) i mea e hoʻouka ai i nā hunaola maʻi ʻaʻai. Hoʻihoʻi ʻia lākou i ka mea maʻi ma o ka hoʻoulu ʻana.
Makemake paha nā mea maʻi e noʻonoʻo e pili ana i ka hoʻokolokolo ʻana.
No kekahi mau mea maʻi, ke komo nei i ka hoʻokolohua hoʻokolohua ke koho lapaʻau maikaʻi loa paha. ʻO nā hoʻokolohua hoʻokolohua kahi ʻāpana o ka noiʻi ʻana o ka maʻi ʻaʻai. Hana ʻia nā hoʻokolohua hoʻokolohua e ʻike inā palekana a maikaʻi a maikaʻi paha nā hoʻomaʻamaʻa maʻi ʻaʻai ma mua o ka maʻamau maʻamau.
ʻO ka hapa nui o nā hana maʻamau no ka maʻi ʻaʻai i kau ʻia ma nā hoʻokolohua hoʻokolohua mua. ʻO nā mea maʻi i komo i ka hoʻokolokolo hoʻokolohua hiki ke loaʻa i ka lāʻau maʻamau a i ʻole i waena o nā mea mua i loaʻa kahi lāʻau hou.
ʻO nā mea maʻi i komo i nā hoʻokolohua hoʻokolohua kōkua pū kekahi i ka hoʻomaikaʻi ʻana i ke ʻano o ka mālama ʻana i ka maʻi ʻaʻai i ka wā e hiki mai ana. ʻOiai ʻaʻole nā alakaʻi hoʻokolohua e alakaʻi i nā hoʻoponopono hou maikaʻi, pane pinepine lākou i nā nīnau nui a kōkua i ka neʻe i mua o ka noiʻi.
Hiki i nā mea maʻi ke komo i nā hoʻokolohua hoʻokolohua ma mua, i ka wā, a ma hope paha o ka hoʻomaka ʻana i kā lākou mālama maʻi ʻaʻai.
Hoʻopili wale kekahi mau hoʻokolohua hoʻokolohua i nā mea maʻi i loaʻa ʻole ka lapaʻau. ʻO nā hoʻokolohua ʻē aʻe e hōʻoia i nā mālama ʻana no ka poʻe maʻi i loaʻa ʻole ka maikaʻi o ka maʻi ʻaʻai. Aia kekahi mau hoʻokolohua hoʻokolohua e hoʻāʻo i nā ala hou e hōʻoki i ka maʻi ʻaʻai mai ka hoʻi hou ʻana (hoʻi ʻana) a hōʻemi paha i nā hopena o ka mālama ʻana i ka maʻi ʻaʻai.
Ke mālama ʻia nei nā hoʻokolohua hoʻokolohua ma nā wahi he nui o ka ʻāina. Hiki ke ʻike ʻia ka ʻike e pili ana i nā hoʻokolohua hoʻokolohua e kākoʻo ʻia e NCI ma ka pūnaewele ʻimi noiʻi hoʻokolohua a NCI. Hiki ke loaʻa nā hoʻokolohua hoʻokolohua i kākoʻo ʻia e nā hui ʻē aʻe ma ka pūnaewele ClinicalTrials.gov.
Pono paha nā hoʻokolohua ukali.
ʻO kekahi o nā hoʻokolohua i hana ʻia e hōʻoia i ka maʻi ʻaʻai a i ʻole e ʻike i ke kahua o ka maʻi ʻaʻaʻa e hana hou ʻia paha. E hana hou ʻia kekahi mau hōʻike i mea e ʻike ai i ka maikaʻi o ka mālama ʻana. Hoʻoholo ʻia nā hoʻoholo e pili ana inā e hoʻomau, hoʻololi, a kū paha i ka lāʻau ʻana ma nā hopena o kēia mau hoʻāʻo.
