Types/myeloproliferative/patient/chronic-treatment-pdq
Nā ʻikepili i loko
- 1 Maʻi Myeloproliferative Neoplasms iapaau ana (®) –Patient Version
- 1.1 ʻO ka ʻikepili ākea e pili ana i nā Neoplasms Myeloproliferative Chronic
- 1.2 ʻO Leukemia Myelogenous mau
- 1.3 ʻO Polycythemia Vera
- 1.4 Myelofibrosis kumu
- 1.5 Pono Thrombocythemia
- 1.6 ʻO Leukemia Neutrophilic mau
- 1.7 ʻO Leukemia Eosinophilic maʻi mau
- 1.8 Nā kahua o ka Myeloproliferative Neoplasms maʻi
- 1.9 Laulā Manaʻo Option Oponopono
- 1.10 Hoʻomaʻamaʻa i nā Chronic Myeloproliferative Neoplasms
- 1.11 E aʻo hou aʻe e pili ana i nā Chronic Myeloproliferative Neoplasms
Maʻi Myeloproliferative Neoplasms iapaau ana (®) –Patient Version
ʻO ka ʻikepili ākea e pili ana i nā Neoplasms Myeloproliferative Chronic
NA MANA KUNI
- ʻO nā neoplasms Myeloproliferative kahi hui o nā maʻi kahi e hoʻonui ai ka iwi iwi i nā ʻulaʻula o ke kokoʻulaʻula, nā hunaola keʻokeʻo, a i ʻole nā platelet.
- Aia he 6 ʻano o neoplasms myeloproliferative mau.
- Hoʻohana ʻia nā hoʻāʻo e nānā i ke koko a me ka iwi o ka iwi e ʻike pono i nā neoplasms myeloproliferative mau.
ʻO nā neoplasms Myeloproliferative kahi hui o nā maʻi kahi e hoʻonui ai ka iwi iwi i nā ʻulaʻula o ke kokoʻulaʻula, nā hunaola keʻokeʻo, a i ʻole nā platelet.
ʻO ka maʻamau, hana ka iwi o ka iwi i nā huna koko (ʻaʻa ʻole) e lilo i mau puʻuwai koko makua ma mua o ka manawa.

Hiki i ke kinipōpō kūpoko ke lilo i cell cell myeloid a i ʻole ka cell stem lymphoid. Lilo ke kinipōpō limapiʻi i keʻena keokeo. E lilo i kahi cell myeloid stem i hoʻokahi o ʻekolu mau ʻano o nā hunaola makua oʻo:
- ʻO nā hunaola ʻulaʻula e lawe i ka oxygen a me nā mea ʻē aʻe i nā kinona āpau o ke kino.
- ʻO nā hunaola keʻokeʻo e hakakā i ka maʻi a me ka maʻi.
- ʻO nā pāpale e hana ana i ke kahe o ke koko e hōʻoki i ke kahe ʻana o ke kahe.
I nā neoplasms myeloproliferative, nui a nui nā aʻa koko i lilo i hoʻokahi a ʻoi aku o nā ʻano koko. Hoʻonui mālie ka neoplasms i ka piʻi ʻana o ka helu o ke keu keu.
Aia he 6 ʻano o neoplasms myeloproliferative mau.
Hoʻokumu ʻia ke ʻano o neoplasm myeloproliferative ma muli o ka hana ʻia o nā hunaola ʻulaʻula, nā ʻula koko keʻokeʻo, a i ʻole nā platelet i hana ʻia. I kekahi manawa e hana ke kino i nā mea ʻoi aku ma mua o hoʻokahi ʻano o ke kele koko, akā ʻo ka maʻamau ʻoi aku ka nui o ke ʻano o ke kele koko ma mua o nā mea ʻē aʻe. Hoʻopili nā neoplasms myeloproliferative mau i nā ʻano 6 aʻe:
- Leukemia myelogenous mau.
- ʻO Polcythemia vera.
- Myelofibrosis kumu (i kapa ʻia he myelofibrosis idiopathic mau).
- Pono thrombocythemia.
- Leukemia neutrophilic mau.
- Leukemia eosinophilic maʻi mau.
Hōʻike ʻia kēia mau ʻano ma lalo. ʻO nā neoplasms myeloproliferative mau loa i kekahi manawa e lilo i leukemia koʻikoʻi, kahi i hana ʻia ai nā hunaola keokeo ʻino ʻē aʻe.
Hoʻohana ʻia nā hoʻāʻo e nānā i ke koko a me ka iwi o ka iwi e ʻike pono i nā neoplasms myeloproliferative mau.
Hiki ke hoʻohana ʻia nā hoʻāʻo a me nā kaʻina hana aʻe:
- ʻO ka hoʻāʻo kino a me ka mōʻaukala olakino: kahi hōʻike o ke kino e nānā i nā hōʻailona laulā o ke olakino, e like me ka nānā ʻana i nā hōʻailona o ka maʻi, e like me nā puʻupuʻu a i ʻole nā mea ʻē aʻe e ʻano ʻē. E lawe ʻia kahi moʻolelo o nā ʻano olakino o ka mea maʻi a me nā maʻi i hala a me nā mālama ʻana.
- Helu piha ke koko (CBC) me ka ʻokoʻa: kahi kaʻina hana e huki ʻia ai kahi hāpana o ke koko a nānā ʻia no kēia mau mea:
- ʻO ka helu o nā hunaola ʻulaʻula a me nā platelet.
- ʻO ka helu a me ke ʻano o nā hunaola keokeo.
