Types/retinoblastoma/patient/retinoblastoma-treatment-pdq

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Retinoblastoma Hoʻolaha Hoʻolaha

ʻO ka ʻike ākea e pili ana iā Retinoblastoma

NA MANA KUNI

  • ʻO Retinoblastoma kahi maʻi kahi e kū ai nā maʻi malignant (cancer) i loko o nā aʻa o ka retina.
  • Hana ʻia ʻo Retinoblastoma i nā ʻano hoʻoilina a me nā hoʻoilina ʻole.
  • Pono e mālama i nā ʻano ʻelua o ka retinoblastoma i ka ʻōlelo aʻoaʻo ʻaoʻao.
  • ʻO nā keiki me ka moʻolelo ʻohana o retinoblastoma e pono e nānā i nā maka e nānā ai no retinoblastoma.
  • ʻO ke keiki i loaʻa iā her retinoblastoma ka mea i hoʻonui i ka makaʻu o trilateral retinoblastoma a me nā maʻi ʻalapula
  • ʻO nā hōʻailona a me nā ʻōuli o retinoblastoma e komo pū me "pupil keʻokeʻo" a me ka ʻeha o ka maka a me ka ʻulaʻula.
  • Hoʻohana ʻia nā hoʻāʻo e nānā i ka retina e ʻike (loaʻa) a hōʻoia i ka retinoblastoma.
  • Kū kekahi mau kumu i ka wānana (kahi o ke ola ʻana) a me nā koho lapaʻau.

ʻO Retinoblastoma kahi maʻi kahi e kū ai nā maʻi malignant (cancer) i loko o nā aʻa o ka retina.

ʻO ka retina ke aʻalolo nerve e laina ana i loko o ka hope o ka maka. Hoʻomaopopo ka retina i ka māmā a hoʻouna i nā kiʻi i ka lolo ma o ka nerve optic.

ʻO Anatomy o ka maka, e hōʻike ana i ka waho a me loko o ka maka e like me ka sclera, cornea, iris, ciliary body, choroid, retina, vitreous humor, a me optic nerve. ʻO ka hoʻomākeʻaka vitreous kahi gel e hoʻopiha i ke kikowaena o ka maka.

ʻOiai retinoblastoma e hana i kēlā me kēia makahiki, hana pinepine ia i nā keiki ma mua o 2 mau makahiki. ʻO ka maʻi ʻaʻai ma hoʻokahi maka (unilateral) a i ʻole i nā maka ʻelua (bilateral). ʻAʻole hoʻolaha iki ʻo Retinoblastoma mai ka maka i nā aʻa kokoke a i ʻole nā ​​ʻāpana ʻē aʻe o ke kino.

ʻO Cavitary retinoblastoma kahi ʻano laha ʻole o retinoblastoma kahi e hana ʻia ai nā lua (hollow space) ma loko o ka tumo.

Hana ʻia ʻo Retinoblastoma i nā ʻano hoʻoilina a me nā hoʻoilina ʻole.

Manaʻo ʻia kahi keiki hoʻoilina o retinoblastoma keʻoiaʻiʻo kekahi o kēia mau mea:

  • Aia kekahi moʻolelo ʻohana o retinoblastoma.
  • Aia kekahi hoʻololi (hoʻololi) i ka gen RB1. Hiki ke hoʻoili ʻia ka hoʻololi ʻana i ka moʻokūʻauhau RB1 mai ka makua a i ke keiki a i ʻole hiki ke hana ʻia i ka hua manu a i ʻole sperm ma mua o ka hapai ʻana a ma hope koke paha o ka hāpai ʻana.
  • Aia kekahi meaʻoi aku ma mua o hoʻokahi tumo i ka maka a i ʻole aia he tumo i nā maka ʻelua.
  • Aia kekahi ʻōpū ma ka maka hoʻokahi a ʻoi aku ka liʻiliʻi o ke keiki ma mua o 1 makahiki.

Ma hope o ka hoʻoilina ʻana o retinoblastoma a me ka mālama ʻana, hiki ke hoʻomau i nā tumors hou no kekahi mau makahiki. ʻO nā hoʻokolohua maka maʻamau e nānā ai no nā tumors hou e hana maʻamau i kēlā me kēia 2 a 4 mau mahina no ka liʻiliʻi ma 28 mau mahina.

ʻO Retinoblastoma nonheritable retinoblastoma ʻaʻole ia ka ʻano hoʻoilina. ʻO ka hapa nui o nā hihia o retinoblastoma ka palapala nonheritable.

Pono e mālama i nā ʻano ʻelua o ka retinoblastoma i ka ʻōlelo aʻoaʻo ʻaoʻao.

Pono i nā mākua ke loaʻa i ka ʻōlelo aʻoaʻo kūlohelohe (kahi kūkākūkā me kahi loea i aʻo ʻia e pili ana i ka makaʻu o nā maʻi genetical) e kūkākūkā i ka hoʻāʻo ʻana i nā genetics e nānā no ka hoʻololi (hoʻololi) i ka gen RB1 Kūkākūkā pū kekahi me kahi kūkākūkā e pili ana i ka makaʻu o retinoblastoma no ke keiki a me nā kaikaina a me nā kaikuahine o ke keiki.

ʻO nā keiki me ka moʻolelo ʻohana o retinoblastoma e pono e nānā i nā maka e nānā ai no retinoblastoma.

Pono kahi keiki me ka moʻolelo o ka ʻohana o retinoblastoma i nā hoʻokolohua maka maʻamau e hoʻomaka ana i ke kakahiaka e nānā no retinoblastoma, ke ʻike ʻole ʻia ʻaʻohe o ke keiki ka loli RB1. ʻO ke kuhi mua ʻana o retinoblastoma ke kumu o ka hoʻomaʻemaʻe iki ʻana o ke keiki.

Pono nā kaikaina a me nā kaikuahine o ke keiki me retinoblastoma e nānā i nā maka e ka ophthalmologist a hiki i ka makahiki 3 a 5 mau makahiki, ke ʻike ʻole ʻia ʻaʻole ka kaikaina a kaikuahine paha i ka loli RB1.

ʻO ke keiki i loaʻa iā her retinoblastoma ka mea i hoʻonui i ka makaʻu o trilateral retinoblastoma a me nā maʻi ʻalapula

ʻO ke keiki me herin retinoblastoma ka mea i hoʻonui i ka makaʻu o kahi tumā pineal i ka lolo. Ke loaʻa ka retinoblastoma a me kahi tumo lolo i ka manawa like, ua kapa ʻia ʻo trilateral retinoblastoma. Hoʻomaopopo pinepine ʻia ka tumo lolo ma waena o 20 a me 36 mau makahiki o kou mau makahiki. Hiki ke hana ʻia ka kānana maʻamau me ka hoʻohana ʻana i ka MRI (imaging resonance imaging) no kahi keiki i manaʻo ʻia e loaʻa iā retinoblastoma hoʻoilina a i ʻole no kahi keiki me retinoblastoma i hoʻokahi maka a me ka moʻolelo ʻohana o ka maʻi. ʻAʻole hoʻohana pinepine ʻia ka CT (kamepiula tomography) no ka loiloi maʻamau i mea e hōʻole ai i ke keiki i ka radiation ʻana.

