Nau'ikan / langerhans / haƙuri / langerhans-treatment-pdq
Abubuwan da ke ciki
- 1 Maganin Tarihin Tarihin Langerhans na Langerhans (®) –Patient Version
- 1.1 Janar Bayani Game da Langerhans Cell Histiocytosis (LCH)
- 1.2 Matakan LCH
- 1.3 Bayanin Zaɓin Jiyya don LCH
- 1.4 Jiyya na ƙananan ƙananan LCH a cikin Yara
- 1.5 Jiyya na Babban Haɗarin LCH a cikin Yara
- 1.6 Jiyya na Maimaitawa, Rashin hankali, da Ci gaban Childhoodananan yara LCH a cikin Yara
- 1.7 Jiyya na LCH a cikin Manya
- 1.8 Don Moreara Koyo Game da Langerhans Cell Histiocytosis
Maganin Tarihin Tarihin Langerhans na Langerhans (®) –Patient Version
Janar Bayani Game da Langerhans Cell Histiocytosis (LCH)
MAGANAN MAGANA
- Langerhans cell histiocytosis wani nau'in ciwon daji ne wanda zai iya lalata nama ko haifar da rauni a cikin wuri ɗaya ko fiye a cikin jiki.
- Tarihin iyali na cutar kansa ko samun mahaifiya wanda aka fallasa shi da wasu sinadarai na iya ƙara haɗarin cutar LCH.
- Alamomi da alamomin cutar LCH sun dogara da inda yake cikin jiki.
- Fata da ƙusoshi
- Baki
- Kashi
- Lymph nodes da thymus
- Tsarin endocrine
- Ido
- Tsarin juyayi na tsakiya (CNS)
- Hanta da baƙin ciki
- Huhu
- Kashin kashin baya
- Gwajin da ke bincika gabobi da tsarin jiki inda LCH na iya faruwa ana amfani dasu don tantance LCH.
- Wasu dalilai suna tasiri hangen nesa (damar dawowa) da zaɓuɓɓukan magani.
Langerhans cell histiocytosis wani nau'in ciwon daji ne wanda zai iya lalata nama ko haifar da rauni a cikin wuri ɗaya ko fiye a cikin jiki.
Langerhans cell histiocytosis (LCH) cuta ce mai saurin kamuwa da cutar kansa wanda ke farawa cikin ƙwayoyin LCH. Kwayoyin LCH sune nau'in kwayar halitta ta dendritic wacce ke yaki da kamuwa da cuta. Wani lokaci akan sami maye gurbi (canje-canje) a cikin ƙwayoyin LCH kamar yadda suke. Wadannan sun hada da maye gurbi na kwayoyin BRAF, MAP2K1, RAS da kwayoyin ARAF. Waɗannan canje-canjen na iya sa ƙwayoyin LCH su girma da ninkawa da sauri. Wannan yana sa ƙwayoyin LCH su ginu a wasu sassan jiki, inda zasu iya lalata nama ko haifar da rauni.
LCH ba cuta ba ce ta ƙwayoyin Langerhans waɗanda ke faruwa koyaushe a cikin fata.
LCH na iya faruwa a kowane zamani, amma ya fi yawa ga yara ƙanana. Maganin LCH a cikin yara ya bambanta da na LCH na manya. An bayyana maganin LCH a cikin yara da kuma kula da LCH a cikin manya a cikin sassa daban-daban na wannan taƙaitaccen bayani.
Tarihin iyali na cutar kansa ko samun mahaifiya wanda aka fallasa shi da wasu sinadarai na iya ƙara haɗarin cutar LCH.
Duk wani abu da zai kara maka hadarin kamuwa da cuta to ana kiran sa mai hadari. Samun haɗari ba ya nufin cewa za ku kamu da cutar kansa; ba tare da haɗarin abubuwan haɗari ba yana nufin cewa ba zaku sami cutar kansa ba. Yi magana da likitanka idan kuna tsammanin kuna iya fuskantar haɗari.
Hanyoyin haɗari ga LCH sun haɗa da masu zuwa:
- Samun mahaifi wanda aka fallasa shi da wasu sinadarai.
- Samun mahaifi wanda aka fallasa shi da ƙarfe, dutse, ko ƙurar itace a wurin aiki.
- Tarihin iyali na cutar kansa, gami da LCH.
- Samun tarihin mutum ko tarihin iyali na cutar thyroid.
- Samun cututtuka kamar jariri.
- Shan taba, musamman ma a cikin samari.
- Kasancewarsa Ba'amurke.
- Ba a yin rigakafin yana yaro.
Alamomi da alamomin cutar LCH sun dogara da inda yake cikin jiki.
Waɗannan da sauran alamu da alamun cutar na iya haifar da LCH ko wasu yanayi. Binciki likitanka idan kai ko ɗanka suna da ɗayan masu zuwa:
Fata da ƙusoshi
LCH a cikin jarirai na iya shafar fata kawai. A wasu lokuta, LCH-kawai LCH na iya zama mafi muni a cikin makonni ko watanni kuma ya zama sifa da ake kira babban haɗarin multisystem LCH.
A cikin jarirai, alamu ko alamomin cutar LCH da ke shafar fata na iya haɗawa da:
- Flaking na fatar kan mutum wanda ka iya zama kamar “mayafin shimfiɗar jariri”
- Yin flaking a cikin gaɓoɓin jiki, kamar gwiwar hannu na ciki ko perineum.
- Tashi, launin ruwan kasa ko shunayya fata a ko'ina a jiki.
A cikin yara da manya, alamu ko alamomin cutar LCH da ke shafar fata da ƙusoshi na iya haɗawa da:
- Flaking na fatar kan mutum wanda zai iya zama kamar dandruff.
- Tashi, ja ko launin ruwan kasa, ɓawon ɓawon burodi a cikin yanki, ciki, baya, ko kirji, wanda ka iya zama mai ƙaiƙayi ko raɗaɗi.
- Kumburi ko ulce a fatar kai.
- Ulcer a bayan kunnuwa, a ƙarƙashin ƙirjin, ko a yankin makwancin gwaiwa.
- Yatsun farce da ke faɗuwa ko kuma masu launin raƙuman duwatsu waɗanda suke tafiya a ƙusa ƙusa.
Baki
Alamomi ko alamun cutar LCH da ke shafar baki na iya haɗawa da:
- Danko kumbura.
- Ciwo a kan rufin bakin, a cikin kunci, ko a kan harshe ko leɓɓa.
Hakorar da suka zama marasa tsari ko fadowa.