E hoʻomau ʻia kekahi o nā hoʻokolohua mai kēlā me kēia manawa ma hope o ka pau ʻana o ka lāʻau. Hiki i nā hopena o kēia mau hoʻāʻo ke hōʻike inā ua loli ke ʻano o kāu keiki a i ʻole ua hoʻi hou ke kanesa. Kapa ʻia kēia mau hoʻāʻo i kekahi manawa nā hoʻokolohua ukali a i ʻole nā loiloi.
Nā koho lapaʻau no ka mea hou Diagnosed Pōpeku Pilikia Tissue Sarcoma
Ma keia Pauku
- ʻO nā tumo momona
- Liposarcoma
- Nā Tumole iwi a me ka iwi
- Extrondreletal mesenchymal chondrosarcoma
- Osteosarcoma Extraskeletal
- ʻO Fibrous (Connective) nā Tumiko Tissue
- Fibromatosis ʻano-Desmoid
- Nā Dermatofibrosarcoma protuberans
- Tumo myofibroblastic ʻōpala
- ʻO Fibrosarcoma
- Myxofibrosarcoma
- ʻO ka sarcoma fibromyxoid haʻahaʻa haʻahaʻa
- ʻO Sclerosing epithelioid fibrosarcoma
- Nā Tumo Musele iwi
- Rhabdomyosarcoma
- Nā Tumo Muso Mele
- Leiomyosarcoma
- ʻO nā Tumors Fibrohistiocytic i kapa ʻia
- Tumo fibrohistiocytic plexiform
- Nā Tumors Pūnaewele Nerve
- Tumo huluhulu ʻaʻano maʻi malignant
- Tumo Triton malignant
- ʻO Ectomesenchymoma
- Nā Tumika Pericytic (Perivascular)
- ʻO Hemangiopericytoma Infantile
- Myofibromatosis Infantile
- Nā Tumors o ka Cell Cell Unknown (kahi i ʻike ʻole ʻia ai ka tumo)
- ʻO ka sarcoma Synovial
- Pākuʻi ʻo Epithelioid
- ʻO Sarvea ʻāpana palupalu ʻo Alveolar
- E hoʻomaʻemaʻe i ka sarcoma o ka pūnaewele
- Extraseletal myxoid chondrosarcoma
- ʻO sarcoma Extremeeletal Ewing
- Desmoplastic liʻiliʻi a puni ka puʻupuʻu tum Tumele
- ʻOi nui-hōʻeha (extracranial) tumo rhabdoid
- ʻO nā tumors cell epithelioid perivascular (PEComas)
- Sarcoma i hoʻokaʻawale ʻia / Unclassified
- ʻO ka sarcoma pleomorphic ponoʻole / malignant fibrous histiocytoma (kūlana kiʻekiʻe)
- ʻO nā Tumors Kapuna Koko
- Epithelioid hemangioendothelioma
- Angiosarcoma o nā mea palupalu
- ʻO Tissue Sarcoma Pōʻino Metastatic
No ka ʻike e pili ana i nā lāʻau i helu ʻia ma lalo, e ʻike i ka ʻaoʻao Overtion Option Overview
ʻO nā tumo momona
Liposarcoma
Hiki i ka mālama ʻana i ka liposarcoma ke hoʻopili i kēia mau mea:
- ʻO ke kaha e hemo loa ai ka tumo. Inā ʻaʻole pau ka maʻi ʻaʻai, hana ʻia paha kahi ʻoki ʻelua.
- Chemotherapy e hoʻoliʻiliʻi i ka tumer, a ukali ʻia e ke kahakaha.
- ʻO ka radiation radiation ma mua a ma hope paha o ke kaha ʻana.
Nā Tumole iwi a me ka iwi
Extrondreletal mesenchymal chondrosarcoma
ʻO ka mālama ʻana i extrondreletal mesenchymal chondrosarcoma hiki ke hoʻopili ʻia i kēia mau mea:
- ʻO ke kaha e hemo loa ai ka tumo. Hāʻawi ʻia ka radiation radiation ma mua a / a ma hope paha o ke kaha ʻana.
