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Kulawa da Ciwan Tumorin Yara (®) –Patient Version

Janar Bayani Game da umanƙara na Jijiyoyin Yara

MAGANAN MAGANA

  • Orsananan ciwace-ciwacen ƙwayoyin cuta suna fitowa daga ƙwayoyin da ke yin jijiyoyin jini ko na lymph.
  • Ana amfani da gwaje-gwaje don ganowa (gano) da kuma gano ƙananan ƙwayoyin cuta na yara.
  • Ana iya rarraba ƙwayar ƙwayar ƙwayar ƙwayar yara zuwa rukuni huɗu.
  • Ciwan ciwan mara kyau
  • Matsakaici (mai saurin tashin hankali) ciwace-ciwacen
  • Matsakaici (da wuya metastasizing) marurai
  • Mummunan marurai

Orsananan ciwace-ciwacen ƙwayoyin cuta suna fitowa daga ƙwayoyin da ke yin jijiyoyin jini ko na lymph.

Ciwan jijiyoyin jijiyoyin jiki na iya zama daga jijiyoyin jini mara kyau ko kuma ƙwayoyin ruwa na lymph a ko'ina cikin jiki. Suna iya zama marasa lafiya (ba ciwon daji ba) ko masu cutar kansa (kansa). Akwai nau'ikan ciwace na jijiyoyin jini. Mafi yawan nau'in cututtukan jijiyoyin jini na yara shine hemangioma na jarirai, wanda shine mummunan ƙwayar cuta wanda yawanci yakan tafi da kansa.

Saboda ƙananan ƙwayoyin cuta na jijiyoyin jini suna da wuya a yara, babu cikakken bayani game da abin da magani ke aiki mafi kyau.

Ana amfani da gwaje-gwaje don ganowa (gano) da kuma gano ƙananan ƙwayoyin cuta na yara.

Za a iya amfani da waɗannan gwaje-gwajen da hanyoyin:

  • Jarabawa ta jiki da tarihi: Jarabawa ce ta jiki don bincika alamomin lafiya gaba ɗaya, gami da bincika alamun cuta, kamar kumburi, raunuka, ko wani abu da kamar baƙon abu. Za a kuma ɗauki tarihin al'adun lafiyar marasa lafiya da cututtukan da suka gabata da magunguna.
  • Gwajin duban dan tayi: Hanya ce wacce ake fitar da igiyar sauti mai karfi (duban dan tayi) daga kyallen ciki ko gabobin ciki kuma suna yin kuwwa. Eararrawa ta haifar da hoton kayan jikin da ake kira sonogram. Ana iya buga hoton don a kalleshi daga baya.
Ciki duban dan tayi. Ana tura na'urar canzawar duban dan tayi tare da kwamfuta akan fatar ciki. Mai fassarar yana tallata raƙuman sauti daga gabobin ciki da kyallen takarda don yin amo wanda ya samar da sonogram (hoton kwamfuta).
  • CT scan (CAT scan): Hanya ce da ke yin jerin hotuna dalla-dalla na wurare a cikin jiki, waɗanda aka ɗauka daga kusurwa daban-daban. Ana yin hotunan ne ta wata kwamfuta da aka haɗa ta da na'urar da ke ɗauke da x-ray. Ana iya yin allurar fenti a cikin jijiya ko haɗiye don taimakawa gabobin ko kyallen takarda su fito fili karara. Wannan hanya ana kiranta yanayin ƙididdigar lissafi, ƙirar kwamfuta, ko ƙirar ƙwaƙwalwar ajiyar kwamfuta.
Utedididdigar hoto (CT) na ciki. Yaron yana kwance a kan tebur wanda yake zamewa ta cikin na'urar daukar hoto na CT, wanda ke ɗaukar hotunan x-ray na cikin ciki.
  • MRI (hoton maganadisu ): Hanya ce wacce ke amfani da maganadisu, raƙuman rediyo, da kuma kwamfuta don yin jerin hotuna dalla-dalla na wurare a cikin jiki. Wannan hanya ana kiranta kuma ana kiranta hoton maganadisu na maganadisu (NMRI).
Hanyoyin fuska ta maganadisu (MRI) na ciki. Yaron yana kwance a kan tebur wanda yake zamewa cikin sikanin MRI, wanda ke ɗaukar hotunan cikin jiki. Kushin da ke jikin yaron yana taimaka wajan bayyana hotunan a bayyane.
  • Biopsy: Cirewar ƙwayoyin halitta ko kyallen takarda don a iya kallon su ta hanyar microscope ta hanyar masanin ilimin ɗan adam don bincika alamun kansar. Ba koyaushe ake bukatar kwayar halitta ba don tantance cututtukan ƙwayar jijiyoyin jini.

Ana iya rarraba ƙwayar ƙwayar ƙwayar ƙwayar yara zuwa rukuni huɗu.

Ciwan ciwan mara kyau

Tumananan ƙwayoyin cuta ba ciwon daji ba ne. Wannan taƙaitaccen bayani yana da bayanai game da ciwace-ciwacen ƙwayoyin cuta masu zuwa:

  • Hanngioma mai haihuwa.
  • Haihuwar hemangioma.
  • Ciwon daji na jijiyoyin hanta.
  • Spindle cell hemangioma.
  • Hanngioma na epithelioid.
  • Pyogenic granuloma (hemangioma mai tsaka-tsalle).
  • Angiofibroma.
  • Yaran yara nasopharyngeal angiofibroma.

Matsakaici (mai saurin tashin hankali) ciwace-ciwacen

Matsakaicin ciwace-ciwacen daji waɗanda ke da saurin rikici a cikin gida sukan yada zuwa yankin da kewayen kumburin. Wannan taƙaitaccen bayanin yana da bayanai game da ƙananan ƙwayoyin cuta na cikin gida masu zuwa:

  • Kaposiform hemangioendothelioma da tufted angioma.

Matsakaici (da wuya metastasizing) marurai

Matsakaici (ƙarancin metastasizing) ciwace-ciwacen wani lokaci yakan bazu zuwa wasu sassan jiki. Wannan taƙaitaccen bayanin yana da bayanai game da ciwace-ciwacen ƙwayoyin jijiyoyin da ke tafe wanda ba safai ya dace da su ba:

  • Hanyoyin cutar shan inna na hemangioendothelioma.
  • Ifaukewar maganin hemangioendothelioma.
  • Papillary intralymphatic angioendothelioma.
  • Hadaddiyar hemangioendothelioma.
  • Kaposi sarcoma.

Mummunan marurai

Mummunan ciwace ciwace. Wannan taƙaitaccen bayani yana da bayanai game da cututtukan ƙwayar jijiyoyin jini masu zuwa:

  • Epithelioid hemangioendothelioma.
  • Angiosarcoma na nama mai laushi.

Bayanin Zaɓin Jiyya

MAGANAN MAGANA

  • Akwai nau'ikan magani daban-daban na ciwan yara na jijiyoyin jini.
  • Yaran da ke da cututtukan jijiyoyin jijiyoyin yara ya kamata a shirya maganin su ta hanyar ƙungiyar masu ba da sabis na kiwon lafiya waɗanda ƙwararru ne wajen kula da cutar kansa a cikin yara.
  • Jiyya don ciwace-ciwacen ƙwayoyin yara na iya haifar da illa.
  • Ana amfani da nau'i goma na daidaitaccen magani:
  • Beta-toshe far
  • Tiyata
  • Photocoagulation
  • Haɓakawa
  • Chemotherapy
  • Sclerotherapy
  • Radiation far
  • Ciwon da aka yi niyya
  • Immunotherapy
  • Sauran maganin magani
  • Lura
  • Ana gwada sababbin nau'ikan magani a gwajin asibiti.
  • Marasa lafiya na iya son yin tunani game da shiga cikin gwaji na asibiti.
  • Marasa lafiya na iya shiga gwajin asibiti kafin, lokacin, ko bayan fara maganin cutar kansa.
  • Ana iya buƙatar gwaje-gwaje na gaba.

Akwai nau'ikan magani daban-daban na ciwan yara na jijiyoyin jini.

