Nau'o'in / pheochromocytoma / haƙuri / pheochromocytoma-magani-pdq

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Pheochromocytoma da Paraganglioma Jiyya (®) -Tsarin haƙuri

Janar Bayani Game da Pheochromocytoma da Paraganglioma

MAGANAN MAGANA

  • Pheochromocytoma da paraganglioma sune ciwace ciwace wadanda basuda yawa wadanda suka fito daga nau'in nama daya.
  • Pheochromocytoma wani ciwo ne wanda ba kasafai yake faruwa a cikin adulla ba (cibiyar adrenal gland).
  • Paragangliomas ya zama waje da gland.
  • Wasu rikicewar gado da canje-canje a cikin wasu ƙwayoyin halitta suna ƙara haɗarin cutar pheochromocytoma ko paraganglioma.
  • Alamomi da cututtukan pheochromocytoma da paraganglioma sun hada da hawan jini da ciwon kai.
  • Alamomi da alamomin pheochromocytoma da paraganglioma na iya faruwa a kowane lokaci ko kuma wasu abubuwa sun kawo su.
  • Ana amfani da gwaje-gwajen da ke bincikar jini da fitsari don ganowa (gano) da kuma tantance pheochromocytoma da paraganglioma.
  • Shawarwarin kwayoyin halitta wani bangare ne na shirin kula da marasa lafiya tare da pheochromocytoma ko paraganglioma.
  • Wasu dalilai suna tasiri hangen nesa (damar dawowa) da zaɓuɓɓukan magani.

Pheochromocytoma da paraganglioma sune ciwace ciwace wadanda basuda yawa wadanda suka fito daga nau'in nama daya.

Paragangliomas ya zama cikin ƙwayar jijiya a cikin gland adrenal da kusa da wasu jijiyoyin jini da jijiyoyi. Paragangliomas wanda ke samuwa a cikin gland adrenal ana kiransa pheochromocytomas. Paragangliomas wanda ke samarwa a wajen gland shine ake kira extra-adrenal paragangliomas. A cikin wannan taƙaitaccen bayani, ana kiran karin adrenal paragangliomas paragangliomas.

Pheochromocytomas da paragangliomas na iya zama marasa lafiya (ba kansar ba) ko mugu (kansar).

Pheochromocytoma wani ciwo ne wanda ba kasafai yake faruwa a cikin adulla ba (cibiyar adrenal gland).

Pheochromocytoma yana samuwa a cikin gland adrenal. Akwai gland din adrenal guda biyu, daya a saman kowacce koda a bayan ciki na sama. Kowace gland tana da sassa biyu. Launin waje na gland din adrenal shine guntun adrenal. Tsakanin adrenal gland shine adrenal medulla.

Pheochromocytoma shine ƙananan ƙwayar ƙwayar adrenal medulla. Yawancin lokaci, pheochromocytoma yana shafar gland daya adrenal, amma yana iya shafar duka gland adrenal. Wani lokaci akan sami ƙari fiye da ɗaya a cikin gland.

Glanden adrenal suna yin mahimmin hormones wanda ake kira catecholamines. Adrenaline (epinephrine) da noradrenaline (norepinephrine) nau'ikan catecholamine ne guda biyu wadanda suke taimakawa wajen magance bugun zuciya, hawan jini, suga, da kuma yadda jiki ke amsa damuwa. Wani lokaci pheochromocytoma zai saki ƙarin adrenaline da noradrenaline cikin jini kuma ya haifar da alamu ko alamomin cuta.

Anatomy na adrenal gland. Akwai gland din adrenal guda biyu, daya a saman kowace koda. Sashin waje na kowace gland shine kwalliyar adrenal; sashin ciki shine adulla.

Paragangliomas ya zama waje da gland.

Paragangliomas ƙananan ciwace-ciwace ne da ke samarwa a kusa da jijiyar carotid, tare da hanyoyin jijiya a kai da wuya, da sauran sassan jiki. Wasu paragangliomas suna yin karin catecholamines da ake kira adrenaline da noradrenaline. Sakin waɗannan ƙarin catecholamines ɗin cikin jini na iya haifar da alamu ko alamomin cuta.

Paraganglioma na kai da wuya. Wani ciwo mai saurin gaske wanda sau da yawa yakan zama kusa da jijiyar carotid. Hakanan yana iya samuwa tare da hanyoyin jijiyoyi a kai da wuya da sauran sassan jiki.

Wasu rikicewar gado da canje-canje a cikin wasu ƙwayoyin halitta suna ƙara haɗarin cutar pheochromocytoma ko paraganglioma.

Duk wani abu da zai kara muku damar kamuwa da cuta to ana kiransa mai hadari. Samun haɗarin haɗari ba yana nufin cewa za ku kamu da cutar kansa ba; ba tare da haɗarin abubuwan haɗari ba yana nufin cewa ba zaku sami cutar kansa ba. Yi magana da likitanka idan kuna tunanin kuna cikin haɗari.