Kashi
Alamomi ko alamun cutar LCH da ke shafar ƙashi na iya haɗawa da:
- Kumburi ko dunƙulewar ƙashi, kamar su kokon kai, ƙashin hanji, haƙarƙari, ƙugu, kashin baya, ƙashin cinya, ƙashin hannu na sama, gwiwar hannu, jijiyar ido, ko ƙashi a kusa da kunne.
- Jin zafi inda akwai kumburi ko dunƙule akan ƙashi.
Yaran da ke fama da cutar LCH a cikin ƙashi a kusa da kunnuwa ko idanu suna da babbar haɗari ga ciwon sukari insipidus da sauran cututtukan tsarin kulawa na tsakiya.
Lymph nodes da thymus
Alamomi ko alamomin LCH waɗanda ke shafar ƙwayoyin lymph ko thymus na iya haɗawa da:
- Magungunan kumbura kumbura.
- Rashin numfashi.
- Ciwon mara mai ƙyama. Wannan na iya haifar da tari, matsalar numfashi, da kumburin fuska, wuya, da manyan hannaye.
Tsarin endocrine
Alamomi ko alamomin cutar LCH waɗanda ke shafar glandon ƙwayar cuta na iya haɗawa da:
- Ciwon sukari insipidus. Wannan na iya haifar da tsananin kishi da yawan fitsari.
- Sannu a hankali.
- Balaga da wuri ko ta makara.
- Yin nauyi sosai.
Alamomi ko alamomin cutar LCH da ke shafar thyroid na iya haɗawa da:
- Kumburin glandon kumburin.
- Hypothyroidism Wannan na iya haifar da gajiya, rashin kuzari, mai saurin damuwa ga sanyi, maƙarƙashiya, bushewar fata, siririn gashi, matsalolin ƙwaƙwalwar ajiya, damuwa da damuwa, da damuwa. A cikin jarirai, wannan ma na iya haifar da ƙarancin abinci da ƙuntata abinci. A cikin yara da matasa, wannan na iya haifar da matsalolin ɗabi'a, riba mai nauyi, jinkirin girma, da kuma ƙarshen balaga.
- Rashin numfashi.
Ido
Alamomi ko alamun cutar LCH da ke shafar ido na iya haɗawa da:
- Matsalar hangen nesa.
Tsarin juyayi na tsakiya (CNS)
Alamomi ko alamomin LCH da ke shafar CNS (kwakwalwa da laka) na iya haɗawa da:
- Rashin daidaituwa, motsin jiki mara hadewa, da matsalar tafiya.
- Matsalar magana.
- Matsalar gani.
- Ciwon kai.
- Canje-canje a cikin hali ko ɗabi'a.
- Matsalar ƙwaƙwalwa.
Wadannan alamomi da alamomin na iya haifar da rauni a cikin CNS ko kuma ciwo na neurodegenerative na CNS.
Hanta da baƙin ciki
Alamomi ko alamun cutar LCH da ke shafar hanta ko baƙin ciki na iya haɗawa da:
- Kumburawa a cikin ciki sanadiyyar tarin ruwa mai yawa.
- Rashin numfashi.
- Raunin fata da fararen idanu.
- Itching.
- Aramar rauni ko zubar jini.
- Jin kasala sosai.
Huhu
Alamomi ko alamun cutar LCH da ke shafar huhu na iya haɗawa da:
- Huhu ya tarwatse Wannan yanayin na iya haifar da ciwon kirji ko matsewa, matsalar numfashi, jin kasala, da launi mai laushi ga fata.
- Matsalar numfashi, musamman ga manya waɗanda ke shan sigari.
- Dry tari.
- Ciwon kirji.
Kashin kashin baya
Alamomi ko alamomin cutar LCH da ke shafar ƙashin kashin na iya haɗawa da:
- Aramar rauni ko zubar jini.
- Zazzaɓi.
- Yawaitar cututtuka.
Gwajin da ke bincika gabobi da tsarin jiki inda LCH na iya faruwa ana amfani dasu don tantance LCH.
Ana iya amfani da waɗannan gwaje-gwajen da hanyoyin don gano (gano) da kuma bincika LCH ko yanayin da LCH ya haifar:
- Jarabawa ta jiki da tarihin lafiya: Jarabawa ta jiki don bincika alamomin lafiya gaba ɗaya, gami da bincika alamun cuta, kamar kumburi ko wani abu da kamar baƙon abu. Za a kuma ɗauki tarihin al'adun lafiyar marasa lafiya da cututtukan da suka gabata da magunguna.
- Nazarin ilimin lissafi: Jerin tambayoyi da gwaje-gwaje don bincika kwakwalwa, laka, da aikin jijiya. Jarabawar tana bincikar halin tunanin mutum, daidaituwarsa, da ikon yin tafiya yadda ya kamata, da kuma yadda ƙarfin jijiyoyi, hankula, da abubuwan da suke nunawa ke aiki. Hakanan ana iya kiransa gwajin neuro ko gwajin neurologic.
- Cikakken ƙidayar jini (CBC) tare da banbanci: Hanyar da za'a zana samfurin jini kuma a bincika ta mai zuwa:
- Adadin haemoglobin (furotin da ke ɗauke da iskar oxygen) a cikin ƙwayoyin jinin jini.
- Yankin samfurin jini ya kunshi jajayen ƙwayoyin jini.
- Adadi da nau'in farin jini.
- Yawan jajayen kwayoyin jini da platelets.
- Nazarin ilimin sunadarai na jini: Hanya ce wacce ake bincika samfurin jini don auna adadin wasu abubuwa da aka saki zuwa cikin jiki ta gabobi da kayan aiki a jiki. Adadin abu na yau da kullun (mafi girma ko ƙasa da al'ada) na iya zama alamar cuta.
- Gwajin aikin hanta : Gwajin jini don auna matakan jini na wasu abubuwa da hanta ya saki. Babban ko ƙarancin waɗannan abubuwa na iya zama alamar cuta a cikin hanta.
- Gwajin kwayar BRAF: Gwajin gwaje-gwaje wanda aka gwada samfurin jini ko nama don wasu canje-canje a cikin kwayar halittar BRAF.
- Yin fitsari : Gwaji ne dan duba kalar fitsari da abinda yake ciki, kamar su suga, furotin, jajayen kwayoyin jini, da kuma farin kwayoyin halitta.
- Gwajin hana ruwa: Gwaji ne dan duba yawan fitsarin da akeyi kuma ko ya zama mai nutsuwa idan aka bashi kadan ko babu ruwa. Ana amfani da wannan gwajin don tantance insipidus na ciwon sukari, wanda ƙila LCH ke haifarwa.