Akwai nau'ikan magani daban-daban ga yara masu fama da jijiyoyin jini. Wasu jiyya suna daidaito (magani da ake amfani dashi yanzu), kuma wasu ana gwada su a gwajin asibiti. Gwajin gwajin magani shine binciken bincike wanda ake nufi don taimakawa inganta ingantattun jiyya na yanzu ko samun bayanai akan sabbin jiyya. Lokacin da gwaji na asibiti ya nuna cewa sabon magani ya fi magani na yau da kullun, sabon magani na iya zama daidaitaccen magani.

Saboda cututtukan ƙwayar jijiyoyin jini a cikin yara ba safai ba, ya kamata a yi la'akari da shiga cikin gwajin asibiti. Wasu gwaji na asibiti ana buɗe su ne kawai ga marasa lafiyar da basu fara magani ba.

Yaran da ke da cututtukan jijiyoyin jijiyoyin yara ya kamata a shirya maganin su ta hanyar ƙungiyar masu ba da sabis na kiwon lafiya waɗanda ƙwararru ne wajen kula da cutar kansa a cikin yara.

Jiyya za ta kula da likitan ilimin likitan yara, likita wanda ya kware kan kula da yara masu cutar kansa. Masanin ilimin likitancin yara yana aiki tare da wasu masu ba da kula da lafiya na yara waɗanda ƙwararru ne wajen kula da yara da ke fama da cutar kansa kuma waɗanda suka ƙware a wasu fannonin magani. Wadannan na iya hada da kwararru masu zuwa:

  • Kwararren likitan yara game da cututtukan jini (masani ne wajen kula da yara masu ciwan jijiyoyin jini).
  • Likitan likitan yara.
  • Likitan Orthopedic.
  • Radiation oncologist
  • Kwararren likitan yara.
  • Gwanayen gyarawa.
  • Masanin ilimin psychologist.
  • Ma'aikacin zamantakewa.

Jiyya don ciwace-ciwacen ƙwayoyin yara na iya haifar da illa.

Don bayani game da illolin da ke farawa yayin magani don cutar kansa, duba shafin Gurbinmu.

Wasu jiyya, kamar su chemotherapy da radiation, suna haifar da illolin da ke ci gaba ko bayyana watanni ko shekaru bayan jiyya ya ƙare. Waɗannan ana kiransu ƙarshen sakamako. Sakamakon sakamako na ƙarshe na iya haɗa da masu zuwa:

  • Matsalolin jiki.
  • Canje-canje a cikin yanayi, ji, tunani, ilmantarwa, ko ƙwaƙwalwar ajiya.
  • Cancer na biyu (sababbin nau'ikan cutar kansa).

Wasu maganganun ƙarshen ana iya magance su ko sarrafa su. Yana da mahimmanci a yi magana da likitocin ɗanka game da yiwuwar ƙarshen cututtukan da wasu jiyya suka haifar. (Dubi taƙaitaccen bayanin akan ƙarshen tasirin Jiyya don Ciwon Childhoodan yara don ƙarin bayani).

Ana amfani da nau'i goma na daidaitaccen magani:

Beta-toshe far

Beta-blockers magunguna ne masu rage karfin jini da bugun zuciya. Lokacin amfani da marasa lafiya da cututtukan jijiyoyin jini, beta-blockers na iya taimakawa rage jijiyoyin. Beta-blocker far na iya bayarwa ta jijiya (IV), da baki, ko sanya shi a kan fata (Topical). Hanyar da ake ba da maganin beta-blocker ya dogara da nau'in ciwace-ciwacen ƙwayoyin cuta da kuma inda ƙari ya fara samuwa.

Beta-blocker propranolol yawanci shine magani na farko don hemangiomas. Yaran da aka yiwa jiyya tare da IV propranolol na iya buƙatar fara maganin su a asibiti. Ana amfani da Propranolol don magance ƙwayar ƙwayar ƙwayar ƙwayar hanta da kaposiform hemangioendothelioma.

Sauran beta-blockers da ake amfani dasu don magance cututtukan jijiyoyin jini sun hada da atenolol, nadolol, da timolol.

Hakanan za'a iya kula da hemangioma na jarirai tare da maganin propranolol da steroid ko kuma propranolol da maganin beta-blocker na asali.

Dubi taƙaitaccen bayanin magungunan ƙwayoyi akan Propranolol Hydrochloride don ƙarin bayani.

Tiyata

Za'a iya amfani da nau'ikan tiyata masu zuwa don cire nau'ikan ciwace ciwace da jijiyoyin jini:

  • Exision: Tiyata don cire duka ƙwayar cuta da kuma wasu lafiyayyun nama kusa da shi.
  • Yin tiyatar Laser: Tsarin tiyata ne wanda ke amfani da katako na laser (ƙuntataccen katako na haske mai ƙarfi) a matsayin wuƙa don yin yankewar jini a cikin nama ko cire raunin fata kamar ƙari. Ana iya amfani da tiyata tare da laser fenti mai laushi don wasu cututtukan hemangiomas. Irin wannan laser yana amfani da katako na haske wanda yake kaiwa ga jini a cikin fata. Hasken ya canza zuwa zafi kuma an lalata jijiyoyin jini ba tare da lalata fatar da ke kusa ba.
  • Curettage: Hanya ce wacce ake cire tsoffin nama ta amfani da ƙaramin abu mai siffar cokali wanda ake kira curette.
  • Jimlar hepatectomy da dashen hanta: Hanyar tiyata ce wacce za a cire dukkanin hanta daga nan kuma a samu dashen hanta mai lafiya daga mai bayarwa.

Nau'in aikin tiyatar da aka yi amfani da shi ya dogara da nau'in ƙwayar jijiyoyin bugun jini da kuma inda ƙari ya zama cikin jiki.

Ga cututtukan ciwace-ciwace, bayan likita ya cire duk cutar daji da za a iya gani a lokacin tiyatar, wasu marasa lafiya za a iya ba da ilimin sanƙarau ko kuma fitilar radiation bayan tiyata don kashe duk ƙwayoyin cutar kansa da suka rage. Maganin da ake bayarwa bayan tiyatar, don rage haɗarin kamuwa da cutar kansa zai dawo, ana kiran sa adjuvant therapy.

Photocoagulation

Photocoagulation shine amfani da katako mai haske, kamar laser, don rufe magudanan jini ko lalata nama. Ana amfani dashi don magance granuloma pyogenic.

Haɓakawa

Embolization hanya ce wacce take amfani da barbashi, kamar ƙananan gelatin sponges ko beads, don toshe hanyoyin jini a hanta. Ana iya amfani dashi don magance wasu cututtukan hanji na hanta da kaposiform hemangioendothelioma.

Chemotherapy

Chemotherapy magani ne wanda ke amfani da kwayoyi don dakatar da haɓakar ƙwayoyin tumo, ko dai ta hanyar kashe ƙwayoyin ko ta hana su rarraba. Akwai hanyoyi daban-daban don ba da cutar sankara:

  • Chemotherapy na systemic: Lokacin da aka ɗauki chemotherapy ta baki ko allura a cikin jijiya ko tsoka, magungunan suna shiga cikin jini kuma suna iya isa ƙwayoyin ƙari a cikin jiki. Wani lokaci ana bada fiye da ɗaya maganin na sankarau. Wannan shi ake kira hade chemotherapy.
  • Topical chemotherapy: Idan ana amfani da chemotherapy ga fata a cikin cream ko shafa fuska, magungunan sun fi shafar ƙwayoyin ƙari a cikin yankin da aka kula.
  • Chemaramar ƙwaƙwalwar yanki: Lokacin da aka sanya chemotherapy kai tsaye zuwa cikin ruwa mai ruɓar ciki, gaɓoɓi, ko rami na jiki kamar ciki, magungunan sun fi shafar ƙwayoyin ƙari a waɗancan yankuna.

Hanyar da ake ba da magani na chemotherapy ya dogara da nau'in ciwon ƙwayar jijiyoyin da ake kula da su. Ana amfani da tsarin jiji da jiki don magance wasu cututtukan jijiyoyin jini.

Sclerotherapy

Sclerotherapy magani ne da ake amfani dashi don lalata jijiyoyin jini wanda yake kaiwa ga ƙari da ƙari. An saka wani ruwa a cikin jijiyoyin jini, wanda hakan ya haifar masa da tabo kuma ya karye. A tsawon lokaci, lalataccen jirgin jini yana shiga cikin nama na al'ada. Jinin yana gudana ta cikin jijiyoyin lafiya na kusa. Sclerotherapy ana amfani dashi don maganin epithelioid hemangioma.

