Nā ʻano / pheochromocytoma / hoʻomanawanui / pheochromocytoma-lapaʻau-pdq

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Pheochromosittoma a me Paraganglioma iapaau ana (®) –Patient Version

ʻO ka ʻike ākea e pili ana iā Pheochromocytoma a me Paraganglioma

NA MANA KUNI

  • ʻO ka Pheochromocytoma a me ka paraganglioma he mau hikoko hikilele ʻole i hele mai ke ʻano like o ke ʻano.
  • ʻO ka Pheochromocytoma kahi tumo laha ʻole e hana i ka medula adrenal (ke kikowaena o ka adrenal gland).
  • Kū ka Paragangliomas ma waho o ka gland adrenal.
  • ʻO kekahi mau maʻi hoʻoilina a me nā loli i kekahi mau ʻāpana e hoʻonui i ka makaʻu o pheochromocytoma a i ʻole paraganglioma.
  • ʻO nā hōʻailona a me nā ʻōuli o pheochromocytoma a me paraganglioma e pili ana i ke kiʻekiʻe o ke koko a me ka ʻeha o ke poʻo.
  • Hiki i nā hōʻailona a me nā ʻōuli o pheochromocytoma a me paraganglioma ke hana ʻia i kēlā me kēia manawa a lawe ʻia mai paha e kekahi hanana.
  • Hoʻohana ʻia nā hoʻokolohua e nānā i ke koko a me ka mimi e ʻike (loaʻa) a hōʻike i ka pheochromocytoma a me ka paraganglioma.
  • ʻO ka ʻōlelo aʻoaʻo ʻana genetic kahi ʻāpana o ka hoʻolālā mālama no nā mea maʻi me pheochromocytoma a i ʻole paraganglioma.
  • Kū kekahi mau kumu i ka wānana (kahi o ke ola ʻana) a me nā koho lapaʻau.

ʻO ka Pheochromocytoma a me ka paraganglioma he mau hikoko hikilele ʻole i hele mai ke ʻano like o ke ʻano.

Hoʻokumu ʻia ʻo Paragangliomas i nā aʻa nerve i loko o nā aʻa adrenal a kokoke i kekahi o nā kīʻaha koko a me nā aʻalolo. Paragangliomas e hana i nā adrenal glands i kapa ʻia pheochromocytomas. Paragangliomas i hana ma waho o ka adrenal glands i kapa ʻia ʻo extra-adrenal paragangliomas. I kēia hōʻuluʻulu manaʻo, kapa ʻia nā paragangliomas keu-adrenal paragonliomas.

Phenochromocytomas and paragangliomas may benign (not cancer) or malignant (cancer).

ʻO ka Pheochromocytoma kahi tumo laha ʻole e hana i ka medula adrenal (ke kikowaena o ka adrenal gland).

Hana ʻia ʻo Pheochromocytoma i loko o nā ʻōpū adrenal. Aia he ʻelua adrenal glands, hoʻokahi ma luna o kēlā me kēia puʻupaʻa ma ke kua o ka ʻōpū o luna. He ʻelua ʻāpana ko kēlā me kēia gland adrenal. ʻO ka papa waho o ka adrenal gland ka adrenal cortex. ʻO ke kikowaena o ka adrenal gland ka adrenal medulla.

ʻO Pheochromocytoma kahi tumo laha ʻole o ka adrenal medulla. ʻO ka maʻamau, hoʻopili ka pheochromocytoma i hoʻokahi gland adrenal, akā hiki ke hoʻopili i nā ʻōpū adrenal. I kekahi manawa aia aku ma mua o hoʻokahi tumora i loko o hoʻokahi gland adrenal.

Hana nā ʻōpū adrenal i nā hormoni koʻikoʻi i kapa ʻia he catecholamines. ʻO Adrenaline (epinephrine) a me noradrenaline (norepinephrine) ʻelua mau ʻano catecholamines e kōkua ana e kaohi i ka helu o ka puʻuwai, ke koko, ke kō a me nā ʻano o ke kino i ka hoʻoluhi. I kekahi manawa e hoʻokuʻu kahi pheochromocytoma i ke adrenaline keu a me ka noradrenaline i loko o ke koko a hana i nā hōʻailona a i ʻole nā ​​hōʻailona o ka maʻi.

Anatomy o ke adrenal gland. Aia he ʻelua adrenal glands, hoʻokahi ma luna o kēlā me kēia puʻupaʻa. ʻO ka ʻaoʻao i waho o kēlā me kēia gland ka adrenal cortex; ʻo ka ʻaoʻao i loko, ʻo ia nō ka medulla adrenal.

Kū ka Paragangliomas ma waho o ka gland adrenal.

ʻO nā Paragangliomas he mau ʻōpū laha ʻole e kū kokoke i ke aʻa carotid, ma nā ala nerve i ke poʻo a me ka ʻāʻī, a ma nā ʻāpana ʻē aʻe o ke kino. Hana kekahi mau paragangliomas i nā catecholamines keu i kapa ʻia ʻo adrenaline a me noradrenaline. ʻO ka hoʻokuʻu ʻia ʻana o kēia mau catecholamines keu i ke koko e kumu i nā hōʻailona a i ʻole nā ​​hōʻailona o ka maʻi.

Paraganglioma o ke poʻo a me ka ʻāʻī. ʻO kahi tumo laha ʻole e kū kokoke ma ke aʻa o carotid. Hiki paha iā ia ke hana ma nā ala nerve i ke poʻo a me ka ʻāʻī a ma nā ʻāpana ʻē aʻe o ke kino.

ʻO kekahi mau maʻi hoʻoilina a me nā loli i kekahi mau ʻāpana e hoʻonui i ka makaʻu o pheochromocytoma a i ʻole paraganglioma.

ʻO nā mea āpau e hoʻonui i kou manawa e loaʻa ai kahi maʻi i kapa ʻia he kumu weliweli. ʻO ka loaʻa ʻana o kahi mea pilikia ʻaʻole ia he kumu e loaʻa ai ʻoe i ka maʻi ʻaʻai. ʻaʻohe o nā kumu pilikia ʻaʻole ia he kumu ʻaʻole ʻoe e loaʻa i ka maʻi ʻaʻai. E kamaʻilio me kāu kauka inā manaʻo ʻoe hiki i ka makaʻu.

