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Wilms Tumor a me nā kamaliʻi kamaliʻi kamaliʻi ʻōiwi ʻē aʻe (®) - Mana Mana Manaʻo

Nā ʻIkepili Nui e pili ana iā Wilms Tumor a me nā Tumine Kidney Childhood ʻē aʻe

NA MANA KUNI

  • ʻO nā ʻōpū puʻukū ʻōpiopio nā maʻi kahi e kū ai nā maʻi malignant (cancer) i loko o nā aʻa o ka puʻupaʻa.
  • Nui a hewahewa nā ʻano ʻōpuʻu o ke keiki.
  • ʻO Wilms Tumor
  • Ka Puʻukū Pūʻali Renal (RCC)
  • ʻO Rhabdoid Tumor o ka hakuʻala
  • Maopopo Cell Sarcoma o ka hakuʻala
  • ʻO Mesoblastic Neproma Congenital
  • ʻO Ewing Sarcoma o ka hakuʻala
  • ʻO Carenaloma Ryo Myoepithelial Renal
  • ʻO Nefroblastoma ʻokoʻa hapa o Cystic
  • ʻO Multrococular Cystic Nefroma
  • ʻO Sarcoma Synovial Renal Maʻamau
  • Anaplastic Sarcoma o ka hakuʻala
  • ʻO ka nephroblastomatosis ʻaʻole ia he maʻi ʻaʻai akā e lilo paha ia i kahi maʻi Wilms.
  • ʻO ka loaʻa ʻana o kekahi mau syndrome a i ʻole nā ​​kūlana ʻē aʻe hiki ke hoʻonui i ka makaʻu o Wilmm tum tum.
  • Hoʻohana ʻia nā hoʻokolohua e pale ai no ka tumo Wilms.
  • Loaʻa i kekahi mau kūlana e hoʻonui i ka makaʻu o ka maʻi ʻaʻai kolone.
  • ʻO ka mālama ʻana no ka lāʻau Wilms a me nā tumors ʻōiwi ʻē aʻe e komo pū paha me ka ʻōlelo aʻoaʻo ʻaoʻao.
  • ʻO nā ʻōuli o Wilms tumor a me nā ʻōpū ʻōiwi ʻōpiopio ʻē aʻe e hoʻopili me ka puʻupuʻu i loko o ka ʻōpū a me ke koko i ka mimi.
  • Hoʻohana ʻia nā hoʻāʻo e nānā i ka puʻupaʻa a me ke koko e ʻike pono ai i nā tumo Wilms a me nā puʻupaʻa puʻupaʻa keiki ʻē aʻe.
  • Kū kekahi mau kumu i ka wānana (kahi o ke ola ʻana) a me nā koho lapaʻau.

ʻO nā ʻōpū puʻukū ʻōpiopio nā maʻi kahi e kū ai nā maʻi malignant (cancer) i loko o nā aʻa o ka puʻupaʻa.

Aia nā puʻupaʻa ʻelua, hoʻokahi ma kēlā me kēia ʻaoʻao o ka iwi ʻaoʻao, ma luna o ka pūhaka. ʻO nā tubula liʻiliʻi i nā kānana e hoʻomaʻemaʻe a hoʻomaʻemaʻe i ke koko. Lawe lākou i nā huahana neoneo a hana i ka mimi. Holo ka mimi mai kēlā me kēia puʻupaʻa ma o kahi paipu lōʻihi i kapa ʻia he ureter i loko o ka pūpū. Mālama ka puhā i ka mimi a hala i ka urethra a haʻalele i ke kino.

ʻO Anatomy o ka ʻōnaehana urinary wahine e hōʻike ana i nā puʻupaʻa, nā adrenal glands, ureter, bladder, a me urethra. Hana ʻia ka mimi i loko o nā tubula o ka puʻupaʻa a ʻohiʻohi i ke pelvis kidney o kēlā me kēia puʻupaʻa. Kahe ka mimi mai nā puʻupaʻa ma o nā ureter i ka pūpū. Mālama ʻia ka mimi i loko o ka pūpū a hiki i ka haʻalele ʻana i ke kino ma o ka urethra.

Nui a hewahewa nā ʻano ʻōpuʻu o ke keiki.

ʻO Wilms Tumor

I ka puʻupuʻu Wilms, loaʻa i hoʻokahi a ʻoi paha nā ʻōpuʻu i hoʻokahi a i ʻole nā ​​puʻupaʻa ʻelua. E pāhola paha ka ʻōpuʻu ʻo Wilms i nā akemāmā, ke ake, ka iwi, ka lolo, a i ʻole nā ​​lymph node kokoke. I nā keiki a me nā ʻōpio ʻōpio ma mua o 15 mau makahiki, ʻo ka hapanui o nā maʻi ʻaʻai ʻōkō nā Wilms tumors.

Ka Puʻukū Pūʻali Renal (RCC)

He kakaikahi ka maʻi ʻaʻai Renal i nā keiki a me nā ʻōpio ma mua o 15 mau makahiki. ʻOi aku ka maʻamau i nā ʻōpio ma waena o 15 a 19 mau makahiki. ʻIke ʻia nā keiki a me nā ʻōpio me ka puʻuwai puʻupaʻa nui a i ʻole ke kanesa i pāhola. Hiki ke pālahalaha ʻia nā maʻi ʻaʻai kuni i nā akemāmā, ke ake, a i ʻole nā ​​lymph node. Kāhea ʻia ka maʻi ʻaʻai pūpū ma ke ʻano he maʻi puʻuwai puʻuwai puʻuwai.

ʻO Rhabdoid Tumor o ka hakuʻala

ʻO ka tumo Rhabdoid o ka puʻupaʻa kahi ʻano o ke kanulau maʻi ʻaʻai e kū nui i nā pēpē a me nā keiki liʻiliʻi. Hoʻonui pinepine ʻia ia i ka manawa o ke kuhi. Piʻi ka tumo Rhabdoid o ka puʻupaʻa a laha koke, pinepine i nā akemāmā a me ka lolo.

Nānā pinepine ʻia nā kamaliʻi me kahi loli i ka moʻokūʻauhau SMARCB1 e ʻike ai inā ua hana ʻia kahi tumo rhabdoid i loko o ka puʻupaʻa a i laha paha i ka lolo.

  • ʻO nā keiki ma mua o hoʻokahi makahiki ka loaʻa ʻana o ka ultrasound o ka ʻōpū i kēlā me kēia ʻelua a ʻekolu paha mahina a me kahi ultrasound o ke poʻo i kēlā me kēia mahina.
  • ʻO nā keiki hoʻokahi a ʻehā mau makahiki i ka ultrasound o ka ʻōpū a me ka MRI o ka lolo a me ka iwi kuamoʻo i kēlā me kēia ʻekolu mahina.

Maopopo Cell Sarcoma o ka hakuʻala

ʻO ka sarcoma pūnaewele ʻino o ka puʻupaʻa kahi ʻano o ka tumora puʻupaʻa e lele paha i ka akemāmā, iwi, lolo, a palupalu paha. Hiki hou paha ia (hoʻi) a 14 mau makahiki ma hope o ka mālama ʻana, a hoʻi pinepine ia i ka lolo a i ʻole ka akemāmā.

ʻO Mesoblastic Neproma Congenital

ʻO ka nephroma Mesoblastic mesoblastic kahi tumo o ka puʻupaʻa e ʻike pinepine ʻia i ka makahiki mua o ke ola. Hiki ke hoʻōla maʻamau.

ʻO Ewing Sarcoma o ka hakuʻala

ʻAʻole pinepine ʻo Ewing sarcoma (i kapa ʻia he neuroepithelial tumor) o ka puʻupaʻa a maʻamau i nā ʻōpio ʻōpio. Piʻi kēia mau tumors a laha koke i nā ʻāpana ʻē aʻe o ke kino.

ʻO Carenaloma Ryo Myoepithelial Renal

ʻO ka carcinoma myoepithelial renal primer kahi ʻano laha ʻole o ka maʻi ʻaʻai e hoʻopili pinepine i nā kinona palupalu, akā i kekahi manawa hana ʻia i loko o nā ʻāpana o loko (e like me ka hakuʻala). Ulu a ʻano pālahalaha kēia ʻano maʻi ʻaʻai.

ʻO Nefroblastoma ʻokoʻa hapa o Cystic

ʻO nephroblastoma ʻokoʻa ʻokoʻa ʻo Cystic kahi ʻano like ʻole o Wilms tumo i hana ʻia me nā cista.

ʻO Multrococular Cystic Nefroma

ʻO nā nephromas cystic multilocular he tumors benign i hana ʻia i nā cist a ʻike pinepine ʻia i nā pēpē, nā keiki ʻōpio, a me nā wahine makua. Hiki i kēia mau tumors ke hana i hoʻokahi a i ʻole nā ​​puʻupaʻa ʻelua.

Loaʻa paha i nā kamaliʻi me kēia ʻano tumo ka pleuropulmonary blastoma, no laila nā hōʻike kiʻi e nānā i nā māmā no nā cyst a i ʻole nā ​​tumors paʻa. No ka mea he ʻano hoʻoilina ka multilocular cystic nephroma, e noʻonoʻo ʻia paha ka ʻolelo aʻoaʻo a me ka hoʻāʻo ʻana. E ʻike i ka hōʻuluʻulu e pili ana i ka Childhood Pleuropulmonary Blastoma Hana no ka ʻike hou aku.

ʻO Sarcoma Synovial Renal Maʻamau

ʻO ka sarcoma synovial renal mua kahi cyst-like tumo o ka puʻupaʻa a maʻamau i nā ʻōpio ʻōpio. Ulu a palahalaha kēia mau tumors.

Anaplastic Sarcoma o ka hakuʻala

ʻO ka sarcoma anaplastic o ka puʻupaʻa kahi tumo laha ʻole i ʻike pinepine ʻia i nā keiki a ʻōpio ma mua o 15 mau makahiki. Hoʻolahalaha pinepine ka sarapona anaplastic o ka puʻupaʻa i nā akemāmā, ke ake, a i ʻole nā ​​iwi. Hiki ke hana i nā hoʻokolohua kiʻi e nānā i nā akemāmā no nā cist a i ʻole nā ​​tumors paʻa. ʻOiai he ʻano hoʻoilina ka anaplastic sarcoma, e noʻonoʻo ʻia paha ka ʻōlelo aʻoaʻo a me ka hoʻāʻo ʻana.

ʻO ka nephroblastomatosis ʻaʻole ia he maʻi ʻaʻai akā e lilo paha ia i kahi maʻi Wilms.