Wadannan cututtukan cututtukan da muka gada ko canjin dabi'u suna kara barazanar cutar pheochromocytoma ko paraganglioma:

  • Maganin cututtukan neoplasia 2 da yawa, iri A da B (MEN2A da MEN2B).
  • von Hippel-Lindau (VHL) ciwo.
  • Neurofibromatosis nau'in 1 (NF1).
  • Ciwon cututtukan paraganglioma.
  • Carney-Stratakis dyad (paraganglioma da cututtukan ciki na ciwon ciki [GIST]).
  • Carney triad (paraganglioma, GIST, da huhu na ciki).

Alamomi da cututtukan pheochromocytoma da paraganglioma sun hada da hawan jini da ciwon kai.

Wasu ciwace-ciwacen ƙwayoyi ba sa yin ƙarin adrenaline ko noradrenaline kuma ba sa haifar da alamu da alamomi. Wadannan cututtukan cututtukan wasu lokuta ana samun su lokacin da dunƙulen ya zama a cikin wuya ko lokacin da aka yi gwaji ko hanya don wani dalili. Alamomi da cututtukan pheochromocytoma da paraganglioma suna faruwa yayin da adrenaline mai yawa ko noradrenaline aka saki cikin jini. Wadannan da sauran alamu da alamomin na iya haifar da cutar pheochromocytoma da paraganglioma ko kuma ta wasu yanayi. Duba tare da likitanka idan kuna da ɗayan masu zuwa:

  • Hawan jini.
  • Ciwon kai.
  • Gumi mai nauyi ba tare da san dalili ba.
  • Strongarfin zuciya, mai ƙarfi, ko mara kyau.
  • Kasancewa mai girgiza.
  • Kasancewa mai kodadde.

Alamar da aka fi sani ita ce hawan jini. Yana iya zama da wahala a iya sarrafawa. Hawan jini sosai na iya haifar da matsaloli na lafiya kamar su bugun zuciya mara kyau, bugun zuciya, bugun jini, ko mutuwa.

Alamomi da alamomin pheochromocytoma da paraganglioma na iya faruwa a kowane lokaci ko kuma wasu abubuwa sun kawo su.

Alamomi da alamomin pheochromocytoma da paraganglioma na iya faruwa yayin da ɗayan abubuwan masu zuwa suka faru:

  • Motsa jiki mai wahala.
  • Raunin jiki ko yawan damuwa.
  • Haihuwar.
  • Tafiya a karkashin maganin sa barci.
  • Yin aikin tiyata, gami da hanyoyin cire kumburin.
  • Cin abinci mai cike da sinadarin tyramine (kamar su jan giya, cakulan, da cuku).

Ana amfani da gwaje-gwajen da ke bincikar jini da fitsari don ganowa (gano) da kuma tantance pheochromocytoma da paraganglioma.

Za a iya amfani da waɗannan gwaje-gwajen da hanyoyin:

  • Jarabawa ta jiki da tarihi: Jarabawa ce ta jiki don bincika alamomin lafiya gaba ɗaya, gami da bincika alamun cuta, kamar hawan jini ko wani abu da kamar baƙon abu. Za a kuma ɗauki tarihin al'adun lafiyar marasa lafiya da cututtukan da suka gabata da magunguna.
  • Gwajin fitsari na awanni ashirin da hudu: Gwaji ne wanda ake tattara fitsari na tsawon awanni 24 don auna adadin catecholamines da ke cikin fitsarin. Ana kuma auna abubuwan da lalacewar waɗannan catecholamines ya haifar. Adadin abu mai ban mamaki (mafi girma ko ƙasa da al'ada) na abu zai iya zama alamar cuta a cikin gaɓaɓɓiyar jiki ko nama da ke yin ta. Adadin da ya fi na al'ada na wasu catecholamines na iya zama alamar cutar pheochromocytoma.
  • Nazarin catecholamine na jini: Aikin da ake bincikar samfurin jini don auna adadin wasu catecholamines da aka saki cikin jini. Ana kuma auna abubuwan da lalacewar waɗannan catecholamines ya haifar. Adadin da ba a saba gani ba (sama da ƙasa ko ƙasa) na abu zai iya zama alamar cuta a cikin gaɓaɓɓiyar jiki ko nama da ke yin ta. Adadin da ya fi na al'ada na wasu catecholamines na iya zama alamar cutar pheochromocytoma.
  • CT scan (CAT scan): Hanya ce da ke yin jerin hotuna dalla-dalla na wurare a cikin jiki, kamar wuya, kirji, ciki, da ƙashin ƙugu, waɗanda aka ɗauka daga kusurwa daban-daban. Ana yin hotunan ne ta wata kwamfuta da aka haɗa ta da na'urar da ke ɗauke da x-ray. Ana iya yin allurar fenti a cikin jijiya ko haɗiye don taimakawa gabobin ko kyallen takarda su fito fili karara. Wannan hanya ana kiranta yanayin ƙididdigar lissafi, ƙirar kwamfuta, ko ƙirar ƙwaƙwalwar ajiyar kwamfuta.
  • MRI (hoton maganadisu ): Hanya ce wacce ke amfani da maganadisu, igiyar ruwa ta rediyo, da kuma kwamfuta don yin jerin hotuna dalla-dalla na wurare a cikin jiki kamar wuya, kirji, ciki, da ƙashin ƙugu. Wannan hanya ana kiranta kuma ana kiranta hoton maganadisu na maganadisu (NMRI).