- Burin kasusuwan kasusuwa da biopsy: Cire kasusuwan kasusuwa da karamin guntun kashi ta hanyar sanya allura mai huhu a cikin kashin hanji. Wani masanin ilimin ɗan adam ya kalli jijiyoyin ƙashi da ƙashi a ƙarƙashin microscope don neman alamun LCH.
Za'a iya yin gwaje-gwaje masu zuwa akan ƙyallen da aka cire:
- Immunohistochemistry: Gwajin gwaje-gwaje wanda ke amfani da kwayoyin cuta don bincika wasu antigens (alamomi) a cikin samfurin jikin mai haƙuri. Magungunan rigakafi yawanci suna da alaƙa da enzyme ko fenti mai kyalli. Bayan kwayoyin sun kunshi wani takamaiman antigen a cikin samfurin, sai a kunna enzyme ko rini, sannan za a iya ganin antigen a karkashin wani madubin likita. Ana amfani da irin wannan gwajin don taimakawa wajen gano kansar da kuma taimakawa gaya ga wani nau'in cutar kansa daga wani nau'in cutar kansa.
- Gudun cytometry: Gwajin dakin gwaje-gwaje wanda ke auna yawan kwayoyin halitta a cikin samfurin, yawan kwayoyin rai a cikin samfurin, da wasu halaye na kwayoyin, kamar girman su, sifar su, da kuma kasancewar ciwace ciwace ciwace (ko wasu) Tantanin tantanin halitta Kwayoyin daga samfurin jinin mai haƙuri, kashin ƙashi, ko wasu kayan suna da datti tare da fenti mai kyalli, sanya shi a cikin ruwa, sannan a wuce ɗaya bayan ɗaya ta hanyar hasken haske. Sakamakon gwajin ya ta'allaka ne akan yadda ƙwayoyin da aka lalata tare da fenti mai kyalli ke amsa ga katangar haske.
- Binciken ƙashi: Hanya ce don bincika idan akwai saurin rarraba ƙwayoyin a cikin ƙashi. Aramin abu kaɗan ne na rediyo ke shiga cikin jijiya kuma yana tafiya ta cikin jini. Kayan aikin radiyo yana tattarawa a cikin kasusuwa tare da cutar kansa kuma na'urar daukar hotan takardu ce ke gano shi.

- X-ray: X-ray na gabobin jiki da ƙashi a cikin jiki. X-ray wani irin katako ne na katako wanda zai iya ratsa jiki zuwa fim, yana yin hoton wurare a cikin jiki. Wani lokaci ana yin binciken kwarangwal. Wannan hanya ce ta x-ray duk kasusuwan da ke cikin jiki.
- CT scan (CAT scan): Hanya ce da ke yin jerin hotuna dalla-dalla na wurare a cikin jiki, waɗanda aka ɗauka daga kusurwa daban-daban. Ana yin hotunan ne ta wata kwamfuta da aka haɗa ta da na'urar da ke ɗauke da x-ray. Ana iya yin allurar fenti a cikin jijiya ko haɗiye don taimakawa gabobin ko kyallen takarda su fito fili karara. Wannan hanya ana kiranta yanayin ƙididdigar lissafi, ƙirar kwamfuta, ko ƙirar ƙwaƙwalwar ajiyar kwamfuta.
- MRI (hoton maganadisu ): Hanya ce wacce ke amfani da maganadisu, raƙuman rediyo, da kuma kwamfuta don yin jerin hotuna dalla-dalla na wurare a cikin jiki. Ana iya yin allurar wani abu da ake kira gadolinium a cikin jijiya. Gadolinium yana tattarawa a kusa da sel na LCH don su nuna da kyau a hoton. Wannan hanya ana kiranta kuma ana kiranta hoton maganadisu na maganadisu (NMRI).
- PET scan (positron emission tomography scan): Hanya ce don gano ƙwayoyin tumo a jiki. An sanya ƙwayar glucose mai ƙarancin rediyo (sukari) a cikin jijiya. Na'urar daukar hoton PET tana juyawa a jiki kuma tana yin hoto inda ake amfani da glucose a jiki. Kwayoyin tumo suna nuna haske a hoton saboda sun fi aiki kuma suna ɗaukar glucose fiye da ƙwayoyin al'ada.

- Gwajin duban dan tayi: Hanya ce wacce ake fitar da igiyar sauti mai karfi (duban dan tayi) daga kyallen ciki ko gabobin ciki kuma suna yin kuwwa. Eararrawa ta haifar da hoton kayan jikin da ake kira sonogram. Ana iya buga hoton don a kalleshi daga baya.
- Gwajin aikin huhu (PFT): Gwaji don ganin yadda huhu ke aiki. Tana auna yawan iskar da huhu zai iya rikewa da kuma yadda iska take saurin shiga da fita daga huhu. Hakanan yana auna yadda ake amfani da iskar oxygen da kuma yadda ake bayar da iskar carbon dioxide yayin numfashi. Wannan kuma ana kiransa gwajin aikin huhu.
- Bronchoscopy: Hanya ce don duba cikin bututun iska da manyan hanyoyin iska a cikin huhu don yankuna masu haɗari. Ana saka broncoscope ta hanci ko baki a cikin bututun iska da huhu. Bronchoscope abu ne na bakin ciki, mai kama da bututu tare da haske da ruwan tabarau don kallo. Hakanan yana iya samun kayan aiki don cire samfuran nama, waɗanda aka bincika a ƙarƙashin microscope don alamun cutar kansa.
- Endoscopy: Hanya ce don duba gabobi da kyallen takarda a cikin jiki don bincika yankuna marasa haɗari a cikin ɓangaren hanji ko huhu. An saka endoscope ta hanyar ragi (yankewa) a cikin fata ko buɗewa a cikin jiki, kamar bakin. Ganin ƙarshen abu mai nauyi ne, mai kama da bututu tare da haske da ruwan tabarau don kallo. Hakanan yana iya samun kayan aiki don cire samfuran jiki ko samfuran kumburin lymph, waɗanda aka bincika a ƙarƙashin microscope don alamun cuta.
- Biopsy: Cire ƙwayoyin halitta ko kyallen takarda don haka ana iya kallon su a ƙarƙashin microscope ta hanyar masanin binciken cuta don bincika ƙwayoyin LCH. Don tantance LCH, ana iya yin biopsy na ƙashi, fata, lymph nodes, hanta, ko wasu wuraren cutar.
Wasu dalilai suna tasiri hangen nesa (damar dawowa) da zaɓuɓɓukan magani.