I kekahi manawa, ma hope o ke kūkulu ʻana o nā puʻupaʻa i loko o ka fetus, noho mau nā hui ʻino ʻole o nā hunaola puʻupaʻa i hoʻokahi a i ʻole nā ​​puʻupaʻa ʻelua. I ka nephroblastomatosis (diffuse hyperplastic perilobar nephroblastomatosis), ulu kēia mau hui ʻino o nā hunaola ma nā wahi he nui i loko o ka puʻupaʻa a i hana i kahi papa mānoanoa a puni ka puʻupaʻa. Ke loaʻa kēia mau pūʻulu o nā hunaola ʻino i loko o kahi puʻupaʻa ma hope o ka lawe ʻia ʻana no ka puʻupuʻu Wilms, ua piʻi ka makaʻu o ke keiki i ka maʻi Wilms i loko o ka puʻuwai ʻē aʻe. ʻO ka hoʻāʻo pinepine ʻana he mea nui ma ka liʻiliʻi i kēlā me kēia 3 mahina, no 7 mau makahiki ma hope o ka mālama ʻia ʻana o ke keiki.

ʻO ka loaʻa ʻana o kekahi mau syndrome a i ʻole nā ​​kūlana ʻē aʻe hiki ke hoʻonui i ka makaʻu o Wilmm tum tum.

ʻO nā mea āpau e hoʻonui i ka makaʻu o ka loaʻa ʻana o ka maʻi i kapa ʻia he kumu weliweli. ʻO ka loaʻa ʻana o kahi mea pilikia ʻaʻole ia he kumu e loaʻa ʻoe i ka maʻi ʻaʻai. ʻaʻohe o nā kumu pilikia ʻaʻole ia he kumu ʻaʻole ʻoe e loaʻa i ka maʻi ʻaʻai. E kamaʻilio me kāu kauka inā makemake ʻoe e pilikia paha kāu keiki.

ʻO Wilms tumo paha kahi ʻāpana o kahi genetical syndrome e hoʻopili ai i ka ulu a i ʻole ke kūkulu ʻana. ʻO ka syndrome syndrome kahi hōʻailona o nā hōʻailona a me nā ʻōuli a i ʻole nā ​​kūlana i kū like a kumu ʻia e kekahi mau hoʻololi i nā gen. Hiki i kekahi mau kūlana ke hoʻonui i ka makaʻu o ke keiki i ka ulu ʻana i ka tumo Wilms. Ua hoʻopili ʻia kēia a me nā hihia ʻē aʻe a me nā kūlana i Wilms tumo:

  • WAGR Syndrome (Wilms tumer, aniridia, abnormal genitourinary system, a me ka noʻonoʻo retardation).
  • ʻO Denys-Drash Syndrome (ʻōnaehana genitourinary ʻōnaehana).
  • Frasier Syndrome (ʻōnaehana genitourinary ʻōnaehana).
  • Beckwith-Wiedemann Syndrome (ulu nui ʻole o kekahi ʻaoʻao o ke kino a i ʻole kahi ʻāpana o ke kino, alelo nui, hernia umbilical i ka wā hānau, a me ka ʻōnaehana genitourinary maʻamau).
  • He moʻolelo ʻohana o ka tumo Wilms.
  • ʻO Aniridia (ka iris, ka hapa kala o ka maka, e nalo ana).
  • Hoʻokaʻawale hemihyperplasia (ulu nui ʻole o kekahi ʻaoʻao o ke kino a i ʻole ʻāpana o ke kino).
  • Nā pilikia o ka mimi e like me cryptorchidism a i ʻole hypospadias.

Hoʻohana ʻia nā hoʻokolohua e pale ai no ka tumo Wilms.

Hana ʻia nā hoʻokolohua loiloi i nā keiki me ka nui o ka makaʻu o ka maʻi tumo Wilms. Hiki i kēia mau hoʻāʻo ke kōkua i ka loaʻa mua ʻana o ka maʻi ʻaʻai a hoʻemi i ka manawa o ka make ʻana i ka maʻi ʻaʻai.

Ma ke ʻano laulā, pono e hoʻopaʻa ʻia nā keiki me ka nui o ka makaʻu o ka lāʻau Wilms no ka puʻupuʻu Wilms i kēlā me kēia ʻekolu mau mahina a hiki i ka liʻiliʻi o 8 mau makahiki. Hoʻohana maʻamau kahi hōʻike ultrasound o ka ʻōpū no ka kānana. Hiki ke ʻike a wehe ʻia nā tumors liʻiliʻi Wilms ma mua o ka loaʻa ʻana o nā ʻōuli.

ʻO nā keiki me ka Beckwith-Wiedemann Syndrome a i ʻole hemihyperplasia e nānā ʻia no ka akepaʻa a me nā adrenal tumors i hoʻopili ʻia i kēia mau genetona gendrome. ʻO kahi ho'āʻo e nānā i ka pae alpha-fetoprotein (AFP) i ke koko a hana ʻia kahi ultrasound o ka ʻōpū a hiki i ka piha ʻana o ke keiki i ka 4 mau makahiki. Hana ʻia kahi ultrasound o nā puʻupaʻa ma waena o nā makahiki o 4 a me 7 mau makahiki. Hana ʻia kahi hoʻokolohua kino e kahi loea (geneticist a pediatric oncologist) i ʻelua mau manawa i kēlā me kēia makahiki. I nā keiki me kekahi ʻano loli, hiki ke hoʻohana ʻia i kahi papa ʻokoʻa no ka ultrasound o ka ʻōpū.

ʻO nā keiki me ka aniridia a me kekahi ʻano loli e nānā ʻia no ka puʻupuʻu Wilms i kēlā me kēia ʻekolu mahina a hiki i ka piha ʻana o 8 mau makahiki. Hoʻohana ʻia kahi hōʻike ultrasound o ka ʻōpū no ka kānana ʻana.

Hoʻomohala kekahi mau keiki i ka ulu lāʻau Wilms i nā puʻupaʻa ʻelua. Hōʻike pinepine ʻia kēia i ka wā e ʻike mua ʻia ai ʻo ka tumo Wilms, akā ʻo Wilms tumo kekahi i loko o ka puʻupaʻa ʻelua ma hope o ka mālama pono ʻia o ke keiki no ka puʻupuʻu Wilms i hoʻokahi puʻupaʻa. ʻO nā keiki me ka hoʻonui nui o ka tumo Wilms ʻelua i ka puʻupaʻa ʻē aʻe e nānā ʻia no ka puʻupuʻu Wilms i kēlā me kēia ʻekolu mahina a hiki i ʻewalu mau makahiki. Hoʻohana ʻia kahi hōʻike ultrasound o ka ʻōpū no ka kānana ʻana.

Loaʻa i kekahi mau kūlana e hoʻonui i ka makaʻu o ka maʻi ʻaʻai kolone.

Pili paha ke kanesa maʻi ʻōpū i kēia mau kūlana:

  • ʻO ka maʻi ʻo Von Hippel-Lindau (kahi ʻano hoʻoilina e hoʻoulu ai i nā kīʻaha koko ʻole). Pono e nānā ʻia nā keiki me ka maʻi ʻo Von Hippel-Lindau i kēlā me kēia makahiki no ka maʻi ʻaʻai pūpū puʻuwai me kahi ultrasound o ka ʻōpū a i ʻole kahi MRI (kiʻi resonance magnetic) e hoʻomaka ana mai ka makahiki 8 a 11 mau makahiki.
  • Tuberous sclerosis (kahi maʻi hoʻoilina i kahakaha ʻia e nā ʻōpū momona ʻole noncancerous i ka puʻupaʻa).
  • ʻO ka maʻi ʻaʻaʻa pūhaka ʻohana (kahi ʻano hoʻoilina i kū ʻia ke hoʻololi ʻia kekahi mau genes e kumu i ka maʻi ʻaʻai kidney mai ka makua a ke keiki).
  • Ka maʻi ʻaʻai medullary ʻōiwi (kahi maʻi ʻaʻai kolo ʻole e ulu a pāhola koke).
  • ʻO leiomyomatosis hoʻoilina (kahi maʻi i hoʻoili ʻia e hoʻonui ai i ka makaʻu o ka maʻi ʻaʻai o ka puʻupaʻa, ʻili, a me ka kōpū).

Ma mua o ka chemotherapy a i ʻole ka radiation therapy no kahi maʻi ʻaʻa kamaliʻi, e like me neuroblastoma, sarcoma mea palupalu, leukemia, a i ʻole ʻo Wilms tumor e hoʻonui ai i ka makaʻu o ka maʻi ʻaʻai pūpū. E ʻike i ka ʻāpana ʻelua Cancers ma ka hōʻuluʻulu e pili ana i nā hopena hope o ka mālama ʻana no ka maʻi ʻaʻa kamaliʻi no ka ʻike hou aku.

ʻO ka mālama ʻana no ka lāʻau Wilms a me nā tumors ʻōiwi ʻē aʻe e komo pū paha me ka ʻōlelo aʻoaʻo ʻaoʻao.

Kūkākūkā genetic (kahi kūkākūkā me kahi loea i aʻo ʻia e pili ana i nā maʻi genetical a inā paha e pono ana ka hoʻāʻo genetika) e pono inā loaʻa i ke keiki kekahi o nā syndrome a i ʻole nā ​​kūlana.

  • ʻO kahi maʻi kūpilikiʻi a i ʻole ke ʻano e hoʻonui i ka makaʻu o Wilms tum tum.
  • ʻO kahi kūlana hoʻoili e hoʻonui ai i ka makaʻu o ka maʻi ʻaʻai kolone.
  • Rhabdoid hikoko o ka hakuʻala.
  • ʻO nephroma cystic Multilocular.

ʻO nā ʻōuli o Wilms tumor a me nā ʻōpū ʻōiwi ʻōpiopio ʻē aʻe e hoʻopili me ka puʻupuʻu i loko o ka ʻōpū a me ke koko i ka mimi.

I kekahi manawa ʻaʻole hana nā ʻōpū puʻukū ʻōpio i nā ʻōuli a me nā ʻōuli a loaʻa i ka makua ka nui i loko o ka ʻōpū ma ke kū wale a loaʻa ʻole ka nui i ka wā o ke olakino olakino keiki maikaʻi. ʻO kēia a me nā ʻōuli a me nā ʻōuli ʻē aʻe i hopena ʻia e nā tumors kidney a i ʻole nā ​​kūlana ʻē aʻe. E nīnau me ke kauka o kāu keiki inā loaʻa i kāu keiki kekahi o kēia mau mea:

  • ʻO kahi puʻupuʻu, ʻōhū, a i ʻole ʻeha ma ka ʻōpū.
  • Koko i ka mimi.
  • Ke kiʻekiʻe o ke koko (ʻeha ke poʻo, e luhi loa, ʻeha o ka umauma, a i ʻole pilikia e ʻike a me ka hanu ʻana).
  • Hypercalcemia (nalo o ka makemake, kahe a me ka luaʻi, nāwaliwali, a luhi paha).
  • Fiva no ke kumu ʻole i ʻike ʻia.
  • Loaʻa ka ʻai ʻole.
  • ʻO ka hōʻemi kaumaha no ke kumu ʻole.

