Nā ʻano / iwi / hoʻomanawanui / ʻewing-treatment-pdq
Nā ʻikepili i loko
Hoʻomaʻo Ewing Sarcoma
ʻO ka ʻike ākea e pili ana iā Ewing Sarcoma
NA MANA KUNI
- ʻO ka Ewing sarcoma kahi ʻano tumo e hana ana i ka iwi a i ʻole nā mea palupalu.
- Hiki ke hana ʻia kahi sarcoma a puni ʻole i hoʻokae ʻole ʻia i ka iwi a i ʻole nā mea palupalu.
- ʻO nā hōʻailona a me nā ʻōuli o ka Ewing sarcoma me ka pehu a me ka ʻeha kokoke i ka tumo.
- Hoʻohana ʻia nā hoʻokolohua e nānā i ka iwi a me nā mea palupalu e kuhikuhi a me ka pae ʻo Ewing sarcoma.
- Hana ʻia kahi biopsy e kuhikuhi i ka sarcoma ʻo Ewing.
- Kū kekahi mau kumu i ka wānana (kahi o ke ola ʻana).
ʻO ka Ewing sarcoma kahi ʻano tumo e hana ana i ka iwi a i ʻole nā mea palupalu.
ʻO ka Ewing sarcoma kahi ʻano tumo e hana aʻe mai kekahi ʻano o nā hunaola i ka iwi a i ʻole nā mea palupalu. Ewing sarcoma paha i loko o nā iwi o nā wāwae, nā lima, nā wāwae, nā lima, ka umauma, nā pelvis, nā iwi kuamoo, a me nā iwi poʻo. Ewing sarcoma i loaʻa i loko o ka palupalu nāʻaʻaʻa o ke kumu, nā lima, nā wāwae, ke poʻo, ka ʻāʻī, retroperitoneum (kahi ma ka hope o ka ʻōpū ma hope o nā mea i kū i ka paia o ka ʻōpū a uhi i ka hapa nui o nā mea i loko o ka ʻōpū), a i ʻole nā wahi ʻē aʻe.
ʻO ka Ewing sarcoma ka mea maʻamau i nā ʻōpio a me nā ʻōpio (ʻōpio ma waena o 20).
Ua kapa ʻia ʻo Ewing sarcoma peripheral primitive neuroectodermal tumor, Askin tumor (Ewing sarcoma o ka paia o ka umauma), extracomseous Ewing sarcoma (Ewing sarcoma i loko o nā mea ʻē aʻe ma mua o ka iwi), a me ka ʻohana ʻo Ewing sarcoma o nā tumors.
Hiki ke hana ʻia kahi sarcoma a puni ʻole i hoʻokae ʻole ʻia i ka iwi a i ʻole nā mea palupalu.
Hana pinepine ʻia ka sarcoma a puni ʻole i nā iwi a i ʻole nā mākala e pili ana i nā iwi a kōkua i ke kino e neʻe. Aia he mau ʻano ʻelua o ka sarcoma a puni ʻole i hoʻokaʻawale ʻia e mālama ʻia e like me Ewing sarcoma:
- ʻO ka sarcoma pūnaewele puni ʻole i hoʻokaʻawale ʻole ʻia me BCOR-CCNB3 hoʻoponopono hou. ʻO kēia ʻano tumo iwi i maʻa mau i ke pelvis, nā lima, a me nā wāwae. Hoʻolahalaha paha ia i nā ʻāpana ʻē aʻe o ke kino. I kēia ʻano sarcoma pūnaewele puni, ua hoʻohui ʻia ka ʻaoʻao BCOR i ka ʻohana CCNB3. No ke kuhi ʻana i ka sarcoma a puni, nānā ʻia nā hunaola tumo no kēia loli.
- ʻO ka sarcoma pūnaewele puni ʻole i hoʻokaʻawale ʻole ʻia me nā hoʻoponopono hou ʻana o CIC-DUX4. ʻO kēia ʻano tumo pulu i palaha i ka pahu, nā lima, a me nā wāwae. ʻO ka mea maʻamau i nā kāne a me nā poʻe ʻōpio ma waena o 21 a 40 mau makahiki. I kēia ʻano sarcoma pūnaewele puni, ua hoʻohui ʻia ka ʻaoʻao CIC i ka ʻāpana DUX4. No ke kuhi ʻana i ka sarcoma a puni, nānā ʻia nā hunaola tumo no kēia loli.
ʻO nā hōʻailona a me nā ʻōuli o ka Ewing sarcoma me ka pehu a me ka ʻeha kokoke i ka tumo.
Nā Ewing sarcoma a i ʻole nā kūlana ʻē aʻe i hoʻokumu ʻia i kēia mau hōʻailona a me nā ʻōuli ʻē aʻe. E nīnau me ke kauka o kāu keiki inā loaʻa i kāu keiki kekahi o kēia mau mea:
- ʻO ka ʻeha a me / a i ʻole ka pehu ʻana, ma nā lima, nā wāwae, ka umauma, kua, a i ʻole ke pelvis.
- ʻO kahi puʻupuʻu (e ʻoluʻolu a mehana paha) i nā lima, nā wāwae, ka umauma, a me nā pelvis.
- Fiva no ke kumu ʻole i ʻike ʻia.
- He iwi e haki no ke kumu ʻole.
Hoʻohana ʻia nā hoʻokolohua e nānā i ka iwi a me nā mea palupalu e kuhikuhi a me ka pae ʻo Ewing sarcoma.
ʻO nā hana e hana ai i nā kiʻi o nā iwi a me nā ʻāpana palupalu a me nā wahi kokoke e kōkua i ke kuhi ʻana iā Ewing sarcoma a hōʻike i ka lōʻihi o ka laha ʻana o ka maʻi ʻaʻai. ʻO ke kaʻina hana e ʻike inā ua pālahalaha ʻia nā hunaola maʻi ʻōpū i loko a puni o nā iwi a me nā mea palupalu a i ʻole nā ʻāpana ʻē aʻe o ke kino i kapa ʻia he staging
E hoʻolālā i ka mālama ʻana, he mea nui e ʻike inā ua pālahalaha ka maʻi ʻaʻai i nā ʻāpana ʻē aʻe o ke kino. ʻO nā hoʻokolohua a me nā kaʻina hana e ʻike, ʻike, a me ka pae Ewing sarcoma e hana maʻamau i ka manawa like.