Hoʻonui pū ka heritable retinoblastoma i ka makaʻu o ke keiki i nā ʻano maʻi ʻē aʻe e like me ka maʻi ʻaʻa pūpū, maʻi ʻaʻa ʻai, a i ʻole melanoma i nā makahiki i hala. He mea nui ka hoʻāʻo pinepine ʻana.

ʻO nā hōʻailona a me nā ʻōuli o retinoblastoma e komo pū me "pupil keʻokeʻo" a me ka ʻeha o ka maka a me ka ʻulaʻula.

ʻO kēia a me nā ʻōuli a me nā ʻōuli ʻē aʻe i hopena ʻia e retinoblastoma a i ʻole nā ​​kūlana ʻē aʻe. E hōʻoia me ke kauka inā loaʻa i kāu keiki kekahi o kēia mau mea:

  • ʻIke keʻokeʻo ka maka o ka maka ma kahi o ka ʻulaʻula ke hoʻomālamalama ke kukui i loko. ʻIke ʻia paha kēia i nā paʻi uila o ke keiki.
  • Ke nānā nei nā maka i nā ʻaoʻao ʻokoʻa (maka palaualelo).
  • ʻEha a ʻulaʻula paha i ka maka.
  • ʻO ka maʻi a puni ka maka.
  • ʻOi aku ka nui o ka ʻōnaka ma mua o ka maʻamau.
  • ʻĀwili ʻāpana o ka maka a me ka haumāna.

Hoʻohana ʻia nā hoʻāʻo e nānā i ka retina e ʻike (loaʻa) a hōʻoia i ka retinoblastoma.

Hiki ke hoʻohana ʻia nā hoʻāʻo a me nā kaʻina hana aʻe:

  • ʻO ka hoʻāʻo kino a me ka mōʻaukala: kahi hōʻike o ke kino e nānā i nā hōʻailona laulā o ke olakino, e like me ka nānā ʻana i nā hōʻailona o ka maʻi, e like me nā puʻupuʻu a i ʻole nā ​​mea ʻē aʻe e ʻano ʻē. E lawe ʻia kahi moʻolelo o nā ʻano olakino o ka mea maʻi a me nā maʻi i hala a me nā mālama ʻana. E nīnau ke kauka inā aia kekahi moʻolelo ʻohana o retinoblastoma.
  • ʻO ka hoʻāʻo ʻana o ka maka me ka haumāna i hoʻomāhuahua ʻia : ʻO kahi hoʻokolohua o ka maka kahi e pāhola ʻia ai ka haumāna (wehe ākea) me nā kulu maka lāʻau e hiki ai i ke kauka ke nānā ma ka aniani a me ka haumāna i ka retina. Nānā ʻia ka loko o ka maka, me ka retina a me ke aʻalolo optic, me kahi kukui. Kaukaʻi ʻia i ka makahiki o ke keiki, hiki ke hana i kēia hōʻike ma lalo o ka anesthesia.

Aia kekahi mau ʻano o nā hoʻāʻo ʻana o ka maka i hana ʻia me ka haumāna i hoʻonui ʻia:

  • Ophthalmoscopy: kahi hoʻokolohua o loko o ka hope o ka maka e nānā i ka retina a me ke aʻalolo optic e hoʻohana ana i kahi aniani hoʻonui liʻiliʻi a me kahi kukui.
  • ʻO ka biomicroscopy Lamp-lamp: kahi hōʻike o loko o ka maka e nānā i ka retina, ke aʻalolo optic, a me nā ʻāpana ʻē aʻe o ka maka e hoʻohana ana i ka kukuna ikaika o ka mālamalama a me kahi microscope.
  • Fluorescein angiography: kahi hana e nānā ai i nā kīʻaha koko a me ke kahe o ke koko i loko o ka maka. Hoʻokomo ʻia kahi ʻalani fluorescent ʻalani i kapa ʻia ʻo fluorescein i loko o kahi kīʻaha koko i ka lima a hele i ke kahe o ke koko. Ke hele nei ke kala i loko o nā kīʻaha koko o ka maka, kahi kāmela kūikawā e kiʻi i nā kiʻi o ka retina a me choroid e ʻike i nā kīʻaha koko i ālai ʻia a i ʻole pū ʻia.
  • Hōʻike ʻāpana RB1: kahi hōʻike keʻena hoʻokolohua kahi e hoʻāʻo ʻia ai kahi laʻana o ke koko a i ʻole nā ​​mea i loaʻa no ka loli o ka ʻāpana RB1
  • ʻO ka hoʻokolohua ultrasound o ka maka: ʻO ke kaʻina hana kahi e kipaku ʻia ai nā nalu kani ikaika (ultrasound) mai nā aʻa o loko o ka maka e hana ai i nā leo. Hoʻohana ʻia nā kulu maka e kolo ai ka maka a kahi ʻimi iki e hoʻouna ai a loaʻa nā nalu kani e kau mālie ma luna o ka maka. Hana nā leo i ke kiʻi o loko o ka maka a ana ʻia ka mamao mai ke kōkō a i ka retina. ʻO ke kiʻi, i kapa ʻia he sonogram, e hōʻike ma ka papakaumaka o ka ultrasound monitor. Hiki ke paʻi ʻia ke kiʻi e nānā ma hope.
  • MRI (magnetic resonance imaging): Kahi hana e hoʻohana ai i ka magnet, nā nalu lekiō, a me kahi kamepiula e hana i nā kiʻi kikoʻī o nā wahi i loko o ke kino, e like me ka maka. Kāhea ʻia kēia kaʻina hana he kiʻi nukelea kiʻi resonance (NMRI).
  • CT scan (CAT scan): Kahi hana e hana ai i ka moʻo o nā kiʻi kikoʻī o nā wahi i loko o ke kino, e like me ka maka, i lawe ʻia mai nā ʻaoʻao ʻokoʻa. Hana ʻia nā kiʻi e kahi kamepiula i hoʻopili ʻia i kahi mīkini x-ray. Hoʻokomo ʻia paha ke kala i loko o ke aa a i ʻole ale ʻia e kōkua i nā ʻōpū a i ʻole nā ​​kino i hōʻike hou aku me ka maopopo. Kāhea ʻia kēia kaʻina hana he tomography i helu ʻia, kamepiula tomography, a i ʻole he tomography axial computerized.
ʻO ka scan tomography compute (CT) o ke poʻo a me ka ʻāʻī. Moe ke keiki ma ka papaʻaina e paheʻe ai i ka scanner CT, e kiʻi ana i nā kiʻi x-ray o loko o ke poʻo a me ka ʻāʻī.

Hiki ke ʻike maʻamau ʻia ʻo Retinoblastoma me ka ʻole o kahi biopsy.

Ke loaʻa ka retinoblastoma i hoʻokahi maka, hana ʻia i kekahi manawa i ka maka ʻē aʻe. Hana ʻia nā hoʻokolohua o ka maka maka ʻole a ʻike ʻia inā ʻo ka retinoblastoma ke ʻano hoʻoilina.