ʻO ka ʻōpala Wilms i pālahalaha aʻe i nā akemāmā a i ʻole ke ake e hana i nā hōʻailona a me nā hōʻailona aʻe:

  • Cough.
  • Koko i ka ʻaʻā.
  • Hī pilikia.
  • ʻEha ma ka ʻōpū.

Hoʻohana ʻia nā hoʻāʻo e nānā i ka puʻupaʻa a me ke koko e ʻike pono ai i nā tumo Wilms a me nā puʻupaʻa puʻupaʻa keiki ʻē aʻe.

Hiki ke hoʻohana ʻia nā hoʻāʻo a me nā kaʻina hana aʻe:

  • ʻO ka hoʻāʻo kino a me ka mōʻaukala olakino: kahi hōʻike o ke kino e nānā i nā hōʻailona laulā o ke olakino, e like me ka nānā ʻana i nā hōʻailona o ka maʻi, e like me nā puʻupuʻu a i ʻole nā ​​mea ʻē aʻe e ʻano ʻē. E lawe ʻia kahi moʻolelo o nā ʻano olakino o ka mea maʻi a me nā maʻi i hala a me nā mālama ʻana.
  • Helu piha o ke koko (CBC): Ke kaʻina hana e huki ʻia ai kahi laʻana o ke koko a nānā ʻia no kēia mau mea:
  • ʻO ka helu o nā hunaola ʻulaʻula, nā aʻa koko keʻokeʻo, a me nā platelet.
  • ʻO ka nui o ka hemoglobin (ka protein i hāpai i ka oxygen) i loko o nā hunaola ʻulaʻula.
  • ʻO ka ʻāpana o ka hāpana koko i hana ʻia i nā hunaola ʻulaʻula.
  • Nā aʻo kemika koko: kahi hana e nānā ʻia ai kahi hāpana koko e ana i ka nui o kekahi mau mea i hoʻokuʻu ʻia i loko o ke koko e nā mea a me nā mea i loko o ke kino. ʻO kahi mea maʻamau (ʻoi aʻe a i ʻole haʻahaʻa ma mua o ka maʻamau) o kahi mea hiki ke lilo i hōʻailona o ka maʻi. Hana ʻia kēia hōʻike e nānā i ke ʻano o ka hana o ke ake a me nā puʻupaʻa.
  • Hōʻike hoʻāʻo Renal: kahi hana e nānā ʻia ai ke koko a i ʻole ka mimi e ana i ka nui o kekahi mau mea i hoʻokuʻu ʻia i loko o ke koko a i ʻole ka mimi e nā puʻupaʻa. ʻO kahi kiʻekiʻe a haʻahaʻa paha ma mua o ka nui maʻamau o kahi mea hiki ke lilo i hōʻailona no ka hana ʻole o nā puʻupaʻa e like me ka mea e pono ai.
  • Urinalysis: kahi hoʻāʻo e nānā i ke kala o ka mimi a me nā mea o loko, e like me ke kō, protein, koko, a me bacteria.
  • ʻO ka hoʻāʻo ʻana o Ultrasound: kahi kaʻina hana e kipaku ʻia ai nā nalu kani ikaika (ultrasound) mai nā aʻa a i ʻole nā ​​ʻola a hana i nā leo. Hoʻokumu nā leo i kahi kiʻi o nā kino o ke kino i kapa ʻia he sonogram. Hana ʻia kahi ultrasound o ka ʻōpū e hōʻoia i kahi tumo tumo.
ʻO ke ultrasound ʻōpū. ʻO kahi transducer ultrasound e pili ana i kahi kamepiula e kaomi ʻia i ka ʻili o ka ʻōpū. Pākuʻi ka transducer i nā nalu kani i nā mea kūloko a me nā aʻa e hana i nā leo e hana i kahi sonogram (kiʻi kamepiula).
  • CT scan (CAT scan): Ke kaʻina hana e hana i kahi moʻo o nā kiʻi kikoʻī o nā wahi i loko o ke kino, e like me ka umauma, ʻōpū, a me nā pelvis, i lawe ʻia mai nā kihi ʻokoʻa. Hana ʻia nā kiʻi e kahi kamepiula i hoʻopili ʻia i kahi mīkini x-ray. Hoʻokomo ʻia kahi kala i loko o ke aa a i ʻole ale ʻia e kōkua i nā ʻōpū a i ʻole nā ​​kino i hōʻike hou aku me ka maopopo. Kāhea ʻia kēia kaʻina hana he tomography i helu ʻia, kamepiula tomography, a i ʻole he tomography axial computerized.
ʻO ka scan tomography compute (CT) o ka ʻōpū. Moe ke keiki ma ka papaʻaina e paheʻe ai i ka scanner CT, e kiʻi ana i nā kiʻi x-ray o loko o ka ʻōpū.
  • MRI (kiʻi resonance ʻume mākenēki) me gadolinium: kahi hana e hoʻohana ai i ka magnet, nā nalu lekiō, a me kahi kamepiula e hana i kahi o nā kiʻi kikoʻī o nā wahi i loko o ke kino, e like me ka ʻōpū. Hoʻokomo ʻia kahi mea i kapa ʻia ʻo gadolinium i kahi aa koko. Hōʻiliʻili ka gadolinium a puni nā hunaola maʻi ʻula i mea e mālamalama ai lākou i ke kiʻi. Kāhea ʻia kēia kaʻina hana he kiʻi nukelea kiʻi resonance (NMRI).
ʻO ke kiʻi ʻana o ka resonance ʻume mākenēki (MRI) o ka ʻōpū. Moe ke keiki ma ka papaʻaina e paheʻe i ka scanner MRI, e paʻi ana i nā kiʻi o loko o ke kino. Kōkua ka pale ma luna o ka ʻōpū o ke keiki e hoʻomaʻemaʻe i nā kiʻi.
  • X-ray: ʻO ka x-ray kahi ʻano kukuna ikehu i hiki ke hele ma waena o ke kino a i ke kiʻi ʻoniʻoni, e hana ana i kiʻi o nā wahi i loko o ke kino, e like me ka umauma a me ka ʻōpū.
  • Nānā PET-CT: kahi hana e hoʻohui i nā kiʻi mai kahi scan tomography emission positron (PET) a me kahi scan tomography i helu ʻia (CT). Hana ʻia nā paʻi PET a me CT ma ka manawa like ma ka mīkini like. Hoʻohui ʻia nā kiʻi mai nā kiʻi ʻelua e hana i kahi kiʻi kikoʻī ma mua o nā hōʻike ʻelua e hana ʻia e ia iho. ʻO kahi PET scan kahi hana e loaʻa ai nā kinikini tumo malignant i loko o ke kino. Hoʻokomo ʻia kahi liʻiliʻi o ka glucose radioactive (kō) i loko o kahi aa koko. Hoʻopili ka scanner PET a puni ke kino a hana i kahi kiʻi o kahi e hoʻohana ʻia ai ka glucose i ke kino. ʻOi aku ka mālamalama o nā hunaola tumo ma ke kiʻi no ka mea ʻoi aku ka hana a lawe i ka glucose ma mua o ka hana ʻana o nā hunaola maʻamau.
  • ʻO Biopsy: Ka lawe ʻia ʻana o nā pūnaewele a i ʻole nāʻaʻaʻa i hiki ai iā lākou ke ʻike ma lalo o kahi microscope e kahi pathologist e nānā i nā hōʻailona o ka maʻi ʻaʻai. Hoʻoholo ʻia ka hoʻoholo inā e hana i kahi biopsy:
  • Ka nui o ka tumo.
  • Ke kahua o ka maʻi ʻaʻai.
  • Inā ʻo ka maʻi ʻaʻai i loko o hoʻokahi a i ʻole nā ​​puʻupaʻa ʻelua.
  • Hōʻike maopopo paha nā hoʻokolohua kiʻi ʻana i ka maʻi ʻaʻai.
  • Hiki ke hemo ʻia ka tumo e ke ʻoki.
  • Inā paha ka mea maʻi i ka hoʻokolokolo hoʻokolohua.

Hiki ke hana ʻia kahi biopsy ma mua o ka hāʻawi ʻia ʻana o kahi lāʻau, ma hope o ka chemotherapy e hoʻoliʻiliʻi ai i ka tumo, a ma hope paha o ke kaha ʻana e wehe i ka tumo.

Kū kekahi mau kumu i ka wānana (kahi o ke ola ʻana) a me nā koho lapaʻau.

ʻO ka wānana a me nā koho lapaʻau no Wilms tumo kaukaʻi ʻia i ka mea aʻe:

  • Pehea ka ʻokoʻa o nā hunaola tumora mai nā puʻupaʻa maʻamau inā nānā ʻia ma lalo o kahi microscope.
  • Ke kahua o ka maʻi ʻaʻai.
  • Ke ʻano o ka tumo.
  • Ka makahiki o ke keiki.
  • Inā hiki ke hemo loa i ka tumo e ke ʻoki.
  • Inā loaʻa kekahi mau hoʻololi i nā chromosome a i ʻole nā ​​genes.
  • Inā ua hōʻoia wale ʻia ka maʻi ʻaʻai a i ʻole ua hoʻi hou (hoʻi.

ʻO ka wānana no ka maʻi ʻaʻai kolone paʻa e pili ana i kēia:

  • Ke kahua o ka maʻi ʻaʻai.
  • Inā ua pālahalaha ka maʻi ʻaʻai i nā lymph node.

ʻO ka wānana no ka tumo rhabdoid o ka hakuʻala e pili ana i kēia:

  • ʻO ka makahiki o ke keiki i ka manawa o ke kuhi.
  • Ke kahua o ka maʻi ʻaʻai.
  • Inā ua pālahalaha ka maʻi ʻaʻai i ka lolo a i ʻole ka iwi kuamoo.

ʻO ka wānana no ka sarcoma o ka puʻupaʻa kikoʻī e pili i kēia:

  • ʻO ka makahiki o ke keiki i ka manawa o ke kuhi.
  • Ke kahua o ka maʻi ʻaʻai.

Nā pae o Wilms Tumor

NA MANA KUNI

  • Hoʻokumu ʻia nā ʻōpala Wilms i ka wā o ke ʻoki ʻana a me nā hoʻokolohua kiʻi.
  • ʻEkolu ala e hoʻolaha ai ka maʻi ʻaʻai i loko o ke kino.
  • E laha paha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i nā ʻāpana ʻē aʻe o ke kino.
  • Ma waho o nā pae, wehewehe ʻia nā puʻukū Wilms e kā lākou mōʻaukala.
  • Hoʻohana ʻia nā pae aʻe no nā histology maikaʻi ʻelua a me nā tumaplastic Wilms tumors:
  • Ke kahua I
  • Kahua II
  • Kahua III
  • Kahua IV
  • Kahua V
  • ʻO ka mālama ʻana i nā ʻōpū puʻuwai ʻōpio ʻē aʻe e pili ana i ka tumo type.
  • I kekahi manawa hoʻi mai ʻo Wilmm tumor a me nā puʻupaʻa ʻōiwi ʻē aʻe ma hope o ka mālama ʻana.