ʻO nā syndrome hoʻoilina a i ʻole nā ​​hoʻololi ʻē aʻe e hoʻonui i ka makaʻu o pheochromocytoma a i ʻole paraganglioma:

  • Nui nā endocrine neoplasia 2 maʻi, ʻano A a me B (MEN2A a me MEN2B).
  • von Hippel-Lindau (VHL) maʻi maʻi.
  • ʻO Neurofibromatosis ʻano 1 (NF1).
  • Hereditary paraganglioma maʻi.
  • Carney-Stratakis dyad (paraganglioma and gastrointestinal stromal tumor [GIST]).
  • ʻO Carney triad (paraganglioma, GIST, a me ka pulmonary chondroma).

ʻO nā hōʻailona a me nā ʻōuli o pheochromocytoma a me paraganglioma e pili ana i ke kiʻekiʻe o ke koko a me ka ʻeha o ke poʻo.

ʻAʻole hana kekahi i nā tumors i adrenaline keu a i ʻole noradrenaline a hana ʻole i nā hōʻailona a me nā ʻōuli. ʻIke ʻia kēia mau tumors i kekahi manawa ke hana ʻia kahi puʻupuʻu ma ka ʻāʻī a i ʻole ke hana ʻia kahi hoʻāʻo a hana paha no kekahi kumu ʻē aʻe. ʻO nā hōʻailona a me nā ʻōuli o ka pheochromocytoma a me ka paraganglioma i ka wā e hoʻokuʻu ʻia ai ka nui adrenaline a i ʻole noradrenaline i loko o ke koko. ʻO kēia a me nā ʻōuli a me nā ʻōuli ʻē aʻe i kumu ʻia e pheochromocytoma a me paraganglioma a i ʻole nā ​​kūlana ʻē aʻe. E hōʻoia me kāu kauka inā loaʻa iā ʻoe kekahi o kēia mau mea:

  • Piʻi koko kiʻekiʻe.
  • ʻEha poʻo.
  • ʻO ka sweating kaumaha no ke kumu kumu ʻole.
  • Kahi puʻuwai puʻuwai ikaika, wikiwiki, a i ʻole maʻamau.
  • Haʻalulu.
  • Ke mae mae loa.

ʻO ka hōʻailona maʻamau ka nui o ke koko. He paʻakikī paha ke kāohi. Hiki i ke kahe koko kiʻekiʻe ke kumu i nā pilikia olakino koʻikoʻi e like me ka puʻuwai kūlohelohe ʻole, ka puʻuwai puʻuwai, ka hahau ʻana, a i ʻole ka make.

Hiki i nā hōʻailona a me nā ʻōuli o pheochromocytoma a me paraganglioma ke hana ʻia i kēlā me kēia manawa a lawe ʻia mai paha e kekahi hanana.

Hiki i nā hōʻailona a me nā ʻōuli o pheochromocytoma a me paraganglioma ke hana ʻia kekahi o nā hanana aʻe:

  • ʻOhana hoʻoikaika kino.
  • He hōʻeha kino a i ʻole ke kaumaha nui o ka naʻau.
  • Hānau keiki.
  • Ke hele nei ma lalo o ka anesthesia.
  • ʻOki kino, me nā kaʻina hana e hemo ai i ka tumo.
  • ʻO ka ʻai ʻana i nā meaʻai kiʻekiʻe i ka tyramine (e like me ka waina ʻulaʻula, kokoleka, a me ka tī).

Hoʻohana ʻia nā hoʻokolohua e nānā i ke koko a me ka mimi e ʻike (loaʻa) a hōʻike i ka pheochromocytoma a me ka paraganglioma.

Hiki ke hoʻohana ʻia nā hoʻāʻo a me nā kaʻina hana aʻe:

  • ʻO ka hoʻāʻo kino a me ka mōʻaukala: kahi hōʻike o ke kino e nānā i nā hōʻailona laulā o ke olakino, e like me ka nānā ʻana i nā hōʻailona o ka maʻi, e like me ke kahe kiʻekiʻe a i ʻole nā ​​mea ʻē aʻe i ʻike ʻia he ʻokoʻa. E lawe ʻia kahi moʻolelo o nā ʻano olakino o ka mea maʻi a me nā maʻi i hala a me nā mālama ʻana.
  • Iwakāluakūmāhā hola ho'āʻo: He hoʻāʻo kahi e ʻohiʻohi ʻia ai ka mimi no 24 mau hola e ana i ka nui o nā catecholamines i ka mimi. Ana ʻia nā mea ma muli o ka haki ʻana o kēia mau catecholamines. ʻO kahi mea maʻamau (ʻoi aku a i ʻole haʻahaʻa ma mua o ka maʻamau) o kahi mea i hiki ke lilo i hōʻailona o ka maʻi i loko o ka meaola a i ʻole ke ʻano. ʻO ke kiʻekiʻe ma mua o ka maʻamau o kekahi mau catecholamines he hōʻailona paha ia o pheochromocytoma.
  • Nā haʻawina catecholamine o ke koko: kahi kaʻina e nānā ʻia kahi hāpana koko e ana i ka nui o kekahi mau catecholamines i hoʻokuʻu ʻia i loko o ke koko. Ana ʻia nā mea ma muli o ka haki ʻana o kēia mau catecholamines. ʻO kahi mea maʻamau (ʻoi aku ma mua a i ʻole haʻahaʻa ma mua o ka maʻamau) o kahi mea i hiki ke lilo i hōʻailona o ka maʻi i loko o ka meaola a i ʻole ke ʻano e hana iā ia. ʻO ke kiʻekiʻe ma mua o ka maʻamau o kekahi mau catecholamines he hōʻailona paha ia o pheochromocytoma.
  • CT scan (CAT scan): kahi hana e hana ai i kahi o nā kiʻi kikoʻī o nā wahi i loko o ke kino, e like me ka ʻāʻī, ka umauma, ʻōpū, a me ke pelvis, i lawe ʻia mai nā ʻaoʻao ʻokoʻa. Hana ʻia nā kiʻi e kahi kamepiula i hoʻopili ʻia i kahi mīkini x-ray. Hoʻokomo ʻia paha ke kala i loko o ke aa a i ʻole ale ʻia e kōkua i nā ʻōpū a i ʻole nā ​​kino i hōʻike hou aku me ka maopopo. Kāhea ʻia kēia kaʻina hana he tomography i helu ʻia, kamepiula tomography, a i ʻole he tomography axial computerized.
  • MRI (magnetic resonance imaging): kahi hana e hoʻohana ai i ka magnet, nā nalu lekiō, a me kahi kamepiula e hana i nā kiʻi kikoʻī o nā wahi i loko o ke kino e like me ka ʻāʻī, ka umauma, ʻōpū, a me ke pelvis. Kāhea ʻia kēia kaʻina hana he kiʻi nukelea kiʻi resonance (NMRI).