LCH a cikin gabobi kamar fata, ƙasusuwa, ƙwayoyin lymph, ko gland pituitary galibi suna samun sauƙi tare da magani kuma ana kiransa "ƙananan haɗari". LCH a cikin saifa, hanta, ko kashin ƙashi ya fi wuyar magani kuma ana kiransa "mai haɗarin gaske"
Hanyoyin hangen nesa da zaɓuɓɓukan magani sun dogara da masu zuwa:
- Shekaru nawa masu haƙuri ke lokacin da aka gano su da cutar LCH.
- Wadanne gabobi ne ko tsarin jikin LCH ya shafa.
- Yaya yawancin gabobi ko tsarin jiki da cutar kansa ke shafar.
- Ko ana samun cutar kansa a cikin hanta, saifa, jijiyar ƙashi, ko wasu ƙasusuwa a cikin kwanyar.
- Yaya saurin ciwon daji ke amsawa ga maganin farko.
- Ko akwai wasu canje-canje a cikin kwayar halittar BRAF.
- Ko dai an gano kansar ne ko kuma ya dawo (maimaituwa).
A cikin jarirai har zuwa shekara ɗaya, LCH na iya wucewa ba tare da magani ba.
Matakan LCH
MAGANAN MAGANA
- Babu tsarin tsararru don Langerhans cell histiocytosis (LCH).
- Jiyya na LCH ya dogara ne akan inda aka samo ƙwayoyin LCH a cikin jiki kuma ko LCH yana da ƙananan haɗari ko babban haɗari.
- Maimaita LCH
Babu tsarin tsararru don Langerhans cell histiocytosis (LCH).
Yawancin lokaci ko yaduwar ciwon daji yawanci ana bayyana shi a matsayin matakai. Babu tsarin aiwatarwa don LCH.
Jiyya na LCH ya dogara ne akan inda aka samo ƙwayoyin LCH a cikin jiki kuma ko LCH yana da ƙananan haɗari ko babban haɗari.
LCH an bayyana shi azaman cuta guda ɗaya ko cuta mai yawan tsarin, dangane da yawan tsarin jikin da abin ya shafa:
- LCH-system LCH: Ana samun LCH a wani sashi na gaɓa ko tsarin jiki ko fiye da ɗaya ɓangaren ɓangaren ko tsarin jikin. Kashi shine mafi yawan wuri guda don LCH da za'a samo.
- Multisystem LCH: LCH yana faruwa a gabobi biyu ko fiye ko tsarin jiki ko kuma ana iya yada shi cikin jiki. Multisystem LCH ba shi da mahimmanci fiye da tsarin LCH.
LCH na iya shafar gabobin haɗari ko gabobin haɗari:
- Organsananan gabobi masu haɗari sun haɗa da fata, ƙashi, huhu, ƙwayoyin lymph, sashin jiki na ciki, gland, planditary gland, thyroid gland, thymus, da kuma tsarin juyayi na tsakiya (CNS).
- Organsananan gabobi masu haɗari sun haɗa da hanta, baƙin ciki, da ƙashi.
Maimaita LCH
Maimaita LCH shine ciwon daji wanda ya sake dawowa (dawo) bayan an magance shi. Ciwon kansa na iya dawowa wuri ɗaya ko a wasu sassan jiki. Sau da yawa yakan sake komawa cikin ƙashi, kunnuwa, fata, ko gland. LCH yakan sake dawowa shekara bayan dakatar da magani. Lokacin da LCH ya sake dawowa, ana iya kiran shi reactivation.
Bayanin Zaɓin Jiyya don LCH
MAGANAN MAGANA
- Akwai nau'ikan magani iri daban-daban ga marasa lafiya da kwayar cutar Langerhans cell histiocytosis (LCH).
- Yaran da ke da cutar LCH ya kamata ƙungiyar masu ba da sabis na kiwon lafiya waɗanda suka ƙware a kula da cutar sankara ta yara suka tsara maganin su.
- Ana amfani da nau'ikan daidaitaccen magani guda tara:
- Chemotherapy
- Tiyata
- Radiation far
- Photodynamic far
- Immunotherapy
- Ciwon da aka yi niyya
- Sauran maganin magani
- Dasawar dasa kara
- Lura
- Ana gwada sababbin nau'ikan magani a gwajin asibiti.
- Jiyya don Langerhans cell histiocytosis na iya haifar da sakamako masu illa.
- Marasa lafiya na iya son yin tunani game da shiga cikin gwaji na asibiti.
- Marasa lafiya na iya shiga gwajin asibiti kafin, yayin, ko bayan fara jiyyarsu.
- Lokacin da maganin LCH ya tsaya, sababbin raunuka na iya bayyana ko tsoffin raunuka na iya dawowa.
- Ana iya buƙatar gwaje-gwaje na gaba.
Akwai nau'ikan magani iri daban-daban ga marasa lafiya da kwayar cutar Langerhans cell histiocytosis (LCH).
Akwai nau'ikan jiyya iri-iri don marasa lafiya da LCH. Wasu jiyya suna daidaito (magani da ake amfani dashi yanzu), kuma wasu ana gwada su a gwajin asibiti. Gwajin gwajin magani shine binciken bincike wanda aka tsara don taimakawa inganta ingantattun jiyya na yanzu ko samun bayanai kan sababbin jiyya ga marasa lafiya da ciwon daji. Lokacin da gwaji na asibiti ya nuna cewa sabon magani ya fi magani na yau da kullun, sabon magani na iya zama daidaitaccen magani. Duk lokacin da zai yiwu, marasa lafiya ya kamata su shiga cikin gwaji na asibiti don karɓar sababbin nau'ikan maganin LCH. Wasu gwaji na asibiti ana buɗe su ne kawai ga marasa lafiyar da basu fara magani ba.
Gwajin gwaji na gudana a sassa da yawa na ƙasar. Ana samun bayani game da gwajin gwaji na ci gaba daga gidan yanar gizon NCI. Zaɓin mafi dacewa magani shine yanke shawara wanda ya dace da haƙuri, iyali, da ƙungiyar kiwon lafiya.
Yaran da ke da cutar LCH ya kamata ƙungiyar masu ba da sabis na kiwon lafiya waɗanda suka ƙware a kula da cutar sankara ta yara suka tsara maganin su.
Jiyya za ta kula da likitan ilimin likitan yara, likita wanda ya kware kan kula da yara masu cutar kansa. Masanin ilimin likitancin yara yana aiki tare da sauran masu ba da kula da lafiyar yara waɗanda ƙwararru ne wajen kula da yara tare da LCH kuma waɗanda suka kware a wasu fannonin magani. Wadannan na iya hada da kwararru masu zuwa:
- Likitan yara.
- Likitan likitan yara.