- Chemotherapy ukali ʻia me ke ʻoki kino. Hāʻawi ʻia ʻo Chemotherapy me a i ʻole a ʻole me ka radiation radiation ma hope o ke kaha ʻana.
Osteosarcoma Extraskeletal
ʻO ka mālama ʻana i ka osteosarcoma extraskeletal hiki ke hoʻopili ʻia i kēia mau mea:
- ʻO ke ʻoki kino e hemo loa i ka tumo, a ukali ʻia e chemotherapy.
E ʻike i ka hōʻuluʻulu ma Osteosarcoma a me Malignant Fibrous Histiocytoma o Bone Treatment no ka ʻike hou aku e pili ana i ka mālama ʻana i ka osteosarcoma.
ʻO Fibrous (Connective) nā Tumiko Tissue
Fibromatosis ʻano-Desmoid
ʻO ka mālama ʻana i ka fibromatosis ʻano desmoid hiki ke hoʻopili ʻia i kēia mau mea:
- ʻO ke kaha e hemo loa ai ka tumo.
- ʻO ka nānā ʻana, no nā ʻōpū ʻaʻole i hoʻoneʻe loa ʻia e ke ʻoki a i ʻole i hoʻi hou (hoʻi hou) a ʻaʻole paha e hōʻino i nā mea ola āpau.
- Chemotherapy no nā hikoko ʻaʻole i hoʻopau loa ʻia e ke ʻoki a i ʻole ua hoʻi hou.
- Hoʻolālā pahuhopu (sorafenib a i ʻole pazopanib).
- Nonsteroidal anti-inflammatory drug (NSAID) therapy.
- Pāpaʻi lāʻau antiestrogen.
- Lapaʻau hoʻomākala.
- ʻO kahi hoʻokolohua hoʻokolohua o ka hoʻomāka hoʻomāka ʻia me kahi mea hoʻopuka ala NOTCH.
Nā Dermatofibrosarcoma protuberans
Hiki i ka mālama ʻana i nā protuberans dermatofibrosarcoma ke hoʻopili i kēia mau mea:
- ʻO ke kaha e hemo loa ai ka tumo ke hiki. Pākuʻi ʻia paha kēia iā Mohs.
- ʻO ka radiation radiation ma mua a ma hope paha o ke kaha ʻana.
- ʻO ka radiation radiation a me ka hoʻomālama ʻia (imatinib) inā ʻaʻole hiki ke hemo a hoʻi mai paha ka tumo.
Tumo myofibroblastic ʻōpala
ʻO ka mālama ʻana i ka tumo myofibroblastic ʻōpala e hoʻopili i kēia mau mea:
- ʻO ke kaha e hemo loa ai ka tumo ke hiki.
- ʻO Chemotherapy.
- Pākuʻi steroid.
- Nonsteroidal anti-inflammatory drug (NSAID) therapy.
- Hoʻolālā pahuhopu (crizotinib a me ceritinib).
ʻO Fibrosarcoma
Fibrosarcoma Infantile
Hiki i ka mālama ʻana i ka fibrosarcoma pēpē ke hoʻopili i kēia mau mea:
- ʻO ke ʻoki kino e hemo ai i ka tumo ke hiki, a ukali ʻia e ka nānā ʻana.
- ʻO ke ʻoki lāʻau i ukali ʻia e chemotherapy.
- Chemotherapy e hoʻoliʻiliʻi i ka tumer, a ukali ʻia e ke kahakaha.
- Hoʻolālā pahuhopu (crizotinib a me larotrectinib).
- ʻO kahi hoʻokolohua hoʻokolohua e nānā i kahi laʻana o ka tumo o ka mea maʻi no kekahi ʻano loli. ʻO ke ʻano o ka hoʻomālama ʻia e hāʻawi ʻia i ka mea maʻi e pili ana i ka ʻano o ka loli.