Kū kekahi mau kumu i ka wānana (kahi o ke ola ʻana) a me nā koho lapaʻau.

ʻO ka wānana (loaʻa o ke ola) a me nā koho lapaʻau e pili i kēia:

  • Inā ʻo ka maʻi ʻaʻai i hoʻokahi a i ʻole ʻelua mau maka.
  • Ka nui a me ka helu o nā tumors.
  • Inā ua pālahalaha ka tumo i ka wahi a puni ka maka, i ka lolo, a i ʻole nā ​​ʻāpana ʻē aʻe o ke kino.
  • Inā he mau ʻōuli i ka manawa o ke kuhi, no ka trinateral retinoblastoma.
  • Ka makahiki o ke keiki.
  • Pehea paha e hiki ai ke mālama i ka hihiʻo i hoʻokahi a ʻelua paha mau maka.
  • Inā ua hoʻokumu ʻia kahi ʻano maʻi ʻelua.

Nā pae o Retinoblastoma

NA MANA KUNI

  • Ma hope o ke kuhi ʻia ʻana o retinoblastoma, hana ʻia nā hoʻokolohua e ʻike inā ua pāhola nā hunaola maʻi ʻino i loko o ka maka a i ʻole nā ​​ʻāpana ʻē aʻe o ke kino.
  • Hiki ke hoʻohana ʻia ka International Retinoblastoma Staging System (IRSS) no ka hoʻonohonoho retinoblastoma.
  • Kahua 0
  • Ke kahua I
  • Kahua II
  • Kahua III
  • Kahua IV
  • ʻEkolu ala e hoʻolaha ai ka maʻi ʻaʻai i loko o ke kino.
  • E laha paha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i nā ʻāpana ʻē aʻe o ke kino.
  • ʻO ka mālama ʻana no retinoblastoma ma muli o ka intraocular (ma loko o ka maka) a i ʻole extraocular (ma waho o ka maka).
  • Retinoblastoma Intraocular
  • Extraocular retinoblastoma (metastatic)

Ma hope o ke kuhi ʻia ʻana o retinoblastoma, hana ʻia nā hoʻokolohua e ʻike inā ua pāhola nā hunaola maʻi ʻino i loko o ka maka a i ʻole nā ​​ʻāpana ʻē aʻe o ke kino.

ʻO ke kaʻina hana e ʻike inā ua pālahalaha ka maʻi ʻaʻai i loko o ka maka a i ʻole nā ​​ʻāpana ʻē aʻe o ke kino i kapa ʻia he staging. ʻO ka ʻikepili i hōʻiliʻili ʻia mai ke kaʻina hana e hoʻoholo inā retinoblastoma wale nō i ka maka (intraocular) a i ʻole ua pālahalaha ʻia ma waho o ka maka (extraocular). He mea nui ia e ʻike i ke kahua i mea e hoʻolālā ai i ka lāʻau. ʻO nā hopena o nā hoʻokolohua e hoʻohana ai e hōʻoia i ka maʻi ʻaʻai e hoʻohana pinepine ʻia e hoʻokumu i ka maʻi. (E ʻike i ka ʻikepili ʻike laulā.)

Hiki ke hoʻohana ʻia nā hoʻokolohua aʻe a me nā kaʻina hana i ke kaʻina hoʻonohonoho:

  • ʻImi iwi: kahi hana e nānā ai inā aia he wikiwiki e hoʻokaʻawale i nā hunaola, e like me nā hunaola maʻi ʻaʻai, i ka iwi. Hoʻokomo ʻia kahi mea liʻiliʻi loa o nā mea radioactive i loko o ke aa a hele i waena o ke kahe o ke koko. Hōʻiliʻili ka mea lekiō i nā iwi me ka maʻi ʻaʻai a ʻike ʻia e kahi scanner e kiʻi pū i ke kiʻi o ke kino. ʻOi aku ka mālamalama o nā wahi o ka iwi me ka maʻi ʻaʻai i ke kiʻi no ka mea lawe lākou i nā mea radioactive ma mua o ka hana ʻana o nā iwi iwi maʻamau.
ʻImi iwi. Hoʻokomo ʻia kahi mea liʻiliʻi o ka radioactive i ke aa o ke keiki a hele i loko o ke koko. Hōʻiliʻili ka mea lekiō i nā iwi. Ke moe nei ke keiki ma kahi pākaukau e heʻe ma lalo o ka scanner, ʻike ʻia ka mea radioactive a hana ʻia nā kiʻi ma ka papapihi kamepiula.
  • ʻO ka ʻiʻo o ka iwi iwi a me ka biopsy: Ka lawe ʻia ʻana o ka iwi iwi a me kahi ʻāpana o ka iwi ma ka hoʻokomo ʻana i kahi nila kuha i loko o ka hipbone a i ʻole ka umauma. ʻIke kahi pathologist i ka momona o ka iwi ma lalo o kahi microscope e nānā i nā hōʻailona o ka maʻi ʻaʻai. Hana ʻia kahi makemake o ka iwi iwi a me ka biopsy inā manaʻo ka kauka ua pālahalaha ka maʻi ʻaʻai ma waho o ka maka.
  • Lumbar puncture: kahi hana i hōʻiliʻili ʻia e hōʻiliʻili ai i ka wai cerebrospinal (CSF) mai ke kolamu iwi kuamoʻo. Hana ʻia kēia ma ke kau ʻana i kahi nila i waena o ʻelua iwi i ka iwi kuamoʻo a i loko o ka CSF a puni ka iwi kuamoʻo a hemo i kahi hāpana o ka wai. Nānā ʻia ka laʻana o ka CSF ma lalo o kahi microscope no nā ʻōuli i palahalaha ʻia ka maʻi ʻaʻai i ka lolo a me ka iwi kuamoʻo. Kāhea ʻia kēia kaʻina hana he LP a i ʻole ka piulawi.

Hiki ke hoʻohana ʻia ka International Retinoblastoma Staging System (IRSS) no ka hoʻonohonoho retinoblastoma.

Aia kekahi mau ʻōnaehana hoʻonohonoho no retinoblastoma. Hoʻokumu ʻia nā pae IRSS i ka nui o ka maʻi ʻaʻai i koe ma hope o ke kaha ʻana e wehe i ka tumo a inā paha ua pāhola ka maʻi ʻaʻai.

Kahua 0

Ma ka maka wale nō ka tumo. ʻAʻole i hemo ka maka a mālama ʻia ka tumo me ka hana ʻole ʻia.

Ke kahua I

Ma ka maka wale nō ka tumo. Ua hemo ka maka a ʻaʻohe pūnana maʻi ʻaʻai.

Kahua II

Ma ka maka wale nō ka tumo. Ua hoʻoneʻe ʻia ka maka a aia kekahi mau maʻi ʻaʻai i koe e hiki ke ʻike wale ʻia me kahi microscope.

Kahua III

Māhele ʻia ka pae III i nā pae IIIa a me IIIb:

  • I ke kahua IIIa, ua pālahalaha ka maʻi ʻaʻai mai ka maka a i nā ʻaʻa a puni ke kumu o ka maka.
  • I ke kahua IIIb, ua pālahalaha ka maʻi ʻaʻai mai ka maka a i nā lymph node kokoke i ka pepeiao a i ka ʻāʻī.