- ʻO ka nui o ka hemoglobin (ka protein i hāpai i ka oxygen) i loko o nā hunaola ʻulaʻula.
- ʻO ka ʻāpana o ka hāpana koko i hana ʻia i nā hunaola ʻulaʻula.

- Perearal blood smear: Kahi hana e nānā ʻia ai kahi hāpana o ke koko no kēia mau mea:
- Inā he mau ʻulaʻula koko e like me nā waimaka.
- Ka helu a me nā ʻano o nā hunaola keʻokeʻo.
- Ka helu o nā platelet.
- Inā he mau ʻāpana blast.
- Nā aʻo kemika koko: kahi hana e nānā ʻia ai kahi hāpana koko e ana i ka nui o kekahi mau mea i hoʻokuʻu ʻia i loko o ke koko e nā mea a me nā mea i loko o ke kino. ʻO kahi mea maʻamau (ʻoi aʻe a i ʻole haʻahaʻa ma mua o ka maʻamau) o kahi mea hiki ke lilo i hōʻailona o ka maʻi.
- ʻO ka ʻiʻo o ka iwi iwi a me ka biopsy: Ka hemo ʻana o ka iwi iwi, ke koko, a me kahi ʻāpana o ka iwi ma ka hoʻokomo ʻana i kahi kui kolo i loko o ka hipbone a i ʻole ka umauma. ʻIke kahi pathologist i ka momona o ka iwi, ke koko, a me ka iwi ma lalo o kahi microscope e nānā no nā hunaola ʻokoʻa.
- Nānā Cytogenetic: kahi hoʻokolohua hoʻokolohua kahi e helu ai nā chromosome o nā hunaola i kahi hāpana o ka iwi iwi a i ʻole ke koko no nā loli, e like me ka haki, nalowale, hoʻoponopono hou ʻia, a i ʻole nā chromosome keu. ʻO nā loli i kekahi mau chromosome he hōʻailona ia o ka maʻi ʻaʻai. Hoʻohana ʻia ka hoʻoponopono Cytogenetic e kōkua i ke kuhi ʻana i ka maʻi ʻaʻai, e hoʻolālā i ka lāʻau ʻana, a i ʻole e ʻike i ke ʻano o ka maikaʻi o ka mālama ʻana.
- Hōʻike hoʻāʻo Gene: kahi hoʻokolohua hoʻokolohua i hana ʻia ma ka iwi iwi a i ʻole ke koko paha e nānā ai no ka hoʻololi ʻana i nā genes JAK2, MPL, a CALR paha. ʻIke pinepine ʻia kahi hoʻololi JAK2 i nā mea maʻi me ka polycythemia vera, thrombocythemia nui, a me myelofibrosis mua. Loaʻa nā MPL a i ʻole CALR hoʻololi mutation i nā mea maʻi me ka thrombocythemia nui a i ʻole myelofibrosis kumu.
ʻO Leukemia Myelogenous mau
ʻO ka leukemia myelogenous mau loa kahi maʻi kahi i hana ʻia ai nā hunaola keokeo he nui i ka iwi o ka iwi. E ʻike i ka hōʻuluʻulu e pili ana i ka Chronic Myelogenous Leukemia Hana no ka ʻike e pili ana i ka ʻike, ka hoʻonohonoho ʻana, a me ka lāʻau.
ʻO Polycythemia Vera
NA MANA KUNI
- ʻO Polycythemia vera kahi maʻi kahi i nui ai nā hunaola ʻulaʻula i hana ʻia i ka iwi o ka iwi.
- ʻO nā ʻōuli o polycythemia vera me nā headache a me ka manaʻo o ka piha ma lalo o nā iwi ʻaoʻao ma ka ʻaoʻao hema.
- Hoʻohana ʻia nā hoʻokolohua koko kūikawā e kuhikuhi i ka polycythemia vera.
ʻO Polycythemia vera kahi maʻi kahi i nui ai nā hunaola ʻulaʻula i hana ʻia i ka iwi o ka iwi.
I ka polycythemia vera, mānoanoa ke koko me nā hunaola ʻulaʻula he nui. E piʻi aʻe paha ka nui o nā hunaola koko keʻokeʻo a me nā platelet. Hiki i kēia mau keʻa keu ke ʻohiʻohi i loko o ka māpala a hoʻowali. ʻO ka hoʻonui ʻia o nā hunaola ʻulaʻula, nā huna koko keʻokeʻo, a i ʻole nā platelet i loko o ke koko e hiki ai i nā pilikia kahe ʻana o ke kahe a hana i nā clots i nā kīʻaha koko. Hiki i kēia ke hoʻonui i ka makaʻu o ka hahau a hōʻeha puʻuwai paha. I nā mea maʻi i ʻoi aku ma mua o 65 mau makahiki a i ʻole he moʻolelo koʻa koko, ʻoi aku ka kiʻekiʻe o ka hopena o ka hahau a me ka puʻuwai puʻuwai. Loaʻa i ka poʻe maʻi i ka nui o ka makaʻu o ka myeloid leukemia a i ʻole myelofibrosis mua.
ʻO nā ʻōuli o polycythemia vera me nā headache a me ka manaʻo o ka piha ma lalo o nā iwi ʻaoʻao ma ka ʻaoʻao hema.