Hiki ke hoʻohana i nā hoʻokolohua a me nā kaʻina hana e kuhikuhi ai a i ʻole ke kahua Ewing sarcoma:
- ʻO ka hoʻāʻo kino a me ka mōʻaukala: kahi hōʻike o ke kino e nānā i nā hōʻailona laulā o ke olakino, e like me ka nānā ʻana i nā hōʻailona o ka maʻi, e like me nā puʻupuʻu a i ʻole nā mea ʻē aʻe e ʻano ʻē. E lawe ʻia kahi moʻolelo o nā ʻano olakino o ka mea maʻi a me nā maʻi i hala a me nā mālama ʻana.
- MRI (kiʻi resonance ʻume mākenēki): kahi hana e hoʻohana ai i ka magnet, nā nalu lekiō, a me kahi kamepiula e hana i kahi o nā kiʻi kikoʻī o nā wahi i loko o ke kino, e like me kahi i hana ai ka tumo. Kāhea ʻia kēia kaʻina hana he kiʻi nukelea kiʻi resonance (NMRI).
- CT scan (CAT scan): Kahi hana e hana ai i ka moʻo o nā kiʻi kikoʻī o nā wahi i loko o ke kino, e like me kahi i hana ʻia ai ka tumo a i ʻole ka umauma, i lawe ʻia mai nā kihi ʻokoʻa. Hana ʻia nā kiʻi e kahi kamepiula i hoʻopili ʻia i kahi mīkini x-ray. Hoʻokomo ʻia paha ke kala i loko o ke aa a i ʻole ale ʻia e kōkua i nā ʻōpū a i ʻole nā kino i hōʻike hou aku me ka maopopo. Kāhea ʻia kēia kaʻina hana he tomography i helu ʻia, kamepiula tomography, a i ʻole he tomography axial computerized.
- PET scan (positron emission tomography scan): kahi hana e loaʻa ai nā puʻupuʻu tumo malignant i loko o ke kino. Hoʻokomo ʻia kahi liʻiliʻi o ka glucose radioactive (kō) i loko o kahi aa koko. Hoʻopili ka scanner PET a puni ke kino a hana i kahi kiʻi o kahi e hoʻohana ʻia ai ka glucose i ke kino. ʻOi aku ka mālamalama o nā hunaola tumo ma ke kiʻi no ka mea ʻoi aku ka hana a lawe i ka glucose ma mua o ka hana ʻana o nā hunaola maʻamau. Hana pinepine ʻia kahi scan PET a me kahi scan CT i ka manawa like. Inā loaʻa kekahi maʻi ʻaʻai, hoʻonui kēia i ka manawa e ʻike ʻia.

- ʻImi iwi: kahi hana e nānā ai inā aia he wikiwiki e hoʻokaʻawale i nā hunaola, e like me nā hunaola maʻi ʻaʻai, i ka iwi. Hoʻokomo ʻia kahi mea liʻiliʻi loa o nā mea radioactive i loko o ke aa a hele i waena o ke kahe o ke koko. Hōʻiliʻili ka mea lekiō i nā iwi me ka maʻi ʻaʻai a ʻike ʻia e kahi scanner.
- ʻO ka ʻiʻo o ka iwi iwi a me ka biopsy: Ka lawe ʻia ʻana o ka iwi iwi a me kahi ʻāpana o ka iwi ma ka hoʻokomo ʻana i kahi nila kuha i loko o ka iwi ʻūʻū. Lawe ʻia nā laʻana mai nā hipbones ʻelua. ʻIke kahi pathologist i ka momona o ka iwi a me ka iwi ma lalo o kahi microscope e ʻike inā ua pālahalaha ka maʻi ʻaʻa.
- X-ray: ʻO kahi x-ray kahi ʻano kukuna ikehu i hiki ke hele ma waena o ke kino a i ke kiʻi ʻoniʻoni, e hana ana i kiʻi o nā wahi i loko o ke kino, e like me ka umauma a i ʻole kahi e hana ai ka tumo.
- Helu piha o ke koko (CBC): Ke kaʻina hana e huki ʻia ai kahi laʻana o ke koko a nānā ʻia no kēia mau mea:
- ʻO ka helu o nā hunaola ʻulaʻula, nā aʻa koko keʻokeʻo, a me nā platelet.
- ʻO ka nui o ka hemoglobin (ka protein i hāpai i ka oxygen) i loko o nā hunaola ʻulaʻula.
- ʻO ka ʻāpana o ka hāpana koko i hana ʻia i nā hunaola ʻulaʻula.
- Nā aʻo kemika koko: kahi hana e nānā ʻia ai kahi laʻana koko e ana i ka nui o kekahi mau mea, e like me ka lactate dehydrogenase (LDH), i hoʻokuʻu ʻia i loko o ke koko e nā mea a me nā mea i loko o ke kino. ʻO kahi mea maʻamau (ʻoi aʻe a i ʻole haʻahaʻa ma mua o ka maʻamau) o kahi mea hiki ke lilo i hōʻailona o ka maʻi.
Hana ʻia kahi biopsy e kuhikuhi i ka sarcoma ʻo Ewing.
Lawe ʻia nā laikini kele i ka wā o kahi biopsy i hiki ai iā lākou ke ʻike ma lalo o kahi microscope e kahi pathologist e nānā i nā hōʻailona o ka maʻi ʻaʻai. He kōkua inā hana ʻia ka biopsy ma ke kikowaena like kahi e hāʻawi ʻia ai ka lāʻau.
- Needle biopsy: No kahi biopsy o ka nila, hemo ʻia kaʻiʻo me ka nila. Hiki ke hana ʻia kēia ʻano biopsy inā hiki ke hemo i nā ʻōpala i lawa ka lawa no ka hoʻāʻo ʻana.