Kahua IV

Māhele ʻia ka pae IV i nā pae IVa a me IVb:

  • I ke kahua IVa, ua pāhola ka maʻi ʻaʻai i ke koko akā ʻaʻole naʻe i ka lolo a i ʻole ka iwi kuamoo. Ua pāhola paha kekahi a ʻoi aku paha i nā ʻāpana ʻē aʻe o ke kino e like me ka iwi a me ke akepaʻa.
  • I ke kahua IVb, ua pāhola ka maʻi ʻaʻai i ka lolo a i ʻole nā ​​iwi kuamoo. Ua pāhola paha ia i nā ʻāpana ʻē aʻe o ke kino.

ʻEkolu ala e hoʻolaha ai ka maʻi ʻaʻai i loko o ke kino.

Hiki ke pālahalaha ʻia ka maʻi ʻaʻai ma o nā meaola, ka ʻōnaehana lymph, a me ke koko.

  • Kāpena. Hoʻolahalaha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i ka ulu ʻana i nā wahi kokoke.
  • ʻŌnaehana Lymph. Hoʻolahalaha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i ke komo ʻana i ka ʻōnaehana lymph. Hele ka maʻi ʻaʻai ma o nā kīʻaha lymph i nā ʻāpana ʻē aʻe o ke kino.
  • Koko. Hoʻolahalaha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i ke komo ʻana i ke koko. Hele ka maʻi ʻaʻai ma o nā kīʻaha koko i nā ʻāpana ʻē aʻe o ke kino.

E laha paha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i nā ʻāpana ʻē aʻe o ke kino.

Ke pālahalaha ʻia ka maʻi ʻaʻai i kekahi ʻāpana o ke kino, ua kapa ʻia ia ʻo metastasis. E haki nā hunaola maʻi 'aʻai mai kahi a lākou i hoʻomaka ai (ka tumo mua) a hele i loko o ka ʻōnaehana lymph a i ʻole ke koko.

  • ʻŌnaehana Lymph. Komo ka maʻi ʻaʻai i loko o ka ʻōnaehana lymph, hele ma waena o nā kīʻaha lymph, a hana i kahi tumo (tumo metastatic) i kekahi ʻāpana o ke kino.
  • Koko. Komo ke kanesa i loko o ke koko, hele ma waena o nā kīʻaha koko, a hana i kahi tumo (tumo metastatic) i kekahi ʻāpana o ke kino.

ʻO ka tumo metastatic ka ʻano like o ke kanesa me ka tumo mua. ʻO kahi laʻana, inā pālahalaha ka retinoblastoma i ka iwi, ʻo nā hunaola maʻi ʻaʻai i ka iwi ka retinoblastoma mau ʻea. ʻO ka retinoblastoma metastatic ka maʻi, ʻaʻole ka maʻi ʻaʻa iwi.

ʻO ka mālama ʻana no retinoblastoma ma muli o ka intraocular (ma loko o ka maka) a i ʻole extraocular (ma waho o ka maka).

Retinoblastoma Intraocular

I ka retinoblastoma intraocular, loaʻa ka maʻi ʻaʻai i hoʻokahi a i ʻole ʻelua mau maka a aia paha ma ka retina wale nō a i ʻole ma nā ʻāpana ʻē aʻe o ka maka e like me ka choroid, ciliary kino, a i ʻole kekahi ʻāpana o ke aʻa optic. ʻAʻole i pālahalaha ka maʻi ʻaʻai i nā aʻa a puni ka maka o ka maka a i ʻole nā ​​ʻāpana ʻē aʻe o ke kino.

Extraocular retinoblastoma (metastatic)

I ka retinoblastoma extraocular, ua pālahalaha ka maʻi ʻaʻai ma ʻō aku o ka maka. ʻIke ʻia paha i loko o nā kinona a puni ka maka (orbital retinoblastoma) a i ʻole pāhola paha i ke kikowaena pūnaewele (lolo a me ka iwi kuamoo) a i ʻole nā ​​ʻāpana ʻē aʻe o ke kino e like me ke ake, nā iwi, ka iwi iwi, a me nā lymph node.

Retinoblastoma holomua a hoʻi hou

ʻO retinoblastoma holomua kahi retinoblastoma e pane ʻole i ka lāʻau. Ma kahi o ka ulu ʻana o ka maʻi ʻaʻai, hohola, a i ʻole lilo i ʻino.

ʻO Retinoblastoma hou ka maʻi ʻaʻai i hoʻi hou (hoʻi) ma hope o ka mālama ʻia ʻana. Hiki paha ke kanesa i ka maka, i nā mea a puni ka maka, a i ʻole nā ​​wahi ʻē aʻe o ke kino.

Laulā Manaʻo Option Oponopono

NA MANA KUNI

  • Aia nā ʻano lapaʻau like ʻole no nā mea maʻi me retinoblastoma.
  • Pono nā kamaliʻi me retinoblastoma i kā lākou lapaʻau e kekahi hui o nā lawelawe mālama ola i loea i ka mālama ʻana i ka maʻi ʻaʻai i nā keiki.
  • ʻO ka mālama ʻana no retinoblastoma ke kumu o nā hopena.
  • Hoʻohana ʻia ʻeono ʻano o ka mālama maʻamau.
  • ʻO Cryotherapy
  • Thermotherapy
  • ʻO Chemotherapy
  • Lapaʻau hoʻomākala
  • ʻO ka chemotherapy kiʻekiʻe loa me ka hoʻopakele ʻana o ka cell stem
  • ʻOki kino (enucleation)
  • Ke hoʻāʻo ʻia nei nā ʻano lapaʻau hou i nā hoʻokolohua hoʻokolohua.
  • Pahuhopu kau ʻia
  • Makemake paha nā mea maʻi e noʻonoʻo e pili ana i ka hoʻokolokolo ʻana.
  • Hiki i nā mea maʻi ke komo i nā hoʻokolohua hoʻokolohua ma mua, i ka wā, a ma hope paha o ka hoʻomaka ʻana i kā lākou mālama maʻi ʻaʻai.
  • Pono paha nā hoʻokolohua ukali.

Aia nā ʻano lapaʻau like ʻole no nā mea maʻi me retinoblastoma.

Loaʻa nā ʻano lapaʻau like ʻole no nā mea maʻi me retinoblastoma. Kūlana maʻamau kekahi mau hōʻailona (ʻo ka lāʻau i hoʻohana ʻia i kēia manawa), a ʻo kekahi e hoʻāʻo ʻia nei i nā hoʻokolohua hoʻokolohua. ʻO kahi hoʻokolohua hoʻokolohua lapaʻau kahi noiʻi noiʻi i manaʻo ʻia e kōkua i ka hoʻomaikaʻi ʻana i nā mālama ʻana i kēia manawa a i ʻole loaʻa ka ʻike e pili ana i nā mālama hou no nā maʻi me ka maʻi ʻaʻai. Ke hōʻike nā hoʻokolohua hoʻokolohua ʻoi aku ka maikaʻi o kahi lapaʻau hou ma mua o ka maʻamau maʻamau, lilo paha ka lāʻau hou i ka lapaʻau maʻamau.