ʻAʻole pinepine ka Polycythemia vera i nā hōʻailona a i ʻole nā ʻōuli. ʻIke ʻia paha i ka wā o kahi hoʻokolohua koko maʻamau. Hiki i nā hōʻailona a me nā ʻōuli ke piʻi aʻe ka nui o nā huna koko. ʻO nā kumu ʻē aʻe paha ke kumu i nā hōʻailona like a me nā ʻōuli. E hōʻoia me kāu kauka inā loaʻa iā ʻoe kekahi o kēia mau mea:
- ʻO ke ʻano o ke kaomi a i ʻole piha ma lalo o nā iwi ʻaoʻao ma ka ʻaoʻao hema.
- Poʻo poʻo poʻo.
- ʻIke pālua a ʻike paha i nā wahi pouli a makapō paha e hele mai ana a hoʻi.
- Ka ʻume ʻana a puni ke kino, keu hoʻi ma hope o ka lilo i loko o ka wai mehana a wela paha.
- ʻO ka helehelena ʻulaʻula e like me ka maka o ka lā a me ka lā.
- Nawaliwali.
- Puʻupuʻu.
- ʻO ka hōʻemi kaumaha no ke kumu ʻole.
Hoʻohana ʻia nā hoʻokolohua koko kūikawā e kuhikuhi i ka polycythemia vera.
Ma waho aʻe o ka helu piha ʻana o ke koko, ka ʻiʻini o ka iwi iwi a me ka biopsy, a me ke anamanaʻo cytogenetic, hoʻohana ʻia kahi hōʻike erythropoietin serum e hōʻoia i ka polycythemia vera. I kēia hoʻokolohua, nānā ʻia kahi laʻana o ke koko no ka pae o erythropoietin (kahi hormone e hoʻoulu ai i nā hunaola ʻulaʻula hou e hana ʻia). I ka polycythemia vera, ʻoi aku ka haʻahaʻa o ka pae erythropoietin ma mua o ka maʻamau no ka mea ʻaʻole pono ke kino e hana hou i nā hunaola ʻulaʻula.
Myelofibrosis kumu
NA MANA KUNI
- ʻO ka myelofibrosis kumu nui kahi maʻi kahi e kūkulu ai nā hunaola a me nā olonā kūpono ʻole i loko o ka iwi iwi.
- ʻO nā ʻōuli o ka myelofibrosis mua me ka ʻeha ma lalo o nā iwi ʻaoʻao ma ka ʻaoʻao hema a luhi loa.
- Hoʻohālikelike kekahi mau mea i ka wānana (kahi o ke ola ʻana) a me nā koho lapaʻau no ka myelofibrosis mua.
ʻO ka myelofibrosis kumu nui kahi maʻi kahi e kūkulu ai nā hunaola a me nā olonā kūpono ʻole i loko o ka iwi iwi.
Hana ʻia ka momona o ka iwi i nā hunaola e hana i nā huna koko (nā ʻulaʻula o ke koko, nā aʻa koko keʻokeʻo, a me nā platelet) a me kahi pūnaewele o nā olonā e kākoʻo ana i nā aʻa koko. I ka myelofibrosis kumu (i kapa ʻia he myelofibrosis idiopathic maʻi mau), nui ka nui o nā hunaola koko i lilo i mau huna koko ʻaʻole oʻo pono (puhi). ʻO ka pūnaewele o nā olonā i loko o ka iwi o ka iwi e lilo i mānoanoa (e like me ka ʻili o ka maka) a hoʻolohi i ka hiki i nā aʻa koko ke hana i nā huna koko. ʻO kēia ke kumu o nā kino e hana ana i ke koko e hana i ka liʻiliʻi a me ka liʻiliʻi o nā huna koko. I mea e hoʻopiha ai i nā helu o ke koko i hana ʻia i ka momona o ka iwi, e hoʻomaka ana ke ake a me ka iwi e hana i nā huna koko.
ʻO nā ʻōuli o ka myelofibrosis mua me ka ʻeha ma lalo o nā iwi ʻaoʻao ma ka ʻaoʻao hema a luhi loa.
ʻAʻole kumu pinepine nā myelofibrosis kumu i nā hōʻailona a i ʻole nā ʻōuli. ʻIke ʻia paha i ka wā o kahi hoʻokolohua koko maʻamau. Hoʻokumu ʻia nā hōʻailona a me nā ʻōuli e ka myelofibrosis mua a i ʻole nā ʻano ʻē aʻe. E hōʻoia me kāu kauka inā loaʻa iā ʻoe kekahi o kēia mau mea:
- ʻO ka ʻeha a i ʻole ka piha piha ma lalo o nā iwi ʻaoʻao ma ka ʻaoʻao hema.
- ʻOi ka piha ma mua o ka maʻamau i ka wā e ʻai ana.
- Luhi nui loa.
- Pokole o ka hanu.
- Pākuʻi maʻalahi a hoʻokahe paha.
- Petechiae (pālahalaha, ʻulaʻula, kiko kiko ma lalo o ka ʻili i pili i ke kahe ʻana o ke kahe).
- Fiva.
- Hoʻoulu ka pulu o ka pō.
- Kaumaha emi.
Hoʻohālikelike kekahi mau mea i ka wānana (kahi o ke ola ʻana) a me nā koho lapaʻau no ka myelofibrosis mua.
Aia ka Prognosis i kēia mau mea:
- ʻO ka makahiki o ka mea hoʻomanawanui.
- ʻO ka helu o nā hunaola ʻulaʻula ʻokoʻa a me nā hunaola keokeo.
- Ka helu o nā pahū i ke koko.
- Inā loaʻa kekahi mau hoʻololi i nā chromosome.
- Inā paha he hōʻailona ko ka mea hoʻomanawanui e like me ke kuni, ka pulu ʻana i ka malo i ka pō, a i ʻole ka pohō kaumaha.