Shawarwarin kwayoyin halitta wani bangare ne na shirin kula da marasa lafiya tare da pheochromocytoma ko paraganglioma.

Duk marasa lafiyar da suka kamu da cutar pheochromocytoma ko paraganglioma yakamata su sami shawarwarin kwayoyin halitta domin gano haɗarin kamuwa da cututtukan gado da sauran cututtukan da suka shafi hakan.

Gwajin kwayar halitta na iya bada shawarar ta mai ba da shawara kan kwayoyin halitta ga marasa lafiya wadanda suka:

  • Kasance da tarihin kai ko na dangi na halaye masu alaƙa da cututtukan cututtukan cututtukan zuciya ko cututtukan paraganglioma.
  • Samun ciwace-ciwacen a cikin gland din.
  • Samun ƙari fiye da ɗaya a cikin gland.
  • Samun alamu ko alamomin ƙarin catecholamines ana sakasu cikin jini ko m (mai cutar kansa) paraganglioma.
  • Ana bincikar lafiya kafin shekaru 40.

Gwajin kwayoyin halitta wani lokaci ana ba da shawarar ga marasa lafiya da pheochromocytoma wanda:

  • Shekaru 40 zuwa 50.
  • Yi ƙari a cikin gland.
  • Ba ku da tarihin kanku ko na iyali na cututtukan da kuka gada.

Lokacin da aka sami wasu canje-canje na kwayar halitta yayin gwajin kwayoyin, yawanci ana bayar da gwajin ga dangin da ke cikin haɗari amma ba su da alamu ko alamu.

Ba a ba da shawarar gwajin kwayar halitta ga marasa lafiyar da suka girmi shekaru 50 ba.

Wasu dalilai suna tasiri hangen nesa (damar dawowa) da zaɓuɓɓukan magani.

Halin hangen nesa (damar dawowa) da zaɓuɓɓukan magani sun dogara da masu zuwa:

  • Ko kumburin yana da kyau ko kuma m.
  • Ko kumburin yana cikin yanki daya kawai ko kuma ya bazu zuwa wasu wurare a cikin jiki.
  • Ko akwai alamomi ko alamomin da yawan catecholamines ya fi girma fiye da al'ada.
  • Ko dai an gano kumburin ko kuma ya sake dawowa (dawo).

Matakan Pheochromocytoma da Paraganglioma

MAGANAN MAGANA

  • Bayan an gano pheochromocytoma da paraganglioma, ana yin gwaji don gano ko kumburin ya bazu zuwa wasu sassan jiki.
  • Akwai hanyoyi uku da kansar ke yaduwa a jiki.
  • Ciwon daji na iya yaduwa daga inda ya fara zuwa sauran sassan jiki.
  • Babu daidaitaccen tsarin tsarkewa don pheochromocytoma da paraganglioma.
  • Pheochromocytoma da paraganglioma an bayyana su a matsayin yankuna, yanki, ko metastatic.
  • Ciwon pheochromocytoma da paraganglioma
  • Yankin pheochromocytoma da paraganglioma
  • Pheochromocytoma da paraganglioma

Bayan an gano pheochromocytoma da paraganglioma, ana yin gwaji don gano ko kumburin ya bazu zuwa wasu sassan jiki.

Yawanci ko yaduwar cutar kansa yawanci ana bayyana shi a matsayin mataki. Yana da mahimmanci a san ko ciwon daji ya bazu don tsara magani. Ana iya amfani da gwaje-gwaje da hanyoyin da ke tafe don sanin ko kumburin ya bazu zuwa wasu sassan jiki:

  • CT scan (CAT scan): Hanya ce da ke yin jerin hotuna dalla-dalla na wurare a cikin jiki, kamar wuya, kirji, ciki, da ƙashin ƙugu, waɗanda aka ɗauka daga kusurwa daban-daban. Ana yin hotunan ne ta wata kwamfuta da aka haɗa ta da na'urar da ke ɗauke da x-ray. Ana iya yin allurar fenti a cikin jijiya ko haɗiye don taimakawa gabobin ko kyallen takarda su fito fili karara. An zana ciki da ƙashin ƙugu don gano kumburin da ke sakin catecholamine. Wannan hanya ana kiranta yanayin ƙididdigar lissafi, ƙirar kwamfuta, ko ƙirar ƙwaƙwalwar ajiyar kwamfuta.
  • MRI (hoton maganadisu ): Hanya ce wacce ke amfani da maganadisu, igiyar ruwa ta rediyo, da kuma kwamfuta don yin jerin hotuna dalla-dalla na wurare a cikin jiki kamar wuya, kirji, ciki, da ƙashin ƙugu. Wannan hanya ana kiranta kuma ana kiranta hoton maganadisu na maganadisu (NMRI).
  • MIBG scan: Hanyar da aka yi amfani da ita don gano ƙwayoyin neuroendocrine, kamar pheochromocytoma da paraganglioma. Wani ɗan ƙaramin abu ne wanda ake kira MIBG na rediyoaktif ana saka shi a cikin jijiya kuma yana tafiya ta cikin jini. Kwayoyin ƙari na Neuroendocrine suna ɗaukar MIBG na radiyo kuma ana yin amfani da na'urar daukar hotan takardu. Ana iya ɗaukar sikan sama da kwanaki 1-3. Za'a iya bada maganin iodine kafin ko yayin gwajin don kiyaye glandar thyroid daga yawan shan MIBG.
  • scan: Wani nau'in sikanin radionuclide ne da aka yi amfani da shi wajen gano wasu ciwace-ciwace, ciki har da ciwace-ciwacen da ke sakin catecholamine. Smallananan adadin rediyoaktif (wani hormone wanda ke haɗuwa da wasu ciwace-ciwacen ƙwayoyi) ana allura shi a cikin jijiya kuma yana tafiya ta cikin jini. Ana amfani da sinadarin radiyo a jikin kumburin kuma ana amfani da kyamara ta musamman wacce ke gano aikin rediyo don nuna inda ciwan jikin yake a jiki.
  • FDG-PET scan (fluorodeoxyglucose-positron emission tomography scan): Hanyar gano ƙwayoyin cuta masu illa a jiki. Amountananan FDG, wani nau'in glucose mai haɗari (sukari), ana yi masa allura a cikin jijiya. Na'urar daukar hoton PET tana juyawa a jiki kuma tana yin hoto inda ake amfani da glucose a jiki. Kwayoyin cuta masu illa suna nuna haske a hoton saboda suna aiki kuma suna ɗaukar glucose fiye da ƙwayoyin al'ada.