Ma muli o ka loaʻa ʻole o ka maʻi ʻaʻai i nā keiki, pono e noʻonoʻo ʻia i ka hoʻokolokolo ʻana. ʻO kekahi mau hoʻokolohua hoʻokolohua e hāmama wale i nā mea maʻi i hoʻomaka ʻole i ka lāʻau.

Pono nā kamaliʻi me retinoblastoma i kā lākou lapaʻau e kekahi hui o nā lawelawe mālama ola i loea i ka mālama ʻana i ka maʻi ʻaʻai i nā keiki.

ʻO nā pahuhopu o ka mālama ʻana e mālama i ke ola o ke keiki, e mālama i ka ʻike a me ka maka, a pale i nā hopena koʻikoʻi. E mālama ʻia ka lapaʻau ʻana e kahi oncologist pediatric, he kauka i loea i ka mālama ʻana i nā keiki me ka maʻi ʻaʻai. Hana ka oncologist pediatric me nā mea lawelawe olakino ʻē aʻe i loea i ka mālama ʻana i nā keiki me ka maʻi ʻaʻai maka a i loea i kekahi mau wahi o ka lāʻau. Hoʻopili paha kēia i kahi ophthalmologist pediatric (kauka maka o nā keiki) nona ka ʻike he nui i ka mālama ʻana i ka retinoblastoma a me nā loea e hiki mai ana.

  • Kauka ʻōpio.
  • Oncologist uila.
  • Kahuna Pediatrician.
  • ʻO ka loea kahu maʻi Pediatric.
  • Lapaʻau hoʻōla.
  • Limahana limahana.
  • Geneticist a i ʻole kākāʻōlelo aʻoaʻo.

ʻO ka mālama ʻana no retinoblastoma ke kumu o nā hopena.

No ka ʻike e pili ana i nā hopena i hoʻomaka i ka wā o ka mālama ʻana no ka maʻi ʻaʻai, ʻike i kā mākou ʻaoʻao ʻaoʻao ʻaoʻao.

ʻO nā hopena ʻē aʻe mai ka mālama ʻana i ka maʻi ʻaʻai e hoʻomaka ma hope o ka mālama ʻana a hoʻomau no nā mahina a i ʻole mau makahiki e kapa ʻia nā hopena hopena. ʻO nā hopena hope loa o ka mālama ʻana no retinoblastoma e hoʻopili pū i kēia mau mea:

  • Nā pilikia o ke kino e like me ka ʻike ʻana a i ʻole ka hoʻolohe ʻana i nā pilikia a i ʻole, inā hemo ka maka, kahi hoʻololi o ke ʻano a me ka nui o ka iwi a puni ka maka.
  • Nā loli i ke ʻano, nā manaʻo, ka noʻonoʻo, ke aʻo ʻana, a me ka hoʻomanaʻo paha.
  • ʻO nā maʻi ʻelua (nā ʻano ʻē aʻe o ka maʻi ʻaʻai), e like me ka maʻi ʻaʻai a me ka maʻi ʻaʻai, osteosarcoma, sarcoma palupalu, a melanoma paha.

ʻO nā kumuhana pilikia aʻe e hoʻonui i ka makaʻu o ka loaʻa ʻana i kahi maʻi ʻaʻai ʻē aʻe:

  • Loaʻa iā ia ka hana hoʻoilina o retinoblastoma.
  • ʻO ka hana i hala me ka radiation radiation, ʻoiai ma mua o ka makahiki 1.
  • Loaʻa i kahi maʻi maʻi ʻelua i hala.

He mea nui e kamaʻilio pū me nā kauka o kāu keiki e pili ana i nā hopena o ka mālama ʻana i ka maʻi ʻaʻai i kāu keiki. ʻO ka ukali maʻamau e nā ʻoihana olakino he loea i ka diagnose a me ka mālama ʻana i nā hopena hopena he mea nui. E ʻike i ka hōʻuluʻulu e pili ana i nā hopena hope o ka mālama ʻana no ka maʻi ʻaʻai kamaliʻi no ka ʻike hou aku.

Hoʻohana ʻia ʻeono ʻano o ka mālama maʻamau.

ʻO Cryotherapy

He lāʻau lapaʻau ʻo Cryotherapy e hoʻohana i kahi mea kani e hoʻopaʻa ai a luku hoʻi i nā kiko ʻole. Kāhea ʻia kēia ʻano lapaʻau ʻo cryosurgery.

Thermotherapy

ʻO Thermotherapy ka hoʻohana o ka wela e luku i nā hunaola maʻi ʻaʻai. Hāʻawi ʻia ka Thermotherapy me ka hoʻohana ʻana i kahi kukuna kukuna i kuhikuhi ʻia ma o ka haumāna ākea a i ʻole ma waho o ka ʻōmaka. Hoʻohana wale ʻia ka Thermotherapy no nā tumors liʻiliʻi a i ʻole hui ʻia me chemotherapy no nā tumors ʻoi aku ka nui. ʻO kēia ʻano lapaʻau he ʻano laser therapy.

ʻO Chemotherapy

ʻO Chemotherapy kahi lāʻau lapaʻau maʻi maʻi e hoʻohana i nā lāʻau e hōʻoki i ka ulu ʻana o nā hunaola maʻi ʻaʻai, ma ka luku ʻana i nā hunaola a i ʻole ke kāpae ʻana iā lākou mai ka hoʻokaʻawale. Hāʻawi ke ala o ka chemotherapy i ka pae o ka maʻi ʻaʻai a me kahi o ka maʻi ʻaʻai i loko o ke kino.

Aia kekahi mau ʻano chemotherapy:

  • ʻO ka chemotherapy ʻōnaehana: ke lawe ʻia ka chemotherapy e ka waha a i ʻole injected ʻia i loko o kahi aa a i ʻole nā ​​mākala, komo nā lāʻau i ke kahe o ke koko a hiki ke hōʻea i nā hunaola kanesa a puni ke kino. Hāʻawi ʻia ka chemotherapy ʻōnaehana e hoʻoliʻiliʻi i ka tumo (chemoreduction) a pale i ke kaha ʻana e hemo ai ka maka. Ma hope o ka chemoreduction, hiki i nā ʻano lāʻau ʻē aʻe ke hoʻopili i ka radiation radiation, cryotherapy, laser therapy, a me chemotherapy ʻāina.

Hiki ke hāʻawi ʻia i kahi chemotherapy ʻōnaehana e pepehi i nā hunaola maʻi ʻea i waiho ʻia ma hope o ka lapaʻau mua a i nā mea maʻi me retinoblastoma e kū ana ma waho o ka maka. ʻO ka lāʻau i hāʻawi ʻia ma hope o ka hana mua, e hoʻohaʻahaʻa i ka hopena o ka maʻi ʻaʻai e hoʻi mai, ua kapa ʻia ʻo adjuvant therapy.