Hoʻokumu ʻia nā ʻōpala Wilms i ka wā o ke ʻoki ʻana a me nā hoʻokolohua kiʻi.

ʻO ke kaʻina hana e ʻike inā ua pālahalaha ka maʻi ʻaʻai i waho o ka puʻuwai i nā ʻāpana ʻē aʻe o ke kino i kapa ʻia he staging. ʻO ka ʻikepili i hōʻiliʻili ʻia mai ke kaʻina hana e hoʻoholo ai i ka pae o ka maʻi. He mea nui ia e ʻike i ke kahua i mea e hoʻolālā ai i ka lāʻau. E hoʻohana ke kauka i nā hopena o nā diagnostics a me nā hoʻokolohua hoʻonohonoho e kōkua ai e ʻike i ke kahua o ka maʻi.

E hana ʻia paha nā hōʻike aʻe e ʻike ai inā ua pālahalaha ka maʻi ʻaʻai i nā wahi ʻē aʻe o ke kino.

  • ʻO ka biopsy Lymph node: Ka lawe ʻana i nā mea āpau a ʻāpana paha o kahi lymph node i loko o ka ʻōpū. ʻIke kahi pathologist i ke kiko o ka lymph node ma lalo o kahi microscope e nānā ai i nā hunaola maʻi ʻaʻai. Kapa ʻia kēia kaʻina hana he lymphadenectomy a i ʻole dissection lymph node.
  • Hōʻoia i ka hana ate: ʻO kahi kaʻina hana e nānā ʻia kahi hāpana koko e ana i ka nui o kekahi mau mea i hoʻokuʻu ʻia i loko o ke koko e ke ake. ʻO kahi kiʻekiʻe ma mua o ka nui maʻamau o kahi mea hiki ke lilo i hōʻailona no ka hana ʻole o ka ate e like me ka mea e pono ai.
  • X-ray o ka umauma a me nā iwi: ʻO ke kukui x kahi ʻano kukuna ikehu i hiki ke hele ma waena o ke kino a i ke kiʻi ʻoniʻoni, e hana ana i kiʻi o nā wahi i loko o ke kino, e like me ka umauma
  • CT scan (CAT scan): kahi hana e hana ai i kahi o nā kiʻi kikoʻī o nā wahi i loko o ke kino, e like me ka ʻōpū, pelvis, umauma, a me ka lolo, i lawe ʻia mai nā ʻaoʻao ʻokoʻa. Hana ʻia nā kiʻi e kahi kamepiula i hoʻopili ʻia i kahi mīkini x-ray. Hoʻokomo ʻia kahi kala i loko o ke aa a i ʻole ale ʻia e kōkua i nā ʻōpū a i ʻole nā ​​kino i hōʻike hou aku me ka maopopo. Kāhea ʻia kēia kaʻina hana he tomography i helu ʻia, kamepiula tomography, a i ʻole he tomography axial computerized.
  • Nānā PET-CT: kahi hana e hoʻohui i nā kiʻi mai kahi scan tomography emission positron (PET) a me kahi scan tomography i helu ʻia (CT). Hana ʻia nā paʻi PET a me CT ma ka manawa like ma ka mīkini like. Hoʻohui ʻia nā kiʻi mai nā kiʻi ʻelua e hana i kahi kiʻi kikoʻī ma mua o nā hōʻike ʻelua e hana ʻia e ia iho. ʻO kahi PET scan kahi hana e loaʻa ai nā kinikini tumo malignant i loko o ke kino. Hoʻokomo ʻia kahi liʻiliʻi o ka glucose radioactive (kō) i loko o kahi aa koko. Hoʻopili ka scanner PET a puni ke kino a hana i kahi kiʻi o kahi e hoʻohana ʻia ai ka glucose i ke kino. ʻOi aku ka mālamalama o nā hunaola tumo ma ke kiʻi no ka mea ʻoi aku ka hana a lawe i ka glucose ma mua o ka hana ʻana o nā hunaola maʻamau.
  • MRI (magnetic resonance imaging): Kahi hana e hoʻohana ai i ka magnet, nā nalu lekiō, a me kahi kamepiula e hana i nā kiʻi kikoʻī o nā wahi i loko o ke kino, e like me ka ʻōpū, pelvis, a me ka lolo. Kāhea ʻia kēia kaʻina hana he kiʻi nukelea kiʻi resonance (NMRI).
  • ʻImi iwi: kahi hana e nānā ai inā aia he wikiwiki e hoʻokaʻawale i nā hunaola, e like me nā hunaola maʻi ʻaʻai, i ka iwi. Hoʻokomo ʻia kahi mea liʻiliʻi loa o nā mea radioactive i loko o ke aa a hele i waena o ke kahe o ke koko. Hōʻiliʻili ka mea lekiō i nā iwi me ka maʻi ʻaʻai a ʻike ʻia e kahi scanner.
ʻImi iwi. Hoʻokomo ʻia kahi mea liʻiliʻi o ka radioactive i ke aa o ke keiki a hele i loko o ke koko. Hōʻiliʻili ka mea lekiō i nā iwi. Ke moe nei ke keiki ma kahi pākaukau e heʻe ma lalo o ka scanner, ʻike ʻia ka mea radioactive a hana ʻia nā kiʻi ma ka papapihi kamepiula.
  • ʻO ka hoʻāʻo ʻana o Ultrasound: kahi kaʻina hana e kipaku ʻia ai nā nalu kani ikaika (ultrasound) mai nā aʻa a i ʻole nā ​​ʻola a hana i nā leo. Hoʻokumu nā leo i kahi kiʻi o nā kino o ke kino i kapa ʻia he sonogram. Hana ʻia kahi ultrasound o nā moku puʻuwai nui e hoʻokumu ai i ka tumemeka Wilms.
  • Cystoscopy: kahi hana e nānā ai i loko o ka puhā a me ka urethra e nānā ai no nā wahi kūpono ʻole. Hoʻokomo ʻia kahi cystoscope ma o ka urethra i loko o ka puhā. ʻO kahi cystoscope kahi mea lahilahi, e like me ka Tube me kahi kukui a me nā aniani no ka nānā ʻana. Loaʻa paha iā ia kahi mea hana e hemo i nā mea kiko kiko, i nānā ʻia ma lalo o kahi microscope no nā hōʻailona o ka maʻi ʻaʻai.

ʻEkolu ala e hoʻolaha ai ka maʻi ʻaʻai i loko o ke kino.

Hiki ke pālahalaha ʻia ka maʻi ʻaʻai ma o nā meaola, ka ʻōnaehana lymph, a me ke koko.

  • Kāpena. Hoʻolahalaha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i ka ulu ʻana i nā wahi kokoke.
  • ʻŌnaehana Lymph. Hoʻolahalaha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i ke komo ʻana i ka ʻōnaehana lymph. Hele ka maʻi ʻaʻai ma o nā kīʻaha lymph i nā ʻāpana ʻē aʻe o ke kino.
  • Koko. Hoʻolahalaha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i ke komo ʻana i ke koko. Hele ka maʻi ʻaʻai ma o nā kīʻaha koko i nā ʻāpana ʻē aʻe o ke kino.

E laha paha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i nā ʻāpana ʻē aʻe o ke kino.

Ke pālahalaha ʻia ka maʻi ʻaʻai i kekahi ʻāpana o ke kino, ua kapa ʻia ia ʻo metastasis. E haki nā hunaola maʻi 'aʻai mai kahi a lākou i hoʻomaka ai (ka tumo mua) a hele i loko o ka ʻōnaehana lymph a i ʻole ke koko.

  • ʻŌnaehana Lymph. Komo ka maʻi ʻaʻai i loko o ka ʻōnaehana lymph, hele ma waena o nā kīʻaha lymph, a hana i kahi tumo (tumo metastatic) i kekahi ʻāpana o ke kino.
  • Koko. Komo ke kanesa i loko o ke koko, hele ma waena o nā kīʻaha koko, a hana i kahi tumo (tumo metastatic) i kekahi ʻāpana o ke kino.

ʻO ka tumo metastatic ka ʻano like o ke kanesa me ka tumo mua. ʻO kahi laʻana, inā pālahalaha ka ʻōpala ʻo Wilms i ka akemāmā, ʻo nā pūnaeho maʻi ʻaʻai i loko o ka akemāi ʻo ia nā Wilms tumor cells. ʻO ka tumeth Wilms metastatic maʻi, ʻaʻole ka maʻi ʻaʻa maʻi.

Ma waho o nā pae, wehewehe ʻia nā puʻukū Wilms e kā lākou mōʻaukala.

ʻO ka histology (ka nānā ʻana o nā hunaola ma lalo o kahi microscope) o ka tumo e pili ana i ka wānana a me ka mālama ʻana i ka tumo Wilms. He ʻoluʻolu a anaplastic paha (ʻaʻohe makemake ʻia ka mōʻaukala). ʻO nā tumors me kahi histology maikaʻi i kahi prognosis ʻoi aku ka maikaʻi a pane maikaʻi i ka chemotherapy ma mua o nā tumo anaplastic. Hoʻokaʻawale wikiwiki nā ʻōpala anaplastic a ma lalo o kahi microscope ʻaʻole e like me ke ʻano o nā pūnaewele i hele mai lākou. ʻOi aku ka paʻakikī o nā kūpuna Anaplastic e mālama me ka chemotherapy ma mua o nā puʻupuʻu Wilms ʻē aʻe i ka manawa like.

Hoʻohana ʻia nā pae aʻe no nā histology maikaʻi ʻelua a me nā tumaplastic Wilms tumors:

Ke kahua I

I ke kahua I, ua hemo loa ka tumo e ka ʻoki kino a he ʻoiaʻiʻo nā mea āpau:

  • Loaʻa ka maʻi ʻaʻai i loko o ka puʻupaʻa a ʻaʻole i pāhola ʻia i nā kīʻaha koko i ka sinus renal (ʻo ka ʻāpana o ke kīʻaha kahi e pili ai i ka ureter) a i ʻole nā ​​lymph node.
  • ʻAʻole i hāmama ka papa waho o ka hakuʻala.
  • ʻAʻole i haki ka tumo.
  • ʻAʻole i hana ʻia kahi biopsy ma mua o ka hemo ʻana o ka tumo.
  • ʻAʻole i loaʻa nā hunaola maʻi ʻaʻai ma nā kihi o kahi i lawe ʻia aku ai ka tumo.