Akwai hanyoyi uku da kansar ke yaduwa a jiki.

Ciwon daji na iya yadawa ta hanyar nama, tsarin lymph, da jini:

  • Nama. Ciwon daji yana yaduwa daga inda ya fara ta girma zuwa yankuna na kusa.
  • Tsarin Lymph. Ciwon daji yana yaduwa daga inda ya faro ta hanyar shiga cikin ƙwayoyin cuta. Ciwon daji yana bi ta cikin jirgin ruwan lymph zuwa wasu sassan jiki.
  • Jini. Ciwon daji yana yaduwa daga inda ya fara ta hanyar shiga cikin jini. Ciwon daji yana bi ta hanyoyin jini zuwa wasu sassan jiki.

Ciwon daji na iya yaduwa daga inda ya fara zuwa sauran sassan jiki.

Lokacin da cutar daji ta bazu zuwa wani sashin jiki, akan kira shi metastasis. Kwayoyin sankara suna ɓata daga inda suka fara (asalin ƙwayar cuta) kuma suna tafiya ta cikin tsarin lymph ko jini.

  • Tsarin Lymph. Ciwon daji ya shiga cikin tsarin laminin, ya ratsa ta cikin jiragen ruwan lymph, kuma ya samar da ƙari (metastatic tumo) a wani ɓangaren jiki.
  • Jini. Ciwon kansa ya shiga cikin jini, ya bi ta hanyoyin jini, ya samar da ƙari (ƙwayar metastatic) a wani ɓangaren jiki.

Ciwon ƙwayar ƙwayar ƙwayar cuta shine irin ciwon daji kamar asalin farko. Misali, idan pheochromocytoma ya bazu zuwa kashi, kwayoyin cutar kansa a cikin kashin hakika kwayoyin halittar pheochromocytoma ne. Cutar ita ce cututtukan cututtukan fuka, ba cutar kansa ba.

Babu daidaitaccen tsarin tsarkewa don pheochromocytoma da paraganglioma.

Pheochromocytoma da paraganglioma an bayyana su a matsayin yankuna, yanki, ko metastatic.

Ciwon pheochromocytoma da paraganglioma

Ana samun ƙwayar cutar a cikin ɗaya ko duka biyun adrenal (pheochromocytoma) ko a wani yanki kawai (paraganglioma).

Yankin pheochromocytoma da paraganglioma

Ciwon daji ya yadu zuwa ƙwayoyin lymph ko wasu kyallen takarda kusa da inda ƙari ya fara.

Pheochromocytoma da paraganglioma

Ciwon daji ya bazu zuwa wasu sassan jiki, kamar hanta, huhu, ƙashi, ko narkakkun hanyoyin lymph.

Maimaita Pheochromocytoma da Paraganglioma

Raunin pheochromocytoma ko paraganglioma shine cutar kansa da ta sake dawowa (dawo) bayan an warke ta. Ciwon kansa na iya dawowa wuri ɗaya ko kuma a wani sashin jiki.

Bayanin Zaɓin Jiyya

MAGANAN MAGANA

  • Akwai nau'ikan magani daban-daban ga marasa lafiya da pheochromocytoma ko paraganglioma.
  • Marasa lafiya tare da pheochromocytoma da paraganglioma waɗanda ke haifar da alamu ko alamomi ana bi da su tare da maganin ƙwayoyi.
  • Ana amfani da nau'i shida na daidaitaccen magani:
  • Tiyata
  • Radiation far
  • Chemotherapy
  • Zubar da ciki
  • Embolization far
  • Ciwon da aka yi niyya
  • Ana gwada sababbin nau'ikan magani a gwajin asibiti.
  • Jiyya don pheochromocytoma da paraganglioma na iya haifar da sakamako masu illa.
  • Marasa lafiya na iya son yin tunani game da shiga cikin gwaji na asibiti.
  • Marasa lafiya na iya shiga gwajin asibiti kafin, lokacin, ko bayan fara maganin cutar kansa.
  • Za a buƙaci gwaje-gwaje na gaba.