- ʻO kahi biopsy incisional : No kahi biopsy incision, ua hoʻoneʻe ʻia kahi laʻana o nā mea i loko o kahi ʻoki o ka ʻili.
- ʻO Biopsy kūikawā: ʻO ka hemo ʻana o kahi puʻupuʻu āpau a i ʻole kahi o nā kiko i kū ʻole i ka nānā maʻamau.
ʻO nā loea (pathologist, radiation oncologist, a me ke kauka) nāna e mālama i ka mea maʻi e hana maʻamau e hoʻoholo i kahi pūnaewele maikaʻi loa e waiho ai i ka nila a biisiona incision. He mea nui ke koho ʻana o ka pūnaewele biopsy. ʻO kahi pūnaewele biopsy i koho ʻole ʻia e hopena paha i kahi ʻoki ʻoi aku ka nui e wehe i ka tumo a i kahi ākea nui paha e mālama ʻia me ka radiation radiation.
Inā loaʻa kahi manawa i palahalaha ka maʻi ʻaʻai i nā lymph node kokoke, hiki ke wehe ʻia hoʻokahi a ʻoi paha mau lymph node a nānā ʻia no nā ʻōuli o ka maʻi ʻaʻai.
E hana ʻia paha kēia mau hoʻāʻo ma ke kiko i lawe ʻia.
- Nānā Cytogenetic: kahi hoʻokolohua hoʻokolohua kahi e helu ai nā chromosome o nā hunaola i kahi hāpana o nā kiko a nānā ʻia no nā loli, e like me ka haki, nalowale, hoʻoponopono hou ʻia, a i ʻole nā chromosome keu. ʻO nā loli i kekahi mau chromosome he hōʻailona ia o ka maʻi ʻaʻai. Hoʻohana ʻia ka hoʻoponopono Cytogenetic e kōkua i ke kuhi ʻana i ka maʻi ʻaʻai, e hoʻolālā i ka lāʻau ʻana, a i ʻole e ʻike i ke ʻano o ka maikaʻi o ka mālama ʻana.
- Immunohistochemistry: ʻO kahi hoʻokolohua hoʻokolohua e hoʻohana ai i nā anti-antibodies e nānā ai no kekahi antigens (markers) i kahi laʻana o kaʻiʻo o ka mea maʻi Hoʻopili pinepine ʻia nā mea ʻino i kekahi enzyme a i ʻole ka waihoʻoluʻu fluorescent. Ma hope o ka hoʻopili ʻana o nā mea ʻume i kekahi antigen kikoʻī i ka laʻana kiko, hoʻōla ʻia ka ʻimene a me ka kala, a laila ʻike ʻia ka antigen ma lalo o kahi microscope. Hoʻohana ʻia kēia ʻano hoʻāʻo e kōkua i ke kuhi ʻana i ka maʻi ʻaʻai a kōkua e haʻi i kekahi ʻano maʻi ʻaʻai mai kekahi ʻano maʻi ʻaʻai.
- Kahe uila ʻili pūnaewele. Hoʻopili ʻia nā hunaola mai kahi hāpana o ke koko o ka mea maʻi, ka iwi o ka iwi, a i ʻole nā mea ʻē aʻe me ka pena wai fluorescent, waiho ʻia i loko o kahi wai, a laila hele kekahi i hoʻokahi manawa i ke kaola o ke kukui. Hoʻokumu ʻia nā hopena o ka hoʻāʻo e pili ana i ka hopena o nā hunaola i hoʻohuehue ʻia me ka pena fluorescent i ke kaola o ke kukui.
Kū kekahi mau kumu i ka wānana (kahi o ke ola ʻana).
ʻO nā kumu e hoʻopili i ka wānana (kahi manawa o ke ola hou) ʻokoʻa ma mua a ma hope o ka mālama ʻana.
Ma mua o ka hāʻawi ʻia ʻana o kekahi lāʻau, pili ka wānana i:
- Inā ua palahalaha ka tumo i nā lymph node a i ʻole nā ʻaoʻao mamao o ke kino.
- Ma kahi o ke kino i hoʻomaka ai ka tumo.
- ʻO ka tumo i hoʻokumu ʻia i ka iwi a i ʻole i nā mea palupalu.
- Pehea ka nui o ka tumo ke ʻike ʻia ka tumo.
- Ua hoʻokumu ʻia ka iwi naha i nā iwi haʻi.
- Inā ʻoi aku ke kiʻekiʻe o ka LDH i ke koko ma mua o ka maʻamau.
- Ua loli paha kekahi ʻōiwi.
- Inā ʻōpio ka mea maʻi ma mua o 15 mau makahiki.
- Ka moekolohe o ka mea maʻi.
- Inā ua mālama ka mea maʻi no kekahi maʻi ʻaʻai ʻokoʻa.
- Inā ua ʻike wale ʻia ka tumo a i ʻole ua hoʻi hou (hoʻi hou).
Ma hope o ka hāʻawi ʻia ʻana o ka lāʻau, hoʻopili ʻia ka wānana e:
- Inā ua hemo loa ka tumo e ka ʻoki kino.
- Ua pane paha ka tumo i ka chemotherapy a i ʻole ka radiation therapy.
Inā piʻi hou ka maʻi ʻaʻai ma hope o ka lapaʻau mua, pili ka wānana i:
- Inā paha i hoʻi mai ka maʻi ʻaʻai ma mua o ʻelua mau makahiki ma hope o ka hana mua.
- Inā i hoʻi mai ka maʻi ʻaʻai i kahi i hana mua ai ʻole i nā ʻāpana ʻē aʻe o ke kino.
Nā Papa o Ewing Sarcoma
NA MANA KUNI
- Hoʻohana ʻia nā hopena o nā hōʻike hōʻoia a me nā hoʻokolohua e ʻike inā ua pāhola nā hunaola maʻi ʻaʻai.
- Hōʻike ʻia ʻo Ewing sarcoma ma ke ʻano he localized, metastatic, a i ʻole recurrent.
- Kūloko ʻEwing sarcoma
- ʻO Metastatic Ewing sarcoma
- Hōʻailona hou ʻo Ewing sarcoma
- ʻEkolu ala e hoʻolaha ai ka maʻi ʻaʻai i loko o ke kino.