Radiation far

Radiation far wani magani ne wanda ke amfani da hasken rana mai ƙarfi ko wasu nau'ikan radiation don kashe ƙwayoyin tumo ko hana su girma. Akwai nau'o'in maganin radiation guda biyu:

  • Magungunan radiation na waje yana amfani da inji a waje da jiki don aika radiation zuwa ƙari.
  • Magungunan radiation na ciki yana amfani da abu mai tasirin rediyo wanda aka rufe a cikin allurai, tsaba, wayoyi, ko catheters waɗanda aka sanya kai tsaye zuwa ko kusa da ƙari.

Hanyar da aka ba da maganin taɗɗar radiation ya dogara da nau'in ciwon ƙwayar jijiyoyin da ake kula da su. Ana amfani da radiation na waje don magance wasu cututtukan jijiyoyin jini.

Ciwon da aka yi niyya

Targeted therapy wani nau'in magani ne wanda yake amfani da magunguna ko wasu abubuwa don afkawa wasu ƙwayoyin ƙari. Ieswararrun hanyoyin kwantar da hankali yawanci suna haifar da toarancin cutarwa ga kwayoyin al'ada fiye da chemotherapy ko maganin radiation. Ana amfani da nau'ikan maganin farfadowa daban-daban da aka yi niyya don nazarin cututtukan ƙwayar jijiyoyin ƙuruciya:

  • Masu hana Angiogenesis: Magunguna masu hana angiogenesis magunguna ne da suke dakatar da ƙwayoyin halitta daga rarrabawa da hana haɓakar sabbin jijiyoyin jini waɗanda ciwace-ciwacen ya kamata su girma. Magungunan maganin da aka yi niyya thalidomide, sorafenib, pazopanib, da sirolimus sune masu hana maganin angiogenesis da ake amfani dasu don magance ciwace-ciwace na ƙananan yara.
  • Manufar Mammalian na masu hana rapamycin (mTOR): masu hana mTOR suna toshe furotin da ake kira mTOR, wanda zai iya hana ƙwayoyin cutar kansa girma da kuma hana haɓakar sabbin jijiyoyin jini waɗanda ciwace-ciwacen ya kamata su girma.
  • Masu hana Kinase: Masu hana Kinase suna toshe siginonin da ake buƙata don ciwace-ciwacen girma. Ana nazarin Trametinib don magance epithelioid hemangioendothelioma.

Immunotherapy

Immunotherapy magani ne wanda ke amfani da garkuwar jikin mara lafiya don yaƙar cuta. Abubuwan da jiki ya yi ko aka yi a dakin gwaje-gwaje ana amfani da su don haɓaka, kai tsaye, ko dawo da kariya ta jiki daga cuta.

Ana amfani da nau'ikan rigakafin rigakafi don magance cututtukan yara na jijiyoyin jini:

  • Interferon wani nau'in rigakafi ne wanda ake amfani dashi don magance ciwace-ciwace na ƙananan yara. Yana tsangwama tare da rarrabuwar ƙwayoyin ƙwayoyin cuta kuma yana iya rage ci gaban ƙari. Ana amfani dashi wajen maganin yara nasopharyngeal angiofibroma, kaposiform hemangioendothelioma, da epithelioid hemangioendothelioma.
  • Maganin hana shiga ciki na kariya: Wasu nau'ikan kwayoyin rigakafi, kamar su kwayoyin T, da wasu kwayoyin cutar kansa suna da wasu sunadarai, wadanda ake kira sunadarin shinge, a saman su wanda ke kiyaye amsoshin rigakafin a duba. Lokacin da ƙwayoyin daji ke da yawancin waɗannan sunadaran, ƙwayoyin T ba za su auka musu ba. Masu hana abubuwan hana ruwa kariya suna toshe wadannan sunadaran kuma karfin kwayar T don kashe kwayoyin cutar kansa ya karu.

Akwai nau'ikan maganin hana hana ruwa guda biyu na kariya:

  • Mai hana CTLA-4: CTLA-4 furotin ne akan saman ƙwayoyin T wanda ke taimakawa ci gaba da ba da kariya ga jiki. Lokacin da CTLA-4 ke haɗuwa da wani furotin da ake kira B7 akan kwayar cutar kansa, yana dakatar da kwayar T daga kashe kwayar cutar kansa. Masu hana CTLA-4 sun haɗa zuwa CTLA-4 kuma suna ba da ƙwayoyin T damar kashe ƙwayoyin kansa. Ipilimumab wani nau'in mai hana CTLA-4 ne wanda ake nazarin shi a cikin maganin angiosarcoma na nama mai laushi.
Mai hana shigowar shinge Abubuwan bincike, kamar B7-1 / B7-2 akan ƙwayoyin gabatarwa na antigen (APC) da CTLA-4 akan ƙwayoyin T, suna taimakawa kiyaye maganganun garkuwar jiki a cikin bincike. Lokacin da mai karɓar T-cell (TCR) ke ɗaure ga antigen da kuma manyan sunadarai masu rikitarwa na tarihi (MHC) akan APC da CD28 suna ɗaure zuwa B7-1 / B7-2 akan APC, ana iya kunna T cell. Koyaya, ɗaura B7-1 / B7-2 zuwa CTLA-4 yana riƙe da ƙwayoyin T a cikin yanayin aiki saboda haka basu sami ikon kashe ƙwayoyin ƙari a cikin jiki (ɓangaren hagu). Katange ɗaurin B7-1 / B7-2 zuwa CTLA-4 tare da mai hana kariya na kariya (anti-CTLA-4 antibody) yana ba da damar ƙwayoyin T suyi aiki kuma su kashe ƙwayoyin tumo (ɓangaren dama).
  • Mai hana PD-1: PD-1 furotin ne akan saman ƙwayoyin T wanda ke taimakawa ci gaba da ba da kariya ga jiki. Lokacin da PD-1 ke haɗuwa da wani furotin da ake kira PDL-1 akan kwayar sankara, yakan dakatar da kwayar T daga kashe kwayar cutar kansa. Masu hana PD-1 sun haɗa zuwa PDL-1 kuma suna ba da ƙwayoyin T damar kashe ƙwayoyin kansa. Nivolumab wani nau'in mai hanawa PD-1 ne wanda ake nazarinsa a cikin maganin angiosarcoma na kayan laushi.
Mai hana shigowar shinge Binciken sunadarai, kamar PD-L1 akan ƙwayoyin tumo da PD-1 akan ƙwayoyin T, suna taimakawa kiyaye maganganun rigakafi a cikin bincike. Ofaurin PD-L1 zuwa PD-1 yana kiyaye ƙwayoyin T daga kashe ƙwayoyin tumo a jiki (ɓangaren hagu). Katange ɗaurin PD-L1 zuwa PD-1 tare da mai hana kariya na kariya (anti-PD-L1 ko anti-PD-1) yana ba wa ƙwayoyin T damar kashe ƙwayoyin tumor (ɓangaren dama)

Sauran maganin magani

Sauran kwayoyi da ake amfani dasu don magance cututtukan yara na jijiyoyin jini ko sarrafa tasirin su sun haɗa da masu zuwa:

  • Magungunan steroid: Steroids sune hormones da aka yi dasu cikin jiki. Hakanan za'a iya yin su a dakin gwaje-gwaje kuma amfani dasu azaman magunguna. Magungunan steroid suna taimakawa rage wasu cututtukan jijiyoyin jini. Corticosteroids, kamar prednisone da methylprednisolone, ana amfani dasu don magance hemangioma na jarirai.
  • Magungunan anti-inflammatory marasa steroidal (NSAIDs): Ana amfani da NSAIDs don rage zazzaɓi, kumburi, zafi, da kuma ja. Misalan NSAIDs sune asfirin, ibuprofen, da naproxen. A cikin maganin cututtukan jijiyoyin jini, NSAIDs na iya ƙara yawan jini ta cikin ƙwayoyin cuta kuma ya rage damar da jini mara ƙyashi zai samu.
  • Antifibrinolytic far: Wadannan kwayoyi suna taimaka wa jini a cikin marassa lafiyar da ke da cutar Kasabach-Merritt. Fibrin shine babban furotin a cikin daskarewar jini wanda ke taimakawa tsayar da zubar jini da kuma warkar da raunuka. Wasu ciwace-ciwace na jijiyoyin jini suna sanya fibrin ya karye kuma jinin mara lafiya baya tabuwa kullum, yana haifar da zub da jini ba bisa ka'ida ba. Antifibrinolytics yana taimakawa hana raunin fibrin.