ʻO ka ʻōlelo aʻoaʻo ʻana genetic kahi ʻāpana o ka hoʻolālā mālama no nā mea maʻi me pheochromocytoma a i ʻole paraganglioma.

ʻO nā mea maʻi āpau i ʻike ʻia me ka pheochromocytoma a i ʻole paraganglioma pono e loaʻa i nā ʻōlelo aʻoaʻo pilikino e ʻike i ko lākou makaʻu no ka loaʻa ʻana o kahi maʻi hoʻoilina a me nā maʻi ʻē aʻe e pili ana.

Hōʻike ʻia paha ka hoʻāʻo genetic e ke kākāʻōlelo no nā maʻi e:

  • Loaʻa kahi moʻolelo pilikino a ʻohana paha o nā ʻano i hoʻopili ʻia me ka pheochromocytoma hoʻoilina a i ʻole paraganglioma syndrome.
  • Loaʻa i nā tumors ma nā adrenal gland.
  • Loaʻa ma mua o hoʻokahi tumo i hoʻokahi gland adrenal.
  • Loaʻa i nā hōʻailona a i ʻole nā ​​hōʻailona o ke keu catecholamines i hoʻokuʻu ʻia i loko o ke koko a i ʻole malignant (cancerous) paraganglioma.
  • ʻIke ʻia ma mua o ka makahiki 40.

Paipai ʻia ka hoʻāʻo genetic i kekahi manawa no nā mea maʻi me pheochromocytoma nāna:

  • He 40 a 50 mau makahiki.
  • Loaʻa i kahi tumo i hoʻokahi gland adrenal.
  • ʻAʻohe ou moʻolelo pilikino a ʻohana paha o kahi maʻi hoʻoilina hoʻoilina.

Ke loaʻa kekahi mau loli i ka hoʻokolohua kūlohelohe, hāʻawi pinepine ʻia ka hoʻāʻo ʻana i nā lālā o ka ʻohana i ka makaʻu akā ʻaʻohe o lākou hōʻailona a hōʻailona paha.

ʻAʻole hōʻike ʻia ka hoʻāʻo genetic no nā mea maʻi ma mua o 50 mau makahiki.

Kū kekahi mau kumu i ka wānana (kahi o ke ola ʻana) a me nā koho lapaʻau.

ʻO ka wānana (loaʻa o ke ola) a me nā koho lapaʻau e pili i kēia:

  • Inā maikaʻi a kolohe paha ka tumo.
  • Inā ʻo ka tumo ma kahi wale nō a ua laha paha i nā wahi ʻē aʻe o ke kino.
  • Inā paha he hōʻailona a hōʻailona paha i hoʻokumu ʻia e nā catecholamines ʻoi aku ka kiʻekiʻe ma mua o ka maʻamau.
  • Inā ua ʻike wale ʻia ka tumo a i ʻole ua hoʻi hou (hoʻi hou).

Nā pae o Pheochromocytoma a me Paraganglioma

NA MANA KUNI

  • Ma hope o ka hōʻoia ʻana o ka pheochromocytoma a me ka paraganglioma, hana ʻia nā hoʻokolohua e ʻike inā ua palahalaha ka tumo i nā ʻāpana ʻē aʻe o ke kino.
  • ʻEkolu ala e hoʻolaha ai ka maʻi ʻaʻai i loko o ke kino.
  • E laha paha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i nā ʻāpana ʻē aʻe o ke kino.
  • ʻAʻohe ʻōnaehana hoʻonohonoho maʻamau no pheochromocytoma a me paraganglioma.
  • Hōʻike ʻia ʻo Pheochromocytoma a me paraganglioma ma ke ʻano he localized, regional, a metastatic paha.
  • ʻO ka pheochromocytoma i hoʻopaʻa ʻia a me ka paraganglioma
  • Pheochromocytoma āpana a me paraganglioma
  • ʻO pheochromocytoma Metastatic a me paraganglioma

Ma hope o ka hōʻoia ʻana o ka pheochromocytoma a me ka paraganglioma, hana ʻia nā hoʻokolohua e ʻike inā ua palahalaha ka tumo i nā ʻāpana ʻē aʻe o ke kino.

ʻO ka laulā a hoʻolaha paha o ka maʻi ʻaʻai e wehewehe pinepine ʻia ma ke ʻano he pae. He mea nui ia e ʻike inā ua laha ka maʻi ʻaʻai i mea e hoʻolālā ai i ka lāʻau. Hiki ke hoʻohana ʻia nā hoʻokolohua a me nā kaʻina hana e ʻike ai inā ua palahalaha ka tumo i nā ʻāpana ʻē aʻe o ke kino.