Akwai nau'ikan magani daban-daban ga marasa lafiya da pheochromocytoma ko paraganglioma.

Akwai nau'ikan jiyya iri-iri ga marasa lafiya da pheochromocytoma ko paraganglioma. Wasu jiyya suna daidaito (magani da ake amfani dashi yanzu), kuma wasu ana gwada su a gwajin asibiti. Gwajin gwajin magani shine binciken bincike wanda aka tsara don taimakawa inganta ingantattun jiyya na yanzu ko samun bayanai game da sababbin jiyya ga marasa lafiya da ciwon daji. Lokacin da gwaji na asibiti ya nuna cewa sabon magani ya fi magani na yau da kullun, sabon magani na iya zama daidaitaccen magani. Marasa lafiya na iya son yin tunani game da shiga cikin gwaji na asibiti. Wasu gwaji na asibiti ana buɗe su ne kawai ga marasa lafiyar da basu fara magani ba

Marasa lafiya tare da pheochromocytoma da paraganglioma waɗanda ke haifar da alamu ko alamomi ana bi da su tare da maganin ƙwayoyi.

Magungunan ƙwayoyi na farawa lokacin da aka gano pheochromocytoma ko paraganglioma. Wannan na iya haɗawa da:

  • Magungunan da ke riƙe jinin jini na al'ada. Misali, wani nau'in magani da ake kira alpha-blockers yana dakatar da noradrenaline daga sanya kananan jijiyoyi su zama kunkuntar. Bude hanyoyin jini da annashuwa yana inganta gudan jini kuma yana rage hawan jini.
  • Magungunan da ke sanya bugun zuciya daidai. Misali, wani nau'in magani da ake kira beta-blockers yana dakatar da tasirin noradrenaline sosai kuma yana rage bugun zuciya.
  • Magungunan da ke toshe tasirin karin homonin da adrenal gland yayi.

Sau da yawa ana ba da magani na makonni ɗaya zuwa uku kafin a yi tiyata.

Ana amfani da nau'i shida na daidaitaccen magani:

Tiyata

Yin aikin tiyata don cire pheochromocytoma yawanci adrenalectomy ne (cire ɗaya ko duka biyun gland). Yayin wannan tiyatar, za a binciki kyallen takarda da ƙwayar lymph a cikin ciki kuma idan kumburin ya bazu, ana iya cire waɗannan ƙwayoyin. Ana iya ba da ƙwayoyi kafin, lokacin, da kuma bayan tiyata don kiyaye bugun jini da bugun zuciya daidai.

Bayan tiyata don cire kumburin, ana bincika matakan catecholamine a cikin jini ko fitsari. Matakan catecholamine na al'ada alama ce cewa an cire dukkan ƙwayoyin pheochromocytoma.

Idan aka cire duka biyun adrenal, ana bukatar maganin rayuwa na tsawon rai don maye gurbin homonin da adrenal gland yayi.

Radiation far

Radiation therapy magani ne na cutar kansa wanda yake amfani da hasken rana mai ƙarfi ko wasu nau'ikan radiation don kashe ƙwayoyin kansa ko hana su girma. Akwai nau'o'in maganin radiation guda biyu:

  • Magungunan radiation na waje yana amfani da inji a waje don aika radiation zuwa ga cutar kansa.
  • Magungunan radiation na ciki yana amfani da abu mai tasirin rediyo wanda aka rufe a cikin allurai, tsaba, wayoyi, ko catheters waɗanda aka sanya kai tsaye zuwa ko kusa da ciwon daji.

Hanyar da aka ba da maganin taɗɗar radiation ya dogara da nau'in cutar kansa da ake kula da ita da kuma ko ta cikin gida, yanki, metastatic, ko maimaituwa. Ana amfani da maganin radiation na waje da maganin 131I-MIBG don magance pheochromocytoma.

Ana amfani da Pheochromocytoma wani lokacin tare da 131I-MIBG, wanda ke ɗaukar radiation kai tsaye zuwa ƙwayoyin tumo. 131I-MIBG wani abu ne mai tasirin rediyo wanda yake tattarawa a cikin wasu nau'ikan kwayoyin tumo, yana kashe su da wani jujjuyawar da aka bayar. Ana ba da 131I-MIBG ta hanyar jiko. Ba duk pheochromocytomas suke ɗaukar 131I-MIBG ba, don haka ana yin gwaji da farko don bincika wannan kafin fara magani.

Chemotherapy

Chemotherapy magani ne na cutar kansa wanda ke amfani da magunguna don dakatar da haɓakar ƙwayoyin kansa, ko dai ta hanyar kashe ƙwayoyin ko ta hana su rarraba. Lokacin da ake shan chemotherapy ta baki ko allura a cikin jijiya ko tsoka, magungunan suna shiga cikin jini kuma zasu iya kaiwa ga kwayoyin cutar kansa a cikin jiki duka (systemotherapy chemotherapy). Lokacin da aka sanya chemotherapy kai tsaye zuwa cikin ruwa mai ruɓaɓɓen ciki, gaɓoɓi, ko rami na jiki kamar ciki, magungunan yawanci suna shafar ƙwayoyin kansa ne a waɗancan yankuna. Haɗaɗɗiyar cutar sanadiyyar magani magani ne ta amfani da fiye da ɗaya maganin ƙwayar cutar kansa. Hanyar da ake ba da cutar sankara ta dogara da nau'in cutar sankara da ake amfani da ita da kuma ko ta cikin gida, ta yanki, ko ta birni, ko ta maimaitawa.