Kahua II

I ke kahua II, ua hemo loa ka tumo e ke ʻoki kino a ʻaʻohe pūnana maʻi ʻaʻai i loaʻa ma nā kihi o kahi i lawe ʻia ai ka maʻi ʻaʻai. ʻAʻole i pālahalaha ka maʻi ʻaʻai i nā lymph node. Ma mua o ka hemo ʻana o ka tumo, he ʻoiaʻiʻo kekahi o kēia mau mea:

  • Ua pālahalaha ʻia ka maʻi ʻaʻai i ka sinus renal (ka ʻāpana o ke kīkī kahi e pili ai i ka ureter).
  • Ua pālahalaha ʻia ka maʻi ʻaʻai i nā kīʻaha koko ma waho o ka wahi o ka puʻupaʻa kahi e hana ai ka mimi, e like me ka sinus renal.

Kahua III

I ke kahua III, noho ka maʻi ʻaʻai i loko o ka ʻōpū ma hope o ke kaha ʻana a he ʻoiaʻiʻo kekahi o kēia mau mea:

  • Ua pālahalaha ʻia ka maʻi ʻaʻai i nā pūnana lymph i loko o ka ʻōpū a i ʻole pelvis (ka ʻāpana o ke kino ma waena o nā pūhaka).
  • Ua pālahalaha ʻia ka maʻi ʻaʻai ma o a i ʻole ma o ka ʻaoʻao o ka peritoneum (ka papa o nā aʻa e kū ana i ka lua o ka ʻōpū a uhi i ka hapa nui o nā ʻōpū i loko o ka ʻōpū).
  • Ua hana ʻia kahi biopsy o ka tumo ma mua o ka lawe ʻia ʻana.
  • Ua haki ka ʻōpū ma mua a i ʻole i ka wā o ke ʻoki e wehe iā ia.
  • Ua wehe ʻia ka tumo ma mua o hoʻokahi ʻāpana.
  • ʻIke ʻia nā hunaola maʻi ʻaʻai ma nā kihi o kahi i hemo aku ai ka tumo.
  • ʻAʻole hiki ke hemo i ka tumo holoʻokoʻa no ka mea e ʻino nā mea nui a i ʻole nā ​​ʻaʻa i loko o ke kino.

Kahua IV

I ka pae IV, ua pālahalaha ʻia ka maʻi ʻaʻai ma o ke koko i nā lālā e like me nā akemāmā, ke ake, ka iwi, a me ka lolo, a i ʻole nā ​​lymph node ma waho o ka ʻōpū a me nā pelvis.

Kahua V

I ke kahua V, loaʻa nā hunaola maʻi ʻaʻai i nā puʻupaʻa ʻelua ke ʻike ʻia ka maʻi ʻaʻai.

ʻO ka mālama ʻana i nā ʻōpū puʻuwai ʻōpio ʻē aʻe e pili ana i ka tumo type.

I kekahi manawa hoʻi mai ʻo Wilmm tumor a me nā puʻupaʻa ʻōiwi ʻē aʻe ma hope o ka mālama ʻana.

Hiki paha i ka tumo kamaliʻi Wilms ke hoʻi hou i ka pūnaewele kumu, a i ʻole i ka akemāmā, ʻōpū, ake, a i ʻole nā ​​wahi ʻē aʻe o ke kino.

Hiki ke hoʻi hou ka sarcoma pūnaewele ʻōmaʻomaʻo o ka puʻupaʻa i ka pūnaewele kumu, a i ʻole i ka lolo, nā akemāmā, a i ʻole nā ​​wahi ʻē aʻe i ke kino.

Hiki paha i ka nephroma mesoblastic keiki ke hoʻi hou i ka puʻupaʻa a i ʻole nā ​​wahi ʻē aʻe i ke kino.

Laulā Manaʻo Option Oponopono

NA MANA KUNI

  • Aia nā ʻano like ʻole o ka mālama ʻana no nā mea maʻi me ka maʻi ʻōmaʻomaʻo Wilms a me nā ʻōpū puʻuwai ʻōpiopio ʻē aʻe.
  • ʻO nā kamaliʻi me ka maʻi ʻōmaʻomaʻo Wilms a i ʻole nā ​​tumors ʻōpio ʻē aʻe e hoʻolālā i kā lākou mālama ʻia e kahi hui o nā lawelawe mālama ola i loea i ka mālama ʻana i ka maʻi ʻaʻai i nā keiki.
  • ʻO ka mālama ʻana no ka ulu lāʻau Wilms a me nā tumors hakuʻala ʻōpio ʻē aʻe e hopena ai i nā hopena ʻaoʻao.
  • Hoʻohana ʻia nā ʻano ʻelima o ka mālama maʻamau.
  • ʻOki kino
  • Lapaʻau hoʻomākala
  • ʻO Chemotherapy
  • Immunotherapy
  • ʻO ka chemotherapy kiʻekiʻe loa me ka hoʻopakele ʻana o ka cell stem
  • Ke hoʻāʻo ʻia nei nā ʻano lapaʻau hou i nā hoʻokolohua hoʻokolohua.
  • Pahuhopu kau ʻia
  • Makemake paha nā mea maʻi e noʻonoʻo e pili ana i ka hoʻokolokolo ʻana.
  • Hiki i nā mea maʻi ke komo i nā hoʻokolohua hoʻokolohua ma mua, i ka wā, a ma hope paha o ka hoʻomaka ʻana i kā lākou mālama maʻi ʻaʻai.
  • Pono paha nā hoʻokolohua ukali.

Aia nā ʻano like ʻole o ka mālama ʻana no nā mea maʻi me ka maʻi ʻōmaʻomaʻo Wilms a me nā ʻōpū puʻuwai ʻōpiopio ʻē aʻe.

Loaʻa nā ʻano lapaʻau like ʻole no nā keiki me Wilms a me nā puʻuwai ʻōpiopio ʻē aʻe. Kūlana maʻamau kekahi mau hōʻailona (ʻo ka lāʻau i hoʻohana ʻia i kēia manawa), a ʻo kekahi e hoʻāʻo ʻia nei i nā hoʻokolohua hoʻokolohua. ʻO kahi hoʻokolohua hoʻokolohua lapaʻau kahi noiʻi noiʻi i manaʻo ʻia e kōkua i ka hoʻomaikaʻi ʻana i nā mālama ʻana i kēia manawa a i ʻole loaʻa ka ʻike e pili ana i nā mālama hou no nā maʻi me ka maʻi ʻaʻai. Ke hōʻike nā hoʻokolohua hoʻokolohua ʻoi aku ka maikaʻi o kahi lapaʻau hou ma mua o ka maʻamau maʻamau, lilo paha ka lāʻau hou i ka lapaʻau maʻamau.

Ma muli o ka loaʻa ʻole o ka maʻi ʻaʻai i nā keiki, pono e noʻonoʻo ʻia i ka hoʻokolokolo ʻana. ʻO kekahi mau hoʻokolohua hoʻokolohua e hāmama wale i nā mea maʻi i hoʻomaka ʻole i ka lāʻau.

ʻO nā kamaliʻi me ka maʻi ʻōmaʻomaʻo Wilms a i ʻole nā ​​tumors ʻōpio ʻē aʻe e hoʻolālā i kā lākou mālama ʻia e kahi hui o nā lawelawe mālama ola i loea i ka mālama ʻana i ka maʻi ʻaʻai i nā keiki.

Mālama ʻia ka mālama ʻana o kāu keiki e ka oncologist pediatric, he kauka i loea i ka mālama ʻana i nā keiki me ka maʻi ʻaʻai. Hana ka oncologist pediatric me nā mea lawelawe olakino pediatric ʻē aʻe i loea i ka mālama ʻana i nā keiki me ka puʻupuʻu Wilms a i ʻole nā ​​tumākō ʻōiwi ʻē aʻe a me ka poʻe loea i kekahi mau wahi o ka lāʻau. Pākuʻi ʻia kēia mau mea i lalo:

  • Kahuna Pediatrician.
  • ʻO ke kauka Pediatric a i ʻole urologist.
  • Oncologist uila.
  • Lapaʻau hoʻōla.
  • ʻO ka loea kahu maʻi Pediatric.
  • Limahana limahana.

ʻO ka mālama ʻana no ka ulu lāʻau Wilms a me nā tumors hakuʻala ʻōpio ʻē aʻe e hopena ai i nā hopena ʻaoʻao.

No ka ʻike e pili ana i nā hopena i hoʻomaka i ka wā o ka mālama ʻana no ka maʻi ʻaʻai, ʻike i kā mākou ʻaoʻao ʻaoʻao ʻaoʻao.

ʻO nā hopena ʻē aʻe mai ka mālama ʻana i ka maʻi ʻaʻai e hoʻomaka ma hope o ka mālama ʻana a hoʻomau no nā mahina a i ʻole mau makahiki e kapa ʻia nā hopena hopena. Hiki i nā hopena hope loa o ka mālama ʻana i ka maʻi ʻaʻai ke hoʻopili i kēia mau mea:

  • Nā pilikia o ke kino, e like me nā pilikia puʻuwai, nā pilikia o ka puʻuwai, a me nā pilikia i ka wā hāpai
  • Nā loli i ke ʻano, nā manaʻo, ka noʻonoʻo, ke aʻo ʻana, a me ka hoʻomanaʻo paha.
  • ʻO nā maʻi ʻelua (nā ʻano ʻē aʻe o ka maʻi ʻaʻai), e like me ka maʻi ʻaʻai o ka gastrointestinal tract a i ʻole ka maʻi ʻaʻai umauma.

E mālama a kāohi ʻia paha kekahi mau hopena hopena. He mea nui e kamaʻilio pū me nā kauka o kāu keiki e pili ana i nā hopena o ka mālama ʻana i ka maʻi ʻaʻai i kāu keiki. (E ʻike i ka hōʻuluʻulu e pili ana i nā hopena hope o ka mālama ʻana no ka maʻi ʻaʻa kamaliʻi no ka ʻike hou aku).

Ke hana ʻia nei nā hoʻokolohua hoʻokolohua e ʻike inā hiki ke hoʻohana ʻia nā lāʻau ʻoi loa o ka chemotherapy a me ka radiation e hoʻemi ai i nā hopena hope o ka mālama ʻana me ka loli ʻole i ke ʻano o ka hana.

Hoʻohana ʻia nā ʻano ʻelima o ka mālama maʻamau.