Pono Thrombocythemia
NA MANA KUNI
- ʻO ka thrombocythemia nui kahi maʻi kahi i hana ʻia ai nā platelet he nui i ka iwi o ka iwi.
- ʻO nā mea maʻi me ka thrombositosis pono ʻaʻohe o lākou hōʻailona a hōʻailona paha.
- Kū kekahi mau kumu i ka wānana (kahi manawa o ke ola hou) a me nā koho lapaʻau no ka thrombositosis pono.
ʻO ka thrombocythemia nui kahi maʻi kahi i hana ʻia ai nā platelet he nui i ka iwi o ka iwi.
Pono ka thrombocythemia nui i ka hoʻonui maʻamau o ka helu o nā platelet i hana ʻia i ke koko a me ka iwi iwi.
ʻO nā mea maʻi me ka thrombositosis pono ʻaʻohe o lākou hōʻailona a hōʻailona paha.
ʻAʻole hiki i ka thrombocythemia nui ke kumu i nā ʻōuli a i ʻole nā hōʻailona mua. ʻIke ʻia paha i ka wā o kahi hoʻokolohua koko maʻamau. Hoʻokumu ʻia nā hōʻailona a me nā ʻōuli e ka thrombositopenia kūpono a i ʻole nā kūlana ʻē aʻe. E hōʻoia me kāu kauka inā loaʻa iā ʻoe kekahi o kēia mau mea:
- ʻEha poʻo.
- Ke puhi ʻana a i ʻole ke kani ʻana i nā lima a me nā wāwae.
- ʻO kaʻulaʻula a me ka mahanahana o nā lima a me nā wāwae.
- Nā pilikia ʻike a i ʻole hoʻolohe.
Pili nā pālaki. Ke nui a lehulehu nā pāhili, hui pū paha lākou a paʻakikī i ke kahe o ke koko. Hiki ke hana i nā Clots i loko o nā kīʻaha koko a ma laila e hoʻonui ʻia ai ke kahe ʻana. Hiki i kēia mau mea ke hoʻopilikia i nā pilikia olakino koʻikoʻi e like me ka hahau ʻana a i ʻole ka puʻuwai puʻuwai.
Kū kekahi mau kumu i ka wānana (kahi manawa o ke ola hou) a me nā koho lapaʻau no ka thrombositosis pono.
ʻO ka koho Prognosis a me nā koho lapaʻau e pili ana i kēia:
- ʻO ka makahiki o ka mea hoʻomanawanui.
- Inā he mau hōʻailona a hōʻailona paha ka mea maʻi a i ʻole nā pilikia ʻē aʻe e pili ana i ka thrombocythemia nui.
ʻO Leukemia Neutrophilic mau
ʻO ka leukemia neutrophilic mau loa kahi maʻi kahi i lilo ai nā keʻa koko he ʻano o ke koko keʻokeʻo i kapa ʻia he neutrophils. ʻO nā Neutrophil nā maʻi koko e hakakā ana i nā maʻi koko e hoʻopuni a luku i nā hunaola make a me nā mea haole (e like me bacteria). Pehu paha ka iwi a me ke akepaʻa no ka mea keu neutrophils. Hiki ke noho like me ka leukemia neutrophilic mau a i ʻole e hele wikiwiki paha i ka leukemia koʻikoʻi.
ʻO Leukemia Eosinophilic maʻi mau
NA MANA KUNI
- ʻO ka leukemia eosinophilic maʻi mau kahi maʻi kahi i hana ʻia ai nā hunaola keokeo he nui (eosinophil) i ka momona o ka iwi.
- ʻO nā hōʻailona a me nā ʻōuli o ka leukemia eosinophilic mau e pili ana i ke kuni a me ka luhi loa.
ʻO ka leukemia eosinophilic maʻi mau kahi maʻi kahi i hana ʻia ai nā hunaola keokeo he nui (eosinophil) i ka momona o ka iwi.
ʻO nā Eosinophil he mau keʻokeʻo koko keʻokeʻo e hana i nā mea āpau (nā mea e hopena i kahi pane maʻi) a kōkua i ke kaua ʻana i nā maʻi i hoʻokumu ʻia e kekahi mau parasite I ka leukemia eosinophilic mau, he nui nā eosinophil i loko o ke koko, ka iwi iwi, a me nā mea ʻē aʻe. Hiki ke noho like ka leukemia eosinophilic mau no nā makahiki he nui a i ʻole e holomua wikiwiki i ka leukemia koʻikoʻi.
ʻO nā hōʻailona a me nā ʻōuli o ka leukemia eosinophilic mau e pili ana i ke kuni a me ka luhi loa.
ʻAʻole hiki i ka leukemia eosinophilic maʻi ke kumu i nā ʻōuli a i ʻole nā ʻōuli. ʻIke ʻia paha i ka wā o kahi hoʻokolohua koko maʻamau. Hoʻokumu ʻia nā hōʻailona a me nā ʻōuli e ka leukemia eosinophilic mau a i ʻole nā kūlana ʻē aʻe. E hōʻoia me kāu kauka inā loaʻa iā ʻoe kekahi o kēia mau mea:
- Fiva.
- Luhi nui loa.
- Cough.
- ʻO ka pehu ma lalo o ka ʻili a puni nā maka a me nā lehelehe, i ka ʻāʻī, a i ʻole nā lima a me nā wāwae.
- ʻEha ʻeha.
- Kāwili.
- Pohā.