Zubar da ciki

Kashewa magani ne don cire ko lalata ɓangaren jiki ko nama ko aikinta. Magungunan cire ciki da ake amfani dasu don taimakawa kashe ƙwayoyin cutar kansa sun haɗa da:

  • Rushewar yanayin yanayin rediyo: Hanya ce wacce ke amfani da raƙuman rediyo don zafi da lalata ƙwayoyin ƙwayoyin cuta. Rigunan rediyo suna tafiya ta cikin lantarki (ƙananan na'urori waɗanda ke ɗaukar wutar lantarki). Ana iya amfani da cirewar rediyo don magance cutar kansa da sauran yanayi.
  • Cryoablation: Hanya ce wacce nama ke daskarewa don lalata ƙwayoyin cuta. Ana amfani da sinadarin nitrogen mai ruwa ko kuma carbon dioxide don daskare nama.

Embolization far

Embolization far shine magani don toshe jijiyoyin da ke haifar da glandon adrenal. Tarewa da kwararar jini zuwa gland din yana taimakawa kashe kwayoyin cutar kansa wanda ke girma a wurin.

Ciwon da aka yi niyya

Targeted therapy wani magani ne wanda yake amfani da magunguna ko wasu abubuwa don ganowa da afkawa takamaiman ƙwayoyin kansa ba tare da cutar ƙwayoyin halitta ba. Ana amfani da hanyoyin kwantar da hankula don magance cututtukan cututtukan zuciya da maimaitowar cutar pheochromocytoma.

Sunitinib (wani nau'in mai hana maganin tyrosine kinase) wani sabon magani ne wanda ake karantashi don maganin cututtukan zuciya. Tyrosine kinase inhibitor far wani nau'in magani ne da ake niyya wanda yake toshe sakonnin da ake buƙata don ciwace-ciwacen ya girma.

Ana gwada sababbin nau'ikan magani a gwajin asibiti.

Ana samun bayani game da gwaji na asibiti daga gidan yanar gizon NCI.

Jiyya don pheochromocytoma da paraganglioma na iya haifar da sakamako masu illa.

Don bayani game da illolin da cutar ta kansar ta haifar, duba shafin mu na Side Side.

Marasa lafiya na iya son yin tunani game da shiga cikin gwaji na asibiti.

Ga wasu marasa lafiya, shiga cikin gwaji na asibiti na iya zama mafi kyawun zaɓin magani. Gwajin gwaji wani bangare ne na aikin binciken cutar kansa. Ana yin gwaje-gwajen asibiti don gano ko sabbin maganin cutar daji suna da lafiya da tasiri ko kuma sun fi magani na yau da kullun.

Yawancin yau da kullun na yau da kullun don cutar kansa sun dogara ne akan gwajin asibiti na farko. Marasa lafiya da ke cikin gwaji na asibiti na iya karɓar daidaitaccen magani ko kuma su kasance cikin farkon waɗanda za su karɓi sabon magani.

Marasa lafiya da ke shiga cikin gwaji na asibiti suma suna taimakawa inganta hanyar da za a bi da kansar a nan gaba. Koda lokacin gwajin asibiti bai haifar da sababbin magunguna ba, sau da yawa sukan amsa mahimman tambayoyi kuma suna taimakawa ci gaba da bincike gaba.

Marasa lafiya na iya shiga gwajin asibiti kafin, lokacin, ko bayan fara maganin cutar kansa.

Wasu gwaji na asibiti kawai sun haɗa da marasa lafiya waɗanda ba su sami magani ba tukuna. Sauran gwaje-gwajen suna gwada jiyya ga marasa lafiya waɗanda cutar kansa ba ta samu sauki ba. Hakanan akwai gwaji na asibiti da ke gwada sabbin hanyoyin dakatar da cutar kansa daga sake dawowa (dawowa) ko rage tasirin maganin kansar.

Gwajin gwaji na gudana a sassa da yawa na ƙasar. Bayani game da gwajin asibiti wanda NCI ke tallafawa ana iya samun shi akan shafin binciken gwaji na NCI. Ana iya samun gwajin gwaji na asibiti wanda wasu kungiyoyi ke tallafawa akan gidan yanar gizon ClinicalTrials.gov.

Za a buƙaci gwaje-gwaje na gaba.

Za a iya maimaita wasu gwaje-gwajen da aka yi don gano kansar ko don gano girman ciwon kansa. Za a maimaita wasu gwaje-gwaje don ganin yadda magani ke aiki. Shawarwarin game da ci gaba, canji, ko dakatar da magani zai dogara ne da sakamakon waɗannan gwaje-gwajen.