ʻOki kino

Hoʻohana ʻia ʻelua ʻano o ke ʻoki e mālama i nā tumors hakuʻala:

  • Nefrectomy: mālama pinepine ʻia ʻo Wilms tumole a me nā ʻōpū puʻuwai kamaliʻi ʻē aʻe me ka nephrectomy (ʻoki e wehe ai ka puʻupaʻa holoʻokoʻa). Hiki ke hoʻoneʻe ʻia a nānā ʻia nā lymph node kokoke a nānā ʻia no nā ʻōuli o ke kanesa. I kekahi manawa hana ʻia kahi transplant kidney (ʻoki e wehe i ka puʻupaʻa a hoʻololi iā ia me kahi puʻupaʻa mai kahi mea hāʻawi) ke hana ʻia ka maʻi ʻaʻai i nā puʻupaʻa ʻelua a ʻaʻole holo pono nā puʻupaʻa.
  • ʻĀpana nephrectomy: Inā loaʻa ka maʻi ʻaʻai i nā puʻupaʻa ʻelua a i ʻole e pāhola paha i nā puʻupaʻa ʻelua, hiki i ke kīʻaha ke komo i kahi nephrectomy ʻāpana (lawe ʻia ʻana o ka maʻi ʻaʻai i ka puʻupaʻa a me kahi liʻiliʻi o nā kikoʻī maʻamau a puni ia). Hana ʻia ka nephrectomy ʻāpana e mālama i ka nui o nā puʻupaʻa e hana ana i hiki. Kāhea ʻia kahi nephrectomy ʻāpana e hōʻoki ʻia i ka hōʻino kōpaʻa.

Ma hope o ka hemo ʻana o ke kauka i nā maʻi ʻaʻai āpau i hiki ke ʻike ʻia i ka manawa o ke ʻoki ʻana, hiki i kekahi mau mea maʻi ke hāʻawi ʻia i ka chemotherapy a i ʻole ka radiation therapy ma hope o ke kaha ʻana e luku i nā hunaola maʻi ʻea i koe. ʻO ka lāʻau i hāʻawi ʻia ma hope o ke kaha ʻana, e hoʻohaʻahaʻa i ka makaʻu e hoʻi mai ka maʻi ʻaʻai, i kapa ʻia ʻo adjuvant therapy. I kekahi manawa, hana ʻia ke kaha ʻelua e ʻike inā kū ka maʻi ʻaʻai ma hope o ka chemotherapy a i ʻole radiation therapy.

Lapaʻau hoʻomākala

ʻO ka radiation radiation kahi lāʻau maʻi maʻi maʻi e hoʻohana i nā kukuna x nui ikaika a i ʻole nā ​​ʻano radiation e hoʻomake i nā hunaola maʻi ʻaʻai a mālama ʻole paha i ka ulu ʻana. ʻElua ʻano o radiation radiation:

  • Hoʻohana ka radiation radiation kūwaho i kahi mīkini ma waho o ke kino e hoʻouna i ka radiation i ka maʻi ʻaʻai.
  • Hoʻohana ka radiation radiation i loko i kahi lāʻau radioactive i hoʻopaʻa ʻia i nā nila, nā hua, nā uea, a i ʻole nā ​​catheters i kau pololei ʻia i loko a kokoke paha i ka maʻi ʻaʻai.

Hāʻawi ʻia ke ala o ka radiation radiation i ke ʻano a me ke kahua o ka maʻi ʻaʻai e mālama ʻia ana a inā he biopsy i hana ʻia ma mua o ke ʻoki ʻana e wehe i ka tumo. Hoʻohana ʻia ka radiation radiation kūwaho e mālama iā Wilms tumo a me nā tumors ʻōpio ʻē aʻe.

ʻO Chemotherapy

ʻO Chemotherapy kahi lāʻau lapaʻau maʻi maʻi e hoʻohana i nā lāʻau e hōʻoki i ka ulu ʻana o nā hunaola maʻi ʻaʻai, ma ka luku ʻana i nā hunaola a i ʻole ke kāpae ʻana iā lākou mai ka hoʻokaʻawale. Ke lawe ʻia ka chemotherapy e ka waha a i ʻole injected i loko o kahi aa koko a i ʻole nā ​​mākala, komo nā lāʻau i ke kahe o ke koko a hiki ke kiʻi i nā hunaola maʻi ʻōpio i loko o ke kino (chemotherapy ʻōnaehana). Ke waiho pololei ʻia ka chemotherapy i loko o ka wai cerebrospinal, kahi hui, a i ʻole ke kino o ke kino e like me ka ʻōpū, ʻo nā lāʻau lapaʻau ka mea nui e hoʻopili i nā hunaola maʻi ʻaʻai i kēlā mau wahi (chemotherapy āpau). Hoʻohui ka chemotherapy me ka hoʻohana ʻana i ʻelua a ʻoi mau lāʻau anticancer.

Hāʻawi ʻia ke ala o ka chemotherapy i ka ʻano a me ke kahua o ka maʻi ʻaʻai e mālama ʻia. Hoʻohana ʻia ka chemotherapy ʻōnaehana e mālama iā Wilms tumo a me nā tumors ʻōpio ʻōpio ʻē aʻe.

I kekahi manawa ʻaʻole hiki ke hemo ʻia ka tumo e ka ʻoki ʻana no kekahi o nā kumu aʻe:

  • Pili loa ka tumo i nā mea nui a i ʻole nā ​​kīʻaha koko.
  • Nui ʻino ka tumo e hoʻoneʻe ai.
  • Aia ka maʻi ʻaʻai i nā puʻupaʻa ʻelua.
  • Aia kekahi ʻōpū koko i loko o nā moku kokoke i ke ake.
  • He pilikia ka mea hoʻomanawanui i ka hanu ʻana no ka mea ua pāhola ka maʻi ʻaʻai i nā akemāmā.

I kēia hihia, hana mua ʻia kahi biopsy. A laila hāʻawi ʻia ka chemotherapy e hōʻemi i ka nui o ka tumo ma mua o ke kaha ʻana, i mea e mālama ai i nā mea olakino e like me ka hiki a hoʻoliʻiliʻi i nā pilikia ma hope o ke kaha ʻana. Kapa ʻia kēia ʻo neoadjuvant chemotherapy. Hāʻawi ʻia ka radiation radiation ma hope o ke kaha ʻana.

E ʻike i nā lāʻau i ʻae ʻia no Wilms Tumor a me nā maʻi maʻi ʻōpio ʻē aʻe no ka ʻike hou aku.

Immunotherapy

ʻO ka Immunotherapy kahi lapaʻau e hoʻohana i ka ʻōnaehana pale maʻi o ka mea maʻi e hakakā i ka maʻi ʻaʻai. Hoʻohana ʻia nā mea i hana ʻia e ke kino a i hana ʻia paha i kahi keʻena hoʻokolohua e hoʻonui, kuhikuhi, a hoʻihoʻi hou i nā pale kūlohelohe o ke kino i ka maʻi ʻaʻai. Kāhea ʻia kēia ʻano lapaʻau maʻi ʻaʻai a biotherapy a i ʻole biologic therapy.

ʻO Interferon a me interleukin-2 (IL-2) kekahi ʻano o ka immunotherapy i hoʻohana ʻia e mālama ai i ka maʻi ʻaʻa kamaliʻi liʻiliʻi. Hoʻopili ʻo Interferon i ka mahele o nā hunaola maʻi ʻaʻai a hiki ke hoʻolohi i ka ulu ʻana o ka tumo. Hoʻonui ka IL-2 i ka ulu a me ka hana o nā hunaola ʻino he nui, keu hoʻi nā lymphocytes (kahi ʻano o ke keʻokeʻo koko keʻokeʻo). Hiki i nā Lymphocytes ke hoʻouka a pepehi i nā hunaola maʻi ʻaʻai.

ʻO ka chemotherapy kiʻekiʻe loa me ka hoʻopakele ʻana o ka cell stem

Hāʻawi ʻia nā lāʻau kiʻekiʻe o ka chemotherapy e pepehi i nā hunaola maʻi ʻaʻai. Hoʻopau pū ʻia nā hunaola olakino, e like me nā hunaola koko, e ka lāʻau maʻi ʻaʻai. ʻO ka hoʻopakele ʻana i ka pūnaeho he lāʻau lapaʻau e pani i nā hunaola koko. Lawe ʻia nā hunaola (ʻaʻaʻa koko ʻole) mai ke koko a i ʻole ka iwi o ka mea maʻi a paʻa a mālama ʻia. Ma hope o ka pau ʻana o ka chemotherapy i ka mea hoʻomanawanui, hoʻoheheʻe ʻia nā pūnaewele i mālama ʻia a hoʻihoʻi ʻia i ka mea maʻi ma o ka infusion. E ulu kēia mau hunaola i (a hoʻihoʻi) i nā huna koko o ke kino.

Hiki ke hoʻohana ʻia i ka chemotherapy kiʻekiʻe me ka hoʻopakele ʻana o ka cell stem e mālama ai i ka ʻōkuʻu Wilms hou.

Ke hoʻāʻo ʻia nei nā ʻano lapaʻau hou i nā hoʻokolohua hoʻokolohua.

Loaʻa nā ʻike e pili ana i nā hoʻokolohua hoʻokolohua mai ka pūnaewele NCI.

Pahuhopu kau ʻia

He lāʻau lapaʻau i hoʻomāka ʻia ʻia e hoʻohana ai i nā lāʻau a i ʻole nā ​​mea ʻē aʻe e ʻike a hoʻouka aku i nā hunaola maʻi ʻaʻai me ka ʻole e hōʻeha i nā hunaola maʻamau. Hoʻohui ʻia ka lāʻau i hoʻohana ʻia e mālama ai i nā puʻupuʻu hakuʻala o ke keiki i kēia mau mea:

  • Nā kinase inhibitors: Kākoʻo kēia ʻano lāʻau hoʻomāka i nā hōʻailona pono e ulu a hoʻokaʻawale nā ​​hunaola maʻi ʻino. ʻO LOXO-101 a me entrectinib nā kinase inhibitors e aʻo ʻia e mālama i ka nephroma mesoblastic kūpuna. Hiki ke hoʻohana ʻia nā mea kāpae ʻo Tyrosine kinase, e like me sunitinib a i ʻole cabozantinib, e mālama ai i ka carcinoma o ke kīhā. ʻO Axitinib kahi mea kāohi kinetona tyrosine e aʻo ʻia e mālama i ka carcinoma cell renal i hiki ʻole ke hemo ʻia e ke ʻoki a pāhola paha i nā ʻāpana ʻē aʻe o ke kino.
  • ʻO nā mea kāohi Histone methyltransferase: Hoʻolohi kēia hana i hoʻomohala ʻia i ka hiki i ka cell cancer ke ulu a mahele. ʻO Tazemetostat kahi histone methyltransferase mea kāohi i aʻo ʻia e mālama i ka tumo rhabdoid o ka puʻupaʻa.
  • Monoclonal antibody therapy: Hoʻohana kēia lāʻau hoʻomālama i nā mea pale i hana ʻia i loko o ke keʻena hoʻokolohua, mai kahi ʻano hoʻokahi o ke kikowaena pale pale. Hiki i kēia mau lāʻau ʻino ke hoʻomaopopo i nā mea ma nā hunaola maʻi ʻaʻai a i ʻole nā ​​mea maʻamau e kōkua ai i nā hunaola maʻi ʻaʻai. Hoʻopili nā mea ʻino i nā mea a pepehi i nā hunaola maʻi ʻaʻai, ālai i ko lākou ulu ʻana, a i ʻole mālama iā lākou mai ka hoʻolaha ʻana. Hāʻawi ʻia nā antibodies Monoclonal e ka hoʻokomo. Hoʻohana wale ʻia lākou a i ʻole lawe i nā lāʻau, toxins, a i ʻole radioactive pono i nā hunaola maʻi ʻaʻai. ʻO Nivolumab kahi antibody monoclonal e hoʻopaʻa ʻia ana e mālama i ka carcinoma o ka pūhaka liʻiliʻi i hiki ʻole ke hemo ʻia e ke ʻoki a ua pāhola paha i nā ʻaoʻao ʻē aʻe o ke kino

Ke aʻo ʻia nei ka lāʻau i hoʻomākaukau ʻia no ka mālama ʻana i nā ʻōpū puʻuwai ʻōpio i hoʻi hou (hoʻi hou).