- E laha paha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i nā ʻāpana ʻē aʻe o ke kino.
Hoʻohana ʻia nā hopena o nā hōʻike hōʻoia a me nā hoʻokolohua e ʻike inā ua pāhola nā hunaola maʻi ʻaʻai.
ʻO ke kaʻina hana e ʻike inā ua pālahalaha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i nā ʻāpana ʻē aʻe o ke kino i kapa ʻia he staging. ʻAʻohe ʻōnaehana hoʻonohonoho maʻamau no ka Ewing sarcoma. ʻO nā hopena o nā hoʻokolohua a me nā kaʻina hana i hana ʻia e diagnose a me ke kahua ʻo Ewing sarcoma e hoʻohana ʻia e wehewehe i nā tumors ma ke ʻano he wahi a metastatic paha.
Hōʻike ʻia ʻo Ewing sarcoma ma ke ʻano he localized, metastatic, a i ʻole recurrent.
Hōʻike ʻia ʻo Ewing sarcoma ma ke ʻano he localized, metastatic, a i ʻole recurrent.
Kūloko ʻEwing sarcoma
ʻIke ʻia ka maʻi ʻaʻai i ka iwi a i ʻole nā mea palupalu kahi i hoʻomaka ai a ua pāhola paha i nā mea kokoke, e like me nā lymph node kokoke.
ʻO Metastatic Ewing sarcoma
Ua pālahalaha ʻia ka maʻi ʻaʻai mai ka iwi a palupalu paha kahi i hoʻomaka ai i nā ʻāpana ʻē aʻe o ke kino. I ka puʻu ʻo Ewing o ka iwi, pālahalaha pinepine ka maʻi ʻaʻai i ka hāhā, nā iwi ʻē aʻe, a me ka iwi iwi.
Hōʻailona hou ʻo Ewing sarcoma
Ua hoʻi hou ka maʻi ʻaʻa (hoʻi mai) ma hope o ka mālama ʻia ʻana. E hoʻi paha ka maʻi ʻaʻai i loko o ka iwi a i ʻole nā mea palupalu kahi i hoʻomaka ai a i ʻole ʻāpana ʻē aʻe o ke kino.
ʻEkolu ala e hoʻolaha ai ka maʻi ʻaʻai i loko o ke kino.
Hiki ke pālahalaha ʻia ka maʻi ʻaʻai ma o nā meaola, ka ʻōnaehana lymph, a me ke koko.
- Kāpena. Hoʻolahalaha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i ka ulu ʻana i nā wahi kokoke.
- ʻŌnaehana Lymph. Hoʻolahalaha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i ke komo ʻana i ka ʻōnaehana lymph. Hele ka maʻi ʻaʻai ma o nā kīʻaha lymph i nā ʻāpana ʻē aʻe o ke kino.
- Koko. Hoʻolahalaha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i ke komo ʻana i ke koko. Hele ka maʻi ʻaʻai ma o nā kīʻaha koko i nā ʻāpana ʻē aʻe o ke kino.
E laha paha ka maʻi ʻaʻai mai kahi i hoʻomaka ai i nā ʻāpana ʻē aʻe o ke kino.
Ke pālahalaha ʻia ka maʻi ʻaʻai i kekahi ʻāpana o ke kino, ua kapa ʻia ia ʻo metastasis. E haki nā hunaola maʻi 'aʻai mai kahi a lākou i hoʻomaka ai (ka tumo mua) a hele i loko o ka ʻōnaehana lymph a i ʻole ke koko.
- ʻŌnaehana Lymph. Komo ka maʻi ʻaʻai i loko o ka ʻōnaehana lymph, hele ma waena o nā kīʻaha lymph, a hana i kahi tumo (tumo metastatic) i kekahi ʻāpana o ke kino.
- Koko. Komo ke kanesa i loko o ke koko, hele ma waena o nā kīʻaha koko, a hana i kahi tumo (tumo metastatic) i kekahi ʻāpana o ke kino.
ʻO ka tumo metastatic ka ʻano like o ke kanesa me ka tumo mua. ʻO kahi laʻana, inā pālahalaha ʻo Ewing sarcoma i ka akemāmā, ʻo nā hunaola maʻi ʻaʻai i loko o ka akemāhā nā ewing sarcoma Ewing maoli ia. ʻO ka maʻi he metastatic Ewing sarcoma, ʻaʻole ka maʻi ʻaʻai māmā.
Laulā Manaʻo Option Oponopono
NA MANA KUNI
- Aia nā ʻano lapaʻau like ʻole no nā keiki me ka Ecoming sarcoma.
- Pono nā keiki me ka Ewing sarcoma i kā lākou lapaʻau ʻana e kekahi kime o nā lawelawe mālama ola he loea i ka mālama ʻana i ka maʻi ʻaʻai i nā keiki.
- Hoʻomaʻamaʻa no ka Ewing sarcoma i nā hopena ʻaoʻao.
- Hoʻohana ʻia nā ʻano ʻehā o ka hoʻoponopono maʻamau:
- ʻO Chemotherapy
- Lapaʻau hoʻomākala
- ʻOki kino
- ʻO ka chemotherapy kiʻekiʻe loa me ka hoʻopakele ʻana o ka cell stem
- Ke hoʻāʻo ʻia nei nā ʻano lapaʻau hou i nā hoʻokolohua hoʻokolohua.
- Pahuhopu kau ʻia
- Immunotherapy
- Makemake paha nā mea maʻi e noʻonoʻo e pili ana i ka hoʻokolokolo ʻana.
- Hiki i nā mea maʻi ke komo i nā hoʻokolohua hoʻokolohua ma mua, i ka wā, a ma hope paha o ka hoʻomaka ʻana i kā lākou mālama maʻi ʻaʻai.
- Pono paha nā hoʻokolohua ukali.
Aia nā ʻano lapaʻau like ʻole no nā keiki me ka Ecoming sarcoma.