Wasu daga cikin gwaje-gwajen za a ci gaba da yi daga lokaci zuwa lokaci bayan an gama jiyya. Sakamakon waɗannan gwaje-gwajen na iya nuna idan yanayin ku ya canza ko kuma idan kansar ta sake dawowa (dawo). Wadannan gwaje-gwajen wasu lokuta ana kiran su gwaje-gwaje na gaba.

Ga marasa lafiya masu cutar pheochromocytoma ko paraganglioma da ke haifar da alamomi, za a duba matakan catecholamine a cikin jini da fitsari a kai a kai. Matakan Catecholamine waɗanda suke sama da al'ada na iya zama alamar cewa ciwon daji ya dawo.

Ga marasa lafiya da ke da paraganglioma wanda ba ya haifar da alamomi, ya kamata a yi gwaje-gwaje masu zuwa kamar CT, MRI, ko MIBG a kowace shekara.

Ga marasa lafiya masu cutar pheochromocytoma, matakan catecholamine a cikin jini da fitsari za'a duba su akai-akai. Sauran gwaje-gwajen binciken za a yi don bincika wasu cututtukan da ke da alaƙa da cututtukan da aka gada.

Yi magana da likitanka game da wane gwaje-gwaje ya kamata a yi da kuma sau nawa. Marasa lafiya tare da pheochromocytoma ko paraganglioma suna buƙatar bin rayuwa har abada.

Zaɓuɓɓukan Jiyya don Pheochromocytoma da Paraganglioma

A Wannan Sashin

  • Gida Pheochromocytoma da Paraganglioma
  • Ciwon Pheochromocytoma
  • Yankin Yankin Pheochromocytoma da Paraganglioma
  • Metheatic Pheochromocytoma da Paraganglioma
  • Maimaita Pheochromocytoma da Paraganglioma

Don bayani game da jiyya da aka jera a ƙasa, duba sashin Kula da Zaɓin Jiyya.

Gida Pheochromocytoma da Paraganglioma

Jiyya na cututtukan fheochromocytoma na asali ko paraganglioma yawanci aikin tiyata ne don kawar da ƙari. Idan ƙari ya kasance a cikin gland, za a cire duka glanden adrenal.

Yi amfani da binciken bincikenmu na asibiti don nemo NCI na goyan bayan gwajin asibiti wanda ke karɓar marasa lafiya. Kuna iya bincika gwaji dangane da nau'in ciwon daji, shekarun mai haƙuri, da kuma inda ake yin gwajin. Ana samun cikakken bayani game da gwaji na asibiti.

Ciwon Pheochromocytoma

A cikin marasa lafiya da cututtukan pheochromocytoma da aka gada suna da alaƙa da cututtukan endocrine neoplasia (MEN2) ko kuma von Hippel-Lindau (VHL), ciwace ciwace ci gaba da kasancewa a cikin gland. Ciwace ciwace yawanci ba shi da kyau.

  • Jiyya don cututtukan pheochromocytoma da aka gada a cikin adrenal gland shine tiyata don cire gland din gaba daya. Wannan tiyata na iya taimaka wa marasa lafiya su guji maye gurbin maye gurbinsu na maye gurbin mutum da rashin ƙarancin adrenal.
  • Jiyya don cututtukan pheochromocytoma da aka gada wadanda ke kasancewa a cikin gland adrenal ko kuma daga baya a sauran gland din na iya zama aikin tiyata don cire kumburin kuma a matsayin karamin abu na al'ada a cikin gyambon ciki kamar yadda zai yiwu. Wannan tiyatar na iya taimaka wa marasa lafiya su guji maganin maye gurbin maye gurbin rai da matsalolin lafiya saboda asarar homonin da glandon adrenal yayi.

Yankin Yankin Pheochromocytoma da Paraganglioma

Jiyya na pheochromocytoma ko paraganglioma wanda ya bazu zuwa gabobin da ke kusa ko lymph nodes shine tiyata don kawar da ƙari gaba daya. Hakanan za'a iya cire gabobin da ke kusa da kansa wanda ya bazu, kamar koda, hanta, wani ɓangare na babban jijiyoyin jini, da ƙugiya.

Yi amfani da binciken bincikenmu na asibiti don nemo NCI na goyan bayan gwajin asibiti wanda ke karɓar marasa lafiya. Kuna iya bincika gwaji dangane da nau'in ciwon daji, shekarun mai haƙuri, da kuma inda ake yin gwajin. Ana samun cikakken bayani game da gwaji na asibiti.

Metheatic Pheochromocytoma da Paraganglioma

Jiyya na pheochromocytoma ko paraganglioma na iya haɗa da masu zuwa:

  • Yin aikin tiyata don kawar da cutar kansa gaba ɗaya, gami da ciwace-ciwacen da suka bazu zuwa sassan jiki masu nisa.
  • Magungunan kwantar da hankali, don sauƙaƙe bayyanar cututtuka da haɓaka ƙimar rayuwa, gami da:
  • Tiyata don cire yawancin ciwon daji kamar yadda zai yiwu.
  • Hade chemotherapy.
  • Radiation na iska tare da 131I-MIBG.
  • Magungunan radiation na waje zuwa yankuna (kamar ƙashi) inda ciwon daji ya bazu kuma ba za a iya cire shi ta hanyar tiyata.
  • Embolization (magani don toshe jijiyoyin da ke ba da jini ga ƙari).
  • Narkar da zubar da ciki ta amfani da raguwa na rediyo ko muryar kuka don ƙari a cikin hanta ko ƙashi.
  • Gwajin gwaji na maganin farfadowa tare da mai hana yaduwar cutar tyrosine kinase.
  • Gwajin gwaji na maganin radiation na ciki ta amfani da sabon abu mai tasirin rediyo.