Lura

Lura yana lura da yanayin mai haƙuri ba tare da ba da magani ba har sai alamu ko alamu sun bayyana ko canzawa.

Ana gwada sababbin nau'ikan magani a gwajin asibiti.

Ana samun bayani game da gwaji na asibiti daga gidan yanar gizon NCI.

Marasa lafiya na iya son yin tunani game da shiga cikin gwaji na asibiti.

Ga wasu marasa lafiya, shiga cikin gwaji na asibiti na iya zama mafi kyawun zaɓin magani. Gwajin gwaji na daga cikin tsarin bincike. Ana yin gwaje-gwajen asibiti don gano idan sababbin jiyya suna da lafiya da tasiri ko sun fi magani mai kyau.

Yawancin magungunan yau da kullun suna dogara ne akan gwajin asibiti na farko. Marasa lafiya da ke cikin gwaji na asibiti na iya karɓar daidaitaccen magani ko kuma su kasance cikin farkon waɗanda za su karɓi sabon magani.

Marasa lafiya da ke shiga cikin gwaji na asibiti suma suna taimakawa inganta yadda za a magance cutar nan gaba. Koda lokacin gwajin asibiti bai haifar da sababbin magunguna ba, sau da yawa sukan amsa mahimman tambayoyi kuma suna taimakawa ci gaba da bincike gaba.

Marasa lafiya na iya shiga gwajin asibiti kafin, lokacin, ko bayan fara maganin cutar kansa.

Wasu gwaji na asibiti kawai sun haɗa da marasa lafiya waɗanda ba su sami magani ba tukuna. Sauran gwaje-gwajen suna gwada jiyya ga marasa lafiya waɗanda ciwace-ciwacensu ba su sami sauki ba. Har ila yau, akwai gwaje-gwaje na asibiti waɗanda ke gwada sababbin hanyoyi don dakatar da ciwace-ciwace daga sake dawowa (dawowa) ko rage tasirin maganin.

Gwajin gwaji na gudana a sassa da yawa na ƙasar. Bayani game da gwajin asibiti wanda NCI ke tallafawa ana iya samun shi akan shafin binciken gwaji na NCI. Ana iya samun gwajin gwaji na asibiti wanda wasu kungiyoyi ke tallafawa akan gidan yanar gizon ClinicalTrials.gov.

Ana iya buƙatar gwaje-gwaje na gaba.

Za'a iya maimaita wasu gwaje-gwajen da aka yi don gano ƙwayar ƙwayar jijiyoyin jini. Za a maimaita wasu gwaje-gwaje don ganin yadda magani ke aiki. Shawarwari game da ci gaba, canji, ko dakatar da magani na iya dogara ne da sakamakon waɗannan gwaje-gwajen.

Wasu daga cikin gwaje-gwajen za a ci gaba da yi daga lokaci zuwa lokaci bayan an gama jiyya. Sakamakon waɗannan gwaje-gwajen na iya nuna idan yanayin ɗanku ya canza ko kuma idan ƙari ya sake dawowa (dawo). Wadannan gwaje-gwajen wasu lokuta ana kiran su gwaje-gwaje na gaba ko dubawa.

Ignananan ƙwayoyi

A Wannan Sashin

  • Hemangioma mai haihuwa
  • Hanyar Hemangioma
  • Ignananan ƙwayoyin cuta na ƙwayar hanta
  • Spindle Cell Hemangioma
  • Hemangioma na Epithelioid
  • Granuloma na Pyogenic
  • Angiofibroma
  • Yara Nasopharyngeal Angiofibroma

Don bayani game da jiyya da aka jera a ƙasa, duba sashin Kula da Zaɓin Jiyya.

Hemangioma mai haihuwa

Hemangiomas na yara shine mafi yawan nau'in ƙwayar ƙwayar ƙwayar ƙwayar cuta a cikin yara. Harshen hemangiomas na yara yana samuwa lokacin da ƙwayoyin da ba su balaga ba waɗanda ake nufi don samar da jijiyoyin jini su zama ƙari a maimakon. Hakanan za'a iya kiran hemangioma na jarirai "alamar strawberry."

Wadannan cututtukan ba kasafai ake ganinsu lokacin haihuwa ba amma suna bayyana lokacin da jaririn ya kasance makonni 3 zuwa 6. Yawancin hemangiomas suna girma kusan na tsawon watanni 5 sannan su daina girma. Hanngiomasmas yana shudewa sannu a hankali a cikin shekaru masu zuwa, amma alamar ja ko sakakkiyar fata ko fata. Yana da wuya jaririn hemangioma ya dawo.

Hemangiomas na yara na iya kasancewa a kan fata, a cikin ƙwayar da ke ƙasan fata, da / ko a cikin wani sashin jiki. Yawancin lokaci suna kan kai da wuya amma suna iya kasancewa ko'ina ko a jiki. Hemangiomas na iya bayyana azaman rauni ɗaya, raunuka ɗaya ko fiye da ke yaɗu a wani ɓangaren jiki mafi girma, ko kuma raunin da yawa a cikin fiye da ɗaya ɓangaren jiki. Raunukan da suka bazu a wani yanki mafi girma na jiki ko raunin da yawa na iya haifar da matsala.

Hemangioma na ciki tare da ƙarami ko ci gaban da aka kama (IH-MAG) wani nau'in ƙwayar hanta ce ta yara da ake gani lokacin haihuwa kuma ba ta da girmanta. Raunin ya bayyana a matsayin haske da wuraren duhu na ja a cikin fata. Raunukan yawanci akan ƙananan jiki amma suna iya kasancewa a kai da wuya. Hemangiomas na wannan nau'in yana wucewa ba tare da magani ba.

Dalilin Hadarin

Duk wani abu da zai kara maka hadarin kamuwa da cuta to ana kiran sa mai hadari. Samun haɗarin haɗari ba yana nufin cewa za ku kamu da cutar ba; ba tare da haɗarin halayen haɗari ba yana nufin cewa ba za ku kamu da cutar ba. Yi magana da likitan ɗanka idan kana tunanin ɗanka na cikin haɗari.

Hannen ciki na yara ya fi yawa a cikin masu zuwa:

  • 'Yan mata.
  • Fari.
  • Yara da wuri.
  • Tagwaye, ‘yan uku, ko wasu haihuwar da yawa.
  • Yaran uwaye waɗanda suka girmi lokacin ciki ko kuma waɗanda ke da matsala tare da mahaifa yayin ɗaukar ciki.

Sauran abubuwan haɗarin haɗarin hemangiomas na yara sun haɗa da masu zuwa:

  • Samun tarihin iyali na yara hemangioma, yawanci a cikin uwa, uba, 'yar'uwa, ko ɗan'uwa.
  • Samun wasu cututtukan cuta.
  • Cutar ciwo ta PHACE: Ciwo ne wanda hemangioma ke yaduwa a cikin babban sashin jiki (yawanci kai ko fuska). Sauran matsalolin lafiya waɗanda suka shafi manyan jijiyoyin jini, zuciya, idanu, da / ko kwakwalwa na iya faruwa.
  • LUMBAR / PELVIS / SACRAL syndrome: Ciwon kansa wanda hemangioma ya bazu a cikin babban yanki na ƙananan baya. Sauran matsalolin kiwon lafiyar da suka shafi tsarin fitsari, al'aura, dubura, dubura, kwakwalwa, laka, da jijiyoyin na iya faruwa.

Samun hemangioma fiye da ɗaya ko hanyar iska ko hawan jini na ido yana ƙara haɗarin samun wasu matsalolin lafiya.