Loaʻa nā ʻano lapaʻau like ʻole no nā keiki me ka Ecoming sarcoma. Kūlana maʻamau kekahi mau hōʻailona (ʻo ka lāʻau i hoʻohana ʻia i kēia manawa), a ʻo kekahi e hoʻāʻo ʻia nei i nā hoʻokolohua hoʻokolohua. ʻO kahi hoʻokolohua hoʻokolohua lapaʻau kahi noiʻi noiʻi i manaʻo ʻia e kōkua i ka hoʻomaikaʻi ʻana i nā mālama ʻana i kēia manawa a i ʻole loaʻa ka ʻike e pili ana i nā mālama hou no nā maʻi me ka maʻi ʻaʻai. Ke hōʻike nā hoʻokolohua hoʻokolohua ʻoi aku ka maikaʻi o kahi lapaʻau hou ma mua o ka maʻamau maʻamau, lilo paha ka lāʻau hou i ka lapaʻau maʻamau.
Ma muli o ka loaʻa ʻole o ka maʻi ʻaʻai i nā keiki a me nā ʻōpio, pono e noʻonoʻo ʻia i ka hoʻokolohua hoʻokolohua. ʻO kekahi mau hoʻokolohua hoʻokolohua e hāmama wale i nā mea maʻi i hoʻomaka ʻole i ka lāʻau.
Pono nā keiki me ka Ewing sarcoma i kā lākou lapaʻau ʻana e kekahi kime o nā lawelawe mālama ola he loea i ka mālama ʻana i ka maʻi ʻaʻai i nā keiki.
E mālama ʻia ka lapaʻau ʻana e kahi oncologist pediatric, he kauka i loea i ka mālama ʻana i nā keiki me ka maʻi ʻaʻai. Hana ka oncologist pediatric me nā mea lawelawe olakino ʻē aʻe i loea i ka mālama ʻana i nā keiki me ka Ecoming sarcoma a ʻo ka poʻe loea i kekahi mau wahi o ka lāʻau. Pākuʻi ʻia kēia mau mea i lalo:
- Kahuna Pediatrician.
- Oncologist ʻoki kino a i ʻole oncologist orthopedic.
- Oncologist uila.
- ʻO ka loea kahu maʻi Pediatric.
- Limahana limahana.
- Lapaʻau hoʻōla.
- ʻOlogistlapa psychologist.
Hoʻomaʻamaʻa no ka Ewing sarcoma i nā hopena ʻaoʻao.
No ka ʻike e pili ana i nā hopena i hoʻomaka i ka wā o ka mālama ʻana no ka maʻi ʻaʻai, ʻike i kā mākou ʻaoʻao ʻaoʻao ʻaoʻao.
ʻO nā hopena ʻē aʻe mai ka mālama ʻana i ka maʻi ʻaʻai e hoʻomaka ma hope o ka mālama ʻana a hoʻomau no nā mahina a i ʻole mau makahiki e kapa ʻia nā hopena hopena. Hiki i nā hopena hope loa o ka mālama ʻana i ka maʻi ʻaʻai ke hoʻopili i kēia mau mea:
- Nā pilikia o ke kino.
- Nā loli i ke ʻano, nā manaʻo, ka noʻonoʻo, ke aʻo ʻana, a me ka hoʻomanaʻo paha.
- Nā maʻi ʻelua (nā ʻano maʻi ʻaʻai hou). ʻO nā mea maʻi i mālama ʻia no ka Ewing sarcoma i ka nui o ka makaʻu o ka maʻi myeloid leukemia a me myelodysplastic syndrome. Aia kekahi piʻi nui o ka sarcoma ma kahi e mālama ʻia me ka radiation radiation.
E mālama a kāohi ʻia paha kekahi mau hopena hopena. He mea nui e kamaʻilio pū me nā kauka o kāu keiki e pili ana i nā hopena o ka mālama ʻana i ka maʻi ʻaʻai i kāu keiki. (E ʻike i ka hōʻuluʻulu e pili ana i nā hopena hope o ka mālama ʻana no ka maʻi ʻaʻai kamaliʻi no ka ʻike hou aku.)
Hoʻohana ʻia nā ʻano ʻehā o ka hoʻoponopono maʻamau:
ʻO Chemotherapy
ʻO Chemotherapy kahi lāʻau lapaʻau maʻi maʻi e hoʻohana i nā lāʻau e hōʻoki i ka ulu ʻana o nā hunaola maʻi ʻaʻai, ma ka luku ʻana paha i nā hunaola a i ʻole ke kū ʻana iā lākou mai ka hoʻokaʻawale Ke lawe ʻia ka chemotherapy e ka waha a i ʻole injected i loko o kahi aa koko a i ʻole nā mākala, komo nā lāʻau i ke kahe o ke koko a hiki ke kiʻi i nā hunaola maʻi ʻōpio i loko o ke kino (chemotherapy ʻōnaehana). Ke waiho pololei ʻia ka chemotherapy i loko o ka wai cerebrospinal, kahi hui, a i ʻole ke kino o ke kino e like me ka ʻōpū, hoʻopili ka lāʻau i nā hunaola maʻi ʻaʻai i loko o kēlā mau wahi (chemotherapy āpana). Hoʻohui ka chemotherapy hui me ka hoʻohana ʻana ma mua o hoʻokahi lāʻau anticancer.
ʻO ka chemotherapy hui pū ʻia kahi ʻāpana o ka mālama ʻana no nā mea maʻi āpau me nā puʻukū ʻEwing. ʻO ia ka lāʻau mua i hāʻawi mua ʻia a mau ma kahi o 6 a 12 mau mahina. Hāʻawi pinepine ʻia ʻo Chemotherapy e hoʻoliʻiliʻi i ka tumo ma mua o ke kaha ʻana a i ʻole ka radiation therapy a e pepehi i nā hunaola tumola i pāhola ʻia i nā ʻāpana ʻē aʻe o ke kino.
E ʻike i nā lāʻau i ʻae ʻia no ka Tissue Tissue Sarcoma no ka ʻike hou aku.