- ʻO kahi hoʻokolohua hoʻokolohua o ka lāʻau hoʻomoe ʻia (larotrectinib a i ʻole entrectinib).
Fibrosarcoma makua
Hiki i ka mālama ʻana i ka fibrosarcoma makua ke hoʻopili i kēia mau mea:
- ʻO ke kaha e hemo loa ai ka tumo ke hiki.
Myxofibrosarcoma
Hiki i ka mālama ʻana i ka myxofibrosarcoma ke hoʻopili i kēia mau mea:
- ʻO ke kaha e hemo loa ai ka tumo.
ʻO ka sarcoma fibromyxoid haʻahaʻa haʻahaʻa
Hoʻomaʻamaʻa ʻia i ka sarcoma fibromyxoid haʻahaʻa haʻahaʻa i kēia mau mea:
- ʻO ke kaha e hemo loa ai ka tumo.
ʻO Sclerosing epithelioid fibrosarcoma
ʻO ka mālama ʻana i ka sclerosing epithelioid fibrosarcoma hiki ke hoʻopili ʻia i kēia mau mea:
- ʻO ke kaha e hemo loa ai ka tumo.
Nā Tumo Musele iwi
Rhabdomyosarcoma
E ʻike i ka hōʻuluʻulu e pili ana i ka mālama ʻana iā Rhabdomyosarcoma Childhood.
Nā Tumo Muso Mele
Leiomyosarcoma
Hiki i ka mālama ʻana i ka leiomyosarcoma ke hoʻopili i kēia mau mea:
- ʻO Chemotherapy.
ʻO nā Tumors Fibrohistiocytic i kapa ʻia
Tumo fibrohistiocytic plexiform
ʻO ka mālama ʻana i ka tumo plexiform fibrohistiocytic e hoʻopili pū paha i kēia mau mea:
- ʻO ke kaha e hemo loa ai ka tumo.
Nā Tumors Pūnaewele Nerve
Tumo huluhulu ʻaʻano maʻi malignant
ʻO ka hoʻomaʻamaʻa ʻana i ka tumer nerve peripheral nerve sheath e hoʻopili pū i kēia mau mea:
- ʻO ke kaha e hemo loa ai ka tumo ke hiki.
- ʻO ka radiation radiation ma mua a ma hope paha o ke kaha ʻana.
- ʻO Chemotherapy, no nā tumors i hiki ʻole ke hemo e ke ʻoki.
- ʻO kahi hoʻokolohua hoʻokolohua e nānā i kahi laʻana o ka tumo o ka mea maʻi no kekahi ʻano loli. ʻO ke ʻano o ka hoʻomālama ʻia e hāʻawi ʻia i ka mea maʻi e pili ana i ka ʻano o ka loli.
- ʻO kahi hoʻokolohua hoʻokolohua o ka lāʻau hoʻomoʻa ʻia.
- ʻO kahi hoʻokolohua hoʻokolohua o ka lāʻau i hoʻomoe ʻia (tazemetostat).
ʻAʻole maopopo inā hāʻawi ʻana i ka radiation therapy a chemotherapy paha ma hope o ke kaha ʻana e hoʻomaikaʻi ai i ka pane a ka tumo i ka lāʻau.
Tumo Triton malignant
Hiki ke mālama ʻia nā tumors Triton malignant e like me ka rhabdomyosarcomas a hoʻopili pū ʻia me ke kaha ʻana, chemotherapy, a i ʻole radiation therapy. ʻAʻole maopopo inā hāʻawi ʻana i ka radiation therapy a chemotherapy paha e hoʻomaikaʻi ai i ka pane a ka tumo i ka lāʻau.
ʻO Ectomesenchymoma
Hiki i ka mālama ʻana i ectomesenchymoma ke hoʻopili i kēia mau mea:
- ʻOki kino.
- ʻO Chemotherapy.