  • Hewayar hemangiomas: Ciwon sama da biyar a jikin fata alama ce ta cewa akwai yiwuwar samun jini a cikin gaɓaɓɓu. Hantar hanta tana yawan tasiri. Hakanan matsalolin zuciya, tsoka, da matsalolin glandar na iya faruwa.
  • Hemanggiomas na Airway: Hemangiomas a cikin hanyar iska yawanci yakan faru tare da babban, yanki mai fasalin gemu na hemangioma a fuska (daga kunnuwa, kusa da bakin, ƙasan ƙugu, da gaban wuya). Yana da mahimmanci ayi maganin hemangiomas na iska kafin yaron ya sami matsalar numfashi.
  • Hanngiomas na ido: Hemangiomas wanda ya shafi ido na iya haifar da matsalolin gani ko makanta. Hemangiomas na yara na iya faruwa a cikin haɗin mahaifa (membrane wanda yake layin farfajiyar fatar ido ya rufe ɓangaren ido). Wadannan hemangiomas na iya zama alaƙa da wasu yanayin mahaukaci na ido. Yana da mahimmanci yara da ke da cutar hemangioma ta ophthalmologist suna duba su ta hanyar likitan ido.

Alamomi da Ciwon

Hanngioman na yara na iya haifar da ɗayan waɗannan alamun da alamomi masu zuwa. Binciki likitan ɗanka idan ɗanka yana da ɗayan masu zuwa:

  • Raunin fata: Yankin jijiyoyin fata ko walƙiya ko canza launin fata na iya bayyana kafin ciwon hanta ya fara. Hemangiomas na faruwa a matsayin tabbatacce, dumi, mai haske ja zuwa raunin Crimson a fata ko kuma yayi kama da rauni. Raunin da ke haifar da ulce shima ciwo ne. Daga baya, yayin da hemangiomas ke tafiya, suna fara dusashewa a cikin tsakiyar kafin su daidaita da kuma rasa launi.
  • Raunin da ke ƙasa da fata: Raunin da ke girma a ƙarƙashin fata a cikin kitse na iya bayyana kamar shuɗi ko shunayya. Idan raunuka suna da zurfin zurfin zurfin fata, ƙila ba za a gansu ba.
  • Raunuka a cikin gaɓaɓɓu: Babu alamun alamun cutar hemangiomas ta samo a kan gaɓa.

Kodayake mafi yawan cututtukan hemangiomas ba abin damuwa bane, idan ɗanka ya sami wani kumburi ko ja ko alama mai alama akan fata tare da likitan ɗanka. Shi ko ita na iya tura ɗan zuwa ga gwani idan an buƙata.

Gwajin gwaji

Jarabawa ta jiki da tarihi yawanci duk abin da ake buƙata ne don gano ƙananan cututtukan jini. Idan akwai wani abu game da ciwon da yake baƙon abu, ana iya yin biopsy. Idan hemangioma ya fi zurfin ciki ba tare da canjin fata ba, ko raunuka suna yaɗu a cikin babban ɓangaren jiki, ana iya yin duban dan tayi. Dubi Babban Bayanin Bayani don bayanin waɗannan gwaje-gwajen da hanyoyin.

Idan hemangiomas wani ɓangare ne na ciwo, za a iya yin ƙarin gwaje-gwaje, kamar su echocardiogram, MRI, maganadisu mai saurin haɗi, da gwajin ido.

Jiyya

Yawancin hemangiomas suna shudewa kuma suna raguwa ba tare da magani ba. Idan hemangioma babba ne ko kuma haifar da wasu matsalolin lafiya, magani na iya haɗawa da masu zuwa:

  • Propranolol ko wani maganin beta-shafi.
  • Magungunan steroid, kafin fara beta-blocker far ko lokacin da baza'a iya amfani da beta-blockers ba.
  • Yin tiyatar fenti mai laushi, don hemangiomas wanda ke da marurai ko kuma bai gama ba.
  • Yin tiyata (cirewa) don cutar hemangiomas waɗanda ke da miki, suna haifar da matsalolin gani, ko kuma ba su tafi gaba ɗaya ba. Hakanan za'a iya amfani da tiyata don raunuka a fuska waɗanda ba sa amsa wani magani.
  • Magungunan beta-shafi na maganin cututtukan hemangiomas waɗanda ke cikin yanki ɗaya na fata.
  • Haɗaɗɗiyar farfajiya, kamar su propranolol da cututtukan steroid ko propranolol da maganin beta-blocker na asali.
  • Gwajin gwaji na maganin beta-blocker (nadolol da propranolol).
  • Gwajin gwaji na maganin beta-blocker na asali (timolol).

Hanyar Hemangioma

Cutar hemangioma na ciki wata cuta ce mai illa ta jiki wanda ke farawa tun kafin a haife shi kuma yana samun cikakkiyar halitta lokacin da aka haifi jariri. Yawancin lokaci suna kan fata amma suna iya zama a cikin wani sashin jiki. Hanngioma na haihuwa na iya faruwa a matsayin ƙuƙumi na ɗigon ruwan hoda kuma fatar da ke kewaye da tabo na iya zama wuta.

Akwai nau'ikan nau'ikan cututtukan jini guda uku:

  • Hanngioma mai saurin haihuwa: Waɗannan ciwace-ciwacen suna tafi da kansu watanni 12 zuwa 15 bayan haihuwa. Zasu iya haifar da ulce, zub da jini, da haifar da matsala ta wucin gadi da daskarewar jini. Fata na iya zama ɗan ɗan bambanci ko da bayan ciwon hanta ya tafi.
  • Hanngioma mai saurin shiga ciki: Waɗannan ciwace-ciwacen ba sa tafi gaba ɗaya.
  • Hanngioma na rashin haihuwa: Waɗannan ciwace-ciwacen ba sa taɓa tafiya da kansu.

Gwajin gwaji

Dubi Babban Bayanin Bayani don bayanin gwaje-gwajen da hanyoyin, kamar su duban dan tayi, wanda ake amfani da shi don bincikar cututtukan hemangioma.

Jiyya

Jiyya cikin hanzari na haifar da hemangioma da ƙananan hanta na haihuwa na iya haɗawa da masu zuwa:

  • Lura kawai.

Jiyya na cututtukan hemangioma mara haɗuwa na iya haɗawa da masu zuwa:

  • Yin aikin tiyata don cire kumburin, ya danganta da inda yake da kuma ko yana haifar da alamun.

Ignananan ƙwayoyin cuta na ƙwayar hanta

Tumananan ƙwayoyin hanta na hanta na iya zama raunin jijiyoyin jijiyoyin jiki (rauni guda a wani yanki na hanta), raunin hanta da yawa (raunuka da yawa a wani yanki na hanta), ko kuma yaduwar cutar hanta (raunuka da yawa a fiye da yanki ɗaya na hanta).

Hanta yana da ayyuka da yawa, gami da tace jini da kuma samar da sunadarai da ake buƙata don haɗa jini. Wani lokaci, jinin da ke gudana ta hanta yakan toshe ko kuma jinkirin da ƙari. Wannan yana aika jini kai tsaye zuwa zuciya ba tare da shiga cikin hanta ba kuma ana kiransa hanta shunt. Wannan na iya haifar da gazawar zuciya da matsaloli tare da daskarewar jini.

Raunin jijiyoyin jijiyoyin jiki

Raunin jijiyoyin jijiyoyin jiki yawanci hanzari ne ke haifar da cutar hemangiomas ko kuma rashin saurin haihuwa.

Gwajin gwaji

Dubi Babban Bayanin Bayani don bayanin gwaje-gwaje da hanyoyin da aka yi amfani da su don gano cututtukan hanta na hanta.

Jiyya

Yin jiyya na cututtukan hanta na hanta ya dogara ne akan ko alamun bayyanar suna faruwa kuma zai iya haɗa da masu zuwa:

  • Lura.
  • Magunguna don magance alamomin, gami da ciwan zuciya da matsalolin daskarewar jini.
  • Sanya hanta don magance alamomin.
  • Yin aikin tiyata, don raunin da bai amsa wani magani ba.

Yawa da Rarraba Raunin Hanta

Raunuka masu yawa da yaduwa na hanta yawanci hemangiomas jariri ne. Yaduwar cutar hanta na iya haifar da mummunan sakamako, gami da matsaloli tare da glandar thyroid da zuciya. Hantar ciki na iya faɗaɗa, danna kan wasu gabobin, kuma yana haifar da ƙarin alamun cuta.