  • CT scan (CAT scan): kahi hana e hana ai i kahi o nā kiʻi kikoʻī o nā wahi i loko o ke kino, e like me ka ʻāʻī, ka umauma, ʻōpū, a me ke pelvis, i lawe ʻia mai nā ʻaoʻao ʻokoʻa. Hana ʻia nā kiʻi e kahi kamepiula i hoʻopili ʻia i kahi mīkini x-ray. Hoʻokomo ʻia paha ke kala i loko o ke aa a i ʻole ale ʻia e kōkua i nā ʻōpū a i ʻole nā ​​kino i hōʻike hou aku me ka maopopo. Hōʻike ʻia ka ʻōpū a me ke pelvis e ʻike i nā tumors e hoʻokuʻu i ka catecholamine. Kāhea ʻia kēia kaʻina hana he tomography i helu ʻia, kamepiula tomography, a i ʻole he tomography axial computerized.
  • MRI (magnetic resonance imaging): kahi hana e hoʻohana ai i ka magnet, nā nalu lekiō, a me kahi kamepiula e hana i nā kiʻi kikoʻī o nā wahi i loko o ke kino e like me ka ʻāʻī, ka umauma, ʻōpū, a me ke pelvis. Kāhea ʻia kēia kaʻina hana he kiʻi nukelea kiʻi resonance (NMRI).
  • MIBG scan: kahi hana e hoʻohana ai e ʻike i nā tumo neuroendocrine, e like me pheochromocytoma a me paraganglioma. Hoʻokomo ʻia kahi liʻiliʻi loa o kahi mea i kapa ʻia he radioactive MIBG i loko o kahi aa a hele i waena o ke kahe o ke koko. Lawe ʻia nā neuroendocrine tumula i ka MIBG radioactive a ʻike ʻia e kahi scanner. Hiki ke lawe ʻia nā scanner ma mua o 1-3 mau lā. Hiki ke hāʻawi ʻia i kahi hopena iodine ma mua a i ʻole ma ka wā o ka hoʻāʻo e mālama i ka gland thyroid mai ka lawe nui ʻana i ka MIBG.
  • scan: ʻO kahi ʻano o ka scan radionuclide i hoʻohana ʻia e ʻike i kekahi mau tumors, me nā tumors e hoʻokuʻu i ka catecholamine. ʻO kahi liʻiliʻi loa o ka radioactive (kahi hormone e hoʻopili i kekahi mau tumors) i injected i loko o kahi aa a hele i loko o ke koko. Hoʻopili ka lekiō i ka tumelo a me kahi kāmela kūikawā e ʻike i ka radioactivity e hoʻohana ʻia e hōʻike i kahi o nā tumors i loko o ke kino.
  • FDG-PET scan (fluorodeoxyglucose-positron emission tomography scan): kahi hana e loaʻa ai nā pūnaewele tumo malignant i loko o ke kino. Hoʻokomo ʻia kahi liʻiliʻi o FDG, kahi ʻano o ka glucose radioactive (kō), i loko o kahi aa koko. Hoʻopili ka scanner PET a puni ke kino a hana i kahi kiʻi o kahi e hoʻohana ʻia ai ka glucose i ke kino. ʻOi aku ka mālamalama o nā hunaola tumo ma ke kiʻi no ka mea ʻoi aku ka hana a lawe i ka glucose ma mua o ka hana ʻana o nā hunaola maʻamau.

ʻEkolu ala e hoʻolaha ai ka maʻi ʻaʻai i loko o ke kino.

Hiki ke pālahalaha ʻia ka maʻi ʻaʻai ma o nā meaola, ka ʻōnaehana lymph, a me ke koko.

  • Kāpena. Hoʻolahalaha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i ka ulu ʻana i nā wahi kokoke.
  • ʻŌnaehana Lymph. Hoʻolahalaha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i ke komo ʻana i ka ʻōnaehana lymph. Hele ka maʻi ʻaʻai ma o nā kīʻaha lymph i nā ʻāpana ʻē aʻe o ke kino.
  • Koko. Hoʻolahalaha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i ke komo ʻana i ke koko. Hele ka maʻi ʻaʻai ma o nā kīʻaha koko i nā ʻāpana ʻē aʻe o ke kino.

E laha paha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i nā ʻāpana ʻē aʻe o ke kino.

Ke pālahalaha ʻia ka maʻi ʻaʻai i kekahi ʻāpana o ke kino, ua kapa ʻia ia ʻo metastasis. E haki nā hunaola maʻi 'aʻai mai kahi a lākou i hoʻomaka ai (ka tumo mua) a hele i loko o ka ʻōnaehana lymph a i ʻole ke koko.

  • ʻŌnaehana Lymph. Komo ka maʻi ʻaʻai i loko o ka ʻōnaehana lymph, hele ma waena o nā kīʻaha lymph, a hana i kahi tumo (tumo metastatic) i kekahi ʻāpana o ke kino.
  • Koko. Komo ke kanesa i loko o ke koko, hele ma waena o nā kīʻaha koko, a hana i kahi tumo (tumo metastatic) i kekahi ʻāpana o ke kino.

ʻO ka tumo metastatic ka ʻano like o ke kanesa me ka tumo mua. ʻO kahi laʻana, inā pāhola ʻia ka pheochromocytoma i ka iwi, ʻo nā hunaola maʻi ʻaʻai i loko o ka iwi he mau pheochromocytoma maoli nā hunaola. ʻO ka maʻi he pheochromocytoma metastatic, ʻaʻole maʻi maʻi iwi.

ʻAʻohe ʻōnaehana hoʻonohonoho maʻamau no pheochromocytoma a me paraganglioma.

Hōʻike ʻia ʻo Pheochromocytoma a me paraganglioma ma ke ʻano he localized, regional, a metastatic paha.

ʻO ka pheochromocytoma i hoʻopaʻa ʻia a me ka paraganglioma

Loaʻa ka tumo i hoʻokahi a i ʻole ʻelua mau adrenal glands (pheochromocytoma) a i ʻole ma hoʻokahi wahi wale nō (paraganglioma).

Pheochromocytoma āpana a me paraganglioma

Ua pālahalaha ka maʻi ʻaʻai i nā pūnana lymph a i ʻole nā ​​mea ʻē aʻe kokoke i kahi i hoʻomaka ai ka tumo.

ʻO pheochromocytoma Metastatic a me paraganglioma

Ua pālahalaha ka maʻi ʻaʻai i nā ʻāpana ʻē aʻe o ke kino, e like me ke akepaʻa, nā akemāmā, ka iwi, a i ʻole nā ​​lymph node mamao.

ʻO Pheochromocytoma hou a me Paraganglioma

ʻO ka pheochromocytoma recurrent a i ʻole paraganglioma ka maʻi ʻaʻai i hoʻi hou (hoʻi) ma hope o ka mālama ʻia ʻana. E hoʻi paha ka maʻi ʻaʻai ma kahi like a i ʻole ʻāpana ʻē aʻe o ke kino.

Laulā Manaʻo Option Oponopono

NA MANA KUNI

  • Aia nā ʻano lapaʻau like ʻole no nā mea maʻi me pheochromocytoma a i ʻole paraganglioma.
  • ʻO nā mea maʻi me ka pheochromocytoma a me ka paraganglioma e hana i nā hōʻailona a i ʻole nā ​​hōʻailona e mālama ʻia me ka lāʻau lapaʻau.
  • Hoʻohana ʻia ʻeono ʻano o ka mālama maʻamau.
  • ʻOki kino
  • Lapaʻau hoʻomākala
  • ʻO Chemotherapy
  • ʻAha hoʻopau maʻi
  • Embolization therapy
  • Pahuhopu kau ʻia
  • Ke hoʻāʻo ʻia nei nā ʻano lapaʻau hou i nā hoʻokolohua hoʻokolohua.
  • ʻO ka mālama ʻana no ka pheochromocytoma a me ka paraganglioma ke kumu o nā hopena.
  • Makemake paha nā mea maʻi e noʻonoʻo e pili ana i ka hoʻokolokolo ʻana.
  • Hiki i nā mea maʻi ke komo i nā hoʻokolohua hoʻokolohua ma mua, i ka wā, a ma hope paha o ka hoʻomaka ʻana i kā lākou mālama maʻi ʻaʻai.
  • E pono nā hoʻokolohua ukali.