Nā kahua o ka Myeloproliferative Neoplasms maʻi
NA MANA KUNI
- ʻAʻohe ʻōnaehana hoʻonohonoho maʻamau no nā neoplasms myeloproliferative mau.
ʻAʻohe ʻōnaehana hoʻonohonoho maʻamau no nā neoplasms myeloproliferative mau.
ʻO ke kau ʻana ke hana e ʻike ai i ka lōʻihi o ka laha ʻana o ka maʻi ʻaʻai. ʻAʻohe ʻōnaehana hoʻonohonoho maʻamau no nā neoplasms myeloproliferative mau. Hoʻokumu ʻia ka lapaʻau ma ke ʻano o ka myeloproliferative neoplasm a ka mea maʻi. He mea nui e ʻike i ke ʻano i mea e hoʻolālā ai i ka lāʻau.
Laulā Manaʻo Option Oponopono
NA MANA KUNI
- Aia nā ʻano lapaʻau like ʻole no nā mea maʻi me nā neoplasma myeloproliferative mau.
- Hoʻohana ʻia ʻumikūmākahi mau ʻano o ka hoʻomaʻamaʻa maʻamau:
- Ke kali kiaʻi nei
- Phlebotomy
- ʻApelika platelet
- Hoʻoiho transfusion
- ʻO Chemotherapy
- Lapaʻau hoʻomākala
- Laau lāʻau ʻē aʻe
- ʻOki kino
- Hoʻolaola biologic
- Pahuhopu kau ʻia
- ʻO ka chemotherapy kiʻekiʻe me ka transplant cell stem
- Ke hoʻāʻo ʻia nei nā ʻano lapaʻau hou i nā hoʻokolohua hoʻokolohua.
- ʻO ka mālama ʻana i nā neoplasma myeloproliferative mau loa ke kumu o ka hopena.
- Makemake paha nā mea maʻi e noʻonoʻo e pili ana i ka hoʻokolokolo ʻana.
- Hiki i nā mea maʻi ke komo i nā hoʻokolohua hoʻokolohua ma mua, i ka wā, a ma hope paha o ka hoʻomaka ʻana i kā lākou mālama maʻi ʻaʻai.
- Pono paha nā hoʻokolohua ukali.
Aia nā ʻano lapaʻau like ʻole no nā mea maʻi me nā neoplasma myeloproliferative mau.
Loaʻa nā ʻano lapaʻau like ʻole no nā mea maʻi me nā neoplasma myeloproliferative mau. Kūlana maʻamau kekahi mau hōʻailona (ʻo ka lāʻau i hoʻohana ʻia i kēia manawa), a ʻo kekahi e hoʻāʻo ʻia nei i nā hoʻokolohua hoʻokolohua. ʻO kahi hoʻokolohua hoʻokolohua hoʻokolohua kahi noiʻi noiʻi i manaʻo ʻia e kōkua i ka hoʻomaikaʻi ʻana i nā mālama ʻana i kēia manawa a i ʻole loaʻa ka ʻike e pili ana i nā mālama hou. Ke hōʻike nā hoʻokolohua hoʻokolohua ʻoi aku ka maikaʻi o kahi lapaʻau hou ma mua o ka maʻamau maʻamau, lilo paha ka lāʻau hou i ka lapaʻau maʻamau. Makemake paha nā mea maʻi e noʻonoʻo e pili ana i ka hoʻokolokolo ʻana. ʻO kekahi mau hoʻokolohua hoʻokolohua e hāmama wale i nā mea maʻi i hoʻomaka ʻole i ka lāʻau.
Hoʻohana ʻia ʻumikūmākahi mau ʻano o ka hoʻomaʻamaʻa maʻamau:
Ke kali kiaʻi nei
Ke kali nei ke kiaʻi me ka nānā pono ʻana i ke ʻano o ka mea maʻi me ka ʻole o ka hāʻawi ʻana i nā lāʻau a hiki i ka wā e ʻike ʻia ai nā hōʻailona a i ʻole nā loli.
Phlebotomy
ʻO Phlebotomy kahi hana e lawe ʻia ai ke koko mai kahi aa koko. Lawe ʻia kahi laʻana o ke koko no nā hoʻokolohua e like me CBC a i ʻole kemika koko. I kekahi manawa hoʻohana ʻia ka phlebotomy ma ke ʻano he lāʻau lapaʻau a lawe ʻia ke koko mai ke kino e lawe i nā keena ʻulaʻula keu. Hoʻohana ʻia ʻo Phlebotomy i kēia ala e mālama ai i kekahi mau neoplasms myeloproliferative mau.
ʻApelika platelet
ʻO ka plather apheresis kahi lapaʻau e hoʻohana ai i kahi mīkini kūikawā e lawe i nā platelet mai ke koko. Lawe ʻia ke koko mai ka mea maʻi a waiho ʻia i loko o kahi hoʻokaʻawale o ke koko kahi e hemo ai nā pā. A laila hoʻihoʻi ʻia ke koena o ke koko i ke kahena o ka mea maʻi.
Hoʻoiho transfusion
ʻO ke Transfusion therapy (ke kōpili ʻana) kahi hana o ka hāʻawi ʻana i nā hunaola ʻulaʻula, nā ʻula koko keʻokeʻo, a i ʻole nā platelet e pani i nā hunaola koko i luku ʻia e ka maʻi a i ʻole ka mālama ʻana i ka maʻi ʻaʻai.