- Kwararren likitan yara.
- Radiation oncologist
- Neurologist.
- Masanin ilimin likita.
- Kwararren likitan yara.
- Gwanayen gyarawa.
- Masanin ilimin psychologist.
- Ma'aikacin zamantakewa.
Ana amfani da nau'ikan daidaitaccen magani guda tara:
Chemotherapy
Chemotherapy magani ne na cutar kansa wanda ke amfani da magunguna don dakatar da haɓakar ƙwayoyin kansa, ko dai ta hanyar kashe ƙwayoyin ko ta hana su rarraba. Lokacin da ake shan chemotherapy ta baki ko allura a cikin jijiya ko tsoka, magungunan suna shiga cikin jini kuma zasu iya kaiwa ga kwayoyin cutar kansa a cikin jiki duka (systemotherapy chemotherapy). Lokacin da aka sanya chemotherapy kai tsaye akan fata ko cikin ruwa mai ruɓaɓɓen ciki, gaɓoɓi, ko rami na jiki kamar ciki, magungunan yawanci suna shafar ƙwayoyin kansa ne a waɗancan yankuna (chemotherapy na yanki).
Ana iya ba da magani ta hanyar allura ko ta baki ko kuma a shafa ta a fata don kula da LCH.
Tiyata
Ana iya amfani da tiyata don cire cututtukan LCH da ƙananan ƙwayoyin lafiya masu kusa. Curettage wani nau'in tiyata ne wanda yake amfani da curette (kaifi, kayan aiki mai siffa cokali) don kankare ƙwayoyin LCH daga ƙashi.
Lokacin da akwai mummunan hanta ko cutar huhu, ana iya cire dukkan sassan jikin kuma a maye gurbinsu da lafiyayyen hanta ko huhu daga mai bayarwa.
Radiation far
Radiation therapy magani ne na cutar kansa wanda yake amfani da hasken rana mai ƙarfi ko wasu nau'ikan radiation don kashe ƙwayoyin kansa ko hana su girma. Magungunan radiation na waje yana amfani da wata na'ura a wajen jiki don aika jujjuyawar zuwa jikin jiki da cutar kansa. Ultraviolet B (UVB) za a iya ba da amfani da fitila ta musamman wacce ke jagorantar iska zuwa raunin fata na LCH.
Photodynamic far
Photodynamic far shine maganin ciwon daji wanda ke amfani da magani da wani nau'in hasken laser don kashe ƙwayoyin kansa. Wani magani ne da baya aiki har sai ya bayyana ga haske ana sanya shi a jijiya. Magungunan ƙwayoyi suna tarawa fiye da ƙwayoyin cuta. Don LCH, hasken laser yana nufin fata kuma maganin yana aiki kuma yana kashe ƙwayoyin kansa. Photodynamic far yana haifar da damagean lahani ga lafiyayyen nama. Marasa lafiya waɗanda ke da ilimin gyaran fotodynamic bai kamata su ɗauki lokaci mai yawa a rana ba.
A cikin wani nau'i na maganin photodynamic, wanda ake kira psoralen da ultraviolet A (PUVA), mai haƙuri ya karɓi wani magani da ake kira psoralen sannan kuma ultraviolet A radiation zai kai ga fata.
Immunotherapy
Immunotherapy magani ne wanda ke amfani da garkuwar jikin mara lafiya don yaƙar kansa. Abubuwan da jiki ya yi ko aka yi a dakin gwaje-gwaje ana amfani da su don haɓaka, kai tsaye, ko maido da kariya ta jiki daga cutar kansa. Wannan nau'in maganin cutar kansa ana kiransa biotherapy ko biologic therapy. Akwai nau'ikan immunotherapy daban-daban:
- Ana amfani da Interferon don magance LCH na fata.
- Ana amfani da Thalidomide don magance LCH.
- Ana amfani da rigakafin rigakafi na cikin jiki (IVIG) don magance cututtukan neurodegenerative na CNS.
Ciwon da aka yi niyya
Targeted therapy wani nau'in magani ne wanda yake amfani da magunguna ko wasu abubuwa don afkawa ƙwayoyin kansar. Therapwararrun hanyoyin kwantar da hankali na iya haifar da ƙasa da cutar ga ƙwayoyin halitta fiye da cutar sankara ko maganin wutan lantarki. Akwai nau'ikan maganin farfadowa daban-daban:
- Masu hana maganin Tyrosine kinase suna toshe siginonin da ake buƙata don ciwace ciwace ci gaba. Tyrosine kinase inhibitors waɗanda ake amfani dasu don kula da LCH sun haɗa da masu zuwa:
- Imatinib mesylate yana tsayar da sel masu juya jini daga juyawa zuwa ƙwayoyin dendritic waɗanda zasu iya zama ƙwayoyin kansa.
- Masu hana BRAF suna toshe sunadaran da ake buƙata don ci gaban kwayar halitta kuma suna iya kashe ƙwayoyin kansa. An samo kwayar BRAF a cikin maye gurbi (canzawa) a cikin wasu LCH kuma toshe shi na iya taimakawa kiyaye ƙwayoyin kansar daga girma.
- Vemurafenib da dabrafenib sune masu hana BRAF amfani dasu don magance LCH.
- Magungunan antibody na Monoclonal yana amfani da kwayar cutar da aka sanya a dakin gwaje-gwaje daga nau'in kwayar halitta guda ɗaya. Wadannan kwayoyin cuta na jikin mutum na iya gano abubuwan da ke jikin kwayoyin cutar kansar ko kuma wasu abubuwa na yau da kullun wadanda zasu iya taimakawa kwayoyin cutar kansa. Kwayoyin rigakafin suna haɗuwa da abubuwan kuma suna kashe ƙwayoyin cutar kansa, toshe haɓakar su, ko kiyaye su daga yaɗuwa. Ana iya amfani da su su kaɗai ko ɗaukar ƙwayoyi, gubobi, ko kayan aikin rediyo kai tsaye zuwa ƙwayoyin kansa. Ana ba da ƙwayoyin cuta na Monoclonal ta hanyar jiko.
- Rituximab wani maganin rigakafi ne wanda aka yi amfani dashi don magance LCH.
Sauran maganin magani
Sauran magungunan da ake amfani dasu don magance LCH sun haɗa da masu zuwa:
- Ana amfani da cututtukan steroid, kamar prednisone, don magance raunin LCH.
- Ana amfani da maganin Bisphosphonate (kamar su pamidronate, zoledronate, ko alendronate) don magance raunin LCH na ƙashi da rage ƙashin kashi.