Aia nā ʻano lapaʻau like ʻole no nā mea maʻi me pheochromocytoma a i ʻole paraganglioma.

Loaʻa nā ʻano lapaʻau like ʻole no nā mea maʻi me pheochromocytoma a i ʻole paraganglioma. Kūlana maʻamau kekahi mau hōʻailona (ʻo ka lāʻau i hoʻohana ʻia i kēia manawa), a ʻo kekahi e hoʻāʻo ʻia nei i nā hoʻokolohua hoʻokolohua. ʻO kahi hoʻokolohua hoʻokolohua lapaʻau kahi noiʻi noiʻi i manaʻo ʻia e kōkua i ka hoʻomaikaʻi ʻana i nā mālama ʻana i kēia manawa a i ʻole loaʻa ka ʻike e pili ana i nā mālama hou no nā maʻi me ka maʻi ʻaʻai. Ke hōʻike nā hoʻokolohua hoʻokolohua ʻoi aku ka maikaʻi o kahi lapaʻau hou ma mua o ka maʻamau maʻamau, lilo paha ka lāʻau hou i ka lapaʻau maʻamau. Makemake paha nā mea maʻi e noʻonoʻo e pili ana i ka hoʻokolokolo ʻana. ʻO kekahi mau hoʻokolohua hoʻokolohua e hāmama wale i nā mea maʻi i hoʻomaka ʻole i ka lāʻau

ʻO nā mea maʻi me ka pheochromocytoma a me ka paraganglioma e hana i nā hōʻailona a i ʻole nā ​​hōʻailona e mālama ʻia me ka lāʻau lapaʻau.

Hoʻomaka ka lāʻau lapaʻau ke ʻike ʻia ka pheochromocytoma a i ʻole paraganglioma. Hoʻopili paha kēia:

  • Nā lāʻau e mālama i ke kaomi koko maʻa mau. ʻO kahi laʻana, hoʻokahi ʻano o nā lāʻau i kapa ʻia nā alpha-blockers e hoʻōki i ka noradrenaline mai ka hana ʻana i nā kīʻaha koko liʻiliʻi i ʻoi iki. ʻO ka mālama ʻana i nā kīʻaha koko a wehe a hoʻomaikaʻi hoʻi i ke kahe o ke koko a hoʻohaʻahaʻa i ke kaomi koko.
  • Nā lāʻau i mālama i ka naʻau i ka helu maʻamau. ʻO kahi laʻana, hoʻokahi ʻano lāʻau i kapa ʻia ʻo beta-blockers e hoʻōki i ka hopena o ka nui noradrenaline a lohi i ka helu o ka puʻuwai.
  • Nā lāʻau i ālai i ka hopena o ke keu hormonone i hana ʻia e ka adrenal gland.

Hāʻawi pinepine ʻia ka lāʻau lapaʻau no hoʻokahi a ʻekolu mau pule ma mua o ke kaha ʻana.

Hoʻohana ʻia ʻeono ʻano o ka mālama maʻamau.

ʻOki kino

ʻO ke kaha e wehe i ka pheochromocytoma kahi adrenalectomy (hemo i hoʻokahi a i ʻole nā ​​adrenal gland). I kēia wā ʻoki kino, e nānā ʻia nā aʻa a me nā lymph i loko o ka ʻōpū a inā ua pālahalaha ka tumo, hiki ke hoʻoneʻe ʻia kēia mau mea. Hāʻawi ʻia nā lāʻau i mua, i ka wā, a ma hope o ke kaha ʻana e mālama i ke kahe o ke koko a me ka helu maʻamau o ka puʻuwai.

Ma hope o ke kaha ʻana e hemo i ka tumo, nānā ʻia nā pae catecholamine i ke koko a i ʻole ka mimi. ʻO nā pae catecholamine maʻamau ka hōʻailona o ka lawe ʻia ʻana o nā hunaola pheochromocytoma āpau.

Inā hoʻoneʻe ʻia nā kūpuna adrenal ʻelua, pono ka hoʻōla hormone lōʻihi e hoʻololi i nā homone i hana ʻia e nā adrenal glands.

Lapaʻau hoʻomākala

ʻO ka radiation radiation kahi lāʻau maʻi maʻi maʻi e hoʻohana i nā kukuna x nui ikaika a i ʻole nā ​​ʻano radiation e hoʻomake i nā hunaola maʻi ʻaʻai a mālama ʻole paha i ka ulu ʻana. ʻElua ʻano o radiation radiation:

  • Hoʻohana ka radiation radiation kūwaho i kahi mīkini ma waho o ke kino e hoʻouna i ka radiation i ka maʻi ʻaʻai.
  • Hoʻohana ka radiation radiation i loko i kahi lāʻau radioactive i hoʻopaʻa ʻia i nā nila, nā hua, nā uea, a i ʻole nā ​​catheters i kau pololei ʻia i loko a kokoke paha i ka maʻi ʻaʻai.

Hāʻawi ʻia ke ala o ka radiation radiation i ke ʻano o ka maʻi ʻaʻai e mālama ʻia ana a inā he localized, regional, metastatic, a i ʻole recurrent. Hoʻohana ʻia ka radiation radiation kūwaho a me ka 131I-MIBG therapy e mālama ai i ka pheochromocytoma.

Hana ʻia ʻo Pheochromocytoma i kekahi manawa me 131I-MIBG, kahi e lawe pololei i ka radiation i nā hunaola tumele. 131I-MIBG kahi mea radioactive e hōʻiliʻili i kekahi ʻano o nā hunaola tumele, e luku ana iā lākou me ka pāhawewe i hāʻawi ʻia. Hāʻawi ʻia ka 131I-MIBG e infusion. ʻAʻole nā ​​pheochromocytomas āpau e lawe iā 131I-MIBG, no laila hana mua ʻia kahi hōʻike e nānā no kēia ma mua o ka hoʻomaka ʻana o ka lapaʻau.