  • ʻO ka chemotherapy āpana: ke kau pololei ʻia ka chemotherapy i loko o ka wai cerebrospinal (chemotherapy intrathecal), kahi ʻokana (e like me ka maka), a i ʻole he kino o ke kino, pili ka lāʻau i nā hunaola maʻi ʻaʻai i kēlā mau wahi. Hoʻohana ʻia kekahi mau ʻano chemotherapy āpana e mālama iā retinoblastoma.
  • Ophthalmic artery infusion chemotherapy: ʻo Ophthalmic artery infusion chemotherapy e lawe pololei i nā lāʻau anticancer i ka maka. Hoʻokomo ʻia kahi catheter i loko o ka artery a hiki i ka maka a hāʻawi ʻia ka lāʻau anticancer ma o ka catheter. Ma hope o ka hāʻawi ʻia ʻana o ka lāʻau, hiki ke hoʻokomo ʻia i kahi pāluna liʻiliʻi i loko o ke aʻa e ālai iā ia a mālama i ka hapa nui o ka lāʻau anticancer i paʻa ma kahi kokoke i ka tumo. Hiki ke hāʻawi ʻia kēia ʻano chemotherapy ma ke ʻano he lapaʻau mua ke loaʻa ka tumo i ka maka wale a i ʻole ke pane ʻole o ka tumo i nā ʻano lapaʻau ʻē aʻe. Hāʻawi ʻia ka chemotherapy ophthalmic arusion infusion i nā kikowaena lapaʻau retinoblastoma kūikawā.
  • Intravitreal chemotherapy: ʻo Intravitreal chemotherapy ka injection o nā lāʻau anticancer pololei i loko o ka hoʻomākeʻaka vitreous (like jelly) i loko o ka maka. Hoʻohana ʻia ia e mālama i ka maʻi ʻaʻai i pālahalaha ʻia i ka hoʻomākeʻaka vitreous a ʻaʻole i pane i ka lāʻau a hoʻi mai paha ma hope o ka lapaʻau.

E ʻike i nā lāʻau i ʻae ʻia no Retinoblastoma no ka ʻike hou aku.

Lapaʻau hoʻomākala

ʻO ka radiation radiation kahi lāʻau maʻi maʻi maʻi e hoʻohana i nā kukuna x nui ikaika a i ʻole nā ​​ʻano radiation e hoʻomake i nā hunaola maʻi ʻaʻai a mālama ʻole paha i ka ulu ʻana. ʻElua ʻano o radiation radiation:

  • Hoʻohana ka radiation radiation kūwaho i kahi mīkini ma waho o ke kino e hoʻouna i ka radiation i ka maʻi ʻaʻai. Hiki i kekahi mau ala o ka hāʻawi ʻana i ka radiation therapy ke pale i ka radiation mai ka hōʻino ʻana i nā mea olakino kokoke. ʻO kēia ʻano ʻano radiation radiation me kēia:
  • Hoʻoikaika radiation-modulated radiation therapy (IMRT): IMRT kahi ʻano 3-dimensional (3-D) radiation radiation kūwaho e hoʻohana nei i kahi kamepiula e hana i nā kiʻi o ka nui a me ke ʻano o ka tumo. ʻO nā kaola lahilahi o ka pāhawewe o nā ʻokoʻa ʻokoʻa (ikaika) e kuhikuhi ʻia i ka tumo mai nā kihi he nui.
  • Hoʻomaʻo radiation radiation Proton-beam: He ʻano ikaika nui ka Proton-beam therapy. Hoʻopaʻa kahi mīkini radiation radiation i nā kahawai o nā protons (nā liʻiliʻi, ʻike ʻole ʻia, nā ʻikikikaʻi i hoʻopiʻi ʻia) i nā hunaola maʻi ʻino e pepehi iā lākou.
  • Hoʻohana ka radiation radiation i loko i kahi lāʻau radioactive i hoʻopaʻa ʻia i nā nila, nā hua, nā uea, a i ʻole nā ​​catheters i kau pololei ʻia i loko a kokoke paha i ka maʻi ʻaʻai. Hiki i kekahi mau ala o ka hāʻawi ʻana i ka radiation therapy ke pale i ka radiation mai ka hōʻino ʻana i nā mea olakino kokoke. Hiki i kēia ʻano radiation radiation internal i kēia aʻe:
  • Pākuʻi radiotherapy: Hoʻopili nā hua radioactive i kekahi ʻaoʻao o kahi diski, i kapa ʻia he pālaki, a kau pono ʻia ma ka paia waho o ka maka kokoke i ka tumo. ʻO ka ʻaoʻao o ka pālaha me nā hua ma luna ke alo i ke kinipōpō, e kuhikuhi ana i ka pāhawewe ma ka tumo Kōkua ka plake i ka pale ʻana i nāʻiʻo kokoke mai mai ka pāhawewe.
Pākuʻi radiotherapy o ka maka. Ke ʻano o ka radiation radiation i hoʻohana ʻia e mālama ai i nā tumors o ka maka. Hoʻonoho ʻia nā ʻano radioactive ma kekahi ʻaoʻao o kahi ʻāpana lahilahi o ka mea hao (maʻa mau ke gula) i kapa ʻia he pālaki. Humuhumu ʻia ka plake ma ka paia o waho o ka maka. Hāʻawi nā hua i ka radiation e make ai i ka maʻi ʻaʻai. Lawe ʻia ka pālolo ma ka hopena o ka mālama ʻana, a he mau no nā lā he nui.

Hāʻawi ʻia ke ala o ka radiation therapy i ka ʻano a me ke kahua o ka maʻi ʻaʻai e mālama ʻia ai a pehea i pane ai ka maʻi ʻaʻai i nā ʻano lāʻau ʻē aʻe. Hoʻohana ʻia ka radiation radiation kūwaho a me loko e mālama iā retinoblastoma.

ʻO ka chemotherapy kiʻekiʻe loa me ka hoʻopakele ʻana o ka cell stem

Hāʻawi ʻia nā lāʻau kiʻekiʻe o ka chemotherapy e pepehi i nā hunaola maʻi ʻaʻai. Hoʻopau pū ʻia nā hunaola olakino, e like me nā hunaola koko, e ka lāʻau maʻi ʻaʻai. ʻO ka hoʻopakele ʻana i ka pūnaeho he lāʻau lapaʻau e pani i nā hunaola koko. Lawe ʻia nā hunaola (ʻaʻaʻa koko ʻole) mai ke koko a i ʻole ka iwi o ka mea maʻi a paʻa a mālama ʻia. Ma hope o ka pau ʻana o ka chemotherapy i ka mea hoʻomanawanui, hoʻoheheʻe ʻia nā pūnaewele i mālama ʻia a hoʻihoʻi ʻia i ka mea maʻi ma o ka infusion. E ulu kēia mau hunaola i (a hoʻihoʻi) i nā huna koko o ke kino.

E ʻike i nā lāʻau i ʻae ʻia no Retinoblastoma no ka ʻike hou aku.