- Lapaʻau hoʻomākala.
Nā Tumika Pericytic (Perivascular)
ʻO Hemangiopericytoma Infantile
ʻO ka mālama ʻana i ka hemangiopericytoma pēpē e hoʻopili i kēia mau mea:
- ʻO Chemotherapy.
Myofibromatosis Infantile
Hiki i ka mālama ʻana i ka myofibromatosis pēpē ke hoʻopili i kēia mau mea:
Hoʻohui chemotherapy.
Nā Tumors o ka Cell Cell Unknown (kahi i ʻike ʻole ʻia ai ka tumo)
ʻO ka sarcoma Synovial
Hiki i ka mālama ʻana i ka sarcoma synovial ke hoʻopili i kēia mau mea:
- ʻOki kino. Hāʻawi ʻia ka radiation radiation a me / a chemotherapy paha ma mua a ma hope paha o ke kaha ʻana.
- ʻO Chemotherapy.
- Hoʻoikaika radiation radiation Stereotactic no nā tumors i palahalaha aʻe i ka lung.
- ʻO kahi hoʻokolohua hoʻokolohua o ka gen therapy.
- ʻO kahi hoʻokolohua hoʻokolohua o ka hoʻomaʻamaʻa hormone.
Pākuʻi ʻo Epithelioid
Hoʻomaʻamaʻa ʻia ka epithelioid sarcoma i kēia mau mea:
- Hoʻopau ke ʻoki e wehe i ka tumer inā hiki.
- ʻO Chemotherapy.
- ʻO ka radiation radiation ma mua a ma hope paha o ke kaha ʻana.
- ʻO kahi hoʻokolohua hoʻokolohua o ka lāʻau i hoʻomoe ʻia (tazemetostat).
ʻO Sarvea ʻāpana palupalu ʻo Alveolar
ʻO ka mālama ʻana i ka sarcoma ʻāpana palupalu alveolar hiki i kēia mau mea:
- ʻO ke kaha e hemo loa ai ka tumo ke hiki.
- ʻO ka radiation radiation ma mua a ma hope paha o ke kaha ʻana, inā ʻaʻole hiki ke hoʻopau loa ʻia ka tumo e ke ʻoki.
- Hoʻolālā pahuhopu (sunitinib).
- ʻO kahi hoʻokolohua hoʻokolohua o ka lāʻau i hoʻomākaukau ʻia (cediranib a i ʻole sunitinib) no nā keiki.
E hoʻomaʻemaʻe i ka sarcoma o ka pūnaewele
ʻO ka mālama ʻana i ka sarcoma pūnaewele ʻino o nā mea palupalu e hoʻopili pū i ka mea aʻe:
- Hoʻopau ke ʻoki e wehe i ka tumer inā hiki.
- ʻO ka radiation radiation ma mua a ma hope paha o ke kaha ʻana.
Extraseletal myxoid chondrosarcoma
ʻO ka mālama ʻana i ka myxoid extraseletal chondrosarcoma hiki ke hoʻopili ʻia i kēia mau mea:
- Hoʻopau ke ʻoki e wehe i ka tumer inā hiki.
- Lapaʻau hoʻomākala.
- ʻO kahi hoʻokolohua hoʻokolohua o ka lāʻau i hoʻomoe ʻia (tazemetostat).
ʻO sarcoma Extremeeletal Ewing
E ʻike i ka hōʻuluʻulu ma ʻo Ewing Sarcoma lapaʻau.
Desmoplastic liʻiliʻi a puni ka puʻupuʻu tum Tumele
ʻAʻohe mālama maʻamau no ka desmoplastic puʻupuʻu liʻiliʻi a puni. Hoʻomaopopo ʻia ka hana penei:
- ʻO ke kaha e hemo loa ai ka tumo ke hiki.
- Chemotherapy ukali ʻia me ke ʻoki kino.
- Lapaʻau hoʻomākala.