Gwajin gwaji

Dubi Babban Bayanin Bayani don bayanin gwaje-gwaje da hanyoyin da aka yi amfani da su don gano ƙwayoyin cuta da yawa ko kuma yaɗuwa.

Jiyya

Jiyya na cututtukan hanta da yawa na iya haɗa da masu zuwa:

  • Lura don raunin da baya haifar da alamu.
  • Beta-blocker far (propranolol) don raunin da ya fara girma.

Jiyya na yaduwar cututtukan hanta na iya haɗa da masu zuwa:

  • Maganin Beta-blocker (propranolol).
  • Chemotherapy.
  • Steroid far.
  • Total hepatectomy da dasawa na hanta, lokacin da raunuka basu amsa maganin magani ba. Ana yin wannan kawai lokacin da raunuka suka bazu a cikin hanta kuma fiye da ɗaya sashin jiki ya gaza.

Idan rauni na jijiyoyin hanta bai amsa magani na yau da kullun ba, ana iya yin biopsy don ganin ko kumburin ya zama m.

Spindle Cell Hemangioma

Spindle cell hemangiomas ya ƙunshi ƙwayoyin da ake kira spindle cells. A karkashin madubin hangen nesa, kwayayen juyayi suna da tsayi da siriri.

Dalilin Hadarin

Duk wani abu da zai kara maka hadarin kamuwa da cuta to ana kiran sa mai hadari. Samun haɗarin haɗari ba yana nufin cewa za ku kamu da cutar ba; ba tare da haɗarin halayen haɗari ba yana nufin cewa ba za ku kamu da cutar ba. Yi magana da likitan ɗanka idan kana tunanin ɗanka na cikin haɗari. Spindle cell hemangiomas na iya faruwa a cikin yara tare da cututtukan da ke tafe:

  • Ciwon Maffucci, wanda ke shafar guringuntsi da fata.
  • Ciwon Klippel-Trenaunay, wanda ke shafar jijiyoyin jini, kayan taushi, da ƙashi.

Alamomi

Spindel cell hemangiomas ya bayyana a kan ko ƙarƙashin fata. Suna da raunin ja-launin ruwan kasa ko rauni mai laushi waɗanda yawanci sukan bayyana akan hannaye ko ƙafafu. Zasu iya farawa azaman rauni ɗaya kuma su zama cikin ƙari na tsawon shekaru.

Gwajin gwaji

Duba sashen Bayani Gabaɗaya don kwatancen gwaje-gwaje da hanyoyin da aka yi amfani da su don gano ƙwayar ƙwayar ƙwayar ƙwayar ƙwayar ƙwayar cuta.

Jiyya

Babu daidaitaccen magani ga spindle cell hemangiomas. Jiyya na iya haɗa da masu zuwa:

  • Tiyata don cire ƙari.

Spindle cell hemangiomas na iya dawowa bayan tiyata.

Hemangioma na Epithelioid

Epithelioid hemangiomas yawanci yakan zama akan ko cikin fata, musamman kansa, amma yana iya faruwa a wasu yankuna, kamar ƙashi.

Alamomi da Ciwon

Epithelioid hemangiomas wani lokaci yakan haifar da rauni. A kan fata, suna iya bayyana a matsayin ruwan hoda mai ƙarfi zuwa kumburi ja kuma yana iya zama ƙaiƙayi. Epithelioid hemangioma na kashi na iya haifar da kumburi, zafi, da rauni kasusuwa a yankin da abin ya shafa.

Gwajin gwaji

Dubi Babban Bayanin Bayani don bayanin gwaje-gwajen da hanyoyin da aka yi amfani da su don tantance cutar hemangioma.

Jiyya

Babu daidaitaccen magani don epithelioid hemangiomas. Jiyya na iya haɗa da masu zuwa:

  • Tiyata (curettage ko resection).
  • Sclerotherapy.
  • Radiation radiation a cikin ƙananan lokuta.

Epithelioid hemangiomas yakan dawo bayan magani.

Granuloma na Pyogenic

Ana kuma kiran Pyogenic granuloma lobular capillary hemangioma. An fi dacewa da yara tsofaffi da matasa amma ana iya faruwa a kowane zamani.

Raunin wasu lokuta yakan haifar da rauni ko daga amfani da wasu magunguna, gami da magungunan hana haihuwa da kuma retinoids. Hakanan zasu iya yin tsari ba tare da sanannen dalili ba a cikin kaifin jini (mafi ƙarancin jijiyoyin jini), jijiyoyi, jijiyoyi, ko sauran wurare a jiki. Yawancin lokaci rauni ɗaya ne kawai, amma wani lokacin raunuka da yawa na faruwa a yanki ɗaya ko raunukan na iya yaɗuwa zuwa wasu sassan jiki.

Alamomi

An tayar da granulomas na Pyogenic, raunin ja mai haske wanda zai iya zama ƙarami ko babba kuma mai santsi ko mai kumburi. Suna girma cikin sauri sama da makonni zuwa watanni kuma suna iya zubar da jini da yawa. Wadannan cututtukan galibi akan saman fata ne, amma suna iya samuwa a cikin kyallen da ke ƙasan fata kuma suyi kama da sauran raunuka na jijiyoyin jiki.

Gwajin gwaji

Dubi Babban Bayanin Bayani don kwatancen gwaje-gwaje da hanyoyin da aka yi amfani da su don tantance ƙwayoyin cuta.

Jiyya

Wasu granulomas na pyogenic suna tafiya ba tare da magani ba. Sauran granulomas na pyogenic suna buƙatar magani wanda zai iya haɗa da masu zuwa:

  • Yin tiyata (cirewa ko warkarwa) don cire rauni.
  • Photocoagulation.
  • Magungunan beta-shafi na asali.

Pyogenic granulomas galibi yakan dawo bayan jiyya.

Angiofibroma

Angiofibromas ba safai ba. Su raunuka ne na fata marasa kyau waɗanda yawanci suke faruwa tare da yanayin da ake kira tuberous sclerosis (cuta mai gado da ke haifar da raunin fata, kamuwa, da nakasar hankali).

Alamomi

Angiofibromas sun bayyana kamar kumburi ja akan fuska.

Gwajin gwaji

Duba sashen Bayani Gabaɗaya don kwatancen gwaje-gwaje da hanyoyin da ake amfani dasu don tantance angiofibroma.

Jiyya

Jiyya na angiofibromas na iya haɗa da masu zuwa:

  • Yin tiyata (cirewa) don cire kumburin.
  • Laser far.
  • Tsarin da aka yi niyya (sirolimus).

Yara Nasopharyngeal Angiofibroma

Yaran yara nasopharyngeal angiofibromas ƙananan ciwace-ciwace amma suna iya girma cikin nama kusa. Suna farawa a cikin ramin hanci kuma suna iya yaɗuwa zuwa nasopharynx, sinadarin paranasal, ƙashi a kusa da idanuwa, wani lokacin kuma zuwa kwakwalwa.

Gwajin gwaji

Duba sashen Bayani Gabaɗaya don kwatancen gwaje-gwaje da hanyoyin da aka yi amfani dasu don bincikar ƙananan yara nasopharyngeal angiofibroma.

Jiyya

Jiyya na yara nasopharyngeal angiofibromas na iya haɗa da masu zuwa:

  • Yin tiyata (cirewa) don cire kumburin.
  • Radiation far.
  • Chemotherapy.
  • Immunotherapy (interferon).
  • Tsarin da aka yi niyya (sirolimus).

Matsakaici Tumor da ke Yada Gida

A Wannan Sashin

  • Kaposiform Hemangioendothelioma da Tufted Angioma

Don bayani game da jiyya da aka jera a ƙasa, duba sashin Kula da Zaɓin Jiyya.