Lapaʻau hoʻomākala
ʻO ka radiation radiation kahi lāʻau maʻi maʻi maʻi e hoʻohana i nā kukuna x nui ikaika a i ʻole nā ʻano radiation e hoʻomake i nā hunaola maʻi ʻaʻai a mālama ʻole paha i ka ulu ʻana. ʻElua ʻano o radiation radiation:
- Hoʻohana ka radiation radiation kūwaho i kahi mīkini ma waho o ke kino e hoʻouna i ka radiation i ka maʻi ʻaʻai.
- Hoʻohana ka radiation radiation i loko i kahi lāʻau radioactive i hoʻopaʻa ʻia i nā nila, nā hua, nā uea, a i ʻole nā catheters i kau pololei ʻia i loko a kokoke paha i ka maʻi ʻaʻai.
Hoʻohana ʻia ka radiation radiation kūwaho e mālama ai iā Ewing sarcoma.
Hoʻohana ʻia ka radiation radiation ke hiki ʻole ke hemo ʻia ka tumo e ka ʻoki ʻana a i ʻole ke ʻoki ʻana e wehe i ka tumo e hoʻopili i nā hana o ke kino a i ʻole ke ʻano o ke keiki. Hiki ke hoʻohana ʻia e hana i ka liʻiliʻi o ka tumo a hoʻoliʻiliʻi i ka nui o nā kiko e pono e hemo i ka wā o ke ʻoki. Hoʻohana ʻia nō ia e mālama i kekahi tumo i koe ma hope o ke kaha ʻana a me nā tumors i palahalaha aʻe i nā wahi ʻē aʻe o ke kino.
ʻOki kino
Hana pinepine ʻia ke ʻoki ʻana e wehe i ka maʻi ʻaʻai i waiho ʻia ma hope o chemotherapy a i ʻole radiation therapy. Ke hiki, lawe ʻia ke tumo holoʻokoʻa e ke ʻoki. Hiki ke pani ʻia ka mū a me ka iwi i hemo ʻia me kahi graft, kahi e hoʻohana ai i kaʻiʻo a me ka iwi i lawe ʻia mai kekahi ʻāpana o ke kino o ka mea maʻi a i ʻole mea hāʻawi. I kekahi manawa hoʻohana ʻia kahi implant, e like me ka iwi ʻoka.
Ma hope o ka hemo ʻana o ke kauka i nā maʻi ʻaʻai āpau i hiki ke ʻike ʻia i ka manawa o ke ʻoki ʻana, hiki i kekahi mau mea maʻi ke hāʻawi ʻia i ka chemotherapy a i ʻole ka radiation therapy ma hope o ke kaha ʻana e luku i nā hunaola maʻi ʻea i koe. ʻO ka lāʻau i hāʻawi ʻia ma hope o ke kaha ʻana, e hoʻohaʻahaʻa i ka makaʻu e hoʻi mai ka maʻi ʻaʻai, i kapa ʻia ʻo adjuvant therapy.
ʻO ka chemotherapy kiʻekiʻe loa me ka hoʻopakele ʻana o ka cell stem
Hāʻawi ʻia nā lāʻau kiʻekiʻe o ka chemotherapy e pepehi i nā hunaola maʻi ʻaʻai. Hoʻopau pū ʻia nā hunaola olakino, e like me nā hunaola koko, e ka lāʻau maʻi ʻaʻai. ʻO ka transplant cell Stem kahi lapaʻau e pani i nā hunaola koko. Lawe ʻia nā hunaola ʻōpala (ʻaʻaʻa ʻole o ke koko) mai ke koko a i ʻole ka iwi o ka mea maʻi a i ʻole he mea hāʻawi a hoʻopaʻa ʻia a mālama ʻia. Ma hope o ka pau ʻana o ka chemotherapy i ka mea hoʻomanawanui, hoʻoheheʻe ʻia nā pūnaewele i mālama ʻia a hoʻihoʻi ʻia i ka mea maʻi ma o ka infusion. E ulu kēia mau hunaola i (a hoʻihoʻi) i nā huna koko o ke kino. Hoʻohana ʻia ʻo Chemotherapy me ka hoʻopakele cell stem e mālama i ka sarcoma Ewing kūloko.
Ke hoʻāʻo ʻia nei nā ʻano lapaʻau hou i nā hoʻokolohua hoʻokolohua.
Hōʻike kēia ʻāpana hōʻuluʻulu manaʻo i nā mālama e hoʻopaʻa ʻia nei i nā hoʻokolohua hoʻokolohua. ʻAʻole paha ia e ʻōlelo i kēlā me kēia lapaʻau hou e hoʻopaʻa ʻia ana. Loaʻa nā ʻike e pili ana i nā hoʻokolohua hoʻokolohua mai ka pūnaewele NCI.
Pahuhopu kau ʻia
He lāʻau lapaʻau i hoʻomākaukau ʻia e hoʻohana i nā lāʻau a i ʻole nā mea ʻē aʻe e hoʻopilikia i nā kaʻina hana e pono ai e ulu a ulu nā maʻi ʻaʻai. ʻO nā ʻano o nā lāʻau hoʻomākalakala i hoʻohana ʻia e mālama i nā maʻi ʻōpio kamaliʻi ʻole me nā mea aʻe:
- Monoclonal antibody therapy: hana ʻia nā Monoclonal antibodies i loko o ke keʻena hoʻokolohua mai kahi ʻano hoʻokahi o ke kikowaena pale pale. Hiki i kēia mau lāʻau ʻino ke hoʻomaopopo i nā mea ma nā hunaola maʻi ʻaʻai a i ʻole nā mea maʻamau e kōkua ai i nā hunaola maʻi ʻaʻai. Hoʻopili nā mea ʻino i nā mea a pepehi i nā hunaola maʻi ʻaʻai, ālai i ko lākou ulu ʻana, a i ʻole mālama iā lākou mai ka hoʻolaha ʻana. Hāʻawi ʻia nā antibodies Monoclonal e ka hoʻokomo. Hoʻohana wale ʻia lākou a i ʻole lawe i nā lāʻau, toxins, a i ʻole radioactive pono i nā hunaola maʻi ʻaʻai. Ke aʻo ʻia nei ʻo Ganitumab no ka mālama ʻana i ka sarcoma metastatic Ewing.