Yi amfani da binciken bincikenmu na asibiti don nemo NCI na goyan bayan gwajin asibiti wanda ke karɓar marasa lafiya. Kuna iya bincika gwaji dangane da nau'in ciwon daji, shekarun mai haƙuri, da kuma inda ake yin gwajin. Ana samun cikakken bayani game da gwaji na asibiti.

Maimaita Pheochromocytoma da Paraganglioma

Jiyya na cututtukan pheochromocytoma ko paraganglioma na iya haɗa da masu zuwa:

  • Yin aikin tiyata don kawar da cutar kansa.
  • Lokacin aikin tiyata don cire kansar ba zai yiwu ba, maganin kwantar da hankali don sauƙaƙe alamun cututtuka da haɓaka ƙimar rayuwa, gami da:
  • Hade chemotherapy.
  • Ciwon da aka yi niyya.
  • Radiation na iska ta amfani da 131I-MIBG.
  • Magungunan radiation na waje zuwa yankuna (kamar ƙashi) inda ciwon daji ya bazu kuma ba za a iya cire shi ta hanyar tiyata.
  • Narkar da zubar da ciki ta amfani da raguwa ta hanyar rediyo ko taƙama.

Yi amfani da binciken bincikenmu na asibiti don nemo NCI na goyan bayan gwajin asibiti wanda ke karɓar marasa lafiya. Kuna iya bincika gwaji dangane da nau'in ciwon daji, shekarun mai haƙuri, da kuma inda ake yin gwajin. Ana samun cikakken bayani game da gwaji na asibiti.

Pheochromocytoma Yayin Ciki

MAGANAN MAGANA

  • Mata masu ciki tare da pheochromocytoma suna buƙatar kulawa ta musamman.
  • Yin jiyya ga mata masu juna biyu tare da pheochromocytoma na iya haɗawa da tiyata.

Don bayani game da jiyya da aka jera a ƙasa, duba sashin Kula da Zaɓin Jiyya.

Mata masu ciki tare da pheochromocytoma suna buƙatar kulawa ta musamman.

Kodayake ba safai ake samunta ba yayin daukar ciki, pheochromocytoma na iya zama mai tsananin gaske ga uwa da jariri. Matan da ke da ƙarin haɗarin cutar pheochromocytoma ya kamata su yi gwaji kafin lokacin haihuwa. Mata masu juna biyu masu dauke da cutar pheochromocytoma ya kamata wasu likitoci su kula da su wadanda kwararru ne a wannan nau'in kulawa.

Alamomin pheochromocytoma a cikin ciki na iya haɗawa da ɗayan masu zuwa:

  • Hawan jini a farkon watanni 3 na ciki.
  • Kwatsam lokacin hawan jini.
  • Hawan jini wanda yake da wahalar magani.

Ganewar cutar pheochromocytoma a cikin mata masu ciki ya haɗa da gwaji don matakan catecholamine cikin jini da fitsari. Dubi Babban Bayanin Bayani don bayanin waɗannan gwaje-gwajen da hanyoyin. Ana iya yin MRI don gano ƙari a cikin mata masu juna biyu cikin aminci saboda ba ya fallasa ɗan tayi zuwa radiation.

Jiyya na mata masu ciki tare da pheochromocytoma na iya haɗawa da tiyata.

Jiyya na pheochromocytoma yayin daukar ciki na iya haɗa da masu zuwa:

  • Yin aikin tiyata don kawar da cutar kansa gaba ɗaya a cikin watanni na biyu (na huɗu zuwa watan shida na ciki).
  • Yin aikin tiyata don kawar da cutar kansa gaba ɗaya haɗe da haihuwar ɗan tayi ta hanyar tiyatar haihuwa.

Don Moreara Koyo Game da Pheochromocytoma da Paraganglioma

Don ƙarin bayani daga Cibiyar Cancer ta aboutasa game da cutar pheochromocytoma da paraganglioma, duba mai zuwa:

  • Pheochromocytoma da Paraganglioma Shafin Gida
  • Yara Pheochromocytoma da Paraganglioma Jiyya
  • Tashin hankali a cikin Jiyya na Cancer: Tambayoyi da Amsoshi
  • Magungunan Ciwon Cutar da Aka Yi niyya
  • Gwajin Halitta don Ciwon Cutar Cancer na Cancer

Don cikakkun bayanai game da cutar kansa da sauran albarkatu daga Cibiyar Cancer ta Kasa, duba mai zuwa:

  • Game da Ciwon daji
  • Tsayawa
  • Chemotherapy da ku: Tallafi ga Mutanen da ke Ciwon daji
  • Radiation Far da Kai: Taimako ga Mutane Tare da Ciwon daji
  • Yin fama da Ciwon daji
  • Tambayoyi don Tambayar Doctor game da Ciwon daji
  • Don Tsira da Kulawa


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