Makemake paha nā mea maʻi e noʻonoʻo e pili ana i ka hoʻokolokolo ʻana.

No kekahi mau mea maʻi, ke komo nei i ka hoʻokolohua hoʻokolohua ke koho lapaʻau maikaʻi loa paha. ʻO nā hoʻokolohua hoʻokolohua kahi ʻāpana o ka noiʻi ʻana o ka maʻi ʻaʻai. Hana ʻia nā hoʻokolohua hoʻokolohua e ʻike inā palekana a maikaʻi a maikaʻi paha nā hoʻomaʻamaʻa maʻi ʻaʻai ma mua o ka maʻamau maʻamau.

ʻO ka hapa nui o nā hana maʻamau no ka maʻi ʻaʻai i kau ʻia ma nā hoʻokolohua hoʻokolohua mua. ʻO nā mea maʻi i komo i ka hoʻokolokolo hoʻokolohua hiki ke loaʻa i ka lāʻau maʻamau a i ʻole i waena o nā mea mua i loaʻa kahi lāʻau hou.

ʻO nā mea maʻi i komo i nā hoʻokolohua hoʻokolohua kōkua pū kekahi i ka hoʻomaikaʻi ʻana i ke ʻano o ka mālama ʻana i ka maʻi ʻaʻai i ka wā e hiki mai ana. ʻOiai ʻaʻole nā ​​alakaʻi hoʻokolohua e alakaʻi i nā hoʻoponopono hou maikaʻi, pane pinepine lākou i nā nīnau nui a kōkua i ka neʻe i mua o ka noiʻi.

Hiki i nā mea maʻi ke komo i nā hoʻokolohua hoʻokolohua ma mua, i ka wā, a ma hope paha o ka hoʻomaka ʻana i kā lākou mālama maʻi ʻaʻai.

Hoʻopili wale kekahi mau hoʻokolohua hoʻokolohua i nā mea maʻi i loaʻa ʻole ka lapaʻau. ʻO nā hoʻokolohua ʻē aʻe e hōʻoia i nā mālama ʻana no ka poʻe maʻi i loaʻa ʻole ka maikaʻi o ka maʻi ʻaʻai. Aia kekahi mau hoʻokolohua hoʻokolohua e hoʻāʻo i nā ala hou e hōʻoki i ka maʻi ʻaʻai mai ka hoʻi hou ʻana (hoʻi ʻana) a hōʻemi paha i nā hopena o ka mālama ʻana i ka maʻi ʻaʻai.

Ke mālama ʻia nei nā hoʻokolohua hoʻokolohua ma nā wahi he nui o ka ʻāina. Hiki ke ʻike ʻia ka ʻike e pili ana i nā hoʻokolohua hoʻokolohua e kākoʻo ʻia e NCI ma ka pūnaewele ʻimi noiʻi hoʻokolohua a NCI. Hiki ke loaʻa nā hoʻokolohua hoʻokolohua i kākoʻo ʻia e nā hui ʻē aʻe ma ka pūnaewele ClinicalTrials.gov.

Pono paha nā hoʻokolohua ukali.

ʻO kekahi o nā hoʻokolohua i hana ʻia e hōʻoia i ka maʻi ʻaʻai a i ʻole e ʻike i ke kahua o ka maʻi ʻaʻaʻa e hana hou ʻia paha. E hana hou ʻia kekahi mau hōʻike i mea e ʻike ai i ka maikaʻi o ka mālama ʻana. Hoʻoholo ʻia nā hoʻoholo e pili ana inā e hoʻomau, hoʻololi, a kū paha i ka lāʻau ʻana ma nā hopena o kēia mau hoʻāʻo.

E hoʻomau ʻia kekahi o nā hoʻokolohua mai kēlā me kēia manawa ma hope o ka pau ʻana o ka lāʻau. Hiki i nā hopena o kēia mau hoʻāʻo ke hōʻike inā ua loli ke ʻano o kāu keiki a i ʻole ua hoʻi hou ke kanesa. Kapa ʻia kēia mau hoʻāʻo i kekahi manawa nā hoʻokolohua ukali a i ʻole nā ​​loiloi.

Nā koho lapaʻau no Wilms Tumor

Ma keia Pauku

  • ʻO ke kahua aʻu ʻo Wilms Tumor
  • ʻOihana II Wilms Tumor
  • ʻOihana III Wilms Tumor
  • ʻOihana IV Wilms Tumor
  • ʻO Stage V Wilms Tumor a me nā mea maʻi i ka makaʻu nui i ka hoʻomohala ʻana i ka tumālā kūloko Wilms

No ka ʻike e pili ana i nā lāʻau i helu ʻia ma lalo, e ʻike i ka ʻaoʻao Overtion Option Overview.

ʻO ke kahua aʻu ʻo Wilms Tumor

ʻO ka mālama ʻana i ka anuʻu ʻo Wilms tumo me ka histology maikaʻi e hoʻopili pū ʻia:

  • ʻO ka nephrectomy me ka hemo ʻana o nā lymph node, a ukali ʻia e ka chemotherapy hui pū.
  • ʻO kahi hoʻokolohua hoʻokolohua o nephrectomy wale nō.

Hoʻomaopopo pū ʻia ka tumo I amaplastic Wilms tumo i:

  • ʻO ka nephrectomy me ka hemo ʻana o nā lymph node a ukali ʻia e ka chemotherapy hui pū ʻia a me ka radiation therapy i ka ʻāpana flank (ʻaoʻao ʻelua o ke kino ma waena o nā iwi ʻaoʻao a me ka hipbone).

E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.

ʻOihana II Wilms Tumor

ʻO ka mālama ʻana i ka tumoma II Wilms tumo me ka histology maikaʻi e hoʻopili pū ʻia:

  • ʻO ka nephrectomy me ka hemo ʻana o nā lymph node, a ukali ʻia e ka chemotherapy hui pū.

Hoʻomaopopo pū ʻia ka tumo o ka anuʻu II anaplastic Wilms:

  • ʻO ka nephrectomy me ka hemo ʻana o nā lymph node, a ukali ʻia e radiation radiation i ka ʻōpū a me ka chemotherapy hui pū.

E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.

ʻOihana III Wilms Tumor

ʻO ka mālama ʻana i ka tumoma III Wilms tumo me ka histology maikaʻi e hoʻopili pū ʻia:

  • ʻO ka nephrectomy me ka hemo ʻana o nā lymph node, a ukali ʻia e radiation radiation i ka ʻōpū a me ka chemotherapy hui pū.

Hoʻomaopopo pū ʻia ka tumo o ke kahua III anaplastic Wilms tumor:

  • ʻO ka nephrectomy me ka hemo ʻana o nā lymph node, a ukali ʻia e radiation radiation i ka ʻōpū a me ka chemotherapy hui pū.
  • Hoʻohui ʻia ka chemotherapy hui pū ʻia e nephrectomy me ka hemo ʻana o nā lymph node, a ukali ʻia e radiation radiation i ka ʻōpū.

E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.

ʻOihana IV Wilms Tumor

Hoʻomaʻamaʻa ʻia ka tumoma IV Wilms tumo me ka histology maikaʻi e komo pū paha:

  • ʻO ka nephrectomy me ka hemo ʻana o nā lymph node, a ukali ʻia e radiation radiation i ka ʻōpū a me ka chemotherapy hui pū. Inā ua pālahalaha ka maʻi ʻaʻai i nā ʻāpana ʻē aʻe o ke kino, e loaʻa pū ka poʻe maʻi i ka radiation radiation i kēlā mau wahi.

Hoʻomaopopo pū ʻia ka tumo o ka anuʻu IV anaplastic Wilms tumo:

  • ʻO ka nephrectomy me ka hemo ʻana o nā lymph node, a ukali ʻia e radiation radiation i ka ʻōpū a me ka chemotherapy hui pū. Inā ua pālahalaha ka maʻi ʻaʻai i nā ʻāpana ʻē aʻe o ke kino, e loaʻa pū ka poʻe maʻi i ka radiation radiation i kēlā mau wahi.
  • Hāʻawi ʻia ka chemotherapy hoʻohui ʻia ma mua o ka nephrectomy me ka hemo ʻana o nā lymph node, a ukali ʻia e ka radiation radiation i ka ʻōpū. Inā ua pālahalaha ka maʻi ʻaʻai i nā ʻāpana ʻē aʻe o ke kino, e loaʻa pū ka poʻe maʻi i ka radiation radiation i kēlā mau wahi.

E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.

ʻO Stage V Wilms Tumor a me nā mea maʻi i ka makaʻu nui i ka hoʻomohala ʻana i ka tumālā kūloko Wilms

ʻOkoʻa paha ka mālama ʻana i ka tumo V Wilms tumo no kēlā me kēia mea maʻi a hiki ke hoʻopili ʻia:

  • Hoʻohui ʻia ka chemotherapy e hoʻoliʻiliʻi i ka tumor, a ukali ʻia e ke kiʻi hou ʻana ma 4 a 8 mau pule e hoʻoholo ai no ka hoʻōla hou ʻana (nephrectomy hapa, biopsy, chemotherapy hoʻomau, a me / a radiation radiation).
  • Hoʻopili ʻia kahi biopsy o nā puʻupaʻa e ka chemotherapy hui e hoʻoliʻiliʻi i ka tumo. Hana ʻia kahi ʻoki ʻelua e wehe i ka nui o ke kanesa i hiki. E ukali paha kēia ma o ka chemotherapy a me / a i ʻole radiation radiation inā koe ka maʻi ʻaʻai ma hope o ka ʻoki ʻana.

Inā makemake ʻia kahi transplan kidney ma muli o nā pilikia o ka hakuʻala, hoʻopaneʻe ia a 1 i ka 2 mau makahiki ma hope o ka pau ʻana o ka mālama ʻana a ʻaʻohe hōʻailona o ka maʻi ʻaʻai.

E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.