- Hoʻoikaika kūpina Kinase: ʻo nā mea hoʻopōpō Kinase nā lāʻau e ālai i kahi protein i pono no nā hunaola maʻi ʻoki e hoʻokaʻawale. Ke aʻo ʻia nei lākou e mālama i ka sarcoma Ewing hou.
- NEDD8-activating enzyme (NAE) inhibitor therapy: NAE mea kāohi i nā lāʻau i hoʻopili iā NAE a kū i nā hunaola maʻi ʻāpana mai ka hoʻokaʻawale. Ke aʻo ʻia nei ʻo Pevonedistat i ka mālama ʻana i ka sarcoma Ewing hou.
Immunotherapy
ʻO ka Immunotherapy kahi lapaʻau e hoʻohana i ka ʻōnaehana pale maʻi o ka mea maʻi e hakakā i ka maʻi ʻaʻai. Hoʻohana ʻia nā mea i hana ʻia e ke kino a i hana ʻia paha i kahi keʻena hoʻokolohua e hoʻonui, kuhikuhi, a hoʻihoʻi hou i nā pale kūlohelohe o ke kino i ka maʻi ʻaʻai. Kāhea ʻia kēia ʻano lapaʻau maʻi ʻaʻai a biotherapy a i ʻole biologic therapy.
- 'Ōnaehana paleʻea ueo ei? Aiiia inhibitor Inc: 'ōnaehana paleʻea ueo ei? Aiiia nā mea kūpale aeie kekahi mau nā polokina i ia e kekahi'ōnaehana paleʻea'ōnaehana keena, e like me T keena, a me kekahi maʻi 'aʻai keena. Kōkua kēia mau protein i ka mālama ʻana i nā pane pale a hiki ke mālama i nā hunaola T mai ka luku ʻana i nā hunaola maʻi ʻaʻai. Ke pale ʻia kēia mau protein, hoʻokuʻu ʻia nā "palaka" ma ka ʻōnaehana pale a hiki i nā hunaola T ke make i nā hunaola maʻi ʻoi aku ka maikaʻi. ʻO Nivolumab a me ipilimumab kahi ʻano o nā mea pale pale nānā pale pale e aʻo ʻia e mālama ai i ka sarcoma Ewing hou.
- Chimeric antigen receptor (CAR) T-cell therapy: ʻo CAR T-cell therapy kahi ʻano o ka immunotherapy e hoʻololi ai i nā hunaola T o ka mea maʻi (kahi ʻano o ke keʻena pale pale) no laila e hoʻouka lākou i kekahi mau protein i luna o nā hunaola maʻi ʻaʻai. Lawe ʻia nā pūnaewele T mai ka mea maʻi a hoʻohui ʻia nā mea loaʻa kūikawā i kā lākou ʻilikai i ka hale hana. Kapa ʻia nā hunaola i kapa ʻia he chimeric antigen receptor (CAR) nā pūnaewele T. Hoʻonui ʻia nā pūnaewele CAR T i loko o ke keʻena hoʻokolohua a hāʻawi ʻia i ka mea maʻi ma ka hoʻoulu ʻana. Hoʻonui nā ʻāpana CAR T i ke koko o ka mea maʻi a hoʻouka i nā hunaola maʻi ʻaʻai. Ke aʻo ʻia nei ʻo CAR T-cell therapy i ka mālama ʻana i ka sarcoma Ewing hou.

Makemake paha nā mea maʻi e noʻonoʻo e pili ana i ka hoʻokolokolo ʻana.
No kekahi mau mea maʻi, ke komo nei i ka hoʻokolohua hoʻokolohua ke koho lapaʻau maikaʻi loa paha. ʻO nā hoʻokolohua hoʻokolohua kahi ʻāpana o ka noiʻi ʻana o ka maʻi ʻaʻai. Hana ʻia nā hoʻokolohua hoʻokolohua e ʻike inā palekana a maikaʻi a maikaʻi paha nā hoʻomaʻamaʻa maʻi ʻaʻai ma mua o ka maʻamau maʻamau.
ʻO ka hapa nui o nā hana maʻamau no ka maʻi ʻaʻai i kau ʻia ma nā hoʻokolohua hoʻokolohua mua. ʻO nā mea maʻi i komo i ka hoʻokolokolo hoʻokolohua hiki ke loaʻa i ka lāʻau maʻamau a i ʻole i waena o nā mea mua i loaʻa kahi lāʻau hou.
ʻO nā mea maʻi i komo i nā hoʻokolohua hoʻokolohua kōkua pū kekahi i ka hoʻomaikaʻi ʻana i ke ʻano o ka mālama ʻana i ka maʻi ʻaʻai i ka wā e hiki mai ana. ʻOiai ʻaʻole nā alakaʻi hoʻokolohua e alakaʻi i nā hoʻoponopono hou maikaʻi, pane pinepine lākou i nā nīnau nui a kōkua i ka neʻe i mua o ka noiʻi.
Hiki i nā mea maʻi ke komo i nā hoʻokolohua hoʻokolohua ma mua, i ka wā, a ma hope paha o ka hoʻomaka ʻana i kā lākou mālama maʻi ʻaʻai.
Hoʻopili wale kekahi mau hoʻokolohua hoʻokolohua i nā mea maʻi i loaʻa ʻole ka lapaʻau. ʻO nā hoʻokolohua ʻē aʻe e hōʻoia i nā mālama ʻana no ka poʻe maʻi i loaʻa ʻole ka maikaʻi o ka maʻi ʻaʻai. Aia kekahi mau hoʻokolohua hoʻokolohua e hoʻāʻo i nā ala hou e hōʻoki i ka maʻi ʻaʻai mai ka hoʻi hou ʻana (hoʻi ʻana) a hōʻemi paha i nā hopena o ka mālama ʻana i ka maʻi ʻaʻai.
Ke mālama ʻia nei nā hoʻokolohua hoʻokolohua ma nā wahi he nui o ka ʻāina. Hiki ke ʻike ʻia ka ʻike e pili ana i nā hoʻokolohua hoʻokolohua e kākoʻo ʻia e NCI ma ka pūnaewele ʻimi noiʻi hoʻokolohua a NCI. Hiki ke loaʻa nā hoʻokolohua hoʻokolohua i kākoʻo ʻia e nā hui ʻē aʻe ma ka pūnaewele ClinicalTrials.gov.