ʻO Chemotherapy

ʻO Chemotherapy kahi lāʻau lapaʻau maʻi maʻi e hoʻohana i nā lāʻau e hōʻoki i ka ulu ʻana o nā hunaola maʻi ʻaʻai, ma ka luku ʻana i nā hunaola a i ʻole ke kāpae ʻana iā lākou mai ka hoʻokaʻawale. Ke lawe ʻia ka chemotherapy e ka waha a i ʻole injected i loko o kahi aa koko a i ʻole nā ​​mākala, komo nā lāʻau i ke kahe o ke koko a hiki ke kiʻi i nā hunaola maʻi ʻōpio i loko o ke kino (chemotherapy ʻōnaehana). Ke waiho pololei ʻia ka chemotherapy i loko o ka wai cerebrospinal, kahi hui, a i ʻole ke kino o ke kino e like me ka ʻōpū, ʻo nā lāʻau lapaʻau ka mea nui e hoʻopili i nā hunaola maʻi ʻaʻai i kēlā mau wahi (chemotherapy āpau). Hoʻohui ka chemotherapy hui me ka hoʻohana ʻana ma mua o hoʻokahi lāʻau anticancer. Hāʻawi ʻia ke ala o ka chemotherapy i ke ʻano o ka maʻi ʻaʻai e mālama ʻia a inā he wahi ʻia, ʻāpana, metastatic, a i ʻole hoʻi hou.

ʻAha hoʻopau maʻi

ʻO Ablasi kahi lapaʻau e wehe a hōʻino paha i kahi ʻāpana o ke kino a i ʻole kāna hana. Hoʻohana ʻia nā mea hōʻoki maʻi e kōkua i ka luku ʻana i nā hunaola maʻi ʻaʻai e:

  • Hoʻomaha abadiofrequency: kahi hana e hoʻohana ai i nā nalu lekiō e wela a luku hoʻi i nā pūnaewele kūpono ʻole. Hele ka nalu uila ma o nā uila (nā mea liʻiliʻi e lawe i ka uila). Hiki ke hoʻohana ʻia ka hoʻopau ʻana o ka radiofrequency e mālama ai i ka maʻi ʻaʻai a me nā ʻano ʻē aʻe.
  • Cryoablation: kahi hana e paʻa ai kaʻiʻo i mea e luku ai i nā hunaola ʻino. Hoʻohana ʻia ka nitrogen wai a i ʻole ke kalapona kalapona e hoʻohana i ka paʻahau.

Embolization therapy

ʻO ka Embolization therapy kahi lapaʻau e pale i ke aʻa e alakaʻi ai i ka momona adrenal. ʻO ka pale ʻana i ke kahe o ke koko i nā kūpuna adrenal kōkua i ka luku ʻana i nā hunaola maʻi ʻaʻai e ulu ana ma laila.

Pahuhopu kau ʻia

He lāʻau lapaʻau i hoʻomāka ʻia ʻia e hoʻohana ai i nā lāʻau a i ʻole nā ​​mea ʻē aʻe e ʻike a hoʻouka aku i nā hunaola maʻi ʻaʻai me ka ʻole e hōʻeha i nā hunaola maʻamau. Hoʻohana ʻia nā mea i hoʻoponopono ʻia e mālama i ka metastatic a me ka pheochromocytoma hou.

ʻO Sunitinib (kahi ʻano o ka inhibitor tyrosine kinase) kahi lapaʻau hou e aʻo ʻia nei no ka metastatic pheochromocytoma. ʻO ke kāohi ʻo Tyrosine kinase inhibitor kahi ʻano o ka hoʻomōhala hoʻomāka ʻia e ālai ai i nā hōʻailona e pono ai e ulu nā tumors.

Ke hoʻāʻo ʻia nei nā ʻano lapaʻau hou i nā hoʻokolohua hoʻokolohua.

Loaʻa nā ʻike e pili ana i nā hoʻokolohua hoʻokolohua mai ka pūnaewele NCI.

ʻO ka mālama ʻana no ka pheochromocytoma a me ka paraganglioma ke kumu o nā hopena.

No ka ʻike e pili ana i nā hopena i hopena ʻia e ka lapaʻau ʻana no ka maʻi ʻaʻai, e ʻike i kā mākou ʻaoʻao ʻaoʻao ʻaoʻao.

Makemake paha nā mea maʻi e noʻonoʻo e pili ana i ka hoʻokolokolo ʻana.

No kekahi mau mea maʻi, ke komo nei i ka hoʻokolohua hoʻokolohua ke koho lapaʻau maikaʻi loa paha. ʻO nā hoʻokolohua hoʻokolohua kahi ʻāpana o ka noiʻi ʻana o ka maʻi ʻaʻai. Hana ʻia nā hoʻokolohua hoʻokolohua e ʻike inā palekana a maikaʻi a maikaʻi paha nā hoʻomaʻamaʻa maʻi ʻaʻai ma mua o ka maʻamau maʻamau.

ʻO ka hapa nui o nā hana maʻamau no ka maʻi ʻaʻai i kau ʻia ma nā hoʻokolohua hoʻokolohua mua. ʻO nā mea maʻi i komo i ka hoʻokolokolo hoʻokolohua hiki ke loaʻa i ka lāʻau maʻamau a i ʻole i waena o nā mea mua i loaʻa kahi lāʻau hou.

ʻO nā mea maʻi i komo i nā hoʻokolohua hoʻokolohua kōkua pū kekahi i ka hoʻomaikaʻi ʻana i ke ʻano o ka mālama ʻana i ka maʻi ʻaʻai i ka wā e hiki mai ana. ʻOiai ʻaʻole nā ​​alakaʻi hoʻokolohua e alakaʻi i nā hoʻoponopono hou maikaʻi, pane pinepine lākou i nā nīnau nui a kōkua i ka neʻe i mua o ka noiʻi.

Hiki i nā mea maʻi ke komo i nā hoʻokolohua hoʻokolohua ma mua, i ka wā, a ma hope paha o ka hoʻomaka ʻana i kā lākou mālama maʻi ʻaʻai.

Hoʻopili wale kekahi mau hoʻokolohua hoʻokolohua i nā mea maʻi i loaʻa ʻole ka lapaʻau. ʻO nā hoʻokolohua ʻē aʻe e hōʻoia i nā mālama ʻana no ka poʻe maʻi i loaʻa ʻole ka maikaʻi o ka maʻi ʻaʻai. Aia kekahi mau hoʻokolohua hoʻokolohua e hoʻāʻo i nā ala hou e hōʻoki i ka maʻi ʻaʻai mai ka hoʻi hou ʻana (hoʻi ʻana) a hōʻemi paha i nā hopena o ka mālama ʻana i ka maʻi ʻaʻai.