- Magungunan rigakafin ƙwayoyin cuta sune magunguna (kamar pioglitazone da rofecoxib) waɗanda yawanci ana amfani dasu don rage zazzaɓi, kumburi, zafi, da ja. Ana iya ba da magungunan kashe kumburi da chemotherapy tare don magance manya da ƙashin LCH.
- Retinoids, kamar isotretinoin, magunguna ne masu alaƙa da bitamin A wanda ke iya rage ci gaban ƙwayoyin LCH a cikin fata. Ana daukar retinoids da baki.
Dasawar dasa kara
Dasawar sel wata hanya ce ta bada chemotherapy da maye gurbin kwayoyin halitta masu jini wanda cutar LCH ta lalata. Ana cire ƙwayoyin sari (ƙwayoyin jinin da basu balaga ba) daga cikin jinin ko ƙashin ƙashin mara lafiya ko mai bayarwa kuma ana daskarar dasu ana adana su. Bayan an kammala maganin, an narke ƙwayoyin ƙwayoyin da aka adana kuma a mayar da su ga mai haƙuri ta hanyar jiko. Waɗannan ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin na ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin na ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin na ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin na ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin ƙwayoyin magungunan za a ɗibar
Lura
Lura yana lura da yanayin mai haƙuri ba tare da ba da magani ba har sai alamu ko alamu sun bayyana ko canzawa.
Ana gwada sababbin nau'ikan magani a gwajin asibiti.
Ana samun bayani game da gwaji na asibiti daga gidan yanar gizon NCI.
Jiyya don Langerhans cell histiocytosis na iya haifar da sakamako masu illa.
Don bayani game da illolin da ke farawa yayin magani don cutar kansa, duba shafin Gurbinmu.
Hanyoyi masu illa daga maganin ciwon daji wanda zai fara bayan jiyya kuma ya ci gaba tsawon watanni ko shekaru ana kiransa sakamako na ƙarshe. Sakamakon sakamako na maganin kansa na iya haɗa da masu zuwa:
- Saurin girma da ci gaba.
- Rashin ji.
- Kashi, hakori, hanta, da matsalolin huhu.
- Canje-canje a cikin yanayi, ji, koyo, tunani, ko ƙwaƙwalwar ajiya.
- Cutar kansa ta biyu, kamar cutar sankarar bargo, retinoblastoma, Ciwan sarcoma, ƙwaƙwalwa ko cutar hanta.
Wasu maganganun ƙarshen ana iya magance su ko sarrafa su. Yana da mahimmanci a yi magana da likitocin ɗanka game da illar da cutar kansa za ta iya yi wa ɗanka. (Dubi taƙaitaccen bayanin akan ƙarshen tasirin Jiyya don Ciwon Childhoodan yara don ƙarin bayani.)
Yawancin marasa lafiya da ke da tsarin LCH da yawa suna da ƙarshen sakamako wanda ya haifar da magani ko cutar kanta. Wadannan marasa lafiya galibi suna da matsalolin lafiya na dogon lokaci waɗanda ke shafar ingancin rayuwarsu.
Marasa lafiya na iya son yin tunani game da shiga cikin gwaji na asibiti.
Ga wasu marasa lafiya, shiga cikin gwaji na asibiti na iya zama mafi kyawun zaɓin magani. Gwajin gwaji wani bangare ne na aikin binciken cutar kansa. Ana yin gwaje-gwajen asibiti don gano ko sabbin maganin cutar daji suna da lafiya da tasiri ko kuma sun fi magani na yau da kullun.
Yawancin yau da kullun na yau da kullun don cutar kansa sun dogara ne akan gwajin asibiti na farko. Marasa lafiya da ke cikin gwaji na asibiti na iya karɓar daidaitaccen magani ko kuma su kasance cikin farkon waɗanda za su karɓi sabon magani.
Marasa lafiya da ke shiga cikin gwaji na asibiti suma suna taimakawa inganta hanyar da za a bi da kansar a nan gaba. Koda lokacin gwajin asibiti bai haifar da sababbin magunguna ba, sau da yawa sukan amsa mahimman tambayoyi kuma suna taimakawa ci gaba da bincike gaba.
Marasa lafiya na iya shiga gwajin asibiti kafin, yayin, ko bayan fara jiyyarsu.
Wasu gwaji na asibiti kawai sun haɗa da marasa lafiya waɗanda ba su sami magani ba tukuna. Sauran gwaje-gwajen suna gwada jiyya ga marasa lafiya waɗanda cutar kansa ba ta samu sauki ba. Hakanan akwai gwaji na asibiti da ke gwada sabbin hanyoyin dakatar da cutar kansa daga sake dawowa (dawowa) ko rage tasirin maganin kansar.
Gwajin gwaji na gudana a sassa da yawa na ƙasar. Bayani game da gwajin asibiti wanda NCI ke tallafawa ana iya samun shi akan shafin binciken gwaji na NCI. Ana iya samun gwajin gwaji na asibiti wanda wasu kungiyoyi ke tallafawa akan gidan yanar gizon ClinicalTrials.gov.
Lokacin da maganin LCH ya tsaya, sababbin raunuka na iya bayyana ko tsoffin raunuka na iya dawowa.
Yawancin marasa lafiya da LCH suna samun sauki tare da magani. Koyaya, idan magani ya tsaya, sababbin raunuka na iya bayyana ko tsofaffin raunuka na iya dawowa. Ana kiran wannan sake kunnawa (sake dawowa) kuma yana iya faruwa tsakanin shekara guda bayan dakatar da magani. Marasa lafiya da ke fama da cututtukan da ke tattare da tsarin na iya samun damar sake kunnawa. Wuraren da aka fi mayar da aiki sune kashi, kunne, ko fata. Har ila yau, ciwon sukari insipidus na iya bunkasa. Sitesananan shafukan yanar gizo na sake kunnawa sun haɗa da ƙwayoyin lymph, ƙashin ƙashi, baƙin ciki, hanta, ko huhu. Wasu marasa lafiya na iya samun fiye da ɗaya sake kunnawa a cikin adadin shekaru.
Ana iya buƙatar gwaje-gwaje na gaba.
Saboda haɗarin sake kunnawa, ya kamata a kula da marasa lafiyar LCH na shekaru da yawa. Wasu gwajin da aka yi don tantance LCH na iya maimaitawa. Wannan don ganin yadda maganin ke tafiya da kyau kuma idan akwai wasu sababbin raunuka. Wadannan gwaje-gwajen na iya haɗawa da:
- Gwajin jiki.
- Nazarin ilimin lissafi.
- Nazarin duban dan tayi.
- MRI.
- CT dubawa.
- PET scan.