Pono paha nā hoʻokolohua ukali.
ʻO kekahi o nā hoʻokolohua i hana ʻia e hōʻoia i ka maʻi ʻaʻai a i ʻole e ʻike i ke kahua o ka maʻi ʻaʻaʻa e hana hou ʻia paha. E hana hou ʻia kekahi mau hōʻike i mea e ʻike ai i ka maikaʻi o ka mālama ʻana. Hoʻoholo ʻia nā hoʻoholo e pili ana inā e hoʻomau, hoʻololi, a kū paha i ka lāʻau ʻana ma nā hopena o kēia mau hoʻāʻo.
E hoʻomau ʻia kekahi o nā hoʻokolohua mai kēlā me kēia manawa ma hope o ka pau ʻana o ka lāʻau. Hiki i nā hopena o kēia mau hoʻāʻo ke hōʻike inā ua loli ke ʻano o kāu keiki a i ʻole ua hoʻi hou ke kanesa. Kapa ʻia kēia mau hoʻāʻo i kekahi manawa nā hoʻokolohua ukali a i ʻole nā loiloi.
Nā koho lapaʻau no Ewing Sarcoma
Ma keia Pauku
- Localwed Ewing Sarcoma
- ʻO Metastatic Ewing Sarcoma
- ʻO Ewing Sarcoma hou
No ka ʻike e pili ana i nā lāʻau i helu ʻia ma lalo, e ʻike i ka ʻaoʻao Overtion Option Overview.
Localwed Ewing Sarcoma
ʻO nā mālama maʻamau no ka sarwoma ʻo Ewing i hoʻopaʻa ʻia:
- ʻO Chemotherapy.
- ʻOki kino a me / a i ʻole radiation radiation.
- ʻO ka chemotherapy kiʻekiʻe loa me ka hoʻopakele ʻana o ka cell stem.
E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.
ʻO Metastatic Ewing Sarcoma
ʻO nā maʻamau maʻamau no ka sarasta metastatic Ewing me:
- ʻO Chemotherapy.
- ʻOki kino.
- Lapaʻau hoʻomākala.
E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.
ʻO Ewing Sarcoma hou
ʻAʻohe mālama maʻamau no ka sarcoma Ewing hou akā hiki i nā koho lapaʻau ke hoʻopili ʻia i kēia mau mea:
- Hoʻohui chemotherapy.
- ʻO ka radiation radiation i nā tumors iwi, ma ke ʻano he palliative therapy e hōʻoluʻolu i nā ʻōuli a hoʻomaikaʻi i ka maikaʻi o ke ola.
- ʻO ka radiation radiation e ukali ʻia paha e ka ʻokiʻoki e wehe i nā tumors i palahalaha aʻe i nā ake māmā.
- ʻO ka chemotherapy kiʻekiʻe loa me ka hoʻopakele ʻana o ka cell stem.
Ke aʻo ʻia nei nā koho lapaʻau no ka sarcoma Ewing hou:
- Ke nānā nei i kahi laʻana o ka tumo o ka mea maʻi no kekahi ʻano loli. ʻO ke ʻano o ka hoʻomālama ʻia e hāʻawi ʻia i ka mea maʻi e pili ana i ka ʻano o ka loli.
- Hoʻopaʻa kaulike ʻia me kahi mea hōʻoki kine tyrosine (cabozantinib).
- ʻO Immunotherapy me kahi mea hōʻoki helu pale pale (nivolumab a i ʻole ipilimumab).
- Chimeric antigen receptor (CAR) T-cell therapy.
- Hoʻolālā pahuhopu ʻia me kahi mea hoʻopōkele enzyme NEDD8-activating (pevonedistat) a me chemotherapy.
- ʻO kahi hoʻokolohua hoʻokolohua o kahi ʻano hou o ke ʻano hoʻomōhala hoʻomōhala.
E hoʻohana i kā mākou ʻimi hoʻokolohua hoʻokolohua e ʻike i nā hoʻokolohua hoʻokolohua maʻi maʻi i kākoʻo ʻia e NCI e ʻae nei i nā mea maʻi. Hiki iā ʻoe ke ʻimi i nā hoʻāʻo e pili ana i ke ʻano o ka maʻi ʻaʻai, ka makahiki o ka mea hoʻomanawanui, a kahi e hana ʻia ai nā hoʻokolokolo. Loaʻa nā ʻike laulā e pili ana i nā hoʻokolohua hoʻokolohua.
E aʻo hou aʻe e pili ana iā Ewing Sarcoma
No ka ʻike hou aku mai ka National Cancer Institute e pili ana iā Ewing sarcoma, e ʻike i ka mea aʻe:
- ʻAoʻao Home Kanu iwi
- Computers Tomography (CT) Scans a me ka maʻi ʻaʻai
- ʻO nā Therapy Cancer i kau ʻia
- Kanesa iwi
No ka ʻike hou aku i ka maʻi ʻaʻai kamaliʻi a me nā kumuwaiwai maʻi ʻaʻai ʻē aʻe, e ʻike i ka mea aʻe:
- E pili ana i ka maʻi ʻaʻai
- Nā maʻi ʻōpio
- Huli ʻo Cure no ka hōʻole ʻana i nā maʻi ʻaʻai keiki
- Nā hopena hope loa o ka mālama ʻana no ka maʻi ʻaʻai kamaliʻi
- ʻO nā ʻōpio a me nā ʻōpio me ka maʻi ʻaʻai
- Nā keiki me ka maʻi ʻaʻai: He alakaʻi no nā mākua
- Ka maʻi ʻaʻai ma nā keiki a me nā ʻōpio
- Ke hoʻokū nei
- Ke kāohi nei i ka maʻi ʻaʻai
- Nā nīnau e nīnau ai i kāu kauka e pili ana i ka maʻi ʻaʻai
- No nā mea ola a me nā mea mālama