Kaposiform Hemangioendothelioma da Tufted Angioma

Kaposiform hemangioendotheliomas da tufted angiomas sune ciwan jijiyoyin jini wanda ke faruwa a cikin jarirai ko ƙananan yara. Wadannan ciwace-ciwacen na iya haifar da abin da ke faruwa na Kasabach-Merritt, yanayin da jini baya iya daskarewa kuma za a iya samun zubar jini mai tsanani. A cikin abin da ya faru na Kasabach-Merritt, kumburin ya kama tarko da lalata platelets (ƙwayoyin jini masu ɗaure jini). Sannan babu wadatattun platelets a cikin jini lokacin da ake buƙatar dakatar da zubar jini. Wannan nau'in ƙwayar jijiyoyin jini ba su da alaƙa da Kaposi sarcoma.

Alamomi da Ciwon

Kaposiform hemangioendotheliomas da tufted angiomas yawanci suna faruwa akan fatar hannu da ƙafafu, amma kuma yana iya zama a cikin ƙwayoyin cuta masu zurfi, kamar tsoka ko ƙashi, ko a kirji ko ciki.

Alamomi da cututtuka na iya haɗa da mai zuwa:

  • Maƙƙan wurare masu raɗaɗi na fata waɗanda suka yi kama da rauni.
  • Yankunan launin ja masu launin ja-launi-masu launi-launi.
  • Sauƙaƙewa mai sauƙi.
  • Zubar jini fiye da yadda aka saba daga membobin mucous, raunuka, da sauran kayan kyallen takarda.

Marasa lafiya waɗanda ke da kaposiform hemangioendothelioma da tufted angioma na iya samun karancin jini (rauni, jin kasala, ko kodadde).

Gwajin gwaji

Duba sashen Bayani Gabaɗaya don kwatancen gwaje-gwaje da hanyoyin da aka yi amfani da su don tantance cutar kaposiform hemangioendothelioma.

Idan gwajin jiki da MRI a bayyane suka nuna kumburin shine hemangioendothelioma ko tufted angioma, ba za'a iya buƙatar biopsy ba. Ba a yin biopsy koyaushe saboda mummunan jini na iya faruwa.

Jiyya

Jiyya na kaposiform hemangioendotheliomas da tufted angiomas ya dogara da alamun yaron. Kamuwa da cuta, jinkirta jiyya, da tiyata na iya haifar da zub da jini wanda ke da haɗari ga rai. Kaposiform hemangioendotheliomas da tufted angiomas suna da mafi kyawun magani daga ƙwararren masanin jijiyoyin jini.

Kulawa da kulawa mai kulawa don sarrafa zubar jini na iya haɗa da mai zuwa:

  • Magungunan cututtukan steroid wanda ƙila za a iya bi da shi ta hanyar chemotherapy.
  • Magungunan anti-inflammatory marasa steroidal (NSAIDs), kamar su asfirin.
  • Immunotherapy (interferon).
  • Antifibrinolytic far don inganta ƙin jini.
  • Chemotherapy tare da ɗaya ko fiye da magungunan ciwon daji.
  • Maganin Beta-blocker (propranolol).
  • Yin tiyata (cirewa) don cire ƙari, tare da ko ba tare da haɓaka ba.
  • Maganin da aka yi niyya (sirolimus), tare da ko ba tare da maganin steroid ba.
  • Gwajin gwaji na ilimin kimiya da magani ko maganin niyya (sirolimus).

Ko da tare da magani, waɗannan ciwace-ciwacen ba sa cika tafiya kuma suna iya dawowa. Jin zafi da kumburi na iya zama mafi muni da shekaru, sau da yawa a lokacin balaga. Abubuwan da za a iya amfani da su na dogon lokaci sun haɗa da ciwo mai ɗorewa, ciwan zuciya, matsalolin ƙashi, da lymphedema (gina ruwan lymph a cikin kyallen takarda).

Matsakaici Tumurai da Bazuwar Yada su

A Wannan Sashin

  • Hanyar Hemangioendothelioma
  • Retiform Hemangioendothelioma
  • Papillary Intralymphatic Angioendothelioma
  • Hadaddiyar Hemangioendothelioma
  • Kaposi Sarcoma

Don bayani game da jiyya da aka jera a ƙasa, duba sashin Kula da Zaɓin Jiyya.

Hanyar Hemangioendothelioma

Pseudomyogenic hemangioendothelioma na iya faruwa a cikin yara, amma ya fi yawa ga maza tsakanin shekara 20 zuwa 50. Wadannan cututtukan suna da wuya, kuma yawanci suna faruwa ne a kan ko ƙarƙashin fata, ko a ƙashi. Suna iya yaɗuwa zuwa kayan da ke kusa, amma yawanci basa yadawa zuwa wasu sassan jiki. A mafi yawan lokuta, akwai ciwace-ciwace masu yawa.

Alamomi da Ciwon

Pseudomyogenic hemangioendotheliomas na iya bayyana kamar dunƙule cikin nama mai taushi ko na iya haifar da ciwo a yankin da abin ya shafa.

Gwajin gwaji

Duba sashen Bayani Gabaɗaya don kwatancen gwaje-gwaje da hanyoyin da aka yi amfani da su don gano cutar hanta da jijiyoyin jini.

Jiyya

Jiyya na pseudomyogenic hemangioendotheliomas na iya haɗa da masu zuwa:

  • Yin aikin tiyata don cire ƙari lokacin da zai yiwu. Za'a iya buƙatar yankewa lokacin da akwai ƙari mai yawa a cikin ƙashi.
  • Chemotherapy.
  • Farfaɗar da aka yi niyya (masu hana mTOR).

Saboda pseudomyogenic hemangioendothelioma ba shi da yawa a cikin yara, zaɓuɓɓukan magani suna dogara ne da gwajin asibiti a cikin manya.

Retiform Hemangioendothelioma

Retiform hemangioendotheliomas suna jinkirin girma, kumburi mai laushi wanda ke faruwa a cikin samari da yara wani lokacin yara. Wadannan ciwace-ciwacen suna yawan faruwa a ko karkashin fata na makamai, ƙafafu, da akwati. Wadannan ciwace-ciwacen ba sa yadawa zuwa wasu sassan jiki.

Gwajin gwaji

Duba sashen Bayani Gabaɗaya don kwatancen gwaje-gwaje da hanyoyin da aka yi amfani dasu don gano hemangioendothelioma mai ritaya.

Jiyya

Jiyya na hemangioendotheliomas mai ritaya na iya haɗawa da masu zuwa:

  • Yin tiyata (cirewa) don cire kumburin. Bin baya zai hada da saka idanu don ganin idan kumburin ya dawo.
  • Radiation radiation da chemotherapy lokacin da ba'a iya yin tiyata ba ko lokacin da kumburin ya dawo.

Motsa jiki na baya baya na iya dawowa bayan jiyya.

Papillary Intralymphatic Angioendothelioma

Papillary intralymphatic angioendotheliomas kuma ana kiranta ciwan Dabska. Wadannan kumburin suna yin ciki ko karkashin fata ko ina a jiki. Lymph nodes wasu lokuta ana cutar su.

Alamomi

Papillary intralymphatic angioendotheliomas na iya bayyana kamar tabbatacce, tashe, tsarkake kumburi, wanda na iya zama ƙarami ko babba.

Gwajin gwaji

Duba sashen Bayani Gabaɗaya don kwatancen gwaje-gwaje da hanyoyin da aka yi amfani dasu don tantance cututtukan cututtukan jini na papillary intralymphatic angioendothelioma.

Jiyya

Jiyya na papillary intralymphatic angioendotheliomas na iya haɗa da masu zuwa:

  • Yin tiyata (cirewa) don cire kumburin.

Hadaddiyar Hemangioendothelioma

Hadadden hemangioendotheliomas yana da fasalulluka na cututtukan ƙwayoyin cuta masu illa da na ciwo. Waɗannan ciwace-ciwacen suna yawan faruwa a kan ko ƙarƙashin fata a kan hannu ko ƙafa. Hakanan suna iya faruwa a kai, wuya, ko kirji. Hadaddiyar hemangioendotheliomas ba za su iya tallata ta ba amma za su iya dawowa wuri ɗaya. Lokacin da ciwace-ciwacen ya yi tasiri, yawanci sukan bazu zuwa sassan lymph.

Gwajin gwaji

Dubi sashen Bayani Gabaɗaya don bayanin gwaje-gwaje da hanyoyin da aka yi amfani da su don gano ƙwayoyin cuta da kuma gano ko kumburin ya bazu.