Sauran gwaje-gwajen da za a iya buƙata sun haɗa da:
- Inwararren ƙwaƙwalwar ƙwaƙwalwar ƙwaƙwalwar ƙwaƙwalwar ƙwaƙwalwar ƙwaƙwalwar ƙwaƙwalwar ƙwaƙwalwa (BAER): Gwajin da ke auna amsar kwakwalwa don danna sauti ko wasu sautuna.
- Gwajin aikin huhu (PFT): Gwaji don ganin yadda huhu ke aiki. Tana auna yawan iskar da huhu zai iya rikewa da kuma yadda iska take saurin shiga da fita daga huhu. Hakanan yana auna yadda ake amfani da oxygen da kuma yadda ake bayar da iskar carbon dioxide yayin numfashi. Wannan kuma ana kiransa gwajin aikin huhu.
- Kirjin x-ray: X-ray na gabobin da kasusuwa a cikin kirji. X-ray wani irin katako ne na katako wanda zai iya ratsa jiki zuwa fim, yana yin hoton wurare a cikin jiki.
Sakamakon waɗannan gwaje-gwajen na iya nuna idan yanayin ku ya canza ko kuma idan kansar ta sake dawowa (dawo). Wadannan gwaje-gwajen wasu lokuta ana kiran su gwaje-gwaje na gaba ko dubawa. Shawarwari game da ci gaba, canji, ko dakatar da magani na iya dogara ne da sakamakon waɗannan gwaje-gwajen.
Jiyya na ƙananan ƙananan LCH a cikin Yara
A Wannan Sashin
- Raunukan Fata
- Rauni a cikin Kasusuwa ko Sauran Lowananan Lowananan Hadari
- Ciwon CNS
Don bayani game da jiyya da aka jera a ƙasa, duba sashin Kula da Zaɓin Jiyya.
Raunukan Fata
Jiyya game da cututtukan fata na Langerhans cell histiocytosis (LCH) na iya haɗawa da:
- Lura.
Lokacin da mummunan rashes, ciwo, ulceration, ko zub da jini ya faru, magani na iya haɗawa da masu zuwa:
- Steroid far.
- Chemotherapy da ake bayarwa ta bakin ko jijiya.
- Chemotherapy amfani da fata.
- Photodynamic far tare da psoralen da ultraviolet A (PUVA) far.
- UVB radiation far.
Rauni a cikin Kasusuwa ko Sauran Lowananan Lowananan Hadari
Jiyya game da sabon cututtukan ƙananan yara na LCH a gaba, gefuna, ko bayan ƙwanƙwasa, ko a cikin kowane ƙashi ɗaya na iya haɗawa da:
- Yin tiyata (curettage) tare da ko ba tare da maganin steroid ba.
- Radiationananan raunin radiation don raunuka waɗanda ke shafar gabobin da ke kusa.
Jiyya na sababbin cututtukan LCH na yara a cikin ƙasusuwan kunnuwa ko idanu ana yin su ne don rage haɗarin ciwon sukari insipidus da sauran matsaloli na dogon lokaci. Jiyya na iya haɗawa da:
- Chemotherapy da maganin steroid.
- Yin aikin tiyata (curettage)
Jiyya na sababbin cututtukan yara na LCH na kashin baya ko ƙashin cinya na iya haɗawa da:
- Lura.
- Radiationananan maganin radiation.
- Chemotherapy, don raunuka waɗanda suka yaɗu daga kashin baya cikin nama kusa.
- Yin aikin tiyata don ƙarfafa kashin da ya raunana ta hanyar yin ɗamfa ko haɗa ƙasusuwan wuri ɗaya.
Jiyya na rauni biyu ko fiye na ƙashi na iya haɗawa da:
- Chemotherapy da maganin steroid.
Yin jiyya na raunin kashi biyu ko fiye haɗe da raunin fata, cututtukan lymph node, ko ciwon sukari insipidus na iya haɗawa da:
- Chemotherapy tare da ko ba tare da maganin steroid ba.
- Bisphosphonate far.
Ciwon CNS
Jiyya na sababbin cututtukan ƙananan yara na LCH (CNS) raunuka na iya haɗawa da:
- Chemotherapy tare da ko ba tare da maganin steroid ba.
Jiyya na sabon cutar LCH CNS neurodegenerative ciwo na iya haɗawa da:
- Anyi niyya tare da masu hana BRAF (vemurafenib ko dabrafenib).
- Chemotherapy.
- Therapyaddara da aka yi niyya tare da antibody na monoclonal (rituximab).
- Rage farfadowa
- Immunotherapy (IVIG) tare da ko ba tare da chemotherapy.
Yi amfani da binciken bincikenmu na asibiti don nemo NCI na goyan bayan gwajin asibiti wanda ke karɓar marasa lafiya. Kuna iya bincika gwaji dangane da nau'in ciwon daji, shekarun mai haƙuri, da kuma inda ake yin gwajin. Ana samun cikakken bayani game da gwaji na asibiti.
Jiyya na Babban Haɗarin LCH a cikin Yara
Don bayani game da jiyya da aka jera a ƙasa, duba sashin Kula da Zaɓin Jiyya.
Jiyya game da cututtukan cututtukan yara da yawa na LCH da ke cikin baƙin ciki, hanta, ko ƙashi da wani sashin jiki ko rukunin yanar gizo na iya haɗawa da:
- Chemotherapy da maganin steroid. Za a iya ba da magungunan fiye da ɗaya na maganin cutar sankara da maganin cututtukan steroid ga marasa lafiya waɗanda ciwace-ciwacensu ba su amsa maganin cutar sankara ta farko ba.
- Tsarin da aka yi niyya (vemurafenib).
- Yin dashen hanta ga marasa lafiya masu cutar hanta mai tsanani.
- Gwajin gwaji wanda ke daidaita maganin mai haƙuri dangane da fasalin cutar kansa da yadda take amsar magani.
- Gwajin gwaji na ilimin kimiya da maganin cututtukan steroid.
Jiyya na Maimaitawa, Rashin hankali, da Ci gaban Childhoodananan yara LCH a cikin Yara
Don bayani game da jiyya da aka jera a ƙasa, duba sashin Kula da Zaɓin Jiyya.
Maimaita LCH shine cutar sankara wacce ba'a iya gano ta dan lokaci bayan magani sannan ta dawo. LCH Refractory LCH cutar daji ce wacce bata samun sauki ta hanyar magani. Ci gaba LCH shine ciwon daji wanda ke ci gaba da girma yayin magani.
Jiyya na maimaitawa, rashin ƙarfi, ko ci gaba mai ƙananan haɗari na LCH na iya haɗawa da:
- Chemotherapy tare da ko ba tare da maganin steroid ba.