- Chemotherapy a me ka hoʻomohala hoʻomohala ʻia (temsirolimus), no nā tumors hou.
ʻOi nui-hōʻeha (extracranial) tumo rhabdoid
ʻO ka mālama ʻana i ke tumo rhabdoid keu-renal (extracranial) hiki ke hoʻopili ʻia i kēia mau mea:
- Hoʻopau ke ʻoki e wehe i ka tumer inā hiki.
- ʻO Chemotherapy.
- Lapaʻau hoʻomākala.
- ʻO kahi hoʻokolohua hoʻokolohua e nānā i kahi laʻana o ka tumo o ka mea maʻi no kekahi ʻano loli. ʻO ke ʻano o ka hoʻomālama ʻia e hāʻawi ʻia i ka mea maʻi e pili ana i ka ʻano o ka loli.
- ʻO kahi hoʻokolohua hoʻokolohua o ka lāʻau i hoʻomoe ʻia (tazemetostat).
ʻO nā tumors cell epithelioid perivascular (PEComas)
ʻO ka mālama ʻana i nā tumors cell epithelioid perivascular e komo pū paha me kēia:
- ʻOki kino e wehe i ka hikoko.
- ʻO ka nānā ʻana ma hope o ke kaha ʻana.
- ʻO ka therapy target (sirolimus), no nā tumors i loaʻa kekahi mau loli a ʻaʻole hiki ke hemo ʻia e ke kaʻe.
Sarcoma i hoʻokaʻawale ʻia / Unclassified
ʻO ka sarcoma pleomorphic ponoʻole / malignant fibrous histiocytoma (kūlana kiʻekiʻe)
ʻAʻohe mālama maʻamau no kēia mau tumors.
E ʻike i ka hōʻuluʻulu ma Osteosarcoma a me Malignant Fibrous Histiocytoma o Bone Treatment no ka ʻike e pili ana i ka mālama ʻana i ka histocytoma fibrous malignant o ka iwi.
ʻO nā Tumors Kapuna Koko
Epithelioid hemangioendothelioma
ʻO ka mālama ʻana i ka epithelioid hemangioendothelioma hiki ke hoʻopili ʻia i kēia mau mea:
- Nānā.
- Hoʻopau ke ʻoki e wehe i ka tumer inā hiki.
- Immunotherapy (interferon) a me ka hoʻomōhala hoʻomōhala (thalidomide, sorafenib, pazopanib, sirolimus) no nā tumors e laha paha.
- ʻO Chemotherapy.
- Huina hepatectomy a me ke kuhi ʻana o ke ake i ka manawa o ka tumo i ke ake.
- ʻO kahi hoʻokolohua hoʻokolohua o ka lāʻau i hoʻomoe ʻia (trametinib).
Angiosarcoma o nā mea palupalu
Hiki i ka mālama ʻana i angiosarcoma ke hoʻopili i kēia mau mea:
- ʻO ke kaha e hemo loa ai ka tumo.
- Hoʻohui ʻia o ke kaha ʻana, chemotherapy, a me radiation therapy no angiosarcomas i pālahalaha ʻia.
- ʻO ka therapy target (bevacizumab) a me ka chemotherapy no angiosarcomas i hoʻomaka ma ke ʻano he hemangiomas pēpē.
- ʻO kahi hoʻokolohua hoʻokolohua o ka chemotherapy me a i ʻole me ka ʻole o ka lāʻau hoʻomoe (pazopanib).
- ʻO kahi hoʻokolohua hoʻokolohua o ka immunotherapy (nivolumab a me ipilimumab).
ʻO Tissue Sarcoma Pōʻino Metastatic
ʻO ka mālama ʻana i ka sarcoma palupalu o ka wā kamaliʻi i pālahalaha ʻia i nā ʻāpana ʻē aʻe o ke kino ma ke kuhi ʻana e komo pū paha me kēia:
- ʻO Chemotherapy a me radiation therapy. Hiki ke hana ʻoki e wehe i nā tumors i palahalaha aʻe i ka akemāmā.