ʻO Chemotherapy
ʻO Chemotherapy kahi lāʻau lapaʻau maʻi maʻi e hoʻohana i nā lāʻau e hōʻoki i ka ulu ʻana o nā hunaola maʻi ʻaʻai, ma ka luku ʻana i nā hunaola a i ʻole ke kāpae ʻana iā lākou mai ka hoʻokaʻawale. Ke lawe ʻia ka chemotherapy e ka waha a i ʻole injected i loko o kahi aa koko a i ʻole nā mākala, komo nā lāʻau i ke kahe o ke koko a hiki ke kiʻi i nā hunaola maʻi ʻōpio i loko o ke kino (chemotherapy ʻōnaehana). Ke waiho pololei ʻia ka chemotherapy i loko o ka wai cerebrospinal, kahi hui, a i ʻole ke kino o ke kino e like me ka ʻōpū, ʻo nā lāʻau lapaʻau ka mea nui e hoʻopili i nā hunaola maʻi ʻaʻai i kēlā mau wahi (chemotherapy āpau). Hāʻawi ʻia ke ala o ka chemotherapy i ka ʻano a me ke kahua o ka maʻi ʻaʻai e mālama ʻia.
E ʻike i nā lāʻau i ʻae ʻia no Myeloproliferative Neoplasms no ka ʻike hou aku.
Lapaʻau hoʻomākala
ʻO ka radiation radiation kahi lāʻau maʻi maʻi maʻi e hoʻohana i nā kukuna x nui ikaika a i ʻole nā ʻano radiation e hoʻomake i nā hunaola maʻi ʻaʻai a mālama ʻole paha i ka ulu ʻana. Hoʻohana ka radiation radiation kūwaho i kahi mīkini ma waho o ke kino e hoʻouna i ka radiation i kahi o ke kino me ka maʻi ʻaʻai.
Hoʻohana ʻia ka radiation radiation kūwaho e mālama ai i nā neoplasms myeloproliferative mau, a kuhikuhi pinepine ʻia i ka mahuna.
Laau lāʻau ʻē aʻe
ʻO Prednisone a danazol nā lāʻau i hiki ke hoʻohana ʻia e mālama ai i ka anemia i nā mea maʻi me ka myelofibrosis mua.
Hoʻohana ʻia ʻo Anagrelide therapy e hōʻemi i ka makaʻu o ke kahe o ke koko i nā mea maʻi i nui nā platelet i loko o ko lākou koko. Hiki ke hoʻohana ʻia ka aspirin haʻahaʻa e hoʻoliʻiliʻi i ka makaʻu o ke koko koko.
ʻO Thalidomide, lenalidomide, a me pomalidomide nā lāʻau e pale aku i nā kīʻaha koko e ulu ana i nā wahi o nā hunaola tumele.
E ʻike i nā lāʻau i ʻae ʻia no Myeloproliferative Neoplasms no ka ʻike hou aku.
ʻOki kino
Hiki ke hana i ka Splenectomy (ʻoki e wehe i ka iwi maha) inā hoʻonui ʻia ka palahalaha.
Hoʻolaola biologic
ʻO Biologic therapy kahi lapaʻau e hoʻohana i ka ʻōnaehana pale maʻi o ka mea maʻi e hakakā i ke kanesa a i ʻole nā maʻi ʻē aʻe. Hoʻohana ʻia nā mea i hana ʻia e ke kino a i hana ʻia paha i kahi keʻena hoʻokolohua e hoʻonui, kuhikuhi, a hoʻihoʻi hou i nā pale kūlohelohe o ke kino i ka maʻi. Kāhea ʻia kēia ʻano lapaʻau ʻo biotherapy a i ʻole immunotherapy. ʻO Interferon alfa a me pegylated interferon alpha nā meaola biologic i hoʻohana pinepine ʻia e mālama i kekahi mau neoplasms myeloproliferative mau.
ʻO nā kumu ulu ulu ʻo Erythropoietic kekahi ʻoihana biologic. Hoʻohana ʻia lākou e hoʻonāuki i ka iwi iwi e hana i nā hunaola ʻulaʻula.
Pahuhopu kau ʻia
ʻO ka therapy target kahi ʻano lapaʻau e hoʻohana i nā lāʻau a i ʻole nā mea ʻē aʻe e ʻike a hoʻouka i nā hunaola maʻi ʻaʻai me ka ʻole e hōʻeha i nā hunaola maʻamau. Hoʻopili ʻia nā mea kāohi ʻo Tyrosine kinase i nā lāʻau lapaʻau e kāohi i nā hōʻailona e pono ai e ulu nā tumors.
ʻO Ruxolitinib kahi mea kāpae tyrosine kinase i hoʻohana ʻia e mālama i ka polycythemia vera a me kekahi mau ʻano myelofibrosis.
E ʻike i nā lāʻau i ʻae ʻia no Myeloproliferative Neoplasms no ka ʻike hou aku.
Ke aʻo ʻia nei nā ʻano ʻano lāʻau hoʻomōhala ʻē aʻe i nā hoʻokolohua hoʻokolohua.
ʻO ka chemotherapy kiʻekiʻe me ka transplant cell stem
Hāʻawi ʻia nā lāʻau kiʻekiʻe o ka chemotherapy e pepehi i nā hunaola maʻi ʻaʻai. Hoʻopau pū ʻia nā hunaola olakino, e like me nā hunaola koko, e ka lāʻau maʻi ʻaʻai. ʻO ka transplant cell Stem kahi lapaʻau e pani i nā hunaola koko. Lawe ʻia nā hunaola ʻōpala (ʻaʻaʻa ʻole o ke koko) mai ke koko a i ʻole ka iwi o ka mea maʻi a i ʻole he mea hāʻawi a hoʻopaʻa ʻia a mālama ʻia. Ma hope o ka pau ʻana o ka chemotherapy i ka mea hoʻomanawanui, hoʻoheheʻe ʻia nā pūnaewele i mālama ʻia a hoʻihoʻi ʻia i ka mea maʻi ma o ka infusion. E ulu kēia mau hunaola i (a hoʻihoʻi) i nā huna koko o ke kino.