Ke mālama ʻia nei nā hoʻokolohua hoʻokolohua ma nā wahi he nui o ka ʻāina. Hiki ke ʻike ʻia ka ʻike e pili ana i nā hoʻokolohua hoʻokolohua e kākoʻo ʻia e NCI ma ka pūnaewele ʻimi noiʻi hoʻokolohua a NCI. Hiki ke loaʻa nā hoʻokolohua hoʻokolohua i kākoʻo ʻia e nā hui ʻē aʻe ma ka pūnaewele ClinicalTrials.gov.

E pono nā hoʻokolohua ukali.

ʻO kekahi o nā hoʻokolohua i hana ʻia e hōʻoia i ka maʻi ʻaʻai a i ʻole e ʻike i ka nui o ka maʻi ʻaʻai e hiki ke hana hou ʻia. E hana hou ʻia kekahi mau hōʻike i mea e ʻike ai i ka maikaʻi o ka mālama ʻana. E hoʻoholo ʻia nā hoʻoholo e pili ana inā e hoʻomau, hoʻololi, a oki paha i ka lāʻau ʻana ma nā hopena o kēia mau hoʻāʻo.

E hoʻomau ʻia kekahi o nā hoʻokolohua mai kēlā me kēia manawa ma hope o ka pau ʻana o ka lāʻau. Hiki i nā hopena o kēia mau hoʻāʻo ke hōʻike inā ua loli kou ʻano a i ʻole inā ua hoʻi hou ke kanesa. Kapa ʻia kēia mau hoʻāʻo i nā manawa he mau hoʻokolohua ukali.

No nā mea maʻi me ka pheochromocytoma a i ʻole paraganglioma i kumu i nā ʻōuli, e nānā ʻia nā pae catecholamine i ke koko a me ka mimi ma kahi manawa mau. ʻO nā kiʻekiʻe o Catecholamine i ʻoi aku ka kiʻekiʻe ma mua o ka maʻamau ke lilo i hōʻailona no ka hoʻi ʻana mai o ka maʻi ʻaʻai.

No nā mea maʻi me ka paraganglioma i kumu ʻole ai nā hōʻailona, ​​pono e hana i nā hoʻokolohua ukali e like me CT, MRI, a me MIBG scan i kēlā me kēia makahiki.

No nā mea maʻi me ka pheochromocytoma hoʻoilina, e nānā ʻia nā pae catecholamine i ke koko a me ka mimi ma kahi manawa mau. E hana ʻia nā hoʻokolohua loiloi ʻē aʻe e nānā i nā ʻōpala ʻē aʻe e pili ana i ka maʻi hoʻoilina.

E kamaʻilio me kāu kauka e pili ana i nā hoʻokolohua e pono ai a pehea ka manawa. ʻO nā mea maʻi me ka pheochromocytoma a i ʻole paraganglioma pono e ukali i ke ola holoʻokoʻa.

Nā koho lapaʻau no Pheochromocytoma a me Paraganglioma

Ma keia Pauku

  • ʻO Pheochromocytoma kūloko a me Paraganglioma
  • Pheochromocytoma hoʻoilina
  • Pheochromocytoma āpana a me Paraganglioma
  • ʻO Metastatic Pheochromocytoma a me Paraganglioma
  • ʻO Pheochromocytoma hou a me Paraganglioma

No ka ʻike e pili ana i nā lāʻau i helu ʻia ma lalo, e ʻike i ka ʻaoʻao Overtion Option Overview.

ʻO Pheochromocytoma kūloko a me Paraganglioma

ʻO ka mālama ʻana i ka pheochromocytoma benign localized a i ʻole paraganglioma ka ʻoki maʻamau e hemo loa i ka tumo. Inā aia ka tumo i loko o ka adrenal gland, ua hoʻoneʻe ʻia ke gland adrenal holoʻokoʻa.

E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.

Pheochromocytoma hoʻoilina

I nā mea maʻi me ka pheochromocytoma hoʻoilina e pili ana i nā endopine neoplasia (MEN2) a i ʻole von Hippel-Lindau (VHL) maʻi, hana pinepine nā tumors i nā adrenal glands. ʻO nā kūpuna he maʻa mau.

  • ʻO ka mālama ʻana no pheochromocytoma hoʻoilina i hana ʻia i hoʻokahi gland adrenal ke ʻoki e hoʻopau loa i ka momona. Hiki i kēia ʻoki ʻana ke kōkua i nā mea maʻi e hōʻalo i ka wīwī steroid lifelong a me ka luhi adrenal.
  • ʻO ka mālama ʻana no ka pheochromocytoma hoʻoilina i hana ʻia i loko o nā kaha adrenal ʻelua a i ʻole nā ​​ʻano hope i loko o ke koena adrenal i koe he ʻoki paha e wehe i ka ʻōpelu a me nā mea liʻiliʻi maʻamau i ka adrenal cortex i hiki. Hiki i kēia ʻoki ʻana ke kōkua i nā mea maʻi e hōʻalo i ka hoʻōla o ke ola lōʻihi a me nā pilikia olakino ma muli o ka nalo ʻana o nā homone i hana ʻia e ka adrenal gland.

Pheochromocytoma āpana a me Paraganglioma

ʻO ka mālama ʻana i ka pheochromocytoma a i ʻole paraganglioma i pāhola aʻe i nā mea kokoke a i ʻole nā ​​lymph node kahi ʻoki e hoʻopau loa i ka tumo. ʻO nā mea kokoke e pili ana i ka maʻi ʻaʻai e laha ai, e like me ka puʻupaʻa, ate, ʻāpana o kahi kīʻaha koko nui, a me nā lymph node, hiki ke lawe ʻia aku hoʻi

E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.