- Bisphosphonate far.
Jiyya na maimaitawa, ƙin yarda, ko ci gaba mai saurin haɗari da yawa na LCH na iya haɗawa da:
- Babban maganin cutar sankara.
- Tsarin da aka yi niyya (vemurafenib).
- Dasawar dasa kara
Magungunan da ake karatun don maimaitawa, rashin ƙarfi, ko ci gaban yarinta LCH sun haɗa da masu zuwa:
- Gwajin gwaji wanda ke daidaita maganin mai haƙuri dangane da fasalin cutar kansa da yadda take amsar magani.
- Gwajin gwaji wanda ke bincikar samfurin ƙwayar cutar mai haƙuri don wasu canje-canje na asali. Nau'in maganin da aka yiwa niyya wanda za'a baiwa mai haƙuri ya dogara da nau'in canjin halittar mutum.
Jiyya na LCH a cikin Manya
A Wannan Sashin
- Jiyya na LCH na huhu a cikin Manya
- Jiyya na LCH na Kashi a cikin Manya
- Jiyya na LCH na Fata a cikin Manya
- Jiyya na Tsarin-Siki-da-tsarin LCH a cikin Manya
Don bayani game da jiyya da aka jera a ƙasa, duba sashin Kula da Zaɓin Jiyya
Langerhans cell histiocytosis (LCH) a cikin manya yana da yawa kamar LCH a cikin yara kuma yana iya samarwa a cikin gabobi da tsarin kamar yadda yake a yara. Wadannan sun hada da endocrin da tsarin jijiyoyi na hanji, hanta, saifa, bargo, da kuma hanyoyin hanji. A cikin manya, LCH mafi yawanci ana samun shi a cikin huhu azaman cuta mai tsarin ɗaya. LCH a cikin huhu yana faruwa sau da yawa a cikin samari waɗanda ke shan sigari. Adult LCH kuma ana samun sa a cikin ƙashi ko fata.
Kamar yadda yake a cikin yara, alamu da alamomin cutar LCH sun dogara ne da inda ake samun sa a jiki. Dubi Babban Bayanin Bayani don alamu da alamomin LCH.
Gwajin da ke bincika gabobi da tsarin jiki inda LCH na iya faruwa ana amfani dasu don gano (samo) da bincika LCH. Duba sashen Babban Bayani don gwaje-gwaje da hanyoyin da ake amfani dasu don tantance LCH.
A cikin manya, babu cikakken bayani game da abin da magani ke aiki mafi kyau. Wani lokaci, bayanai na zuwa ne kawai daga rahotannin cutar, magani, da kuma bin babba ko ƙaramin rukuni na manya waɗanda aka ba su irin jiyya.
Jiyya na LCH na huhu a cikin Manya
Jiyya ga LCH na huhu a cikin manya na iya haɗawa da:
- Barin shan sigari ga duk marasa lafiyar da ke shan sigari. Lalacewar huhu zaiyi tsanani a kan lokaci a cikin marasa lafiyar da basu daina shan sigari. A cikin marasa lafiyar da suka daina shan sigari, lalacewar huhu na iya samun sauƙi ko kuma zai iya zama mafi muni a kan lokaci.
- Chemotherapy.
- Dasawar huhu ga marasa lafiya da cutar mai tsananin huhu.
Wani lokaci LCH na huhu zai tafi ko kuma ba zai kara muni ba koda kuwa ba a magance shi ba.
Jiyya na LCH na Kashi a cikin Manya
Jiyya don LCH wanda ke shafar ƙashi kawai a cikin manya na iya haɗawa da:
- Yin tiyata tare da ko ba tare da maganin steroid ba.
- Chemotherapy tare da ko ba tare da magani mai sauƙi ba.
- Radiation far.
- Bisphosphonate far, don ciwo mai tsanani.
- Magungunan anti-inflammatory tare da chemotherapy.
Jiyya na LCH na Fata a cikin Manya
Jiyya don LCH wanda ke shafar fata kawai a cikin manya na iya haɗawa da:
- Tiyata.
- Steroid ko wani maganin farji ana amfani dashi ko allura cikin fata.
- Photodynamic far tare da psoralen da ultraviolet A (PUVA) radiation.
- UVB radiation far.
- Chemotherapy ko immunotherapy da aka bayar ta bakin, kamar methotrexate, thalidomide, hydroxyurea, ko interferon.
- Za a iya amfani da farfadowa na retinoid idan raunin fata bai sami sauki ba tare da sauran magani.
Jiyya don LCH wanda ke shafar fata da sauran tsarin jiki a cikin manya na iya haɗawa da:
- Chemotherapy.
Jiyya na Tsarin-Siki-da-tsarin LCH a cikin Manya
Jiyya na tsarin-tsari da cuta da yawa a cikin manya wanda baya shafar huhu, ƙashi, ko fata na iya haɗawa da:
- Chemotherapy.
- Tsarin da aka yi niyya (imatinib, ko vemurafenib).
Don ƙarin bayani game da gwajin LCH na manya, duba gidan yanar gizon Tarihin Tarihi na Disclaimer.
Yi amfani da binciken bincikenmu na asibiti don nemo NCI na goyan bayan gwajin asibiti wanda ke karɓar marasa lafiya. Kuna iya bincika gwaji dangane da nau'in ciwon daji, shekarun mai haƙuri, da kuma inda ake yin gwajin. Ana samun cikakken bayani game da gwaji na asibiti.
Don Moreara Koyo Game da Langerhans Cell Histiocytosis
Don ƙarin bayani daga Cibiyar Cancer ta Kasa game da maganin Langerhans cell histiocytosis, duba masu zuwa:
- Tomography Tomography (CT) Scans da Ciwon daji
- Photodynamic Far don Ciwon daji
- Immunotherapy don Kula da Ciwon daji
- Magungunan Ciwon Cutar da Aka Yi niyya
- Tattara Kwayoyin Halitta mai Yin jini
Don ƙarin bayani game da cutar sankarar yara da sauran albarkatun kansar gaba ɗaya, duba masu zuwa:
- Game da Ciwon daji
- Ciwon Yara
- Binciken Cure don Ciwon Childrenan yara
- Matsayi na Late na Jiyya don Ciwon Yara
- Matasa da Samari da Ciwon daji
- Yara da Ciwon daji: Jagora ga Iyaye
- Ciwon daji a cikin Yara da Matasa
- Tsayawa
- Yin fama da Ciwon daji
- Tambayoyi don Tambayar Doctor game da Ciwon daji
- Don Tsira da Kulawa
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