Ke hoʻāʻo ʻia nei nā ʻano lapaʻau hou i nā hoʻokolohua hoʻokolohua.
Loaʻa nā ʻike e pili ana i nā hoʻokolohua hoʻokolohua mai ka pūnaewele NCI.
ʻO ka mālama ʻana i nā neoplasma myeloproliferative mau loa ke kumu o ka hopena.
No ka ʻike e pili ana i nā hopena i hopena ʻia e ka lapaʻau ʻana no ka maʻi ʻaʻai, e ʻike i kā mākou ʻaoʻao ʻaoʻao ʻaoʻao.
Makemake paha nā mea maʻi e noʻonoʻo e pili ana i ka hoʻokolokolo ʻana.
No kekahi mau mea maʻi, ke komo nei i ka hoʻokolohua hoʻokolohua ke koho lapaʻau maikaʻi loa paha. ʻO nā hoʻokolohua hoʻokolohua kahi ʻāpana o ka noiʻi ʻana o ka maʻi ʻaʻai. Hana ʻia nā hoʻokolohua hoʻokolohua e ʻike inā palekana a maikaʻi a maikaʻi paha nā hoʻomaʻamaʻa maʻi ʻaʻai ma mua o ka maʻamau maʻamau.
ʻO ka hapa nui o nā hana maʻamau no ka maʻi ʻaʻai i kau ʻia ma nā hoʻokolohua hoʻokolohua mua. ʻO nā mea maʻi i komo i ka hoʻokolokolo hoʻokolohua hiki ke loaʻa i ka lāʻau maʻamau a i ʻole i waena o nā mea mua i loaʻa kahi lāʻau hou.
ʻO nā mea maʻi i komo i nā hoʻokolohua hoʻokolohua kōkua pū kekahi i ka hoʻomaikaʻi ʻana i ke ʻano o ka mālama ʻana i ka maʻi ʻaʻai i ka wā e hiki mai ana. ʻOiai ʻaʻole nā alakaʻi hoʻokolohua e alakaʻi i nā hoʻoponopono hou maikaʻi, pane pinepine lākou i nā nīnau nui a kōkua i ka neʻe i mua o ka noiʻi.
Hiki i nā mea maʻi ke komo i nā hoʻokolohua hoʻokolohua ma mua, i ka wā, a ma hope paha o ka hoʻomaka ʻana i kā lākou mālama maʻi ʻaʻai.
Hoʻopili wale kekahi mau hoʻokolohua hoʻokolohua i nā mea maʻi i loaʻa ʻole ka lapaʻau. ʻO nā hoʻokolohua ʻē aʻe e hōʻoia i nā mālama ʻana no ka poʻe maʻi i loaʻa ʻole ka maikaʻi o ka maʻi ʻaʻai. Aia kekahi mau hoʻokolohua hoʻokolohua e hoʻāʻo i nā ala hou e hōʻoki i ka maʻi ʻaʻai mai ka hoʻi hou ʻana (hoʻi ʻana) a hōʻemi paha i nā hopena o ka mālama ʻana i ka maʻi ʻaʻai.
Ke mālama ʻia nei nā hoʻokolohua hoʻokolohua ma nā wahi he nui o ka ʻāina. Hiki ke ʻike ʻia ka ʻike e pili ana i nā hoʻokolohua hoʻokolohua e kākoʻo ʻia e NCI ma ka pūnaewele ʻimi noiʻi hoʻokolohua a NCI. Hiki ke loaʻa nā hoʻokolohua hoʻokolohua i kākoʻo ʻia e nā hui ʻē aʻe ma ka pūnaewele ClinicalTrials.gov.
Pono paha nā hoʻokolohua ukali.
ʻO kekahi o nā hoʻokolohua i hana ʻia e hōʻoia i ka maʻi ʻaʻai a i ʻole e ʻike i ke kahua o ka maʻi ʻaʻaʻa e hana hou ʻia paha. E hana hou ʻia kekahi mau hōʻike i mea e ʻike ai i ka maikaʻi o ka mālama ʻana. Hoʻoholo ʻia nā hoʻoholo e pili ana inā e hoʻomau, hoʻololi, a kū paha i ka lāʻau ʻana ma nā hopena o kēia mau hoʻāʻo.
E hoʻomau ʻia kekahi o nā hoʻokolohua mai kēlā me kēia manawa ma hope o ka pau ʻana o ka lāʻau. Hiki i nā hopena o kēia mau hoʻāʻo ke hōʻike inā ua loli kou ʻano a i ʻole inā ua hoʻi hou ke kanesa. Kapa ʻia kēia mau hoʻāʻo i kekahi manawa nā hoʻokolohua ukali a i ʻole nā loiloi.
Hoʻomaʻamaʻa i nā Chronic Myeloproliferative Neoplasms
Ma keia Pauku
- ʻO Leukemia Myelogenous mau
- ʻO Polycythemia Vera
- Myelofibrosis kumu
- Pono Thrombocythemia
- ʻO Leukemia Neutrophilic mau
- ʻO Leukemia Eosinophilic maʻi mau
No ka ʻike e pili ana i nā lāʻau i helu ʻia ma lalo, e ʻike i ka ʻaoʻao Overtion Option Overview.