ʻOki kino (enucleation)

ʻO ka Enucleation kahi ʻoki e wehe i ka maka a me kahi ʻāpana o ke aʻalolo optic. E nānā ʻia kahi laʻana o ka maka o ka maka i hemo ʻia ma lalo o kahi microscope e ʻike ai inā aia kekahi mau hōʻailona e lele paha ka maʻi ʻaʻai i nā ʻāpana ʻē aʻe o ke kino. Pono e hana i kēia mea e ka pathologist ʻike, ka mea kamaʻāina me retinoblastoma a me nā maʻi ʻē aʻe o ka maka. Hana ʻia ka hoʻouluulu inā liʻiliʻi a ʻaʻohe paha manawa hiki ke mālama ʻia ka hihiʻo a ke nui ka tumo, ʻaʻole i pane i ka lāʻau, a hoʻi mai paha ma hope o ka lapaʻau. Hoʻokomo ʻia ka mea maʻi no ka maka kuʻi.

Pono ka ukali kokoke no 2 mau makahiki a ʻoi paha e nānā i nā hōʻailona o ka hoʻi hou ʻana ma ka wahi a puni ka maka i hoʻopilikia ʻia a e nānā i ka maka ʻē aʻe.

Ke hoʻāʻo ʻia nei nā ʻano lapaʻau hou i nā hoʻokolohua hoʻokolohua.

Hōʻike kēia ʻāpana hōʻuluʻulu manaʻo i nā mālama e hoʻopaʻa ʻia nei i nā hoʻokolohua hoʻokolohua. ʻAʻole paha ia e ʻōlelo i kēlā me kēia lapaʻau hou e hoʻopaʻa ʻia ana. Loaʻa nā ʻike e pili ana i nā hoʻokolohua hoʻokolohua mai ka pūnaewele NCI.

Pahuhopu kau ʻia

ʻO ka therapy target kahi ʻano lapaʻau e hoʻohana i nā lāʻau a i ʻole nā ​​mea ʻē aʻe e hoʻouka aku i nā hunaola maʻi ʻaʻai. Hoʻolālā pinepine nā mea i hoʻomākaukau ʻia i ka hōʻemi ʻana i nā hunaola maʻamau ma mua o ka chemotherapy a i ʻole radiation radiation.

Ke aʻo ʻia nei ka lāʻau i hoʻomākaukau ʻia no ka mālama ʻana i retinoblastoma i hoʻi hou (hoʻi hou).

Makemake paha nā mea maʻi e noʻonoʻo e pili ana i ka hoʻokolokolo ʻana.

No kekahi mau mea maʻi, ke komo nei i ka hoʻokolohua hoʻokolohua ke koho lapaʻau maikaʻi loa paha. ʻO nā hoʻokolohua hoʻokolohua kahi ʻāpana o ka noiʻi ʻana o ka maʻi ʻaʻai. Hana ʻia nā hoʻokolohua hoʻokolohua e ʻike inā palekana a maikaʻi a maikaʻi paha nā hoʻomaʻamaʻa maʻi ʻaʻai ma mua o ka maʻamau maʻamau.

ʻO ka hapa nui o nā hana maʻamau no ka maʻi ʻaʻai i kau ʻia ma nā hoʻokolohua hoʻokolohua mua. ʻO nā mea maʻi i komo i ka hoʻokolokolo hoʻokolohua hiki ke loaʻa i ka lāʻau maʻamau a i ʻole i waena o nā mea mua i loaʻa kahi lāʻau hou.

ʻO nā mea maʻi i komo i nā hoʻokolohua hoʻokolohua kōkua pū kekahi i ka hoʻomaikaʻi ʻana i ke ʻano o ka mālama ʻana i ka maʻi ʻaʻai i ka wā e hiki mai ana. ʻOiai ʻaʻole nā ​​alakaʻi hoʻokolohua e alakaʻi i nā hoʻoponopono hou maikaʻi, pane pinepine lākou i nā nīnau nui a kōkua i ka neʻe i mua o ka noiʻi.

Hiki i nā mea maʻi ke komo i nā hoʻokolohua hoʻokolohua ma mua, i ka wā, a ma hope paha o ka hoʻomaka ʻana i kā lākou mālama maʻi ʻaʻai.

Hoʻopili wale kekahi mau hoʻokolohua hoʻokolohua i nā mea maʻi i loaʻa ʻole ka lapaʻau. ʻO nā hoʻokolohua ʻē aʻe e hōʻoia i nā mālama ʻana no ka poʻe maʻi i loaʻa ʻole ka maikaʻi o ka maʻi ʻaʻai. Aia kekahi mau hoʻokolohua hoʻokolohua e hoʻāʻo i nā ala hou e hōʻoki i ka maʻi ʻaʻai mai ka hoʻi hou ʻana (hoʻi ʻana) a hōʻemi paha i nā hopena o ka mālama ʻana i ka maʻi ʻaʻai.

Ke mālama ʻia nei nā hoʻokolohua hoʻokolohua ma nā wahi he nui o ka ʻāina. Hiki ke ʻike ʻia ka ʻike e pili ana i nā hoʻokolohua hoʻokolohua e kākoʻo ʻia e NCI ma ka pūnaewele ʻimi noiʻi hoʻokolohua a NCI. Hiki ke loaʻa nā hoʻokolohua hoʻokolohua i kākoʻo ʻia e nā hui ʻē aʻe ma ka pūnaewele ClinicalTrials.gov.

Pono paha nā hoʻokolohua ukali.

ʻO kekahi o nā hoʻokolohua i hana ʻia e hōʻoia i ka maʻi ʻaʻai a i ʻole e ʻike i ke kahua o ka maʻi ʻaʻaʻa e hana hou ʻia paha. E hana hou ʻia kekahi mau hōʻike i mea e ʻike ai i ka maikaʻi o ka mālama ʻana. Hoʻoholo ʻia nā hoʻoholo e pili ana inā e hoʻomau, hoʻololi, a kū paha i ka lāʻau ʻana ma nā hopena o kēia mau hoʻāʻo.

E hoʻomau ʻia kekahi o nā hoʻokolohua mai kēlā me kēia manawa ma hope o ka pau ʻana o ka lāʻau. Hiki i nā hopena o kēia mau hoʻāʻo ke hōʻike inā ua loli ke ʻano o kāu keiki a i ʻole ua hoʻi hou ke kanesa. Kapa ʻia kēia mau hoʻāʻo i kekahi manawa nā hoʻokolohua ukali a i ʻole nā ​​loiloi.

Nā koho lapaʻau no Retinoblastoma

Ma keia Pauku

  • Ka mālama ʻana i ka Unilateral, Bilateral, a me ka Cavitary Retinoblastoma
  • Lapaʻau o Extraocular Retinoblastoma
  • Ka mālama ʻana i ka Retinoblastoma Holomua a Holomua paha

No ka ʻike e pili ana i nā lāʻau i helu ʻia ma lalo, e ʻike i ka ʻaoʻao Overtion Option Overview.

Ka mālama ʻana i ka Unilateral, Bilateral, a me ka Cavitary Retinoblastoma

Inā hiki ke mālama ʻia ka maka, hiki i ka mālama ʻana ke hoʻopili i kēia mau mea:

  • ʻO ka chemotherapy ʻōnaehana a i ʻole ka ophthalmic artery infusion chemotherapy, me a i ʻole me ka ʻole o ka chemotherapy intravitreal, e hoʻoliʻiliʻi i ka tumo. E ukali ʻia paha kēia e kekahi a ʻoi paha o kēia mau mea:
  • ʻO Cryotherapy.
  • Thermotherapy.
  • Pā radiotherapy.
  • ʻO ka radiation radiation kūwaho no ka retinoblastoma intraocular bilateral e pane ʻole i nā ʻano lāʻau ʻē aʻe.