- ʻO ka radiation radiation body Stereotactic no nā tumors i palahalaha aʻe i ka lung.
No ka mālama ʻana i nā ʻano tumo kikoʻī, e ʻike i nā koho Koina no ka ʻāpana Pahu Paʻa Pulu Tissue Sarcoma.
Nā koho lapaʻau no ka hoʻi pinepine a me ka holomua o ke kamaliʻi Tissue Sarcoma
Hoʻomaʻamaʻa ʻia i ka sarcoma palupalu o ka wā kamaliʻi e holomua a holomua paha i kēia mau mea:
- ʻO ke ʻoki kino e hemo ai i ka maʻi ʻaʻai i hoʻi mai i kahi i hana mua ai a i pāhola paha i ka akemāmā.
- ʻO ke ʻoki lāʻau e ukali ʻia e ka radiation radiation kūwaho a i ʻole ʻoloko, inā ʻaʻole i hāʻawi ʻia ʻia ka radiation radiation.
- ʻO ke keʻoki e wehe i ka lima a me ka wāwae me ka maʻi ʻaʻai, inā i hāʻawi ʻia ʻia ka radiation therapy.
- ʻO ke kaha me me ka ʻole o ka chemotherapy no ka sarcoma synovial hou.
- ʻO Chemotherapy.
- Hoʻolālā pahuhopu (pazopanib).
- Immunotherapy (pembrolizumab).
- ʻO ka radiation radiation body Stereotactic no ka maʻi ʻaʻai i pālahalaha ʻia i nā ʻāpana ʻē aʻe o ke kino, ʻo ia hoʻi ka akemāmā.
- ʻO kahi hoʻokolohua hoʻokolohua o kahi regima chemotherapy hou me me a i ʻole me ka lāʻau i hoʻomāka ʻia (pazopanib).
- ʻO kahi hoʻokolohua hoʻokolohua e nānā i kahi laʻana o ka tumo o ka mea maʻi no kekahi ʻano loli. ʻO ke ʻano o ka hoʻomālama ʻia e hāʻawi ʻia i ka mea maʻi e pili ana i ka ʻano o ka loli.
E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.
E aʻo hou e pili ana i ke kamaliʻi Tissue Sarcoma
No ka ʻike hou aku mai ka National Cancer Institute e pili ana i ka sarcoma palupalu o nā kamaliʻi, e ʻike i ka mea aʻe:
- ʻAoʻao Home Tissue Sarcoma Palapala
- Computers Tomography (CT) Scans a me ka maʻi ʻaʻai
- Ua ʻae ʻia nā lāʻau no Sarcoma Tissue Kaha
- ʻO nā Therapy Cancer i kau ʻia
- MyPART - ʻO kaʻu Pediatric a me nā mākua ʻo ka Launa Tumor Rare
No ka ʻike hou aku i ka maʻi ʻaʻai kamaliʻi a me nā kumuwaiwai maʻi ʻaʻai ʻē aʻe, e ʻike i ka mea aʻe:
- E pili ana i ka maʻi ʻaʻai
- Nā maʻi ʻōpio
- Huli ʻo Cure no ka hōʻole ʻana i nā maʻi ʻaʻai keiki
- Nā hopena hope loa o ka mālama ʻana no ka maʻi ʻaʻai kamaliʻi
- ʻO nā ʻōpio a me nā ʻōpio me ka maʻi ʻaʻai
- Nā keiki me ka maʻi ʻaʻai: He alakaʻi no nā mākua
- Ka maʻi ʻaʻai ma nā keiki a me nā ʻōpio
- Ke hoʻokū nei
- Ke kāohi nei i ka maʻi ʻaʻai
- Nā nīnau e nīnau ai i kāu kauka e pili ana i ka maʻi ʻaʻai
- No nā mea ola a me nā mea mālama