ʻO Leukemia Myelogenous mau
E ʻike i ka hōʻuluʻulu e pili ana i ka Chronic Myelogenous Leukemia Hana no ka ʻike.
ʻO Polycythemia Vera
ʻO ke kumu o ka mālama ʻana no polycythemia vera e hōʻemi i ka nui o nā keena koko keu. Hiki i ka mālama ʻana i ka polycythemia vera ke hoʻopili i kēia mau mea:
- Phlebotomy.
- Chemotherapy me a i ʻole phlebotomy. Inā ʻaʻole holo ka chemotherapy, hāʻawi ʻia i kahi lāʻau hoʻomāka ʻia (ruxolitinib).
- ʻO ka biologic therapy e hoʻohana ana i ka alfa interferon alfa a i ʻole pegylated interferon alpha.
- Aspirin haʻahaʻa
E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.
Myelofibrosis kumu
ʻO ka mālama ʻana i ka myelofibrosis mua i nā mea maʻi me ka ʻole o nā hōʻailona a i ʻole nā hōʻailona e kakali pinepine ana.
ʻO nā mea maʻi me ka myelofibrosis mua he mau hōʻailona a hōʻailona paha o ka anemia. Mālama mau ʻia ʻo Anemia me ka transfusion o nā hunaola ʻulaʻula e hōʻoluʻolu ai i nā ʻōuli a hoʻomaikaʻi i ke ola. Eia hou, hiki ke mālama ʻia me ka anemia me:
- Nā kumu ulu ulu ʻErythropoietic.
- Prednisone.
- Danazol.
- ʻO Thalidomide, lenalidomide, a i ʻole pomalidomide, me a i ʻole prednisone.
ʻO ka mālama ʻana i ka myelofibrosis mua i nā mea maʻi me nā ʻōuli a i ʻole nā hōʻailona ʻē aʻe e like me kēia:
- Hoʻopaʻa kaulike ʻia me ruxolitinib.
- ʻO Chemotherapy.
- Ke kuʻi ʻana o ke koʻokoʻo Donor.
- Thalidomide, lenalidomide, a i ʻole pomalidomide.
- Splenectomy.
- ʻO ka radiation radiation i ka spleen, lymph nodes, a i ʻole nā wahi ʻē aʻe ma waho o ka iwi iwi kahi e hana ai nā hunaola.
- ʻO ka biologic therapy e hoʻohana ana i nā alfa interferon alfa a i ʻole erythropoietic ulu.
- ʻO kahi hoʻokolohua hoʻokolohua o nā lāʻau lapaʻau i hoʻomāka ʻia
E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.
Pono Thrombocythemia
ʻO ka mālama ʻana i ka thrombositosis pono i nā mea maʻi ma mua o 60 mau makahiki i loaʻa ʻole nā hōʻailona a me nā hōʻailona a ke kali nei ka helu platelet ʻoluʻolu. ʻO ka mālama ʻana i nā mea maʻi ʻē aʻe i kēia mau mea:
- ʻO Chemotherapy.
- ʻAnagrelide therapy.
- ʻO ka biologic therapy e hoʻohana ana i ka alfa interferon alfa a i ʻole pegylated interferon alpha.
- ʻApelika platelet.
- ʻO kahi hoʻokolohua hoʻokolohua o kahi lapaʻau hou.
E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.
ʻO Leukemia Neutrophilic mau
ʻO ka mālama ʻana i ka leukemia neutrophilic mau e komo pū paha me kēia:
- Ke kuʻi iwi o ka mea hāʻawi.
- ʻO Chemotherapy.
- ʻO Biologic therapy e hoʻohana ana i interferon alfa.
- ʻO kahi hoʻokolohua hoʻokolohua o kahi lapaʻau hou.
E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.
ʻO Leukemia Eosinophilic maʻi mau
ʻO ka mālama ʻana i ka leukemia eosinophilic mau e komo pū me kēia:
- Hoʻoneʻe iwi iwi.
- ʻO Biologic therapy e hoʻohana ana i interferon alfa.
- ʻO kahi hoʻokolohua hoʻokolohua o kahi lapaʻau hou.
E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.
E aʻo hou aʻe e pili ana i nā Chronic Myeloproliferative Neoplasms
No ka ʻike hou aku mai ka National Cancer Institute e pili ana i nā neoplasms myeloproliferative mau, e ʻike i ka mea aʻe:
- ʻAoʻao Myopoproliferative Neoplasms
- Ua ʻae ʻia nā lāʻau no Myeloproliferative Neoplasms
- Immunotherapy e mālama i ka maʻi ʻaʻai
- ʻO nā Transplant Cell-Blood Stem
- ʻO nā Therapy Cancer i kau ʻia
No ka ʻike ākea maʻi ʻaʻai a me nā kumuwaiwai ʻē aʻe mai ka National Cancer Institute, e ʻike i ka mea aʻe:
- E pili ana i ka maʻi ʻaʻai
- Ke hoʻokū nei
- ʻO Chemotherapy a ʻo ʻoe: Kākoʻo no ka poʻe me ka maʻi ʻaʻai
- Radiation Therapy a ʻo ʻoe: Kākoʻo no ka poʻe me ka maʻi ʻaʻai
- Ke kāohi nei i ka maʻi ʻaʻai
- Nā nīnau e nīnau ai i kāu kauka e pili ana i ka maʻi ʻaʻai
- No nā mea ola a me nā mea mālama