Jiyya

Jiyya na hemangioendotheliomas na iya haɗa da masu zuwa:

  • Tiyata don cire ƙari.
  • Radiation therapy da chemotherapy don ciwace-ciwacen da suka bazu.

Kaposi Sarcoma

Kaposi sarcoma shine ciwon daji wanda ke haifar da rauni don girma cikin fata; kwayoyin mucous wadanda suke rufe bakin, hanci, da makogwaro; ƙwayoyin lymph; ko wasu gabobin. Yana haifar da kwayar cutar Kaposi sarcoma herpes (KSHV). A Amurka, yana faruwa galibi ga yara waɗanda ke da rauni na garkuwar jiki wanda ke haifar da rikice-rikicen tsarin garkuwar jiki, kamuwa da kwayar cutar HIV, ko magungunan da ake amfani da su a dashen sassan jikinsu.

Alamomi

Alamomin shiga yara na iya haɗa da mai zuwa:

  • Raunuka a cikin fata, baki, ko maƙogwaro. Raunukan fata ja ne, ko shunayya, ko launin ruwan kasa kuma suna canzawa daga lebur, zuwa ɗagawa, zuwa wuraren banƙyama da ake kira plaques, zuwa nodules.
  • Magungunan kumbura kumbura.

Gwajin gwaji

Duba sashen Babban Bayani don bayanin gwaje-gwaje da hanyoyin da ake amfani dasu don tantance Kaposi sarcoma.

Jiyya

Jiyya na Kaposi sarcoma na iya haɗawa da masu zuwa:

  • Chemotherapy.
  • Immunotherapy (interferon).
  • Radiation far.

Saboda Kaposi sarcoma yana da wuya a yara, wasu zaɓuɓɓukan magani sun dogara da gwajin asibiti a cikin manya. Dubi taƙaitaccen akan Kaposi Sarcoma Jiyya don bayani game da Kaposi sarcoma a cikin manya.

Mummunan umanƙara

A Wannan Sashin

  • Abun Hemangioendothelioma
  • Angiosarcoma na Tsarin Nama

Don bayani game da jiyya da aka jera a ƙasa, duba sashin Kula da Zaɓin Jiyya.

Abun Hemangioendothelioma

Epithelioid hemangioendotheliomas na iya faruwa a cikin yara, amma sun fi yawa ga manya tsakanin shekaru 30 zuwa 50. Yawanci suna faruwa ne a cikin hanta, huhu, ko cikin ƙashi. Suna iya saurin girma ko jinkirin girma. A kusan kashi ɗaya cikin uku na cututtukan, ƙwayar tana yaduwa zuwa wasu sassan jiki da sauri.

Alamomi da Ciwon

Alamomi da alamu sun dogara da inda ƙari yake:

  • A kan fata, za a iya ɗaga kumburin kuma a zagaye ko lebur, launuka masu launin ja-ja-ɗumi waɗanda suke jin dumi.
  • A cikin huhu, ƙila babu alamun farko. Alamomi da alamomin da zasu iya faruwa sun hada da:
  • Ciwon kirji.
  • Zubar da jini.
  • Anemia (rauni, jin kasala, ko kodadde).
  • Rashin numfashi (daga jikin huhu mai rauni).
  • A cikin kashi, ciwace-ciwacen na iya haifar da karyewa.

Tumoshin da ke faruwa a cikin hanta ko nama mai laushi na iya haifar da alamu da alamomi.

Gwajin gwaji

Epithelioid hemangioendotheliomas a cikin hanta ana samun su tare da sikanin CT da sikanin MRI. Dubi Babban Bayanin Bayani don bayanin waɗannan gwaje-gwajen da hanyoyin da aka yi amfani da su don bincikar maganin epithelioid hemangioendothelioma da kuma gano ko kumburin ya bazu. Hakanan za'a iya yin radiyoyin X-ray.

Jiyya

Jiyya na sanyin-girma epithelioid hemangioendotheliomas ya hada da masu zuwa:

  • Lura.

Jiyya na saurin girma na hemangioendotheliomas na iya haɗa da masu zuwa:

  • Yin aikin tiyata don cire ƙari lokacin da zai yiwu.
  • Immunotherapy (interferon) da niyya far (thalidomide, sorafenib, pazopanib, sirolimus) don ciwace-ciwacen da za su iya yaduwa.

Chemotherapy.

  • Total hepatectomy da kuma dashen hanta lokacin da ciwon yake a cikin hanta.
  • Gwajin gwaji na maganin warkewa (trametinib).
  • Gwajin gwaji na ilimin kimiya da magani (pazopanib).

Angiosarcoma na Tsarin Nama

Angiosarcomas sune ciwowin ci gaba masu saurin girma wanda ke samuwa a cikin jijiyoyin jini ko tasoshin lymph a kowane bangare na jiki, yawanci a cikin laushi mai taushi. Yawancin angiosarcomas suna cikin ko kusa da fata. Waɗanda ke cikin ƙaramin taushi mai laushi na iya samarwa a cikin hanta, saifa, da huhu.

Wadannan cututtukan suna da wuya a yara. Yara wani lokacin suna da ƙari fiye da ɗaya a cikin fata da / ko hanta.

Dalilin Hadarin

Duk wani abu da zai kara maka hadarin kamuwa da cuta to ana kiran sa mai hadari. Samun haɗarin haɗari ba yana nufin cewa za ku kamu da cutar ba; ba tare da haɗarin halayen haɗari ba yana nufin cewa ba za ku kamu da cutar ba. Yi magana da likitan ɗanka idan kana tunanin ɗanka na cikin haɗari. Hanyoyin haɗari ga angiosarcomas sun haɗa da masu zuwa:

  • Kasancewa ga radiation.
  • Lymphedema na zamani (na dogon lokaci), yanayin da ƙarin ruwa na lymph ke haɓaka a cikin kyallen takarda kuma yana haifar da kumburi.
  • Samun ciwon ƙwayar cuta na jijiyoyin jini. Ciwan mara, kamar hemangioma, na iya zama angiosarcoma amma wannan ba safai ba.

Alamomi

Alamun angiosarcoma ya dogara da inda ƙari yake kuma yana iya haɗawa da masu zuwa:

  • Red faci a fatar da ke zubar da jini cikin sauki.
  • Ciwan daji na Purple.

Gwajin gwaji

Dubi sashen Bayani Gabaɗaya don bayanin gwaje-gwaje da hanyoyin da aka yi amfani da su don bincikar angiosarcoma da gano ko kumburin ya bazu.

Jiyya

Maganin angiosarcoma na iya haɗawa da masu zuwa:

  • Tiyata don cire ƙari gaba daya.
  • Haɗuwa da tiyata, jiyyar cutar sankara, da kuma jujjuyawa don angiosarcomas waɗanda suka bazu.
  • Maganin da aka yi niyya (bevacizumab) da chemotherapy don angiosarcomas wanda ya fara a matsayin jaririn hemangiomas.
  • Gwajin gwaji na ilimin kimiya tare da ko ba tare da niyya ba (pazopanib).
  • Gwajin gwaji na maganin rigakafi (nivolumab da ipilimumab).

Don Moreara Koyo Game da umanƙara na Jijiyoyin Yara

Don ƙarin bayani game da cututtukan ƙwayar jijiyoyin yara, duba waɗannan:

  • Tattakin Naman Sarcoma Home Page
  • Tomography Tomography (CT) Scans da Ciwon daji
  • Magungunan Ciwon Cutar da Aka Yi niyya
  • MyPART - Cibiyar Sadarwar Yara da Yara

Don ƙarin bayani game da cutar sankarar yara da sauran albarkatun kansar gaba ɗaya, duba masu zuwa:

  • Game da Ciwon daji
  • Ciwon Yara
  • Binciken Cure don Ciwon Childrenan yara
  • Matsayi na Late na Jiyya don Ciwon Yara
  • Matasa da Samari da Ciwon daji
  • Yara da Ciwon daji: Jagora ga Iyaye
  • Ciwon daji a cikin Yara da Matasa
  • Tsayawa
  • Yin fama da Ciwon daji
  • Tambayoyi don Tambayar Doctor game da Ciwon daji
  • Don Tsira da Kulawa