Nā koho lapaʻau no nā Tumine haku mele ʻē aʻe

Ma keia Pauku

  • Ka Puʻukū Pūʻali Renal (RCC)
  • ʻO Rhabdoid Tumor o ka hakuʻala
  • Maopopo Cell Sarcoma o ka hakuʻala
  • ʻO Mesoblastic Neproma Congenital
  • ʻO Ewing Sarcoma o ka hakuʻala
  • ʻO Carenaloma Ryo Myoepithelial Renal
  • ʻO Nefroblastoma ʻokoʻa hapa o Cystic
  • ʻO Multrococular Cystic Nefroma
  • ʻO Sarcoma Synovial Renal Maʻamau
  • Anaplastic Sarcoma o ka hakuʻala
  • Nefroblastomatosis (Diffuse Hyperplastic Perilobar Nefroblastomatosis)

No ka ʻike e pili ana i nā lāʻau i helu ʻia ma lalo, e ʻike i ka ʻaoʻao Overtion Option Overview.

Ka Puʻukū Pūʻali Renal (RCC)

Hoʻomaopopo pū ʻia ka mālama ʻana i ka maʻi ʻaʻai cell.

  • ʻOki kino, ʻo ia paha:
  • nephrectomy me ka hemo ʻana o nā lymph node; a i ʻole
  • nephrectomy hapa me ka hemo ʻana o nā lymph node.
  • Immunotherapy (interferon a me interleukin-2) no ka maʻi ʻaʻai i pāhola ʻia i nā ʻāpana ʻē aʻe o ke kino.
  • ʻO ka therapy target (tyrosine kinase inhibitors) no ka maʻi ʻaʻai i pāhola ʻia i nā ʻāpana ʻē aʻe o ke kino.
  • ʻO kahi hoʻokolohua hoʻokolohua o ka hoʻomālama ʻia me kahi tyrosine kinase mea kāohi a me / a i ʻole monoclonal antibody therapy no ka maʻi ʻaʻai i loaʻa kekahi loli a ʻaʻole hiki ke hemo e ke ʻoki a ua pāhola paha i nā ʻāpana ʻē aʻe o ke kino.

E ʻike i ka hōʻuluʻulu e pili ana i ka mālama ʻana i ka maʻi ʻaʻai maʻi ʻo Renal Cell for more information.

E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.

ʻO Rhabdoid Tumor o ka hakuʻala

ʻAʻohe mālama maʻamau no ka tumo rhabdoid o ka puʻupaʻa. Hiki ke hoʻopili ʻia i ka mālama ʻana:

  • Hoʻohui ʻia o ke kaha ʻana, chemotherapy, a me / a i ʻole radiation radiation.
  • ʻO kahi hoʻokolohua hoʻokolohua o ka lāʻau i hoʻomoe ʻia (tazemetostat).

E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.

Maopopo Cell Sarcoma o ka hakuʻala

ʻO ka mālama ʻana i ka sarcoma pūnaewele ʻino o ka puʻupaʻa e hoʻopili pū paha:

  • ʻO ka nephrectomy me ka hemo ʻana o nā lymph node a ukali ʻia e ka chemotherapy hoʻohui a me ka radiation radiation i ka ʻōpū.
  • ʻO kahi hoʻokolohua hoʻokolohua o kahi lapaʻau hou.

E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.

ʻO Mesoblastic Neproma Congenital

Hoʻomaʻamaʻa no nā pae I, II, a me kekahi mau mea maʻi me ka pae III congenital mesoblastic nephroma i loko o:

  • ʻOki kino.

Hoʻomaʻamaʻa no kekahi mau mea maʻi me ka pae III congenital mesoblastic nephroma i loko o:

  • ʻO ke ʻoki kino e ukali ʻia e chemotherapy.

E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.

ʻO Ewing Sarcoma o ka hakuʻala

ʻAʻohe mālama maʻamau no ka Ewing sarcoma o ka puʻupaʻa. Hiki ke hoʻopili ʻia i ka mālama ʻana:

  • Hoʻohui ʻia o ke kaha ʻana, chemotherapy, a me radiation therapy.

Hiki ke mālama ʻia i ke ala like e mālama ʻia ai ʻo Ewing sarcoma. E ʻike i ka hōʻuluʻulu e pili ana iā Ewing Sarcoma Hana no ka ʻike hou aku.

E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.

ʻO Carenaloma Ryo Myoepithelial Renal

ʻAʻohe lāʻau lapaʻau maʻamau no ka maʻi maʻi myoepithelial renal kumu. Hiki ke hoʻopili ʻia i ka mālama ʻana:

  • Hoʻohui ʻia o ke kaha ʻana, chemotherapy, a me radiation therapy.

ʻO Nefroblastoma ʻokoʻa hapa o Cystic

ʻO ka mālama ʻana i ka nephroblastoma ʻokoʻa ʻokoʻa i ka cystic:

  • ʻO ke ʻoki kino e ukali ʻia e chemotherapy.

ʻO Multrococular Cystic Nefroma

Hoʻomaʻamaʻa pinepine ʻia ka nephroma cystic multilocular:

  • ʻOki kino.

ʻO Sarcoma Synovial Renal Maʻamau

Hoʻomaʻamaʻa pinepine ʻia i ka sarcoma synovial renal mua:

  • ʻO Chemotherapy.

Anaplastic Sarcoma o ka hakuʻala

ʻAʻohe lāʻau lapaʻau maʻamau no ka sarapoma anaplastic o ka puʻupaʻa. ʻO ka hoʻomaʻamaʻa ka maʻamau like i hāʻawi ʻia no ka tumapona Wilms tumo.

Nefroblastomatosis (Diffuse Hyperplastic Perilobar Nefroblastomatosis)

ʻO ka mālama ʻana i nephroblastomatosis kaukaʻi i ka mea aʻe:

  • Inā loaʻa i nā keiki nā hui ʻokoʻa o nā hunaola i hoʻokahi a i ʻole nā ​​konāhua ʻelua.
  • Inā loaʻa i ke keiki ka maʻi ʻōpū ʻo Wilms i hoʻokahi puʻupaʻa a me nā hui o nā hunaola ʻē aʻe i ka puʻuwai ʻē aʻe.

Hoʻomaʻamaʻa ʻia ka nephroblastomatosis me:

  • Chemotherapy ukali ʻia e nephrectomy. I kekahi manawa hiki ke hana ʻia kahi nephrectomy ʻāpana e mālama i ka hana o ka hakuʻala i hiki.

Hoʻomaʻo i nā Tumors Kidney Childhood hou

No ka ʻike e pili ana i nā lāʻau i helu ʻia ma lalo, e ʻike i ka ʻaoʻao Overtion Option Overview.

Hiki ke hoʻopili ʻia i ka lāʻau Wilms hou:

  • Hoʻohui chemotherapy, ʻoki kino, a me radiation radiation.
  • Hoʻohui chemotherapy, ʻoki kino, a me radiation radiation, a ukali ʻia e ka cell cell rescue, me ka hoʻohana ʻana i nā hunaola koko ponoʻī o ke keiki.
  • ʻO kahi hoʻokolohua hoʻokolohua e nānā i kahi laʻana o ka tumo o ka mea maʻi no kekahi ʻano loli. ʻO ke ʻano o ka hoʻomālama ʻia e hāʻawi ʻia i ka mea maʻi e pili ana i ka ʻano o ka loli.

ʻO ka mālama ʻana i ka tumo rhabdoid hou o ka hakuʻala e hoʻopili pū paha:

  • ʻO kahi hoʻokolohua hoʻokolohua e nānā i kahi laʻana o ka tumo o ka mea maʻi no kekahi ʻano loli. ʻO ke ʻano o ka hoʻomālama ʻia e hāʻawi ʻia i ka mea maʻi e pili ana i ka ʻano o ka loli.

Hoʻomaʻamaʻa ʻia i ka sarcoma pūnaewele ʻokoʻa o ka puʻupaʻa i loko:

  • Hoʻohui chemotherapy, ʻoki e wehe i ka tumo (inā hiki), a me / a i ʻole radiation radiation.
  • ʻO kahi hoʻokolohua hoʻokolohua e nānā i kahi laʻana o ka tumo o ka mea maʻi no kekahi ʻano loli. ʻO ke ʻano o ka hoʻomālama ʻia e hāʻawi ʻia i ka mea maʻi e pili ana i ka ʻano o ka loli.

Hoʻomaʻamaʻa ʻia i ka ne recroma mesoblastic hou e hiki ke hoʻopili ʻia:

  • Hoʻohui chemotherapy, ʻoki kino, a me radiation radiation.
  • ʻO kahi hoʻokolohua hoʻokolohua e nānā i kahi laʻana o ka tumo o ka mea maʻi no kekahi ʻano loli. ʻO ke ʻano o ka hoʻomālama ʻia e hāʻawi ʻia i ka mea maʻi e pili ana i ka ʻano o ka loli.
  • ʻO kahi hoʻokolohua hoʻokolohua o ka lāʻau i hoʻomākaukau ʻia (LOXO-101 a i ʻole entrectinib).

ʻO ka mālama ʻana i nā ʻōpū puʻuwai ʻōpio ʻē aʻe pinepine i loko o kahi hoʻokolohua hoʻokolohua.

E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.

E aʻo hou aʻe e pili ana iā Wilms Tumor a me nā Tumine Kidney Childhood ʻē aʻe

No ka ʻike hou aku mai ka National Cancer Institute e pili ana iā Wilms tumo a me nā ʻōpū puʻuwai ʻōpio ʻē aʻe, e ʻike i ka mea aʻe:

  • ʻAoʻao Kākoʻo Hale Kanaka
  • Computers Tomography (CT) Scans a me ka maʻi ʻaʻai
  • Ua ʻae ʻia nā lāʻau no Wilms Tumor a me nā maʻi maʻi ʻōpio ʻē aʻe
  • Immunotherapy e mālama i ka maʻi ʻaʻai
  • Ke hoʻāʻo genetic no ka hoʻoilina hoʻoilina maʻi maʻi maʻi Syndromes

No ka ʻike hou aku i ka maʻi ʻaʻai kamaliʻi a me nā kumuwaiwai maʻi ʻaʻai ʻē aʻe, e ʻike i ka mea aʻe:

  • E pili ana i ka maʻi ʻaʻai
  • Nā maʻi ʻōpio
  • Huli ʻo Cure no ka hōʻole ʻana i nā maʻi ʻaʻai keiki
  • Nā hopena hope loa o ka mālama ʻana no ka maʻi ʻaʻai kamaliʻi
  • ʻO nā ʻōpio a me nā ʻōpio me ka maʻi ʻaʻai
  • Nā keiki me ka maʻi ʻaʻai: He alakaʻi no nā mākua
  • Ka maʻi ʻaʻai ma nā keiki a me nā ʻōpio
  • Ke hoʻokū nei
  • Ke kāohi nei i ka maʻi ʻaʻai
  • Nā nīnau e nīnau ai i kāu kauka e pili ana i ka maʻi ʻaʻai
  • No nā mea ola a me nā mea mālama


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