ʻO Metastatic Pheochromocytoma a me Paraganglioma

ʻO ka mālama ʻana i ka pheochromocytoma metastatic a i ʻole paraganglioma e komo pū paha me kēia:

  • ʻO ke keʻena hana e hoʻopau loa i ka maʻi ʻaʻai, me nā tumors i palahalaha aku i nā wahi mamao o ke kino.
  • Palliative therapy, e hōʻoluʻolu i nā hōʻailona a hoʻomaikaʻi i ka maikaʻi o ke ola, e like me:
  • ʻO ke keʻoki e wehe i ka maʻi ʻaʻai e like me ka hiki.
  • Hoʻohui chemotherapy.
  • ʻO ka radiation radiation me 131I-MIBG.
  • ʻO ka radiation radiation kūwaho i nā wahi (e like me ka iwi) kahi i pālahalaha ʻia ai ka maʻi ʻaʻai a ʻaʻole hiki ke hemo ʻia e ka ʻoki kino.
  • Embolization (lapaʻau e ālai i ke aʻa e hāʻawi i ke koko i kahi tumo).
  • ʻO ka Ablathapy therapy me ka hoʻohana ʻana i ka radiofrequency ablasi a i ʻole cryoablation no nā tumors i ke ake a i ʻole ka iwi.
  • ʻO kahi hoʻokolohua hoʻokolohua o ka lāʻau hoʻomoʻa ʻia me kahi mea hōʻoki kine tyrosine kinase.
  • ʻO kahi hoʻokolohua hoʻokolohua o ka radiation radiation i loko e hoʻohana ana i kahi mea radioactive hou.

E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.

ʻO Pheochromocytoma hou a me Paraganglioma

ʻO ka mālama ʻana i ka pheochromocytoma hou a i ʻole paraganglioma e komo pū paha me kēia:

  • ʻO ke keʻoki e hoʻopau loa i ka maʻi ʻaʻai.
  • Ke hiki ʻole ke ʻoki e wehe i ka maʻi ʻaʻai, palliative therapy e hōʻoluʻolu i nā ʻōuli a hoʻomaikaʻi i ke ʻano o ke ola, e like me:
  • Hoʻohui chemotherapy.
  • Pahuhopu kau ʻia.
  • ʻO ka radiation radiation e hoʻohana ana iā 131I-MIBG.
  • ʻO ka radiation radiation kūwaho i nā wahi (e like me ka iwi) kahi i pālahalaha ʻia ai ka maʻi ʻaʻai a ʻaʻole hiki ke hemo ʻia e ka ʻoki kino.
  • Hoʻomaʻemaʻe hoʻopau ʻana me ka hoʻohana ʻana i ka radiofrequency ablation a i ʻole cryoablation.

E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.

ʻO Pheochromocytoma i ka wā o ka hāpai ʻana

NA MANA KUNI

  • Pono nā wahine hāpai me ka pheochromocytoma i kahi mālama kūikawā.
  • ʻO ka mālama ʻana i nā wahine hāpai me ka pheochromocytoma e komo pū paha me ke keʻoki.

No ka ʻike e pili ana i nā lāʻau i helu ʻia ma lalo, e ʻike i ka ʻaoʻao Overtion Option Overview.

Pono nā wahine hāpai me ka pheochromocytoma i kahi mālama kūikawā.

ʻOiai ʻike pinepine ʻole ʻia i ka wā hāpai, hiki i ka pheochromocytoma ke koʻikoʻi loa no ka makuahine a me ka hānau hou. Pono nā wahine i loaʻa ka nui o ka makaʻu o ka pheochromocytoma i ka hoʻāʻo mua. Pono e mālama ʻia nā wahine hāpai me ka pheochromocytoma e kahi hui o nā kauka he loea i kēia ʻano mālama.

ʻO nā hōʻailona o ka pheochromocytoma i ka hāpai hāpai ʻana e hoʻopili pū i kekahi o kēia mau mea:

  • ʻO ke koko kiʻekiʻe i ka manawa o 3 mau mahina mua o ka hāpai ʻana.
  • Nā wā kūpikipiki o ke koko kiʻekiʻe.
  • ʻO ke kiʻekiʻe o ke koko e paʻakikī e mālama.

ʻO ke kuhi o ka pheochromocytoma i nā wahine hāpai me ka hoʻāʻo ʻana no nā pae catecholamine i ke koko a me ka mimi. E ʻike i ka ʻikepili ʻike ākea no ka wehewehe ʻana o kēia mau hoʻāʻo a me nā kaʻina hana. Hiki ke hana ʻia kahi MRI e loaʻa palekana i nā tumors i nā wahine hāpai no ka mea ʻaʻole ia e hōʻike i ka fetus i ka radiation.

ʻO ka mālama ʻana i nā wahine hāpai me ka pheochromocytoma e komo pū paha me ke keʻoki.

ʻO ka mālama ʻana i ka pheochromocytoma i ka wā hāpai hāpai e hoʻopili pū i kēia mau mea:

  • ʻO ke keʻoki e hoʻopau loa i ka maʻi ʻaʻai i ka manawa o ka trimester ʻelua (ʻo ka hā ma o ka ono o ka malama o ka hāpai ʻana).
  • ʻO ke kaha e hoʻopau loa i ka maʻi ʻaʻai e hui pū ʻia me ka lawe ʻana o ka fetus e ka ʻāpana cesarean.

E aʻo hou aʻe e pili ana iā Pheochromocytoma a me Paraganglioma

No ka ʻike hou aku mai ka National Cancer Institute e pili ana i ka pheochromocytoma a me ka paraganglioma, e nānā i kēia:

  • ʻO Pheochromocytoma a me Paraganglioma Home ʻAoʻao
  • ʻO ke kamaliʻi Pheochromocytoma a me Paraganglioma lapaʻau
  • ʻO Cryosurgery i ka mālama ʻana i ka maʻi ʻaʻai: Nā nīnau a me nā pane
  • ʻO nā Therapy Cancer i kau ʻia
  • Ke hoʻāʻo genetic no ka hoʻoilina hoʻoilina maʻi maʻi maʻi Syndromes

No ka ʻike ākea maʻi ʻaʻai a me nā kumuwaiwai ʻē aʻe mai ka National Cancer Institute, e ʻike i ka mea aʻe:

  • E pili ana i ka maʻi ʻaʻai
  • Ke hoʻokū nei
  • ʻO Chemotherapy a ʻo ʻoe: Kākoʻo no ka poʻe me ka maʻi ʻaʻai
  • Radiation Therapy a ʻo ʻoe: Kākoʻo no ka poʻe me ka maʻi ʻaʻai
  • Ke kāohi nei i ka maʻi ʻaʻai
  • Nā nīnau e nīnau ai i kāu kauka e pili ana i ka maʻi ʻaʻai
  • No nā mea ola a me nā mea mālama


Hoʻohui i kāu manaʻo
aloha aloha.co i nā ʻōlelo a pau . Inā ʻaʻole ʻoe makemake e lilo i inoa inoa ʻole , kau inoa a ʻeʻe . Manuahi ia.