Inā nui ka tumo a ʻaʻole paha he hiki i ka maka ke hoʻopakele, hiki i ka mālama ʻana ke hoʻopili i kēia mau mea:

  • ʻOki kino (enucleation). Ma hope o ke kaha ʻana, hiki ke hāʻawi ʻia i ka chemotherapy ʻōnaehana e hoʻohaʻahaʻa i ka makaʻu e laha ka maʻi ʻaʻai i nā ʻāpana ʻē aʻe o ke kino.

Ke loaʻa ka retinoblastoma i nā maka ʻelua, ʻokoʻa paha ka mālama ʻana i kēlā me kēia maka, kaukaʻi ʻia i ka nui o ka tumo a inā paha e hiki ke hoʻopakele ka maka. Hoʻokumu pinepine ʻia ka lāʻau o chemotherapy ʻōnaehana ma ka maka i ʻoi aku ka maʻi ʻaʻai.

ʻO ka mālama ʻana no ka retinoblastoma cavitary, kahi ʻano o intraocular retinoblastoma, hiki ke hoʻopili ʻia i kēia mau mea:

  • ʻO ka chemotherapy ʻōnaehana a i ʻole chemotherapy infusion artery infusion.

E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.

Lapaʻau o Extraocular Retinoblastoma

ʻO ka mālama ʻana no retinoblastoma extraocular i palahalaha aʻe i ka wahi a puni ka maka e hoʻopili pū paha i kēia mau mea:

  • ʻO ka chemotherapy ʻōnaehana a me ka radiation radiation kūwaho.
  • ʻO ka chemotherapy ʻōnaehana i ukali ʻia e ke kahakaha (enucleation). Hiki ke hāʻawi ʻia i ka radiation radiation kukulu a me nā chemotherapy hou aʻe ma hope o ke kaha.

ʻO ka mālama ʻana no retinoblastoma extraocular i palahalaha aʻe i ka lolo e pili pū paha me kēia:

  • ʻO chemotherapy ʻōnaehana a i ʻole intrathecal.
  • ʻO ka radiation radiation kūwaho i ka lolo a me ka iwi kuamoo.
  • ʻO Chemotherapy a ukali ʻia e ka chemotherapy lāʻau kiʻekiʻe me ka hoʻopakele ʻana o ka cell stem.

ʻAʻole maopopo inā ka hoʻomaʻamaʻa ʻana me chemotherapy, radiation radiation, a chemotherapy kiʻekiʻe loa me ka hoʻopakele cell cell e kōkua i nā mea maʻi me retinoblastoma extraocular e ola hou.

No retinoblastoma trilateral, hiki i ka mālama ke hoʻopili i kēia mau mea:

  • ʻO ka chemotherapy ʻōnaehana e ukali ʻia e ka chemotherapy o ka lāʻau kiʻekiʻe me ka hoʻopakele ʻana i ka pūnaukū
  • ʻO ka chemotherapy ʻōnaehana e ukali ʻia e ke ʻoki a me ka radiation radiation kūwaho.

No retinoblastoma i pālahalaha aʻe i nā ʻāpana ʻē aʻe o ke kino, akā ʻaʻole ka lolo, hiki i ka mālama ke hoʻopili i kēia mau mea:

  • ʻO Chemotherapy a ukali ʻia e ka chemotherapy kiʻekiʻe loa me ka hoʻopakele ʻana o ka cell stem a me ka radiation radiation waho.

E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.

Ka mālama ʻana i ka Retinoblastoma Holomua a Holomua paha

ʻO ka mālama ʻana i ka retinoblastoma intraocular Holomua a i ʻole hoʻi hou paha e hoʻopili i kēia mau mea:

  • ʻO ka radiation radiation kūwaho a me ka radiotherapy plaque.
  • ʻO Cryotherapy.
  • Thermotherapy.
  • ʻO ka chemotherapy ʻōnaehana a i ʻole chemotherapy infusion artery infusion.
  • ʻO ka chemotherapy Intravitreal.
  • ʻOki kino (enucleation).

ʻO kahi hoʻokolohua hoʻokolohua e nānā i kahi laʻana o ka tumo o ka mea maʻi no kekahi ʻano loli. ʻO ke ʻano o ka hoʻomālama ʻia e hāʻawi ʻia i ka mea maʻi e pili ana i ka ʻano o ka loli. ʻO ka mālama ʻana i ka retinoblastoma extraocular holomua a hoʻi hou paha i kēia mau mea:

  • ʻO ka chemotherapy ʻōnaehana a me ka radiation radiation radiation kūwaho no retinoblastoma i hoʻi mai ma hope o ke kahakaha ʻana e hemo ai ka maka.
  • ʻO ka chemotherapy ʻōnaehana e ukali ʻia e ka chemotherapy kiʻekiʻe loa me ka hoʻopakele ʻana o ka cell stem a me ka radiation radiation waho.
  • ʻO kahi hoʻokolohua hoʻokolohua e nānā i kahi laʻana o ka tumo o ka mea maʻi no kekahi ʻano loli. ʻO ke ʻano o ka hoʻomālama ʻia e hāʻawi ʻia i ka mea maʻi e pili ana i ka ʻano o ka loli.

E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.

E aʻo hou e pili ana i ka maʻi ʻaʻai kamaliʻi

No ka ʻike hou aku mai ka National Cancer Institute e pili ana i ka mālama ʻana o retinoblastoma, e ʻike i kēia:

  • ʻAoʻao Home Retinoblastoma
  • Computers Tomography (CT) Scans a me ka maʻi ʻaʻai
  • ʻO Cryosurgery i ka mālama ʻana i ka maʻi ʻaʻai: Nā nīnau a me nā pane
  • Ua ʻae ʻia nā lāʻau no Retinoblastoma
  • Ke hoʻāʻo genetic no ka hoʻoilina hoʻoilina maʻi maʻi maʻi Syndromes

No ka ʻike hou aku i ka maʻi ʻaʻai kamaliʻi a me nā kumuwaiwai maʻi ʻaʻai ʻē aʻe, e ʻike i ka mea aʻe:

  • E pili ana i ka maʻi ʻaʻai
  • Nā maʻi ʻōpio
  • Huli ʻo Cure no ka hōʻole ʻana i nā maʻi ʻaʻai keiki
  • Nā hopena hope loa o ka mālama ʻana no ka maʻi ʻaʻai kamaliʻi
  • ʻO nā ʻōpio a me nā ʻōpio me ka maʻi ʻaʻai
  • Nā keiki me ka maʻi ʻaʻai: He alakaʻi no nā mākua
  • Ka maʻi ʻaʻai ma nā keiki a me nā ʻōpio
  • Ke hoʻokū nei
  • Ke kāohi nei i ka maʻi ʻaʻai
  • Nā nīnau e nīnau ai i kāu kauka e pili ana i ka maʻi ʻaʻai
  • No nā mea ola a me nā mea mālama